Eisenmenger Syndrome hi eng nge ni? Chipchiar takin kan sawi dawn em ni?

Pianpui thinlung lama harsatna ṭhenkhat chuan nakin lawkah natna khirh tak a thlen thei tih i hre ngai em? Chutiang dinhmun khirh tak pakhat chu Eisenmenger syndrome a ni. A hming hi i tan chuan thil thar a ni mai thei a, mahse a chungchang hriat a pawimawh hle a, a bik takin i chhungkuaa mi pakhatin pianpui thinlung natna a neih chuan. Hemi chungchang hi chipchiar deuhin han sawi ila, a chhan chu he natna hi a hmaa hriatchhuah leh hriat chian a pawimawh hle a ni.

Eisenmenger Syndrome hi eng nge ni tak tak?

A awlsam zawngin sawi ila, Eisenmenger Syndrome hi i thinlung atanga i lung thlenga thisen phurtu thisen kalna kawng (arteries) atanga thisen tam lutuk a luang chhuak a ni. Faucet chhunga tui luang rang lutuk ang maiin han ngaihtuah teh. Hei hian i lung thisen kalna kawng leh i thinlung dinglamah thisen sang a thlen a, chu chu Pulmonary Hypertension tih a ni. Pipe te tak te hmanga tui tam tak nawr tum ang mai a ni a, chu chuan pipe chhungah pressure nasa tak a siam a ni.

Chu bakah, thinlung veilam leh dinglam inkarah thisen a luang dik lo tan bawk (`blood shunting`). Chumi awmzia chu inzawmna pangngai lo (pian tirh laia khur awm ang chi) avang hian thinlung veilam (oxygen tamna) atanga thisen dinglam (oxygen tlem) a luang chhuak tihna a ni. Hun kal zelah he dinhmun hi tihdanglam theih a ni bawk a, chu chu thisen oxygen tlem zawk chu dinglam atanga veilamah a luang tihna a ni.

He natna, Eisenmenger syndrome tia koh hi, pianpui thinlung natna pakhat emaw, a aia tam emaw enkawl loh emaw, hriat chhuah loh emaw a nih chuan a lo awm fo . Hetiang dinhmun hi rei tak a awm reng chuan lung tihchhiat nghet leh nunna atana hlauhawm dang a thlen thei a ni. Chuvangin hei hi ngun taka ngaihven ngai dinhmun a ni.

He natna hi tuin nge vei tam zawk?

Eisenmenger syndrome hi naupang leh puitling tleirawl, Ventricular Septal Defect (VSD) neia piang, thinlung pumping chamber hnuai lam pahnih (ventricle veilam leh dinglam) inkar bang chhunga khur awmte zingah a awm tlangpui.

Tin, Eisenmenger syndrome hi pianpui heart defect dang thenkhat chu uluk taka enkawl a nih loh chuan a lo awm thei bawk. Entirna tlemte chu hetiang hi a ni:

• Atrioventricular canal a chhiat vang a ni
• Atrial septal defect a ni
• Cyanotic heart disease (taksa chu a rawn sen chhuak) .
• Patent ductus arteriosus (nau piang hnua thisen kalna kawng khar tur) .
• Tetralogy of Fallot (thinlung chhiatna pali inzawmkhawm) .
• Truncus arteriosus `(Truncus thisen kalna kawng)`

Thil dang pakhat chu, Down syndrome tih hi a ni.Down syndrome nei naupangte pawhin pianpui thinlung natna an vei theihna a sang zawk bawk. Chuvang chuan Eisenmenger syndrome vei an tam zawk thei bawk. Dik tak chuan statistics atanga a lan dan chuan Eisenmenger syndrome vei puitling zinga 25% leh 50% inkar hian Down syndrome an nei ve bawk.

Eisenmenger syndrome hi engtiang chiahin nge a awm?

