I thinlungah hian thil awm lo tak a awm tih i hria em: Ebstein’s Anomaly?

Kan thinlung hi taksa peng mak tak a ni tak zet a ni lawm ni? Mahse a chang chuan pian tirh atanga inthlak danglamna thenkhat avang hian thinlung hnathawh danah harsatna tenau te a awm thei a ni. Vawiin hian mi tam takin an neih loh thinlung natna rare tak chungchang kan sawi dawn a ni. Hei hi Ebstein’s Anomaly an ti a. A hming hi a hlauhawm deuhin a lang thei a, mahse awlsam takin i hrethiam ang u.

Chuti a nih chuan Ebstein-a Anomaly chu eng nge ni?

A awlsam zawngin sawi ila, Ebstein’s Anomaly hi thinlung natna a ni a, nau piang lai hian a awm thin . "Congenital" an ti bawk a, chu chu pian tirh lamah a awm tihna a ni. "Anomaly" tih hian thil danglam emaw, beisei loh emaw a kawk a ni. Hetiang dinhmunah hian , kan thinlunga valve pali zinga pakhat tricuspid valve hi a nghawng ber a ni.

Ngaihtuah teh, kan thinlung pindan inkarah hian kawngkhar ang chi thil a awm a, chu chuan thisen chu kawng khat chauh a luang chhuak thei a ni. Chu chu valve kan tih chu a ni. Tricuspid valve hi chutiang zinga mi a ni. He natna hi kum 1866 khan German doctor pakhat Wilhelm Ebstein-a’n a sawi hmasak ber a ni. Chuvang chuan a hming chawia sak a ni.

Ebstein anomaly-ah hian tricuspid valve hi eng nge thleng?

Hetiang natna vei mi pakhat tricuspid valve-ah hian inthlak danglamna lian tak pahnih hmuh tur a awm a:

1. Valve hi a insiam tha lo (deformed): Leaflets, thinlung beat apianga inhawng leh khar thin flap te hi a pianzia pangngai a ni lo. A châng chuan thinlung bangah pawh an innghah mai thei.

2. Valve awmna hmun hi a danglam: He valve hi a awm dan pangngai aia hniam zawkah a awm a.

Heng harsatnate hian valve chu a khar tha lo va, thisen chu upper right atrium-ah a leak leh thin. Doctor te chuan hei hi regurgitation an ti a. Thisen chu hnunglam hawia a luang chhunzawm zel chuan dinglam atrium chu zawi zawiin a lian chho zel a. Hun a kal zel a, thinlung dinglam chu a chak lo thei a, thinlung chak lohna a thlen thei bawk . Hei hi heart attack a ni lo va, thinlungin thisen a pump tha thei lo tihna a ni zawk.

Hetiang dinhmun hian tute nge a nghawng nasa ber?

Ebstein’s Anomaly vei tam tak chuan thinlung lam natna dang an nei bawk. Ebstein’s Anomaly vei zinga zaa 94 vel chuan thinlung chunglam pindan pahnih (atria) inkar bangah khur an nei a. Hei hi Atrial Septal Defect (ASD) emaw Patent Foramen Ovale (PFO) emaw an ti a.

Tin, thinlung valve dang leh veilam chamber-ah pawh chhiatna thenkhat hmuh tur a awm bawk.

Ebstein-a Anomaly hi engtiang chiahin nge a awm?

Hei hi a awm lo hle a ni . Nau piang thar sanghnih zinga pakhat vel a nghawng a ni. Congenital heart diseases zingah hian 1% aia tlem lovah hmuh tur a awm.

Ebstein-a Anomaly natna lan chhuah dan chu engte nge ni?

Hetiang natna lan chhuah dan hi mi hrang hrangah a inang lo thei a, valve deformity degree a zirin a nasat loh atanga na tak thlengin a awm thei .

Chu natna chu a nasat chuan, a lan chhuahna chu nau piang emaw, naupan thla hmasa berah emaw a lang tlangpui . Naute tê têah chuan a châng chuan:

• Thisenah oxygen tlakchham (cyanosis) vangin vun chu a sen thei a ni .
• Lung chak lohna chhinchhiahna hmasa ber chu:
• Thâwk rang tak.
• Thâwk harsa.
• Weight gain hi a awm fo thin.
• Ke, pum, mit vel emaw a hring (edema) a awm.

