I taksa ruhte chu a nghet nghal a, a inher a, a nih loh leh hmun khatah a innghat nghal tih i hmu ngai em, a nih loh leh i tawng tawh em? A châng chuan hei hi a nuam lo thei a, a hrehawm hial thei bawk. He natna hi ``Dystonia`` kan ti a.`` Muscle problem angin lang mahse, a takah chuan kan thluak emaw nervous system-ah emaw a awm a ni. Hemi chungchang hi chipchiar zawkin sawi ila, kan sawi dawn em ni?
Dystonia hi eng nge ni tak tak?
A awlsam zawngin sawi ila, dystonia hi nervous system lama harsatna a ni. I thunun theih loh leh i thawhrimna tel lova i duh loh zawnga taksa ruh inzawmkhawm (involuntary muscle contractions) a awm thin. "Dystonia" tih thumal hi Latin tawng "dys" (dik lo/chhia) leh Greek tawng "tonos" (muscle tension) atanga lo chhuak a ni. Muscle te hi a inzawm khawm dik lo, a dik lo tihna a ni.
Dystonia leh Dyskinesia hi eng nge an danglamna?
Heng thumal pahnih hi a inang deuh niin lang mahse, a danglamna tlem a awm.
- Dyskinesia: Hei pawh hi Greek tawng a ni. "Kinesia" tih awmzia chu "chevement" tihna a ni. Dyskinesia tih awmzia chu chetna dik lo, thleng tur ni lo tihna a ni. Hengte hi involuntary movement , chu chu i thunun loha lo awm muscle movement a ni.
- Dystonia: Hei hi dyskinesia chi khat a ni. Dystonia-ah chuan taksa ruhte chu rei tak a inzawm khawm thin . Taksa peng eng nge a nghawng dan azirin, dinhmun hrang hrangah i awm niin a lang thei.
Tute nge dystonia vei thei?
Dystonia awm chhan a zirin tu pawh a nghawng thei. A chhan ṭhenkhat chu kum bithliah a ni a, chu chu pian tirh emaw, naupan lai emaw a nghawng thei che tihna a ni. Mi dangte chu nakin lawkah an lo ṭhang chho thei a ni.
Research-in United States-ah ringawt pawh mi 300,000 velin dystonia an vei tih sawi mah se, mithiamte chuan a zat tak tak chu a tam zawk hle mai thei niin an ngai. Dystonia hi chi hrang hrang a awm theih avangin a chang chuan dik taka hriat a harsa thin.
Engtin nge dystonia hian ka taksa a nghawng?
Dystonia hi thluak natna a ni a, i thluak in i taksa ruh a thunun dan a nghawng a ni. Muscle hrang hrang emaw, muscle group hrang hrang emaw chu kawng hrang hrangin a nghawng thei a ni. Engtin nge leh engvangin nge hetiang thil hi a thlen tih dik tak hi chu thil mak deuh a la ni.
Dystonia symptoms hi i chau emaw, i stress emaw, caffeine emaw zu emaw ang chi i in chuan a na zual thei.
Dystonia chi thenkhat chu genetic mutations emaw, thluak hmun thenkhat hnathawh tibuaitu condition emaw avanga lo awm a ni. Hei hian a nghawng cell te chu a tichhe thin. Chumi hnuah chuan signal dik lo chu taksa peng hrang hrangah a kal a, dystonia a thlen thin.
Dystonia hi hliam emaw, damdawi lam thil dang emaw, thluak hnathawh tibuaitu vang pawh a ni thei. Heng dinhmun thenkhat hi imaging scan hmangin hriat theih a ni. Mahse a chang chuan dystonia hi heng zawng zawng hi a awm lo thei a ni.
Dystonia natna lan chhuah dan chu engte nge ni?