Vanneihthlak takin Eisenmenger syndrome hi a awm lo hle a ni . Puitling pianpui, pianpui thinlung natna nei zinga 1% leh 6% inkar a nghawng a ni. Amaherawhchu, a tlem hle chung pawhin a pawizia avang hian hriat chian a pawimawh hle.

Eng thilin nge Eisenmenger syndrome hi a thlen?

Chutiang thil a thlen chhan dik tak hriat chian nan chuan kan thinlunga thisen kal dan hi tlem tal i neih a ngai a ni. Kan thinlung hi pindan pali nei in ang maiin han ngaihtuah teh.

Thinlung hrisel takah thisen kal dan chu hetiang hian a thleng thin:

1. Right atrium: Taksa hman, deoxygenated thisen chu hetah hian a lo kal hmasa a, a khawlkhawm thin. He thisen hi ventricle dinglamah pump chhuah a ni.

2. Right ventricle: Hei hi oxygen tlachham thisen chu lungah oxygen thar dawng turin an thawn a ni.

3. Left atrium: Lung chhunga thisen thianghlim oxygen awm tawh chu hetah hian thinlungah a kir leh thin. He thisen hi veilam ventricle-ah thawn a ni.

4. Left ventricle: Hei hi thinlung pump ber a ni. Hei hi taksa pum puiah oxygen tamna thisen a insem darh na hmun a ni.

Tunah chuan thinlungah hian structural defect a awm tih han ngaihtuah teh, chu chu right leh left ventricles (VSD) inkar wall-ah hole a awm ang. Chuti a nih chuan eng nge thleng? Oxygen tamna thisen (khawi lamah) leh thisen oxygen tlachham (dinglamah) te chu an inhmeh tan ta a ni . Chuvang chuan thisen tam lutuk chu lungah a luang lut thin. Hei hi a chunga kan sawi tak pulmonary hypertension thlentu a ni. Tin, taksa peng dang pan tura oxygen tamna thisen mamawh zat pawh a tlem phah bawk. Hei hi Eisenmenger syndrome chungchanga harsatna bulpui ber a ni.

Eisenmenger syndrome natna lan chhuah dan chu engte nge ni?

Eisenmenger syndrome symptoms hi mi hrang hrangah a inang lo thei. Lung chhiatna chi leh taksa peng hrang hrang a nghawng danah an innghat a ni. Vawi tam tak chu heng symptoms te hi vawi khatah a lang vek lo. Puitling lai emaw, puitling naupan lai emaw hian an lo lang tan tlangpui. Tichuan, a natna lan chhuah dan chu a zual sauh sauh a.

Hengte hi a lan chhuah tam ber thenkhat chu an ni:

• Chhuak na emaw, tightness emaw (Angina) .
• Lungphun mumal lo (Arrhythmias) - Chumi awmzia chu thinlung chu kawng khata thawk lovin kawng hrang hrangin a thawk tihna a ni.
• Kut zungtang tawp lian leh nail curvature (Clubbing) - drumstick tip ang mai.
• Thisen a khuh chhuak.
• Blue or grayish discoloration of the skin (Cyanosis) - Hei hi thisen a oxygen awm zat tlahniam vang a ni.
• Luak chhuak emaw, muhil emaw.
• Ke, ke ruh, ke emaw, pum emaw a hring (edema).
• I thinlung a thawk chak ang maia inhriatna, i rilru ri (heart palpitations) ri hriat.
• Chauhna nasa tak leh chakna tlakchhamna (Lethargy).
• Dyspnea - Tlemte thawhrimna pawh nise thawk harsa.

Heng symptoms pakhat emaw a aia tam emaw i neih chuan doctor thurawn lak nghal a pawimawh hle.

Eisenmenger syndrome avanga harsatna awm thei te chu engte nge ni?