Ngaihtuah teh, nausen piang thar chu a rawn sen chhunzawm zel a, thawk harsatna a neih chuan doctor-te chuan chutiang dinhmun chu an ringhlel ang.

A natna hi a na lo a nih chuan natna lan chhuahna engmah i nei lo thei a , puitlingah pawh chhinchhiahna a lang thei bawk. Puitlingah symptoms a lan tak tak chuan, hetiang hi i hmu thei ang:

• Vun (a bik takin hmui leh kut zungtang) blue discoloration.
• Thinlung thawk mumal lo (arrhythmia).
• Heart failure a awm chuan:
• A rilru a na.
• Luak chhuak emaw, muhil emaw.
• Chau tih hriat reng reng.
• Thâwk harsa, a bik takin exercise lak laiin.
• Ke emaw pum emaw a hring chhuak.

Eng thilin nge Ebstein-a Anomaly hi a thlen?

Dik tak chuan doctor-te chuan he natna hi a lo awm chhan chiang takin an la sawi thei lo . Genetic (i.e. inherited) leh environmental factors inzawmkhawm avanga lo awm niin an ngai. Mahse chutiang thilte chu eng nge ni tih erawh hriat chian a la ni lo.

Engtin nge he natna hi hriat chhuah a nih? (Diagnosis) tih a ni.

Doctor i hmuh hunah i symptoms te an zawt ang a, i pulse rate leh blood pressure te an check ang. I thinlung a thawh thatzia hriat nân test ṭhenkhat an ti thei bawk a, chu chu:

• Cardiac imaging hmanga thil tih dan: 1.1.
• Chest X-ray: Hei hian thinlung a lian em tih enfiah theih a ni.
• Cardiac MRI: Hei hian thinlung valve leh chamber-te thlalak chiang zawk, chipchiar zawk a siam thei a ni.
• Echocardiogram: Hei hi thinlung ultrasound ang a ni. Doctor chuan thinlung valve leh chamber awm dan te, an hnathawh dan te a hmu thei a ni. Ebstein anomaly-a valve abnormalities awmte chu chiang takin a lantir thei.
• Electrocardiogram (ECG): Hei hian thinlunga electric hnathawh dan a teh a. Heartbeat mumal lo (arrhythmias) eng pawh a hmu thei.
• Exercise stress test neih dan tur:Hemi ah hian treadmill emaw bike emaw ah dahin ECG lak a ni ang. Hei hi i stress laiin i thinlung hnathawh dan tur hriat nan tih a ni.
• Holter monitor: Hei hi hmanraw te tak te a ni a, darkar 24 atanga darkar 48 chhung i ha thin. Hemi chhung hian thinlung thawk zawng zawng a record vek a ni. Hei hian i doctor hnenah nitin i heart rate leh rhythm a inthlak dan tur ngaihtuahna tha tak a pe thei a ni.

Ebstein-a Anomaly hi engtin nge enkawl a nih?

Enkawlna chu i natna lan chhuah dan a nasat danah a innghat.

• Symptoms a na lo emaw, a awm lo emaw a nih chuan: I doctor chuan i thinlung chu a enfiah fo ang a, a danglamna a awm leh awm loh a enfiah ang. Enkawlna engmah i mamawh lo mai thei.
• Heart failure emaw heartbeat mumal lo (arrhythmia) symptom i neih chuan:
• Chutiang dinhmun control turin damdawi pek theih a ni.
• Thinlung lian zawk emaw, thinlung thawk mumal lo emaw i neih chuan taksa tihchakna tihtlem turin an ti thei che a ni . Doctor thupek dik takin i zawm tur a ni.

