I taksa hmun hrang hrangah lump mak tak tak i nei em? Ha i chhuah dawna i neih tur aia tam ha i nei mai thei em? Chûngte chu thil pangngai angin lang mah se, a châng chuan a hnung lamah thawnthu pawi tak a awm thei a ni. Vawiin hian hetiang damdawi lama harsatna awm lo, mahse pawimawh tak, mi zawng zawngin kan hriat tur kan sawi a ni. Chu chu Gardner Syndrome a ni.
Gardner Syndrome hi eng nge ni, a awlsam zawngin?
A awlsam zawngin, hei hi kan nu leh pate hnen atanga genes hmanga kan hmuh theih thil awm lo tak a ni. Natna rochun a ni. He natna vei hian an taksa hmun hrang hrangah tumor pangngai lo a nei tan thin.
Thil thleng chu colon chhungah hian thinghnah tenau za tam tak a lo piang chhuak thin. Heng a lo thang lian te hi damdawi lam chuan polyps an ti a . Thil hlauhawm ber chu enkawl loh chuan heng polyp zawng zawng hi colon cancer-ah an chan theihna a sang hle a ni .
Colon bakah hian cancer ni lo tumor hi ruh, intestine, vun leh soft tissue dangteah pawh a lo awm thei bawk. He natna vei te hi cancer chi dang engemaw zat vei theihna an nei bawk.
Hetiang dinhmun hi engtiang chiahin nge a awm? Tuin nge dawng?
Hei hi a takah chuan thil awm lo tak a ni. Entirnan, America ang ramah hian mi maktaduai khat zinga pakhat chauh he natna hi an vei tih hmuhchhuah a ni.
Natna thlahtu a nih avangin Gardner syndrome vei tam tak chuan he natna vei nu emaw pa emaw an neih theihna chance a sang zawk a ni. Chumi awmzia chu genes kaltlangin thlah khat atanga thlah dangah a kal zel tihna a ni.
Hei hi eng symptoms nge ni?
Gardner syndrome symptoms hi hun kal zelah a danglam thin. Naupan laiah symptom thenkhat a lang thei.
| Symptoms lo awm tan hun | Hmuh theih thil chi hrang hrang |
|---|---|
| Naupan lai chuan |
|
| Thalai hunah chuan | Colon polyp za tam tak a awm a. Mahse, hengte hian a tir lamah chuan symptoms an nei lo mai thei. A lan chhuah hun chuan natna hi a lo zual tawh hle mai thei. |
A pawimawh ber chu colon polyp symptoms a lan chhuah hunah chuan natna hi a lo zual tawh hle mai thei. Chuvangin i chhungkuaa mi tu emaw hian hetiang dinhmun hi a nei a nih chuan test hmasak phawt a pawimawh hle.
Gardner syndrome nen hian eng dinhmun dang nge inzawm?
Gardner syndrome vei chuan a hnuaia natnate hi a vei theihna a sang zawk a ni.
- Ha dang a awm
- Osteomas (ruh natna) 1.1.
- Desmoid tumors - Hengte hi cancer ni lo mahse, a thang chak hle a, a chhehvel tissue a tichhe thei bawk.
- Thau natna (Lipomas) 1.1.
- Fibromas (fibromas) te
- Adenomas - Cancer ni lo tumor, glands-a lo awm.
- Epithelial cyst a awm thin
- Mit mit (retina) tichhe thei dinhmun (CHRPE - congenital hypertrophy of retinal pigment epithelium) .
- Pum cancer a ni
- Liver cancer a ni
- Colon cancer a ni
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
A chhan chu kan gene pakhata chhiatna vang a ni. A dik tak chuan APC gene tih gene a awm a. A hna ber chu kan taksa chhunga cell awmte inthen darh leh pung chak lutuk lo tura thunun hi a ni. Car brake ang bawkin. Hetiang gene hi tumor suppressor genes an ti a, chu chu tumor lo awm tur a veng tihna a ni.
Gardner syndrome vei chuan APC gene chhia a nei a. Chumi awmzia chu cell inthenna control tu brake hian hna a thawk lo tihna a ni. Chumi avang chuan cell te chu thunun theih lohvin an inthen a, tumor leh polyp an siam tan thin.
He natna hi engtin nge doctor hian a hriat theih ang?
He natna hian symptom hrang hrang a neih avangin doctor pakhatin test eng emaw zat hmangin a hriat theih nan a hmang thin.
- Genetic tests: He test hi i APC gene-ah chhiatna i neih leh neih loh enfiah nan tih a ni. I doctor chuan hei hi a rawt mai thei a, a bik takin i chhungte zinga mi tu emaw chuan he natna hi a vei a nih chuan.
- Camera test: Hengte hi taksa chhungah camera te tak te dahin intestine chhung lam enfiah a ni.
- Sigmoidoscopy hmanga enfiah a ni
- Endoscopy hmanga enfiah a ni
- Colonoscopy - Hei hi colon chhunga polyp awmte chiang taka hriat theihna a ni.
