I fa hi a kum rualpui naupang dangte nena khaikhin chuan a seilian tlai deuhin i hria em? A châng chuan a ni thei bawk. Chu chu naupangin a puitlin hun chu a tlangpuiin an beisei aia tlaiah a tan tihna a ni. Hei hi delayed puberty emaw "delayed puberty" emaw kan tih chu a ni. Mi thenkhat chuan "delayed sexual development" an ti bawk. Pangpar thenkhat chu a par tlai deuh ang bawkin naupang thenkhat chu "late bloomer" deuh an ni thei bawk. Mahse hei hi a tlai deuh mai a ni lo. A châng chuan puitlin hun chu a inṭan nghâl thei a, chutah chuan a tawp thei a, a nih loh leh a kal zawi hle bawk. Tichuan naupang chuan beisei angin puitlin hun chhung zawng zawng a zo vek lo. He thu i hriat hian hlauthawng deuha inhriat hi thil pangngai tak a ni a, mahse chiang taka kan hriat chian chuan harsatna tam tak chu chinfel theih a ni.
Chuti a nih chuan, eng kum nge puitlin hun hi tlai anga ngaih?
Hei hi a takah chuan hmeichhia leh mipa inkarah hian a danglam deuh hlek a ni. Doctor-te sawifiah dan chu hetiang hi a ni:
Hmeichhe naupang puitlin hun sawn hlat tih awmzia chu:
- Kum 13 i tlin hmaa i hnute a lo than chhoh tan loh chuan.
Emaw,
- Kum 15 i tlin hmaa thlasik i neih tan loh chuan, emaw, i hnute a lo than chhoh tan atanga kum thum hnuah pawh thlasik i tan loh chuan.
Mipa naupang puitlin hun sawn hlat tih awmzia chu:
- Kum 14 an tlin chuan testicles a lian tan lo a nih chuan.
Emaw,
- Testicles hi a lian tan tawh a, mahse puitlin hun a la thleng lo.
Heng kum bithliah te hian hlauthawng suh. Hengte hi kaihhruaina tlangpui chauh a ni. I fa chungchangah harsatna i neih chuan naupang enkawltu doctor nen inbiakna neih a tha ber.
Puitling tlai lutuk hian eng symptoms nge a neih?
A lan chhuah dan ber chu hnute than (hmeichhiaah) leh testicular development (mipaah) a ni. Mahse, thil dang pawh a awm thei:
- I fa chu an kum a zirin beisei aia tawi zawk a ni thei. Hei hi a chhan chu puitlin hunlaia thleng tlangpui "growth spurt" an la tawn loh vang a ni.
- Naupang ruh chu an kum a zirin beisei angin a puitling lo mai thei. Hei hi "delayed bone age" an ti a. Doctor chauhin chiang takin a hre thei a, X-ray lak a ngai bawk.
- Naupang private area-a pubic hair than loh.
Mahse hei hi a ni. Naupang thenkhat chuan pubic hair an nei thei a, mahse puitlin hun tlai anga ngaih an la ni thei. Armpit hair emaw body rim emaw an nei tan thei bawk. Heng symptoms te hi natural process adrenarche an tih atanga lo chhuak a ni. Hei hi puitlin hmaa thil thleng a ni. Adrenarche tichhuak tura puitu hormone te hi puitlin hun control tu hormone te nen an danglam a ni. Chuvangin, i fain adrenarche a paltlang pawhin beisei angin an puitlin tan lo mai thei.
Puitling hun sawn hlat chhan ber chu eng nge ni?
Vawi tam tak chu puitlin hun sawn hlat chhan ber chu genetic a ni. Chu chu chhungkaw naupang dangte pawhin an lo neih tawh thil a ni thei tihna a ni. Naupang thenkhat chuan an gene kaltlangin thuchah an dawng a, puitlin hun chu a hnu deuhah a intan dawn tih hi a ni. Naupang taksa peng hrang hrang, glands, hormone te hi a pawi lo. Engkim hi a thawk tha vek a ni. A awlsam zawngin, i fa taksa hian naupang dangte aiin schedule danglam takah hna a thawk mai mai a ni.
Hei hi Doctor-te chuan `(Constitutional Delay of Growth and Puberty)` emaw `(CDGP)` emaw an ti a. Doctor thenkhat chuan `(self-limited delayed puberty)` an ti bawk. Hei hi a chhan chu, damdawi lam enkawlna engmah awm lo pawhin, puitlin hun chu a hun ruatah a thleng a, a pangngaiin a kal zel a ni. Ngaihtuah teh, chhungkaw pa emaw, pa emaw chu tlemin a lo seilian tlai a nih chuan naupang pawhin chutiang bawk chuan a tih ve theihna chance tlemte a awm.
