I kut emaw, i ke emaw vun hnuaiah hian hnim hring, hring, emaw, natna emaw i nei nghal tawh em? Workout tha tak hnuah a thleng pawh a ni mai thei. Hetiang thil hi i tawng tawh em? Chuvangin, hetah hian i tan thil pawimawh tak ni thei tur dinhmun hriat tlemte chu a awm.
Eosinophilic Fasciitis hi eng nge ni?
A awlsam zawngin sawi ila, Eosinophilic Fasciitis hi kan vun hnuaia kan taksa ruh leh tissue te khuh tu tissue – damdawi lam atanga kan sawi chuan fascia kan tih – chu rang takin a inflamed a, a thicked a, a tight ta a ni. Kan vun leh ruhte inzawmkhawmtu leh an kal kualna tura puitu mesh ang maiin han ngaihtuah teh, kan car trunk-a kan dah mesh ang bawkin, thil lei tur kan kal dawn a ni.
Hei hi `autoimmune disease` tiin an dah a ni. Chumi awmzia chu kan taksa defence system, immune system hian tihsual takin kan taksa peng hrisel tak takte chu a rawn bei tan tihna a ni. Kan chhungte ngei pawhin rukbo an nih nia an inhriat laia kan beih ang mai a ni.
A hmaa hmuhchhuah leh enkawl loh chuan vun a tidanglam reng thei a, joint range of motion a hloh thei bawk . Chuvang chuan natna lanchhuahna a lan veleh damdawi lam pan vat a pawimawh hle.
Engtin nge he dinhmun hian nghawng a neih ber? Tute nge a nghawng?
Eosinophilic Fasciitis hian taksa khawi hmunah pawh fascia a nghawng thei a, mahse kut leh ke a nghawng tam ber . Mi tam tak tân chuan, natna lan chhuahna, natna emaw, hring emaw ang chi chu exercise nasa tak emaw, nilenga ding ngai hna emaw hnuah a lang hmasa thei a ni.
Heng symptoms, muscle na leh swelling te hi natna tlanglawn dang nen a inang thei a, chuvangin i vun, taksa ruh leh ruh ah danglamna thar emaw, natna emaw i hmuh chuan doctor pan nghal a pawimawh hle . Rheumatologist, ruh leh ruh natna dang lama tui tak doctor pan a ngai mai thei bawk.
Tunah hian he natna hi damdawi a la awm lo . Mahse, thu lawmawm tak chu mi tam zawk tan chuan kum tlemte chhungin natna lanchhuahna chu a reh a, chu chu natna chu `remission`, a nih loh leh dormant state-ah a kal tihna a ni. Mahse, mi thenkhat chuan symptoms a lo lang leh thei a ni.
Eosinophilic Fasciitis leh Scleroderma te hi an danglamna
Heng natna pahnih chungchang kan sawi hian mi thenkhat chuan natna dang `Scleroderma` tih nen an buaipui thei a ni. `Eosinophilic Fasciitis` leh `Scleroderma` te hi `autoimmune` natna hmuh tur awm lo tak tak an ni. Tin, heng natna pahnihah hian taksa tissue te chu a thim a, a nghet lo hle bawk.
Chuti a nih chuan eng nge a danglamna? A danglamna chu tissue chi hrang hrang a nghawng danah a awm a ni.
- Eosinophilic Fasciitis-ah hian kan sawi tawh ang khan vun hnuaia connective tissue te tak te, elastic tak fascia hi a nghawng a ni. Hun a kal zel a, he fascia hi a thim a, a zau chho zel a, chu chuan taksa peng natna hmun chu a tiharh harsa hle.
- Mahse `Scleroderma`-ah chuan immune system hian cell dangte chu a tichak a, chu chu protein `collagen` (kan vun leh tissue-te chakna pe thei thil) an siam tam zawk a ni. He collagen tam lutuk hi vun leh chhungril peng hrang hrangah a awm a, chu chuan a thim a, a khauh a, hliam hlui ang maiin a siam a ni. Mahse hliam tidam ai chuan he collagen tam lutuk hian tissue hrisel a tichhe thei bawk.