• Symptoms a nasat chuan: Tricuspid valve surgery hi a tha ber. Hei hian hun rei tak chhungin valve hnathawh a titha thei a ni.
• Mahni valve tissue hmanga siamthat tum hi enkawlna tha ber a ni.
• A chhiatna chu siamthat theih loh khawpa na a nih chuan valve thlak a ngai mai thei . Hei hi mechanical valve emaw biological tissue valve emaw hmangin tih theih a ni. Mahse, mechanical valve dah a nih chuan i dam chhung zawng thisen tithianghlimtu damdawi i ei a ngai dawn a ni.

A chang chuan heart surgery dang pawh tricuspid valve surgery nen a rualin tih theih a ni. Entirnan, thinlung pindan chunglam inkar khur khar (ASD siamthat) emaw, thinlung thawk mumal lo enkawl (arrhythmia enkawlna) emaw. Heartbeat mumal lo enkawlnaah hian catheter ablation emaw pacemaker dah emaw a ni.

A tlem hle a, enkawlna dang zawng zawng a hlawhchham chuan thinlung thlak a ngai mai thei.

Ebstein-a Anomaly hi a veng thei ang em?

Doctor-te chuan he natna hi engtin nge a lo awm tih chiang taka an hriat loh avangin tunah hian ven theih dan tur a awm lo .

Hetiang dinhmun nen hian engtin nge nun hian hma a sawn ang? (Hmuh dan tur) .

Ebstein’s Anomaly vei te thlirna hi mi hrang hrangah a inang lo hle.Nausen thenkhat chu he natna hi an damchhuak lo. Amaherawhchu, mi dangte erawh chu enkawlna engmah awm lovin dam rei tak, pangngai takin an nung thung. A tlangpuiin, natna chi hrang hrang nei tan chuan outlook a tha zawk.

Operation hnuah pawh thinlung lama harsatna thenkhat chu a awm reng thei. Zirna hrang hrangah chuan operation hnuah dam rei zawng hi a tlahniam deuh thei tih hmuhchhuah a ni. Zirchianna pakhat (kum 1972 leh 2006 inkara operation nei tawhte enfiahna) chuan operation an neih atanga kum 20 hnuah mi 65% chu lung natna avangin vawi khat tal damdawi inah dah an ni tawh a, 76% chu an la dam tih a tarlang.

Mahse hei hi a pawimawh a ni: Tûn laia surgery hmanraw hmasawn tak tak leh follow-up care awm tawhte avângin, tûn laia operation neite tân chuan a rah chhuah chu a ṭha zâwk hle a rinawm.

Engtikah nge Doctor ka hmuh ang?

Ebstein’s Anomaly i neih chuan i natna lan chhuah dan a zual emaw, natna lan chhuah thar i neih chuan doctor hnenah i hrilh nghal tur a ni . Heng thilte hi hre reng ang che:

• Vun a rawn sen zual zel chuan.
• I taksa chakna a hloh nia i hriat chuan.
• I taksa chu tuiin a khat ang maia i hriat chuan (swelling).
• Lung na a chak chuan.

In lama hruai tur thuchah pawimawh ber

Ebstein’s Anomaly hi thinlung natna hmuh tur awm lo, pianpui atanga lo chhuak a ni. He natna hian a nghawng dan hi mi hrang hrangah a inang lo hle. Nausen laia hmuhchhuah a nih chuan a natna hi a na lo tlangpui. Puitling thlenga dam khawchhuakte chuan he natna hi a na zawk fo thin. Mahse, hun kal zelah heartbeat mumal lo (arrhythmia) leh heart failure ang chi harsatna an nei thei bawk. Chutiang a nih chuan tricuspid valve siamthat emaw thlak emaw nan operation neih a ngai mai thei a, chubakah a kaihhnawih thinlung lama harsatna dangte pawh enkawl a ngai thei bawk.

A pawimawh ber chu i thinlung hnathawh danah danglamna a awm tih hriat theih nan checkup neih fo a, a tul chuan a rang thei ang bera enkawlna tha tak dawng tur a ni. Ngaihtuah buai suh, Doctor te chu tanpui turin an awm reng a ni.

` Ebstein’s Anomaly, Lung natna, Tricuspid Valve, Pianpui Lung chhiatna, Lung chak lohna, Lung zai, Symptoms