Dystonia chhinchhiahna ber chu taksa ruh chetna thunun theih loh a ni tlangpui . Heng movement te hi a tam zawkah chuan:
- A nuam lo a, a chang chuan a hrehawm a, electric shock ang maiin a awm thei bawk.
- Recurring (a bik takin tremors nen).
- Hun rei zawng hi a inang lo thei. Ṭhenkhat chu second emaw minute emaw chhung an awm a, chutah chuan an bo leh ṭhin. Mi dangte chu thla tam tak chhung an daih thei bawk.
- Twisting leh pulling nature a nei a. Hei hian mi chu dinhmun mak takah a ding thei a ni.
- A nghawng ruh te hi hman a nih chuan a na zual thei a ni.
Taksa chhunga khawi hmunah nge dystonia hian a nghawng tih a zirin symptoms ah hian danglamna tlem a awm thei. Symptoms awm dan tlangpui panga a awm a, chungte chu:
- Focal dystonia a awm thin
- Segmental dystonia a awm thin
- Multifocal dystonia a awm thin
- Hemidystonia `(Hemidystonia)` tih a ni
- Dystonia tlangpui (generalized dystonia) a awm
Heng zawng zawng hi a hranin han thlir ila.
Focal dystonia a awm thin
Hei hi i taksa peng pakhat chauh a nghawng lai a ni. Mithiamte chuan he natna chi hi midang aiin a let sawm velin a tam zawk niin an sawi. Kawng hrang hrangin a rawn lang thei a, taksa peng a nghawng dan azirin:
- Mitmeng: Blepharospasm a ni. Hei hi a nasat em avangin mi thenkhat chuan an mit an khap tlat a ngai thei a ni.
- Jaw: Ha hrual (Bruxism).
- Kut emaw kutphah emaw: Muscle twitching emaw tightness emaw. Hei hi ``writer's cramp'' emaw ``musician's cramp'' emaw an ti bawk.Golfer leh cricketer te chuan ``the yips'' an ti a ni.I kut a khauh a, a ziak thei lo emaw, violin ang chi thil i tum hian i kut zungtang te chu a thunun theih loh ang tih han ngaihtuah teh.
Segmental dystonia a awm thin
Hei hi taksa peng pahnih emaw a aia tam emaw inhnaih tak takte a nghawng hun a ni. Entirnan, hmai hmun hrang hrang, lu leh kawr, a nih loh leh kut leh kut chunglam. Hei hi entirnan tha tak chu cervical dystonia hi a ni . Hei hian lu leh kawr ruhte a nghawng a ni. Entirna dang chu Meige syndrome hi a ni . Hei hian hmai hmun engemaw zat a nghawng a ni.
Multifocal dystonia a awm thin
Hei hian taksa peng inzawm lo pahnih emaw a aia tam emaw a nghawng a ni . Entirnan, dystonia hian kut pahnih a nghawng a. Tardive dyskinesia a awm thinHei hi taksa peng hrang hrang inzawm lo engemaw zat tuar thei dinhmun entir nan a hmang bawk.
Hemidystonia `(Hemidystonia)` tih a ni
"Hemi" tih thumal hi Greek tawnga "half" tihna atanga lo chhuak a ni. Chuvangin hei hian i taksa sir khat (dinglam emaw veilam emaw) chauh a nghawng tihna a ni. I kut dinglam emaw, i hmai dinglam emawa taksa ruhte chu thunun theih lohvin a che tih han ngaihtuah teh. Stroke hi hemidystonia thlentu lian tak a ni.
Dystonia tlangpui (generalized dystonia) a awm
Hei hian i ke leh i ke ruh (i taksa peng ber, i kut, ke, leh lu inzawmkhawmtu) emaw, i taksa pum pui emaw a nghawng thei a ni . Hei hi dystonia a lo zual zel chuan a thleng thin. Focal dystonia chu generalized dystonia a nih chuan a natna lan chhuah dan chu ke ruh atanga ke ruh thlengin a darh thin.
Dystonia hi engte nge ni?