Eosinophilic Fasciitis leh COVID-19 natna vei te a ni
Eosinophilic Fasciitis ang chi autoimmune natna vei te chu mipui zahawm tak aiin COVID-19 kai theihna chance sang deuhah ngaih an ni.
Hetiang natna vei te hian COVID-19 natna lanchhuahna na tak an nei tam zawk em tih chu mithiamte chuan an la chiang lo. Chuvang chuan hri kai laka inven nan hriselna lama thuneitute, Centres for Disease Control and Prevention (CDC) te rawtna zawm a tha ber.
He natna hi tuin nge vei tam ber?
Eosinophilic Fasciitis hian tu pawh a vei thei a, mahse kum 30 leh 60 inkar mi a vei tam ber.
Tin, hriselna lama harsatna rei tak nei thenkhatte chuan he natna hi an vei tam zawk bawk. Chung dinhmun thenkhat chu:
- Aplastic anemia (aplastic anemia - thisen cell siam chhuah tlem zawkna thisen tlakchhamna) .
- Hemolytic anemia (thisen thisen zam (red blood cells) a chhe nghal vat thin thisen tlakchhamna) .
- Lymphoma (lymphatic system-a cancer) 1. A rilru a hah lutuk chuan a rilru a buai em em a.
- Leukemia (thisen cancer) 1.1.
- `Thyroid natna` chi thenkhat
Hei hi engtiang chiahin nge a hluar?
Eosinophilic Fasciitis hi a takah chuan natna hmuh tur awm lo tak a ni . Tun thleng hian khawvel puma scientific journal-ah hian case tlemte chauh, 300 vel chauh report a la ni. Mahse, underdiagnosis emaw underreporting emaw vang pawh a ni mai thei, case hi a tam zawk hle mai thei.
Engtin nge Eosinophilic Fasciitis hian ka taksa a nghawng?
Kan sawi tawh ang khan he natna hi vun hnuaia connective tissue te tak te, flexible tak fascia inflammation vang a ni. He fascia layer hian kan taksa ruh leh chhungril taksa peng thenkhat a khuh a, a humhim bawk. Tin, vun leh ruh te chu a hmunah a vawng tlat a, an che vel pawhin a thlawp bawk.
Ngaihtuah teh, he fascia hian kan taksa peng hrang hrangte chu a inthlak danglam theih nan a pui a, mahse a hnuai lama innghat mai mai a ni lo. Mahse `Eosinophilic Fasciitis` vei tan chuan he fascia membrane hi a inflamed a, zawi zawiin a thick a, a stiffen ta a ni. A tawpah chuan he inflammation hian a chhehvela vun leh taksa ruhte chu a ti che a harsa thin. Enkawl loh chuan he fascia hi hmun khatah a innghat thei a, a tight thei bawk. Hei hi `contracture` an ti \hin. Chu chu, ruh (joint) chu a zau thei lo va, a ben thei lo tihna a ni.
Fascia elasticity pangngai ai chuan taksa peng hrang hrangte chu a na emaw, a che harsa emaw a ni.
Taksa peng hrang hrang a nghawng tam ber chu:
- Kut (a bik takin kutphah, chu chu kut chhung lam) .
- Ke (a bik takin hmalam, hip ruh bulah chiah) .
- Joints emaw a chhehvel emaw
A tlem hle nachungin, he natna hian hmai, rilru leh pum vun a nghawng thei bawk.
Eosinophilic Fasciitis vei thenkhat pawhin Rheumatoid Arthritis ang chi joint inflammation an nei thei bawk. He ruh inflammation hi control a nih loh chuan ruh chhunga cartilage chu a chhe thei a, hun rei tak chhung arthritis a thlen thei a ni.