Mahse, a châng chuan naupang taksaa thil awm dân dangte hian puitlin hun leh a kal zêlna a nghawng thei a ni. Heng avang hian tihkhawtlai a nih chuan enkawl a ngai tlangpui.
Puitlin hun sawn hlat chhan dangte
Genetics tih loh chu a chhan dang pawh a awm thei. He list hi en la:
- Addison natna a ni
- Kidney natna rei tak awm thei
- Cystic fibrosis natna (cystic fibrosis) a awm thin
- Genetic natna, chromosomal abnormalities te, Turner syndrome leh Klinefelter syndrome te.
- Exercise tam lutuk. Hei hian taksa thau nasa takin a tihhniam thei a, hormone hnathawh a tibuai thei bawk. (Hei hi naupang tê, competitive sports khelte tan chuan a pawimawh hle.)
- Growth hormone tlakchham vang a ni
- Hypothyroidism (Thyroid chak lo) .
- Inflammatory bowel natna (IBD) a awm thei lo.
- Malnutrition hi chhan hrang hrang avangin a awm thei a. Hei hi ei leh in lama harsatna ang chi thilte pawhin a nghawng thei bawk.
- Damdawi emaw, enkawlna emaw ṭhenkhat, corticosteroid, chemotherapy, emaw, radiation therapy emaw ang chi.
- Naupang thluak emaw gonads (ovaries emaw testicles emaw) accident emaw chhiatna emaw.
- Naupang thluak emaw, ruhro emaw nghawng thei tumor.
- Type I zunthlum vei a ni.
Hêng thil chi hrang hrang zawng zawng hian engtin nge puitlin hun a nghawng tih i ngaihtuah mai thei. A chhanna chu hormone-ah a awm a ni.
Puitling tlai lama hormone te chanvo
Hormone te hi kan taksa thuruk thuruk ang mai a ni. Puberty initiate leh sustain turin behind the scenes thawktute an ni. Heng hormone te hi endocrine glands atanga siam a ni. I fa chuan an taksaah inthlak danglamna a hmu thei a, chu chu hnute lo thanglian emaw, an kut hnuaia sam lo sei emaw ang chi hi a ni. Mahse, i hmuh loh tur thil thenkhat a awm:
1. Gonadotropin-releasing hormone (GnRH) hi i naute thluak hmun thenkhat Hypothalamus an tih atanga siam leh chhuah a ni.
2. He hormone `(GnRH)` hian naupang thluaka pituitary gland chu luteinizing hormone `(LH)` leh follicle-stimulating hormone `(FSH)` siam chhuak tur leh chhuah tir turin a hrilh a. Heng pahnih hi an inzawm khawm chuan gonadotropins `(gonadotropins).` an ti a
3. Heng gonadotropin hormone te hian naute gonads (hmeichhiaah chuan ovary leh mipa testes) te chu sex hormone (estrogen emaw testosterone emaw) chhuah tir turin a hrilh a ni.
4. Heng sex hormone te chhuak hi a ni a, puitlin huna taksa chhinchhiahna, hnute than leh testicular thanlenna te a thlen thin.
Hei hi team lian tak thawhhona ang mai a ni lawm ni? Team member pakhat chunga thil thleng a nih chuan team pumpui a nghawng a ni. Doctor-te chuan a hnung lama thil thleng sawifiah nan hetiang thumal hi an hmang a:
- Hypogonadotropic hypogonadism: Hei hian naupang hypothalamus emaw pituitary gland emaw a thawk tha lo tihna a ni. Hormone tha tawk an siam chhuak lo va, an tichhuak lo bawk. Hei hi damdawi lam dinhmun avanga lo awm a ni fo. Doctor-te’n an enkawl hnuah chuan puitlin hun chu a pangngaiin a awm tan tawh ang. Exercise tam lutuk leh ei leh in tha lo pawh hi a chhan tlangpui a ni.
- Hypergonadotropic hypogonadism: Hei hi naupang hypothalamus leh pituitary gland tha taka an thawh lai a ni. Amaherawhchu, an gonads (testicles emaw ovaries) te hian hna a thawk tha lo hle. Hei hi Turner syndrome leh Klinefelter syndrome nei naupangte zingah a thleng thin. Hetiang dinhmun hi cancer enkawlna avanga side effect angin emaw, chhan dang vang emaw pawhin a awm thei.
Heng thute hi a buaithlak deuhin lang mahse, a awlsam zawngin sawi ila, hei hian a sawi tum chu buaina chu hormonal control system-a khawiah nge a awm tih hi a ni.
Engtin nge doctor-te hian he natna hi an hriat theih?