Dystonia hi i thluak hnathawh dan tihbuai vang a ni. Hei hian thluak hmun thenkhat `Basal Ganglia` tih a huam tlangpui. Hei hi thluak hmun hrang hrang inzawmkhawmtu leh chu peng hrang hrangte hnathawh dun dan tur inzawmkhawmtu thluak structure pawl a ni.
Mithiamte chuan dystonia thlentu hi chi thum ah an then a, chungte chu:
- Primary dystonia: Dystonia hi a chhan ber a ni. Idiopathic a ni tlangpui a, a chhan hmuh tur a awm lo tihna a ni. Mithiamte chuan genetic component pawh a awm thei niin an ngai a, chu chu chhungkaw hrang hrangah a kal thei tihna a ni.
- Secondary dystonia: Hetiang a nih chuan dystonia hi natna dang emaw harsatna dang emaw chhinchhiahna a ni.
- "Dystonia plus" conditions: Hengte hi nervous system natna a ni. Dystonia hi a lan chhuahna ber ni mahse, a lan chhuah dan dang pawh a awm bawk.
Secondary dystonia thlentu awm thei te
Hei hi chhan hrang hrang avangin a thleng thei a ni:
- Thluak natna (brain tumor) a awm
- Thluak natna dang (e.g. epilepsy, Parkinsonism, Parkinson’s disease) .
- Cerebral hypoxia (a bik takin nau piang thar, an pian tirh atanga oxygen tlakchham tawhte) .
- Damdawi (damdawi pek emaw, dan loa hman emaw) .
- Genetic natna (e.g. Wilson natna, Huntington natna) .
- Hri kai (e.g., rilru lam natna) .
- Metabolic dinhmun (metabolic conditions) a awm
- Thai
- Thil tha lo (e.g. carbon monoxide rimchhia, manganese rimchhia) .
- Thluak hliam na tak tak
Dystonia hi natna hrik kai theih a ni lo. Midang hnen atangin i man thei lo va, midang hnenah pawh i thehdarh thei hek lo.
Engtin nge Dystonia hi hmuhchhuah a nih?
Doctor, a tam zawkah chuan neurologist chuan i symptoms te, neurological exam te, leh medical test hrang hrang te a zirin dystonia hi a hre thei a ni. Dystonia hi a chang chuan hriat a harsa thei a, a chhan chu heng symptoms te hi natna dang tam tak avanga lo awm thei a nih vang a ni. Chuvangin, natna dang pawh hi paih chhuah a pawimawh a, a then chu nunna atana hlauhawm medical emergency a nih theih avangin.
Dystonia hriat theihna atan eng test nge hman thin?
Dystonia awm leh awm loh enfiah nan laboratory, diagnostic, leh ``imaging`` test hrang hrang neih theih a ni. Test order tlangpui chu i symptoms leh i doctor-in a rinhlelh damdawi lam dinhmun a zirin a ni. Test tih theih thenkhat chu hetiang hi a ni:
- Thisen test: Hengte hian thil tam tak a hmuchhuak thei a, chu chu immune system lama harsatna leh toxins (a bik takin metals copper leh manganese ang chi) te hi a ni.
- CT scan (Computer hmanga tomography scan) hmanga tih a ni.
- EEG (Electroencephalogram): Thluak electric hnathawh dan tehna test a ni.
- EMG (Electromyogram): Nerve kal tlanga signal kal dan enfiahna test a ni.
- Genetic testing neih a ni
- MRI scan (MRI - Magnetic resonance imaging) hmanga enfiah a ni.
- PET scan (Positron emission tomography hmanga enfiah) hmanga enfiah a ni.
- Spinal tap / Lumbar puncture tih a ni
Hei bakah hian test dang pawh tih theih a ni. Chuvangin, i dinhmun nena inmil test engte nge tih doctor hnenah zawt la a tha ber. Tichuan i dinhmun nena inmil tur thu dik ber i hmu thei ang.