Tin, he natna hian i kut emaw, i kutphah emaw fascia a nghawng a nih chuan, chu inflammation chuan kut chhunga nerve lian ber pakhat, median nerve chu a ti compress thei a, Carpal Tunnel Syndrome (kut natna, na leh chak lohna) an tih natna a thlen thei bawk.
A pawimawh ber chu Eosinophilic Fasciitis hi a danglam thei a, a lo thang chak hle bawk. Hun rei lote chhungin hmuh theiha nghawng i hmu tan thei a, kar tlemte ang bawkin. Chuvangin, i taksaah symptom emaw, inthlak danglamna emaw i hmuh chuan doctor pan nghal rawh.
Eosinophilic Fasciitis natna lan chhuah dan chu engte nge ni?
Chuti a nih chuan, engtin nge he natna hi i rinhlelh ang? A lan chhuah dan tlangpui thenkhat chu hetiang hi a ni:
- Muscle na a awm .
- Vun nêm tak .
- Inflammation emaw swelling emaw a awm thei .
- `Carpal Tunnel Syndrome` chhinchhiahna (kut na, na, chak lohna ang chi).
- Arthritis (arthritis - ruh natna, ruh na, zing khawvar).
- Vun hi a tlangpui aia thim leh tight zawkin a lang.
- Hmun thenkhatah chuan vun chu a hring hring leh a hring hring ang maiin a lang a, chu chu orange (`puckered skin` emaw "peau d'orange" appearance) peel ang mai a ni .
Hei hi eng nge a chhan?
Dik tak chuan mithiamte chuan Eosinophilic Fasciitis thlen chhan dik tak hi an la hre lo. Autoimmune natna tam tak ang bawkin, a lo thleng nghal thei a, a châng chuan chhan hriat lohvin a lo thleng thei bawk.
Mahse, zirchianna thenkhatah chuan heng autoimmune natna te hi thil engemaw avanga ``triggered`` theih a ni tih hmuhchhuah a ni. Chu chu natna hi thil dang vangin a lo awm thei tihna a ni. Entir nan:
- Infection chi hrang hrang .
- Allergic reaction thenkhat.
- Damdawi thenkhat hman .
- Damdawi thenkhat hman .
Eosinophilic Fasciitis vei ṭhenkhat chuan an natna lan chhuah hmasak ber chu taksa tihchakna nasa tak , tlan, rit phurh, emaw, exercise lak emaw, emaw, an kut emaw, an ke emawa taksa thawhrimna nasa tak mamawh hna an thawh lai emaw a nih thu an sawi.
Hetiang autoimmune disease vei theihna tur risk factors te hi doctor nen inbiakna neihpui a tha.
He natna hi Doctor ten engtin nge an hriat chian? (Diagnosis) tih a ni.
Heng symptoms te hi i neih chuan doctor chuan Eosinophilic Fasciitis i vei em tih hriat nan test eng emaw zat a ti thei ang:
1. Fascia Biopsy: Biopsy chu i doctor-in i tissue sample te tak te a la a, microscope hmanga en turin lab-ah a thawn a. Hei hian vun natna leh a hnuaia fascia te chu la chhuakin enfiah a ngai a ni. A tam zawkah chuan hei hi natna hriat dan rintlak ber a ni.
2. Thisen test: Eosinophilic Fasciitis i vei chuan i thisenah thisen var chi khat Eosinophils an tih (chu chu natna hming puanna hmun a ni) a tam thei. Amaherawhchu, thisen test ringawt pawh hian natna hi a finfiah thei lo. Vawi tam tak chu biopsy lak a ngai thin.
3. Imaging test: MRI (Magnetic Resonance Imaging) ang chi test hian taksa chhunga inflammation awmte hriatchhuah nan a pui thei a, a bik takin fascia leh a chhehvel tissue-ah inflammation a awm tih hriat theih a ni. Mahse, thisen test ang bawkin natna hriat theihna tur biopsy angin a chiang lo.
