Darthlalangah i en a, i hmai lai takah line dik tak, a sir khat chu a sen hle a, a thawmhnaw a chhuak a, a sir lehlamah chuan normal, a hring deuh pawh a ni mai thei... Chu chu a hlauhawm leh mak deuh lo em ni?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..?..? A nih loh leh, i naute piang thar taksa sir khat chu a sen thut a, a sir lehlamah a pangngai a nih i hmuh chuan engtin nge ni ang? Hei hi damdawi lama Harlequin Sign kan tih chu a ni. A hming hi a mak deuh a nih avangin a chungchang leh hei hi hlauh tur a ni tak tak em tih hi i hrechiang ang u.
He Harlequin Sign hi eng nge ni tak tak?
A awlsam zawngin, Harlequin Sign chu i taksa emaw i hmai emaw sir khatah vun rawng a inthlak (redness emaw darkening emaw) a awm a, a sir lehlamah a awm reng a, a chang chuan a sen pawh a awm reng a ni. Heng a sir pahnih hi line dinglam hmanga inthen niin a lang a, taksa lai tak thlengin a inthen a ni.
He vun rawng inang lo tak nen hian a sir lehlamah thil dang hmuh tur a awm bawk.
- Redness: He hmun hi hyperhidrosis (thaw hah lutuk) a ni thei. Chu hmuna vun pawh chu khawih chuan a lum deuh thei bawk.
- Pale/Normal Side: He lam hian a thawk hah lo. Vun pawh khawih chuan a vawt ang.
He Harlequin Sign hi a chang chuan `Harlequin syndrome` ang chi damdawi lam dinhmun chhinchhiahna ni thei mahse, a tam zawkah chuan a tha lo a, a bo mai mai thin.
Hei hi a chhan berte chu engte nge ni?
Hei hi a chhan chiang tak hmuh theih a ni ngai lo. A chhan ber chu kan taksa autonomic nervous system-a inbiakpawhna lama harsatna a awm vang a ni. Hei hi kan taksa "auto-pilot" system angin han ngaihtuah teh. He system hian kan neih kan hriat loh thil te, kan thawk dan te, kan thinlung thawk dan te, leh kan thawmhnaw te hi a thunun a ni.
Chuvangin, thluak (hypothalamus) atanga spinal cord kaltlangin hmai leh taksa chunglam thlenga thuchah thawntu nerve pathway-ah blockage emaw defect emaw a awm chuan, chu message chu taksa sir khatah chauh a thawn tha lo mai thei. Hei vang hian a sir khata thisen kalna kawngte chu a zau a, a sen a, a sir lehlamah chuan thuchah chu a dawng lo va, a pangngai reng a ni.
Nausen piang tharte chungah pawh hetiang hi a thleng ve em?
Ni e, hei hi nausen piang tharte hmuh tur a ni. Survey-a a lan dan chuan naute hrisel zinga 10% velin he Harlequin Sign hi an nei thei a ni. Chuvangin, i naute hian hetiang hi a nei a nih chuan lungngai suh.
Hei hi naute pian hnu ni hnih leh ni nga inkarah a thleng tlangpui a, mahse a chang chuan kar thum hnuah pawh a tlai thei.
A pawimawh ber chu he Harlequin Sign hi naute piang tharte neih hi a ni.A hlauhawm lo tak zet a ni. He rawng inthlak danglamna hi second 30 chhungin a bo vek a ni. A chang chuan minute 20 thleng a daih thei bawk. Naute chu a sir lama dah a nih chuan a rawn lang leh thei.
Pawimawh tak: He Harlequin Sign an tih hi `Harlequin ichthyosis` nen hian inthlau lo tur a ni a, hei hi hlauhawm tak, nunna atana hlauhawm leh genetic condition hmuh tur awm lo tak a ni. `Harlequin ichthyosis` hi naute taksa pum pui chu plate ang maia thuk tak, a inkar ah chhe thuk tak tak in a khuh a ni. Thil danglam tak a ni.
Natna kaihhnawih dangte
Harlequin Sign hi a chang chuan damdawi lam thil dang chhinchhiahna angin a lang thei bawk.
Harlequin Syndrome natna a ni
Hei hi kan sympathetic nervous system tichhe thei dinhmun a ni. He nervous system hian kan "fight-or-flight" response hi a control a, chu chu kan phur lai, kan hlauhthawn lai, kan exercise lai hian taksaa inthlak danglamna a ni. Harlequin Syndrome vei (entir nan exercise neih laiin) he system hi activate a nih apiangin hmai leh taksa sir khat chu a sen ang a, a thawmhnaw a chhuak ang a, a sir lehlamah erawh a sen lo ang.