Dystonia hi engtin nge enkawl a nih? A dam kim thei ang em?
Dystonia hi damdawi a awm lo a , mahse enkawl theih a ni . Enkawlna tam tak chu i natna chhan leh i natna lan chhuah danah a innghat a ni. I doctor chuan i tan eng treatment option nge tha ber tih ngaihtuah turin a pui thei ang che.
I doctor chuan caffeine leh zu ei loh turin a hrilh mai thei che a, hengte hian mi thenkhat tan dystonia symptoms a ti na zual thei a ni.
Eng ang damdawi emaw, eng ang damdawi nge hman a nih?
Dystonia enkawlna chu a chhan leh i natna lan chhuah dan bik a innghat a ni. Enkawlna hman tlanglawn tak takte chu:
- Deep brain stimulation (DBS): Hei hi surgery hmanga tih a ni. I thluak chhungah electrode a lut a. Heng electrode te hian i thluak hmun bik ah electrical current nem tak a pe chhuak thin. Hei hian dystonia symptoms a tidam thei a ni. Hei hi dystonia enkawlna atana hman tlanglawn leh tangkai ber a ni.
- Damdawi hman tur: 1.1.Dystonia awm chhan a zirin damdawi hmanga enkawl theih a ni. Damdawi (pakhat emaw a aia tam emaw) pek tur chu a natna lan chhuah dan leh a chhan bulpui (a awm chuan) ah a innghat ang.
- Botulinum toxin injection: Botulinum toxin – mi tam takin brand name Botox® tia an hriat – chu hmun dik takah inject a nih chuan kar tam tak, a chang chuan thla tam tak chhung nerve signal a block thei a ni. Hei hian dystonia thlentu signal te chu taksa ruh (muscles) a thlen loh nan a veng a ni. Hei hi focal dystonia leh segmental dystonia symptom thenkhat enkawlna tha tak a ni.
- Physical, occupational leh speech therapy: Dystonia hi hun eng emaw chen hriselna lama harsatna avanga lo awm a nih chuan heng therapies te hian mi chu dystonia nena insiamrem emaw, a dam leh emaw theih nan a pui thei a ni.
Enkawlna atanga harsatna leh nghawng tha lo awm thei te hi thil engemaw zatah a innghat a, chu chu enkawl danah pawh a ni. I doctor chuan i dinhmun a zirchiang thei a, i beisei theih turte a hrilhfiah thei bawk.
Engtin nge ka in enkawl ang a, ka symptoms te hi ka enkawl ang?
Dystonia hi nervous system-ah harsatna a awm a. Chumi awmzia chu nangmah ngeiin i diagnose thei lo va, i enkawl thei lo tihna a ni. Dystonia hi natna khirh tak, nunna atana hlauhawm tak nen pawh a inzawm thei a, chuvangin doctor pan nghal a pawimawh .
Enkawlna hnua i rilru hahdam leh dam leh theihna hun chhung hi thil tam takah a innghat a, chung zingah chuan i dystonia lo awm chhan, a nasat dan, eng enkawlna nge i dawn, leh hriselna lama harsatna dang i neih te pawh a tel. I doctor chuan i rilru a hahdam theih nan leh i dam theih nan eng chen nge hun a duh dawn tih chiang takin a hrilh thei che a ni.
Dystonia hi eng nge a nih? Ka neih chuan eng nge ka beisei ang?
Dystonia vei theihna tur thlirna chu thil tam takah a innghat a, chung zingah chuan a chhan, i vei kum, taksaa a natna lan chhuahna hmun, i hriselna chanchin leh enkawlna i dawnte pawh a tel. I doctor chuan i dinhmun thlirletna chu a hrilh thei ber che a ni.