Vanduaithlak takin Eisenmenger syndrome hi hmun khata awm reng natna a ni lo. Hriselna lama harsatna hrang hrang a thlen thei a ni. Chung zinga ṭhenkhat chu:

• Thluak chhunga thisen chhuak.
• Infection avanga thluaka abscess.
• Thluak-a thisen tam tawk lo (Cerebral vascular insufficiency).
• Gout tih hi a ni.
• Lung natna.
• Lung lam chak lohna.
• Lung natna, entirnan, endocarditis.
• Thisen a thim (Hyperviscosity syndrome) a ni.
• Kidney tha lo a awm.
• Naupai laiin harsatna (complication) (hei hi a hlauhawm hle).
• Thai.
• Thihna thut.

Heng harsatnate hi en hian he dinhmun hi a pawi zia i hmu thei ang, a dik em? Chuvang chuan hei hi kan ngaihven bik a ngai a ni.

Engtin nge Eisenmenger syndrome hi hmuhchhuah a nih?

Doctor chuan taksa enfiahnaah Eisenmenger syndrome chhinchhiahna a zawng tlangpui ang. Entirnan, i vun a sen em tih te, i kut zungtang te chu a club a ni em tih te, leh i thinlung ngaihthlak laiin thawm pangngai lo i hriat leh hriat loh te.

Tichuan, doctor chuan a natna hriat chian nan a hnuaia test pakhat emaw a aia tam emaw a ti thei ang:

• Thisen a oxygen level enfiah.
• Cardiac catheterization: Hei hi thinlung chhungah tube te tak te dahin pressure tehna leh a structure en a ni.
• Chest X-ray neih a ni.
• Thisen chhiar kim (CBC).
• Echocardiogram (Echocardiogram - echo): Hei hi thinlung ultrasound scan a ni. Thinlung pindan, valve leh thisen kal dan te a en thei a ni.
• Electrocardiogram (EKG/ECG): Hei hian thinlung electrical activity a test thin.
• Lung lam MRI test a ni.
• Pulmonary function testing neih a ni.

Heng test atanga information a hmuhte atang hian doctor chuan natna hi dik takin a hre thei a ni.

Eisenmenger syndrome hi engtin nge enkawl a nih?

Eisenmenger syndrome enkawlna tum ber chu symptoms control leh heart emaw lung emaw tihchhiat belh zel tur ven hi a ni.

A hnuaia mite hi enkawlna atan hman theih a ni:

• Antibiotics: Thinlung leh lungah bacteria infection a veng thei.
• Anticoagulants: Thisen kalna kawnga thisen zam (blood clots) siam a ti tlem.
• Diuretics (tui pills): Taksa chhunga tui tam lo awm zat tihtlem.
• Dual endothelin receptor antagonists: Hei hi damdawi chi khat, lung chhunga thisen sang tihziaawmna atana pek thin a ni.
• Iron supplement: Iron tlakchham vanga thisen tlakchhamna (anemia) enkawl.
• Supplemental oxygen: Thâwk a awlsam a, thisenah oxygen level a tisang bawk.

A pawimawh ber chu Eisenmenger syndrome a lo awm tawh chuan congenital heart defect chu surgery hmanga siamthat a tlai fo thin a, a chhan chu chutih lai chuan lung chhiatna chu a lo awm tawh a ni.

Mahse, mi thenkhat , symptom na tak tak leh taksa peng chhiatna nasa tak nei te chuan thinlung emaw, lung emaw thlak a ngai mai thei. Mahse chu pawh chu kalphung buaithlak tak leh risky tak a ni bawk.

Eisenmenger syndrome hi a veng thei ang em?

Ni e, Eisenmenger syndrome laka invenna awmchhun chu a hma thei ang bera, naupan lai atanga pianpui thinlung natna te hriatchhuah a, uluk taka enkawl a, a tul chuan operation tih hi a ni. Naupan lai atanga heng chhiatna te hi hriatchhuah a, enkawl a nih chuan Eisenmenger syndrome ang chi natna khirh tak hi ven theihna chance a sang hle.

Eisenmenger syndrome vei te dam rei zawng chu engzat nge ni?