Horner Syndrome natna a ni
Hei hi neurological condition hmuh tur awm lo tak a ni bawk. Mit leh a chhehvel tissue te chu hmai sir khatah a nghawng a ni. `Oculosympathetic palsy` an ti bawk. Thluak atanga mit leh hmai lam panna nerve pathway a block vang a ni. Hetah pawh hian hmai a natna lam chu a sen thei a ni.
| Nihna | Tute nge a nghawng? | Thil langsar ber berte | Tihtakzetin? |
|---|---|---|---|
| Harlequin Sign (nau piang tharte zingah) . | Nausen piang thar hrisel (10% vel) . | Taksa sir khatah hun eng emaw chen a sen thin. | Ni lo , a hlauhawm lo tak zet a, a mah chauhin a bo ang. |
| Harlequin Syndrome natna a ni | Kum eng pawh tan | Exercise emaw, exciting emaw laiin a sir khatah a sen leh thawk hah. | A chhan bulpuiah a innghat. A tam zawkah chuan hlauhawm lo. |
| Horner Syndrome natna a ni | Kum eng pawh tan | Hmai sir khatah mitmeng hnuai lam, mit dum te tak te, thawmhnaw a tlahniam a, hmai a sen bawk. | A chhan bulpui (e.g., tumor) chu a na hle thei. Medical examination neih a pawimawh hle. |
Engtin nge enkawl a nih?
Enkawlna chu Harlequin Sign awm chhan a innghat a ni.
- Nau piang thar tan: Enkawl a ngai lo. Second tlemte emaw minute engemaw zat hnuah a mah chauhin a bo vek ang.
- Harlequin Syndrome tan: Enkawl a ngai ngai lo. A châng chuan he dinhmun hi a mah chauhin a ṭha chho thei bawk. Amaherawhchu, i doctor-in enkawl ngai a tih chuan a chhan a zirin enkawlna a pe ang. Chung zingah chuan:
- Vaccine `Stellate ganglion block` an tih hi vun rawng inthlak danglamna control nan hman a ni.
- Botulinum toxin injection hmanga thawk hah loh tur.
- A hnuaia tumor a awm chuan surgery emaw radiation therapy hmangin emaw lakchhuah theih a ni.
- Hetiang hmel lan dan avanga rilru hahna awm thei tur counselling.
- Horner Syndrome tan: Natna a awm loh chuan enkawl a ngai lo mai thei. Chutiang a nih chuan doctor chuan a chhan bulpui chu a enkawl ang.
Engtikah nge doctor i hmuh ang?
Nangmah emaw, i chhungte zinga mi emaw chuan Harlequin Sign, taksa sir khatah a sen, a thawmhnaw a chhuak a, a lum tih i hriat chuan a tha ber chu doctor pan a, in enfiah hi a ni.
I doctor chuan a enfiah ang che, i natna lan chhuah dan a zawt ang che a, a tul chuan test thenkhat a ti ang a, natna dang a awm loh nan. A tlem hle nachungin, tumor emaw, natna dang emaw chu paih chhuah a pawimawh a, hei hi a chhan a nih theih avangin.
Heng symptoms te hi symptoms na tak dang (e.g. lu na nasa tak, mitdelna, hriatna hloh) nen a inzawm nghal a nih chuan, damdawi in hnai ber Emergency Department (ETU) pan nghal a pawimawh hle
Take-Home Thuchah a ni
- Harlequin Sign hi taksa emaw hmai emaw sir khat chu a sen a, a sir lehlamah a sen vek a ni. Hei hi a tlangpuiin a pawi lo.
- Hei hi nausen piang tharah a awm fo thin. Amah chauhin, minute tlemte chhungin, enkawl lohvin a bo vek a, ngaihtuahawm a ni lo. Hei hi `Harlequin ichthyosis` natna hlauhawm tak a ni lo tih hre reng ang che.
- Hei hi puitlingah a thleng a nih chuan nervous system condition `Harlequin syndrome` emaw `Horner syndrome` emaw ang chi symptom a ni thei.
- Nangmah emaw, i naute emaw hian he symptom hi i neih chuan hlauthawng lo ila, a chhan dik tak hriat theih nan leh natna khirh tak dang a awm loh nan i doctor hmu tur a ni.
💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh