I taksaah lump mak tak mai a awm em? Hamartoma a ni mai thei! I sawi dawn nia - Nirogi Lanka

I taksaah lump mak tak mai a awm em? Hamartoma a ni mai thei! I sawi dawn nia - Nirogi Lanka

Physician Reviewed — Not Medical Advice

I taksaah hian lump emaw bump te tak te i nei a, "Hei hi eng nge ni?" A nih loh leh doctor pakhatin "Hamartoma" tih thumal a sawi a, buai takin i awm ta mai thei em? Hamartoma chu eng nge ni tak tak? Hetah hian Nirogi Lanka-ah hian thumal awlsam tak, hriatthiam awlsam tak hmangin han then ila.

Hamartoma tih hi eng nge ni? I Keep It Simple Tak Tawh Rawh!

Chuti a nih chuan, hamartoma chu eng nge ni tak tak? A awlsam zawngin sawi ila, cancer nei lo (benign) growth a ni. Chu chu i taksa peng pakhata awm tlangpui cell ang chiah atanga siam a ni. Mahse, a danglamna tlem a awm: heng cell te hi a inrual lo emaw, a mumal lo emaw a inrem a ni. Infiamna inang chiah chiah pile la a, uluk taka buatsaih ai chuan heap-a paih ang mai a ni.

"Hamartoma" tih thumal hi Greek tawng pahnih atanga lo chhuak a ni a, chungte chu: "hamartia," tih awmzia chu "a dik lohna" emaw "defect" emaw tihna a ni a, "oma," tih awmzia chu "tumor" tihna a ni. A bul berah chuan structural irregularity avanga lo piang chhuak growth a kawk a ni.

Hriat tur pawimawh ber chu hamartomas hi cancer a ni LO tih hi a ni . Cancer cells ang lo takin i taksa pum puiah an darh lo. Chuvangin, hlauhthawn a ngai lo. Mahse, an awmna hmun azirin a chang chuan thil tenawm tak tak an siam thei a ni.

Khawiah nge taksaah Hamartoma a lo awm theih ang?

Hamartomas hi theoretically chuan taksa hmun tinah te pawh a lang thei a, mahse hmun tlangpui tlemte a awm a:

  • Lungs : Hamartomas hi lungah hmuh tur a awm fo. Dik tak chuan lung tumor tha lo zawng zawng zinga 10% vel an ni. Vawi tam tak chu chhan dang vangin rilru X-ray tih dan pangngaiah accident-in an hmuchhuak thin.
  • Vun: Cutaneous hamartomas hi lu, kawr leh a bik takin hmai, hmui emaw beng emaw ah hmuh tur a awm fo thin. A châng chuan, pianpui chhinchhiahna ang maiin an lang mai thei.
  • Thinlung : Hengte hi thinlungah pawh a lo piang thei bawk. "Cardiac rhabdomyoma" hi heart hamartoma chi khat hmuh tur awm lo tak a ni. Chungte chu naute pum chhunga a la awm lai ( naupai lai ) emaw, a pian hnu rei vak loah emaw hmuhchhuah a ni fo thin. A tlem hle laiin, nausen thinlung natna (heart tumor) awm tam ber zinga mi an ni.
  • Thluak: "Hypothalamic hamartomas" tia hriat chi khat chu hypothalamus-ah a awm a, chu chu taksa kalphung pawimawh tak takte inthlauhna siamtu hmun a ni. Chûngte chu pian tirh aṭanga awm thei mah se, naupan lai emaw, tleirawl lai emawa chhinchhiahna an lantîr fo ṭhîn a, chu chu seizures , mit hmuhna lama harsatna , a nih loh leh precocious puberty te hi a ni.
  • Breast: Hmeichhiaah chuan benign breast lumps 5% vel chu hamartomas a ni thei. Hmeichhia kum 35 chunglam zingah an lang tam ber.

Tin, PTEN hamartoma tumor syndrome (PHTS) ang chi genetic condition thenkhat nena inzawm, heng growth te hi kidney, spleen, thyroid gland leh ruh ah te pawh a lang thei bawk.

Hamartomas hi taksa pum puiah a darh em?

Hei hi ngaihtuahna tlanglawn tak a ni. Ni lo, hamartomas hi cancer ang a ni lo; an darh lo. An siamna hmunah chiah an awm reng a ni. Mahse, a lo thang lian tawk a nih chuan a bula tissue hrisel emaw, taksa peng emaw chu a compress thei a, chu chuan harsatna a thlen thei a ni. Mahse, hei hi a tlem hle.

Hamartomas nena inzawm natna dang a awm em?

Ni e, hamartomas hi genetic syndrome hmuh tur awm lo thenkhat nen a inzawm thei a, chutah chuan genetic mutation chuan an lo piang ta a ni.