Doctor-te chuan puitlin hun sawn hlat tih hriat nan a hnuaia mi ang hian an ti thin:
- Taksa enfiahna tih.
- I fa damdawi lam chanchin leh chhungkaw (biological parents) damdawi lam chanchin kan sawipui ang che.
- Test thenkhat pawh tih mek a ni.
Doctor-te’n an zawn ber tur pakhat chu chhungkaw history-a puitlin hun sawn hlat a awm em tih hi a ni. Chutiang a nih chuan i fa chu "late bloomer" a ni thei bawk a, chu chu a tlai chhan bulpui (underlying medical cause) a awm lo thei tihna a ni.
Mahse, doctor-te chuan chhungkuaah a kal niin an ngai a nih pawhin, a chhan dang a awm loh nan test an nei fo thin. Hei hi a chhan chu doctor-te chuan ``Constitutional Delay of Growth and Puberty (CDGP)`` chu ``diagnosis of exclusion.`` an tih vang a ni.`` Chu chu, a chhan dang zawng zawng chu paih chhuah a nih thu an finfiah hnuah chauh ``(CDGP)`` a ni tih an thutlukna siam tihna a ni.
Chhungkaw history awm lo leh doctor ten a chhan zawn an tum lai pawhin heng test te hi a pawimawh hle.
Puitling hun sawn hlat tih hriat theihna tur test neih thin
Hetiang test hi i ti thei ang:
- Thisen test: Hormone level enfiah la, damdawi lam thil engemaw zat chhinchhiahna a awm leh awm loh en rawh.
- Genetic testing: Puitling hun sawn hlat thei tur genetic change awm leh awm loh enfiah thin ang che.
- Imaging test: MRI scan emaw ultrasound scan ang chi thil hi condition thenkhat confirm emaw rule out emaw nan an ti thin.
I chhungkaw naupang enkawltu chuan naupang endocrinologist emaw, specialist dang emaw hnenah he natna hi hriatchhuah leh enkawl tura pui turin a refer thei che a ni.
Engtin nge delayed puberty hi enkawl a nih?
Enkawlna chu a tlai chhanah a innghat. I fa medical team chuan a hnuaia mite hi an rawt thei ang:
- A "wait and see approach": Hei hi naupang tê tê, damdawi lam harsatna emaw, tihkhawtlai chhan hriat dang emaw nei lote tan chuan zawm a ni tlangpui. Doctor-te chuan puitlin hun hi a pianphungah a intan thei em tih an en ang. Chutiang a nih chuan i fa chuan enkawlna engmah a mamawh lo mai thei a, beisei angin puitlin hun a thleng ang.
- Damdawi lam dinhmun enkawl: A tlai chhan chu natna bik vang a nih chuan doctor-te chuan chu natna chu an enkawl ang. Hei hian puitlin hun a tan tir tur a ni a, beisei angin hma a sawn zel tur a ni.
- Hormone thlak danglamna damdawi:Naupang taksain puitlin hun thleng thei tur khawpa hormone (testosterone emaw estrogen) a siam chhuah loh chuan chu hormone pe turin damdawi an mamawh mai thei. Medical team chuan i fa mamawh bik a zirin eng chen nge hormone therapy a mamawh tih an hrilhfiah ang che.
Naupang damdawi lam chhan nei lo "late bloomers" te chuan hormone therapy an mamawh lo. Mahse, puitlin hun sawn hlat lutuk hian naupang tan a buaithlak hle a nih chuan duhthlan tur a ni thei. Naupang tê tê ṭhenkhat chuan puitlin hun nghah chu harsa an ti a, he hun sawn hian khawtlâng buaina a thlen thei a, mahni inngaihhlutna a nghawng thei bawk. I fa chungah hetiang thil hi a thleng tih i ngaihtuah a nih chuan i medical team te nen sawiho rawh.
Engtikah nge ka fa tan damdawi lam thurawn ka zawn ang?
I fa chu well-check neih fo turin hruai la, i ngaihtuahna eng pawh chu i pediatrician hnenah hrilh rawh. I fate thanlenna leh thanlen dan an enfiah ang a, i chhungkaw chanchin chungchangah zawhna an zawt mai thei bawk. I fain beisei angin a puitlin tan loh chuan eng test leh follow-up nge a mamawh tih i pediatrician chuan a sawifiah ang.
I fa rilru hriselna pawh uluk hle ang che.