Eosinophilic Fasciitis natna enkawl dan
A tlem hle a, enkawlna engmah awm lovin a natna lan chhuahna chu a mah chauhin a bo thei. Mahse a tam zawkah chuan doctor-te chuan Eosinophilic Fasciitis hi damdawi chi khat corticosteroids an tih hmangin an enkawl thin. Hengte hi steroid chi khat a ni.
Corticosteroids hian taksaa inflammation tihziaawmna leh overactive immune system tihtawp nan hna a thawk a ni. Prednisone hi corticosteroid an pek tam ber a ni.
Corticosteroid bakah hian i doctor chuan enkawlna dang a pe thei bawk a, chungte chu:
- `NSAIDs`: Damdawi dawr-a non-steroidal anti-inflammatory drugs (NSAIDs) – entirnan, ibuprofen leh diclofenac – te hian natna leh hliam ang chi symptoms te chu a tiziaawm thei a ni. Mahse, `corticosteroids` i ei tawh a nih chuan `NSAIDs` i ei hmain doctor nen inbia ang che. Doctor remtihna lo chuan `NSAIDs` hi vawi khatah ni 10 aia tam ei loh tur a ni.
- Immune system titawptu damdawi: I natna nasat dan azirin i doctor chuan Eosinophilic Fasciitis thlentu overactive immune system titawp thei damdawi dang (e.g., Methotrexate) a pe thei bawk.
- Physical therapy: Physical therapy hian i fascia a tight laiin a tizau thei a, a tizau thei bawk a, joint mobility pawh a vawng reng thei bawk. I doctor emaw physical therapist emaw chuan i symptoms nena inmil exercise leh stretch te a zirtir ang che.
- Thil dang enkawl dan: Thil dang, carpal tunnel syndrome emaw, arthritis emaw ang chi natna lan chhuah dan enkawl hian i hlim zawk thei.
- Surgery: I Eosinophilic Fasciitis hi a na lutuk a, contracture a thlen thei a nih chuan i fascia (fascial release) thenkhat chhuah emaw lakchhuah emaw nan operation i neih a ngai mai thei. Hei hi a tawp ber a ni fo thin.
Engtin nge symptoms te hi kan enkawl ang?
- Damdawi hi doctor-in a sawi ang chiah chiah, a pek hun chhung atan ei a pawimawh hle .
- I doctor emaw physical therapist emaw chuan stretch emaw exercise dang emaw a pek che chuan, fascia natna chu stretch-na tura pui turin an hrilh che vawi tam tak ti rawh. Hei hi harsa viau mah se, i tih chhunzawm zel chuan a hlawkpui thei a ni.
- Carpal Tunnel Syndrome i neih chuan i mut laiin i kutphah a awm reng theih nan brace i bun a ngai mai thei. Doctor-in a tih angin hmang rawh.
Engtiang chiahin nge enkawl hnuah ka dam leh thuai ang?
Corticosteroids dose hmasa ber ei atanga darkar tlemte chhungin Eosinophilic Fasciitis avanga inflammation chu a reh tan tur a ni. He hahdamna hi hun eng emaw chen atan a ni thei a, damdawi a reh deuh deuh chuan natna lan chhuahna a lo lang leh thei bawk. Damdawi hi doctor-in a pek hun chhung zawng zawng ei a pawimawh.
Eosinophilic Fasciitis hi ven theih a ni em?
Vanduaithlak takin he natna laka inven dan tur bik a awm lo. Mithiamte chuan autoimmune natna thlentu leh engtin nge a lo awm tih chiang takin an hre lo a, chuvangin engtikah nge i vei dawn tih leh engvangin nge i vei dawn tih an sawi thei lo.
He natna vei hian eng nge a beisei ang?