Eisenmenger syndrome vei te hian mipui zawng zawng aiin an dam rei zawk thei. Hei hi a natna nena inzawm harsatna avang a ni. Mahse, mi thenkhat chu kum chanve (middle age) thlengin an nung thin. An dam rei theih hun chhung hi an natna lan chhuah dan nasat dan te, an pianpui thinlung natna awm dan te, enkawlna an dawn danah te a innghat a ni. Chuvang chuan Doctor thurawn zawm a, hriselna enkawl a pawimawh.

Eisenmenger syndrome ka neih chuan nau ka pai thei ang em?

Hei hi zawhna pawimawh tak a ni. Eisenmenger syndrome vei tan chuan naupai hi a hlauhawm hle. Lung chak lohna, thisen zam, thihna thut ang chi hlauhawm tak tak a thlen thei a ni. Hetiang dinhmun hi i nei a, naupai i ngaihtuah a nih chuan heng hlauhawmnate hi sawipui turin puitling pianpui heart conditions (`(specialist in adult congenital heart conditions)`) specialist i hmu ngei ang. Thurawn tha ber pe theitu tur che chu amah hi a ni ang.

Engtin nge Eisenmenger syndrome nei hian ka in enkawl theih ang?

Eisenmenger syndrome i neih chuan harsatna i neih theihna tur tihtlem nan thil engemaw zat i tih theih a awm. Heng step te hi zawm hian i dam chhung leh nunphung a tichangtlung thei ang.

Thil tih tur: 1.1.

• Sodium-controlled diet ei: Chi ei tam lutuk hian tui a tikhawlo thei a, thisen sang a tisang thei bawk.
• Vaccine dik tak la rawh: Pneumonia leh influenza ang chi natna laka inveng rawh.
• Tui tam tak in la, i taksa chu tui tlakchham tir suh (`(Staying hydrated)`) : Mahse i doctor-in a thurawn ang zat chauh.
• I cardiologist-in damdawi leh enkawlna dang a pek zawng zawng chu dik takin zawm rawh. Dose pakhat mah lo hmang lo la.
• Ha enkawl emaw, zai emaw hmain antibiotics ei hmasa phawt ang che: Hei hian thinlung natna a veng thei a ni. Hemi chungchang hi doctor zawt rawh.

Thil tih loh tur: 1.1.

• Tuipui atanga sang tak tak (`(High altitudes)`)-a kal loh tur: Hmun sang takah oxygen tlakchham vangin thawk harsatna a pung thei.
• Sauna, steam room, hot tub hman loh tur: Hengte hian thisen sang a ti tlahniam nghal thei a ni.
• Meizial zu leh zuk leh hmuam hman loh vek tur a ni.
• Exercise hahthlak tak tak pumpelh: I doctor-in a pawmpui level-ah chauh exercise light tak ti rawh.

Take-Home Thuchah a ni

Eisenmenger syndrome hi lungphun leh thinlung dinglam thisen kalna kawng hrang hrangah thisen sang a awm a, hei hi a ni. Congenital heart defects enkawl loh avanga lo awm a ni tlangpui. A lan chhuah dan hi tleirawl emaw, puitling tleirawl emaw atang hian a lang tan tlangpui. A lan chhuah dan chu vun sen (cyanosis), exercise laiin thawk hah, leh thinlung thawk mumal lo te a ni.

He natna enkawlna hian a natna lan chhuah dan tihziaawmna leh thinlung leh lung chhiatna tihtlem a tum ber a ni. He natna hi operation hmanga tihdam a tlai tawh hle. Chuvangin congenital heart defects te hi a hma thei ang bera hriatchhuah leh enkawl a tha ber.

Hemi chungchangah hian zawhna dang i neih chuan i doctor biak pawh hlau suh. An pui ang che.

` Eisenmenger syndrome, lung natna, pulmonary hypertension, cyanosis, pianpui thinlung natna, thawk harsatna, thinlung hriselna