  • Pallister-Hall syndrome (PHS): GLI3 gene-a mutations nena inzawm a ni. Hypothalamic hamartomas vei zinga 5% vel chuan he syndrome hi an nei thei a ni.
  • Tuberous sclerosis: He natna hian thluak, thinlung, kal, vun leh mit ah hamartomas a siam thei a ni.
  • Neurofibromatosis Type 1 (NF1) : Genetic condition hmuh tur awm lo tak, taksa pum puia nerve-ah hamartomas a lo awm thei.
  • PTEN hamartoma tumor syndrome (PHTS): Cowden syndrome leh Bannayan-Riley-Ruvalcaba syndrome (BRRS) te bakah natna chi khat, hnute, nausen pum, thyroid, GI tract leh vunah hamartomas a lo awm thei a ni.
  • Peutz-Jeghers syndrome (PJS): STK11/LKB1 gene mutation nena inzawm hian PJS vei mimalte hian lung, pum, bladder, small intestine, colon, leh rectum-ah hamartomas vei an tam zawk.

Chutiang genetic condition i neih chuan i doctor chuan genetic test emaw counseling emaw a rawt thei ang.

Hamartoma natna lan chhuah dan chu engte nge ni?

A tam zawkah chuan hamartomas hi asymptomatic , chu chu engmah hrehawmna nei ngai lovin i nei thei tihna a ni. Symptoms a awm chuan a tlangpuiin a thanna chu a lian tawk a, a kianga tissue te chu a press thei a ni. A natna lan chhuah dan chu hamartoma awmna hmunah a innghat vek a ni.

Entirnan, lung hamartoma hian a lian chuan khuh reng emaw, thawk hah emaw a thlen thei. Brain hamartoma hian seizures emaw, mitdelna emaw a thlen thei.

Eng thilin nge Hamartoma a thlen?

Scientist te hian hamartoma zawng zawng hi a chhan dik tak an hre vek lo. Mahse, kan sawi tawh ang khan, an genetic condition nen an inzawm fo a, chu chu nu leh pate hnen atanga rochun, genetic mutation bik avang a ni thei.

Hamartoma hian harsatna a thlen thei em?

Hamartoma tam zawk hi chu a hlauhawm lo. Mahse, taksa peng pawimawh tak hnathawh tibuai thei khawpa lian an lo lian chuan harsatna a awm thei a ni. Entirnan, cardiac rhabdomyoma hian thinlung hnathawh a tichhe thei a, chu chuan thinlung a tichhe thei a ni. Chutiang bawkin hypothalamic hamartoma hian hormone balance emaw cognitive function emaw a tibuai thei bawk. Khawngaihin i doctor chuan heng a lo thang lian te hi a enfiah thei a, a tul chuan a paih thei tih hi hre reng ang che.

Engtin nge Hamartomas hi an hriat theih?

Hamartoma tam zawk hi asymptomatic an nih avangin thil dang atana scan an tih laiin accident-in an hmuchhuak fo thin. Hamartoma leh cancer tumor thliar hran chu a awmna hmun a zirin a harsa thei fo. I doctor chuan taksa a enfiah ang a, i medical history a enfiah ang. Vawi tam tak chu, a lo thang lian chu hamartoma a ni tak zet tih finfiah nan diagnostic imaging emaw test dang emaw neih belh a ngai dawn a ni. I ngaihtuah ngai a nih chuan damdawi lam thurawn la nghal la, a nih loh leh natna lan chhuah thut, na tak i neih chuan emergency service-te biak rawh.

Eng diagnostic test nge hman thin?

  • X-ray: I ruh leh soft tissue te thlalak siam nan low-dose radiation a hmang thin. Lung hamartomas hi X-ray-ah hian "popcorn" pattern angin a lang fo a, hei hian doctor-te chu cancer tumor atanga thliar hrang turin a pui thin.
  • Ultrasound: Sound wave hmangin i taksa chhunga tissue nem tak takte thlalak a siam chhuak thin.
  • CT scan (Computed tomography): X-ray beam tam tak hmangin i chhungril soft tissue leh ruh te cross-sectional image a pe thin. CT scan hi lung hamartomas hriat theihna atan a tangkai hle.
  • MRI (Magnetic resonance imaging): Magnet chak tak leh radio wave hmangin i taksa soft tissue te chipchiar tak, high-resolution image a siam thin.
  • Mammogram: Hnute tissue enfiah nan low-dose radiation a hmang thin. Breast hamartomas tam tak hi cancer screening mammogram tih dan pangngaiah hmuh chhuah a ni mai.
  • Biopsy atanga lak chhuah:Doctor chuan a thanna sample te tak te chu a la chhuak a, laboratory-ah a thawn ta a ni. Chumi hnuah pathologist chuan microscope hmangin cell te chu a enfiah leh thin. He biopsy hi a thang lian chu hamartoma ang chi benign cell atanga siam a nih leh nih loh leh malignant a nih leh nih loh hriat theihna tur definitive method a ni. Hei hi diagnosis atana gold standard a ni.