Eosinophilic Fasciitis i vei tih hmuhchhuah a nih chuan hun engemaw chen chu i symptoms te hi i enkawl theih beisei tur a ni. I natna lan chhuahnaah danglamna i hmuh chuan, a bik takin a na zual a nih chuan i doctor nen inbia nghal rawh.
Kan sawi tawh ang khan hei hi damdawi a awm lo. Mi tam tak chu kum engemaw zat an khawsa a, chutah chuan a natna lan chhuah dan chu a bo vek (`remission` ah kal rawh). Mi thenkhat chuan an nei leh tawh ngai lo va, thenkhat erawh chuan a hnuah symptoms an nei leh thei (`recur`).
Hnathawh emaw, sikul emaw i kal thei lo ang em?
I fascia natna kha tibuai lutuk lovin i hna emaw, sikul hna emaw i thawk thei a nih chuan Eosinophilic Fasciitis atanga i dam leh hma loh chuan hna emaw sikul emaw i kal leh thei tur a ni. Mahse, i doctor chuan i dam hma chuan eng thiltih nge i pumpelh tur tih a hrilh ang che. Heng thupekte hi zawm a pawimawh hle.
Run, rit phurh, exercise tih ang chi taksa tihchakna hahthlak tak tak i thawh leh hmain i doctor nen inbiakna neih hmasak phawt la, phalna la hmasa phawt ang che.
Engtikah nge doctor i hmuh ang?
- I kut, ke, ruhkawr-ah natna lan chhuah thar i hmuh chuan – a bik takin ni engemaw zat chawlh hnua i natna emaw, a hring emaw i neih chuan – doctor pan nghal rawh.
- Eosinophilic Fasciitis i vei tih hmuhchhuah tawh i nih chuan i natna lan chhuah dan a zual a nih chuan, emaw, i taksa peng eng emaw zat a nghet emaw, a hring emaw a nih i hriat chuan doctor hnenah hrilh nghal rawh .
Engtikah nge Emergency Treatment Unit (ETU) ah i kal ang ?
I taksa peng pakhat i che thei lo va, i hmang thei lo va, emaw, tuar theih loh khawpa natna i neih chuan, emergency room hnai ber pan nghal rawh .
Doctor hnenah eng zawhna nge i zawh tur?
Doctor hmu tura i kal hian hetiang zawhna hi i zawt thei ang:
- Eosinophilic Fasciitis ka nei em, a nih loh leh thil dang a ni em?
- Engtiang chiahin nge ka symptoms te hi a na zual theih ang?
- Eng ang enkawlna nge ka mamawh? Eng chen nge enkawlna ka mamawh ang?
- Surgery ka mamawh dawn em?
- Engtikah nge taksa tihchakna pangngai ka thawh leh theih ang?
- He dinhmun hian engtin nge ka nitin nun a nghawng?
He thawnthu atanga kan hriat reng tur pawimawh tak tak thenkhat chu
Eosinophilic fasciitis hi natna awm lo mahse na tak a ni a, a nghawng nghal vat thei che a ni. I kut emaw ke emaw-ah natna thar, hring, emaw, tightness thar i hmuh chuan, a bik takin ni rei lote chhunga a reh loh chuan doctor pan chu tihkhawtlai suh. Since this condition can develop very quickly , i symptoms i check hma poh leh i doctor chuan a chhan a hmu thuai thei a, a tul anga enkawlna a tan thei bawk.
I doctor chuan i natna lan chhuah dan control turin a tul chuan corticosteroid leh enkawlna dang a dah belh ang. Hlauthawng suh la, i natna lan chhuah dan fimkhur la, i doctor thupek chu uluk takin zawm rawh. Dam leh thuai turin duhsakna kan hlan e!
` Eosinophilic Fasciitis, Eosinophilic Fasciitis, Vun natna, Fascia, Joint Pain, Muscle Natna, Autoimmune Diseases











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