- Primary dystonia outlook: A tlangpuiin primary dystonia hi naupan lai atanga lo awm a nih chuan outlook chu a tha tawk lo thei. Hei hi a chhan chu primary dystonia hi focal (hmun khatah) atanga generalized (taksa pum pui) thlengin a awm thei a ni. Naupan laia he natna hi i neih hma poh leh a darh theihna a sang zawk. Focal dystonia hi taksa hmun tlemte chauh a nghawng avangin a thlir dan a tha hle.
- Secondary dystonia outlook: Hei hi a bulpui ber dinhmunah a innghat nasa hle. Underlying condition chu enkawl theih leh reversible a nih chuan prognosis a tha zawk. Mahse, natna khirh tak avanga lo awm a nih chuan prognosis a tha lo zawk. Mahse, natna khirh tak tak thenkhat awm mahse dystonia hi enkawl leh tihdam theih a ni.
Primary dystonia a lo awm tawh chuan dam chhung zawnga natna a ni. Enkawl theih a ni a, mahse a dam kim thei lo va, a mah chauhin a dam lo vang .
Secondary dystonia hi hun rei lote chhunga awm thei a ni. A chhan bulpuiah a innghat. Infection, hliam, leh damdawi thenkhat ang chi thil nen a awm tam zawk.
Engtin nge dystonia vei theihna hi ka tihtlem theih ang, a nih loh leh ka ven vek theih ang?
Dystonia hi beisei loh takin a lo awm a, chuvangin i veng thei lo. Primary dystonia vei theihna pawh i tihtlem thei lo bawk. Rochun theih a ni a, chhan hriat lohvin a lo thang lian thei bawk.
Mahse, secondary dystonia thlentu thil ṭhenkhat chu i vei thei lo va, i tihziaawm thei bawk . I tih theih ṭhenkhat chu hetiang hi a ni:
- Ei leh in inthlau tak ei la, taksa rihna hrisel tak vawng reng rawh. I circulatory system leh heart health nena inzawm natna tam tak, a bik takin stroke hian i thluak hmun thenkhat a tichhe thei a, dystonia a thlen thei bawk.
- Infection hi ngaihthah suh. Mit leh beng natna hi enkawl vat a ngai a ni. Heng natna hrik te hi thluaka a darh chuan hlauhawm tak a ni thei. Infection hian thluak a inflammation (encephalitis) a thlen thei a, chu chuan dystonia a thlen thei a ni.
- Invenna hmanrua bun rawh. Traumatic brain injuries hian i thluak a tichhe thei a, dystonia a thlen thei bawk.
- I hriselna dinhmun enkawl rawh. Hun rei tak chhunga natna chi hrang hrang, type 2 diabetes, thisen sang, leh epilepsy te hian natna dang a thlen thei a, a thlen thei bawk a, chu chuan dystonia a thlen thei bawk.
Engtin nge ka in enkawl ang?
Dystonia i neih chuan i in enkawl dan tur thil engemaw zat a awm a:
- Doctor-in a rawt loh chuan caffeine leh zu ei loh tur a ni. Hengte hian dystonia symptoms a ti na zual thei.
- I stress kha enkawl rawh. Lungkhamna leh stress hian dystonia a ti na zual thei. He hlauhawmna hi meditation, relaxation training, leh exercise ang chi thil tih hian i tihziaawm thei a ni.
- I natna lan chhuahna tizual thei thil tih loh tur. Dystonia chi thenkhat chu hun engemaw chen a awm tam zawk. Chutiang hun chu pumpelh chuan, a theih chuan, i natna lan chhuahna nasatzia chu a tihziaawm thei a ni.