Puberty tlai hian i fa naupang rilru hriselnaah nghawng lian tak a nei thei a – mahse, rilru natna leh inthlak danglamna tam tak an hmachhawn tawh hun a ni bawk. I fain therapist a biak theihna tur ruahmanna siam chu a ṭha mai thei. Counselling hian i fate chu puitlin hun chungchanga an rilru put hmang leh an ngaihtuah thil dangte hmangin a sawi chhuak thei a, chu chu a thawk chhuak thei bawk. "Ka thiante zawng zawng hi an puitling vek tawh a, keimah chauh hi ka la naupang hle a ni," tiin an ngaihtuah mai thei. Hetiang hunah hian tanpuina an mamawh a ni.
Ka fa doctor-te hnenah eng zawhna nge ka zawh ang?
Puberty hi naupang tin tan chuan thil danglam tak a ni a, "a hun takah" emaw, beisei aia tlai emaw pawh nise. I naupang enkawltu doctor leh enkawlna pe thin specialist tu pawhin i fate tana thil chiang tak tak an hrilh thei a ni. Inbiakna ṭan nâna zawhna i zawh theih ṭhenkhat chu hetiang hi a ni:
- Engtin nge ka fa hian puitlin a tan tawh tih ka hriat theih ang?
- Engtin nge puitlin hun chu beisei angin a kal zel lo tih ka hriat theih ang?
- Ka fa hian puitlin hun a tikhawtlai em? A nih chuan eng chhinchhiahnate nge ni?
- Ka fa hian test a mamawh em?
- Enkawlna eng emaw tal i rawt em?
- Engtin nge ka fa chu ka enkawl ṭhat theih ang?
Ka fa hian puitlin hun a tikhawtlai a nih chuan eng nge ka beisei ang?
I fa medical team chuan i beisei tur chu an hrilh ang che, chu chu puitlin hun sawn hlat chhan leh i fa enkawl dan eng pawh a zirin a ni. Engtikah nge puitlin hun a tan dawn tih chiang taka sawi a harsa hle. Naupang tê ``Constitutional delay of growth and puberty (CDGP)'' nei te hian kum 18 an tlin chuan an puitlin tan tlangpui a, mahse, i fa chu a hmain a tan hma hle mai thei. Naupang tin hian kan tawn dan a inang lo.
Hriat reng tur chu, puitlin hun sawn hi hun eng emaw chen atan a ni a, a tul chuan enkawl theih a ni.
Puberty tlai hian san zawng a tisang em?
Puberty tlai hian i fa puitling san zawng a nghawng dawn tih chiang taka sawi a harsa hle. Naupang tê ṭhenkhat chuan an nu leh pa tak takte san zawng a zirin beisei aia puitling san zawng tawi zawk an thleng ṭhin. Mahse, naupang tê dangte tan chuan puitlin hun sawn tlai hian an puitlin san zawng a nghawng lo niin a lang.
Doctor-te chuan naupang puitling san zawng hriat theih nan "bone age" test (X-ray) an ti fo thin. I pediatrician chuan he test chungchang leh a lan dan te a hrilh belh thei che a ni.
Melatonin hman hian puitlin hun a tikhawtlai em?
Melatonin hian puitlin hun a tikhawtlai thei a , mahse chiang taka hriat theih nan zirchianna tam zawk a ngai a ni. Researcher-te chuan melatonin hmanga enkawlna hian naupang leh puitling naupangte chunga nghawng a neih dan an la zirchiang mek a ni. I fate melatonin pek a thatna leh that lohna chungchang chu i pediatrician nen sawiho rawh.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Puitlin hun sawn hi nang leh i fa tan pawh a buaithlak thei hle. I fa chu i lungngai a, a nih loh leh engvangin nge an thanlenna a tlai tih i ngaihtuah mai thei. Naupang tin hi mahni kawng zawh vek an ni tih hre reng ang che. I fa chu an taksa a inpeih hunah puitlin hun a thleng thei. A nih loh leh, an taksa chuan chu hmun thlen theihna turin ṭanpuina tlem a mamawh mai thei bawk. Mahse, i naupang enkawltu doctor chuan eng thil nge thleng tih hriat tumin a pui thei che a, a tha ber tur a rawt thei bawk.
Hetih lai hian i fa hian a ngaihtuahna tam tak a nei thei a – a rualpui nena inmil atanga a hmel lan danah inrintawkna a neih thlengin. I fate rilru lama a mamawh chu engtin nge a ṭha ber ang tih chu i naupang enkawltu doctor zawt rawh. Tin, i fain lungngaihna emaw, lungngaihna emaw a neih apiangin a biak theih nan kawngkhar chu hawng reng ang che. Cuddle tlemte emaw, "I'm proud of you" tih note emaw pawh hian tun dinhmunah hian kawng thui tak a zawh thei.
` Puitlin hun tlai, Hormone, Naupang hriselna, Tleirawl, thanlenna, Sexual Development











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