Hamartomas hi engtin nge enkawl an nih?

I enkawl dan tur chu hamartoma awmna hmun leh a natna lanchhuahna a thlen leh neih loh a zirin a ni.

  • Symptomatic a nih chuan: A lo thang lian hian harsatna emaw, symptom emaw a thlen lo a nih chuan i doctor chuan a enfiah mai mai thei. Hei hian a size emaw, a lan dan emaw a inthlak danglam leh awm loh enfiah nan periodic scan a huam a ni.
  • Symptoms i neih emaw, malignancy rinhlelh a nih chuan: Heng hunah hian surgical removal hi a tlangpuiin enkawlna hmasa ber a ni.

Hamartomas tihbo nan hian eng surgery bik nge hman thin?

Hamartoma awmna hmun a zirin approach hi a inang lo.

Lung hamartomas tan chuan:

  • Wedge resection: Lung atanga a thanna awmna hmun te tak te, wedge ang chi chu lakchhuah a ni a, chubakah chuan tissue hrisel margin a awm bawk.
  • Lobectomy: Lung lobe pum pui chu hamartoma chu chutah chuan localized a nih chuan lakchhuah a ni. Kan lung dinglamah lobe pathum kan nei a, veilam ah pahnih kan nei bawk.
  • Pneumonectomy: Lung pum pui lakchhuah. Hei hi hamartoma tan chuan a tul lo hle.

Thluak (Hypothalamic hamartomas) tan chuan:

  • Resection surgery: Neurosurgeon chuan surgery hmangin a lo thang lian chu a paih chhuak thin.
  • Ablation: Heat sang tak emaw laser energy hmanga tissue tihchhiat a ni.
  • GammaKnife® radiosurgery: Traditional surgery a ni lo va, he procedure hian surgical removal ang bawkin a thanna chu a tichhe thei a, chu chuan radiation beam dik tak, energy sang tak a hmang a ni.

Hamartoma ka neih chuan eng nge thleng ang?

Hamartoma tam zawk hi chu natna khirh tak a ni lo va, chuvangin khawngaihin a tul lovah lungkham suh. Hamartoma hian taksa peng pakhat a nghawng emaw, nakin lawka harsatna a thlen theihna tur a keng tel emaw a nih chuan, a tlangpuiin operation hian a buaina chu a titawp thei a ni.

A châng chuan, paih chhuah chu a harsa thei hle. Entirnan, hypothalamic hamartoma chu optic nerve bulah a awm a nih chuan surgery hian nerve a tichhe thei a ni.

Chuvangin, i hamartoma hi lakchhuah a ngai em tih leh, chutiang thil tih avanga hlauhawm emaw, harsatna emaw awm thei tur chungchangah i doctor nen inbiakna zau tak neih a pawimawh hle.

Hamartoma hi cancer ah a chang thei em?

Hei hi ngaihtuahna tlanglawn tak a ni. Hamartoma cancer vei theihna chance a hniam hle a; thil thleng tlem tak a ni.

Mahse, hamartomas nena inzawm genetic condition thenkhat (Cowden syndrome, PHTS subtype ang chi) hian cancer hlauhawmna zawng zawng a tipung thei tih hre reng ang che. Hetiang hunah hian hamartoma ngei ni lovin, a hnuaia awm genetic condition hian a hlauhawmna a tipung a ni. Chutiang genetic condition i neih chuan cancer screening neih fo a pawimawh.

Doctor hnenah eng zawhna nge ka zawh ang?

Hamartoma i vei tih hriat a nih hnuah zawhna engemaw zat i nei thei. I doctor hnenah a hnuaia mi hi zawt la:

  • Eng thilin nge he hamartoma hi a lo awm chhan?
  • A paih chhuah a ngai tak tak em?
  • Enkawl a ngai em tih hriat nan eng symptom nge ka en tur?
  • He hamartoma hi a hnuaia natna khirh zawk chhinchhiahna a ni thei ang em?
  • Genetic counseling emaw, test emaw hi keimah emaw, ka chhungte tan emaw a hlawkpui ang em?

Take-Home Thuchah hnuhnung ber

He thu hian hamartomas chungchang hi chiang zawkin a hriat theih ka beisei. A pawimawh ber chu hamartoma hi a hlauhawm lo tlangpui tih hre reng ang che. Cancer an ni lo va, taksa pum puiah an darh lo.

Thil tam takah chuan enkawl ngai a awm lo. Mahse, symptoms i neih chuan emaw, i doctor-in ngaihtuahna a neih chuan surgery hi chu buaina chinfelna kawng \ha tak a ni.

Hamartoma i nei tih an hrilh che chuan hlau lutuk suh. I doctor nen uluk takin inbiakna nei la, i tan a hnuaia hmalakna tur dik ber tur chu i hre thei ang. Nirogi Lanka-a i tih theih pawimawh ber chu i hriselna enkawl hi a pawimawh ber a ni.