Hei hi eng enkawlna nge ni?
Enkawlna chu i natna lan chhuah danah a innghat.
Ha extra i nei tih han ngaihtuah teh. Chu chu he natna chhinchhiahna hmasa ber a ni thei. Tichuan, chu ha chu dentist hnenah la chhuakin i ha dang zawng zawng chu a siam tha tur a ni. Desmoid tumor i neih chuan a tihtlem nan chemotherapy ang chi enkawlna i dawng thei bawk.
Mahse, he natna chungchanga harsatna lian ber leh hlauhawm ber chu colon-a polyp lo awm hi a ni. Hengte hi cancer-a a chan loh nan surgery neih a ngai a ni.
| Surgery neihna hmun hming | Eng nge tih a nih |
|---|---|
| Colectomy tih a ni | Colon thenkhat emaw, a pum emaw lakchhuah. He surgery hi polyp 20-30 vel a awm chuan tih a tha tlangpui. |
| Proctocolectomy tih a ni | Colon leh rectum tam zawk lakchhuah. |
He surgery hi colon-a polyp lo awm a, cancer-a a chan lohna tur kawng awmchhun a ni tih hre reng ang che.
He natna hi a dam kim thei ang em?
Vanduaithlak takin Gardner syndrome hi a dam kim thei lo.
Mahse, hei hi uluk taka enkawl theih a ni. Enkawlna dik leh check-up neih reng a nih chuan cancer ang chi natna khirh tak takte chu hriatchhuah leh enkawl hmasak theih a ni. Chuvangin hlauhthawn a ngai lo.
He natna nen hian nun pangngaia nun theih a ni em?
Ni e, i ti thei. Mahse, operation hnuah i nunphungah inthlak danglamna engemaw zat a awm thei. Entirnan, i colon lakchhuah a nih chuan ei tur i ei dan leh i bawlhhlawh i pass dan a tidanglam ang. Tin, kawngpui hran i neih a ngai thei bawk a, i pum chhungah ostomy bag dah a ngai thei bawk a, chu chuan bawlhhlawh a paltlang thei ang. I doctor chuan hei hi chipchiar takin a hrilhfiah ang che.
He natna avanga colon cancer lo awm tur venna atana surgery neih hian dam rei theihna a ti rei thei a ni. Zirchianna pakhatah chuan proctocolectomy nei zinga 100% chu kum 5 hnuah pawh an la dam tih hmuhchhuah a ni.
Engtin nge i in enkawl ang?
Gardner syndrome neia nun tih awmzia chu kum naupang tak atanga cancer vei theihna hlauhawma nun tihna a ni. A awlsam lo. Chu rinhlelhna hmachhawn chu rilru lamah a harsa thei hle.
Chuvangin, a hun takah cancer screening test neih a pawimawh hle. Chumi awmzia chu cancer a lo awm chuan a tir lamah hriatchhuah leh enkawl theih a ni tihna a ni.
Hemi avanga stress i neih chuan i doctor nen sawiho rawh. A tul chuan counseling service zawng rawh.
Engtikah nge Doctor ka hmuh ang?
I taksaa inthlak danglamna thar i hmuh chuan, entirnan, lump thar, emaw, i rilru a inthlak danglam emaw, a bik takin i bawlhhlawh chhunga thisen i hmuh chuan , doctor pan nghal rawh.
I doctor hnenah eng zawhna nge i zawh tur?
Doctor i hmuh hunah heng zawhnate hi zawh loh theihnghilh suh.
- Tuna ka symptoms te enkawlna tur engte nge ni?
- Surgery ka mamawh dawn em?
- Eng test nge ka neih ang? Eng chen nge ka neih ang?
- Ka taksaa inthlâk danglamna engte nge ka ngaihven bîk tûr?
- Ka chhungkaw dangte tan chuan genetic testing neih hi thil tha tak a ni em?
Gardner syndrome hi hlauh tur a ni lo a, mahse fimkhur leh enkawl dan dik taka hmachhawn tur a ni. Damdawi lam thurawn dik tak leh test neih chuan hrisel tak, dam rei tak i nung thei a ni.
Take-Home Thuchah a ni
- Gardner syndrome hi nu leh pa atanga lo chhuak, genetic condition hmuh tur awm lo tak a ni.
- Hetah hian hlauhawm ber chu colon-a polyp lo awm zawng zawng deuhthaw chu cancer-ah a chang vek a ni.
- Hei hi a lan hmasak ber chu naupan laia ha dang lo lang emaw, taksaa cancer ni lo tumor lo awm emaw a ni thei.
- Hei hi tihdam kim theih ni lo mah se, damdawi lam check-up leh surgery neih fo pawhin a enkawl tha hle.
- Nangmah emaw, i chhungte zinga tu emaw hian heng symptoms hi i neih chuan doctor lam pan vat a pawimawh. I taksa leh rilru hriselna chungchangah i doctor nen zalen takin sawi rawh.











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