- I dinhmun enkawl dan tur zir rawh.Dystonia chi hrang hrang hi "sensory tricks" hmangin enkawl theih a ni. Chumi atana thumal pawimawh tak chu "geste antagoniste" (French tawng pakhat, "opposite gesture" tihna) a ni. Heng kut zungtang chi hrang hrangte hian dystonia symptoms chu rei lo te chhung atan a tidam thei a ni. Mahse mithiamte chuan engvangin nge hetiang thil hi a thlen tih erawh an hre chiang lo. Entirnan, chin emaw hmai sir emaw khawih hian cervical dystonia (kawng ruh tichhe thei) symptoms a tihziaawm thei a ni. I doctor chuan heng kut zungtang chi hrang hrangte hi i chhân lêt leh chhân lêt loh a en thei a, hman dân a zirtîr thei bawk.
- I damdawi ei tur dik takin ei rawh. Dystonia damdawi i ei a nih chuan a tih angin ei tur a ni. Damdawi ei khap nghal chuan dystonia symptoms a ti na zual thei a, side effect dang pawh a thlen thei bawk.
Engtikah nge Doctor ka hmuh ang? Engtikah nge emergency care ka zawn ang?
Dystonia i neih chuan doctor-in a rawt angin follow-up visit i nei tur a ni. I natna lan chhuah dan a danglam emaw, a zual emaw a nih chuan doctor hmu rawh, a bik takin nitin nun a tibuai a nih chuan. Tin, damdawi emaw, enkawlna dang emaw a hlawhtlin loh chuan, emaw, tuar theih loh emaw, tibuaitu emaw side effect i neih chuan doctor pan rawh.
Engtikah nge Emergency Department (ETU) ah ka kal ang ?
Stroke i neih theihna tur symptoms i neih chuan emergency room-ah i kal tur a ni. Stroke symptoms nei tan 1990 (Sri Lanka emergency ambulance service) ah biak theih reng a ni tih hre reng la, FAST tih pawh hre reng ang che.
- F (Hmêl): Miin nuih a tum hian hmai sir khat emaw, a sir lehlamah emaw a tla thla em?
- A (Arm): Chu mi chuan a kut pahnih chawi sang a tum hian a kut pakhat chu a tla thla em?
- S (Speech): Chu mi chuan chiang takin thu a sawi thei em, mi dangte thusawi pawh a hrethiam thei em?
- T (Hun): Miin heng symptoms te hi a neih chuan 911 ah call nghal rawh! Stroke hi hun nena intlansiak a ni. Enkawl hmasak hi result tha leh damna tha ber a ni.
Dystonia hi thluak natna a ni a, i taksa ruhte chu thunun theih lohvin a che thei a ni. Thil chi hrang hrang avanga lo awm thei a ni a, rochun natna atanga hun rei lote chhunga natna thlengin a awm thei.
I tana pawimawh ka tih thenkhat (Take-Home Message) .
Chuvangin, Dystonia nena kan sawi dun thin kha in hriatthiam ka beisei. Hei hi dinhmun buaithlak tak ni mah se, nangmah chauh i ni lo tih hre reng ang che .
- Nangmah emaw, i hriat emaw chuan heng natna lan chhuah dan hi i neih chuan doctor pan hreh suh . A hmuhchhuah hma poh leh enkawl a awlsam zawk.
- Dystonia zawng zawng hi a inang vek lo va, chuvangin i dinhmun atana enkawlna tha ber tur chu i doctor nen sawiho rawh.
- A châng chuan, nunphung tihdanglamna tê tê (caffeine leh zu in tlem te, leh lungkhamna tihziaawmna ang chi) siam hian natna lan chhuahnate chu a thunun thei a ni.
- Doctor thupek chu uluk takin zawm rawh. I damdawi ei tur chu a tih angin ei rawh. Mahni chauha ei kha bansan suh.
He thu hi i tan a tangkai ngei kan beisei. Hrisel takin awm rawh!
` Dystonia, Nervous system disorder, Muscle contraction, Duh loh vanga chetna, Thluak dinhmun, Dyskinesia, Dystonia, Nervous system disorder, Muscle contraction, Duh loh vanga chetna, Thluak dinhmun, Dyskinesia











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