I naute hian pooping harsatna a nei em? Hirschsprung natna chungchang hi han sawi ila

Thil tenawm tak tak te bakah nau piang thar in lama hruai luh hlimna te pawh hi thil pangngai tak a ni lawm ni? Nu leh pate hian an naute ei leh in, inbual, leh ek chhuah (‘ peeing ’ kan ti) te hi an ngaihtuah ber a ni. Chuvangin, i naute hian ni hnih chhung, a nih loh leh darkar 48 vel a poop lo a nih chuan, emaw, a pum chu a danglamin a hring a, a khauh a nih chuan, hei hi i tan thil pawimawh tak a ni ang. Vawiin hian naute thenkhat piangsualna Hirschsprung’s Disease tih kan sawi dawn a ni.

Hirschsprung natna hi eng nge ni?

A awlsam zawngin, Hirschsprung’s Disease hi i naute pianpui (i.e., pianpui natna) a ni. I naute intestine lian (colon) hmun thenkhata bawlhhlawh kalna chu a ti hniam emaw, a titawp vek emaw a ni. A châng chuan doctor-te chuan congenital megacolon'' an ti ṭhin.

Ngaihtuah teh, chaw kan ei hian bawlhhlawh anga ei chhuah leh paih chhuah a ngai a ni. Hetiang kalphung hi a dik taka a awm theih nan kan intestines chhunga muscle te hi an inzawm khawm a, an relax a ngai a ni. Hei hi nerve cells hmanga signal a ni. Hirschsprung’s Disease vei nauteah chuan , a chhungril tawp lam, hnute bula nerve cell te chu a lo thang tha lo hle. Heng nerve cell bikte hi neural crest cells'' an ti a.

Chuvangin, ek chu naute intestines kal tlanga a kal a, nerve cells te hnathawh that lohna hmun a thlen chuan a block a, a kal tlang thei lo. Hei hi constipation a awm lai a ni. He natna hi enkawl nghal a nih loh chuan harsatna lian tak a thlen thei a ni . Chuvang chuan hei hi kan hriat chian a pawimawh hle a ni.

He natna hi engtiang chiahin nge a hluar?

Hirschsprung’s Disease hi a nasat vak lo. Nau piang 5,000 zinga pakhat vel a nghawng a ni . Tin, hmeichhia aiin mipaah ​​a let thum atanga a let liin a tam zawk bawk.

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He natna lan chhuah dan engte nge ni?

Naute thenkhat chu an pian tirh lamah Hirschsprung’s Disease vangin bowel obstruction an nei thei a. If your naute hasn’t had a bowel movement within 48 hours of birth , chu chu he natna chhinchhiahna lian tak a ni thei. Chuvangin fimkhur a pawimawh hle.

Nausen piang tharte zingah hian symptom dang hmuh tur awm thei te chu:

• Abdominal bloating: Naute pum chu gas khat ang maiin a awm thei a, khawih harsa a ti thei bawk.
• Constipation: Ek chhuah hi a harsa hle a, a nih loh leh ni eng emaw zat a liam lo.
• Luak chhuak: A chang chuan luak chhuak chu sen emaw, sen emaw a ni thei.
• Diarrhea: Nausen thenkhat chuan constipation ai chuan diarrhea an nei thei.
• Chaw ei chakna hloh leh taksa rihna tlahniam: Naute hian bawnghnute a in duh lo mai thei a, chuvangin a thau tha lo thei bawk.
• Growth tihkhawtlai a ni.

I naute hian heng symptoms pakhat emaw, a aia tam emaw a neih chuan doctor lam pan nghal a tha ber.

Engvangin nge Hirschsprung natna hi a lo awm?

Nausen chu nausen pum chhunga a awm hian, a hmaa kan sawi tawh neural crest cells te chu naute intestine te tak te chung lam atanga a hnute thlengin a lo thang lian thin. Mahse, Hirschsprung’s Disease vei nauteah chuan heng nerve cells te hi intestine lian hmun dangah an lo thang lian tawh lo. Doctor-te chuan hetiang thil hi a thlen chhan chiang takin an la hre lo.

Amaherawhchu, 20% aia tlem loah chuan he natna hi chhungkaw tinah thlah khat atanga thlah dangah a darh zel tih hmuh theih a ni. Hei hian a awmzia chu genetic mutation vang a ni thei tihna a ni .

He natna vei theihna tur risk factors te chu engte nge ni?

Chhungkaw zinga mi tu emaw, nu leh pa emaw, unau emaw pawhin he natna hi a vei a nih chuan naute pawhin a vei theihna tur hlauhawm tak a awm a ni. Tin, naute a hnuaia natna nei te pawh hi Hirschsprung’s Disease vei theihna a sang zawk a ni:

• Congenital heart disease i neih chuan .
• Down syndrome i neih chuan .

He natna hian eng harsatna nge a thlen theih?

Hirschsprung natna vei naute zinga 40% vel chuan enterocolitis an tih natna an nei a. Hei hian naute intestines te leh lian te chu a ti na a, a infect a ni. Hei hi naute thenkhatah chuan a na lo hle laiin, thenkhatah chuan nunna atana hlauhawm thei khawpin a na thei bawk. Enterocolitis na tak a lo awm chuan naute chu khawsik a nei thei a, rang takin riltam na tak a nei thei bawk.

Pawimawh: Hirschsprung’s Disease hi enkawl tha a nih loh chuan natna khirh tak, nunna atana hlauhawm tak tak a thlen thei a, chungte chu:

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* Large bowel obstruction: Hemiah hian naute intestine lian tak kal tlanga chaw kalna chu a tawp vek a ni.

* Toxic megacolon: Hei hi a awm lo hle a, mahse nunna atana hlauhawm tak a ni. Naute intestine lian tak chu a hring nasa hle a, a lian hle bawk. Gas leh bawlhhlawh chu intestine hring dup chhungah a kal thei lo va, a block thei lo. Hei hian intestine chhungah pressure a tisang a, thisenah bacteria a lut thei a ni. Hei hian nunna atana hlauhawm tak Enterocolitis leh Sepsis tih te a thlen thei a ni. A nasat deuh thenkhatah chuan intestine-ah khur (perforation) a awm thei.

Harsatna dang hmuh theihte chu:

• Duh loh vanga chaw ei fo thin.
• Kawthalo.
• Khawsik.
• Ei leh in lama harsatna (malnutrition) a awm.
• Constipation na tak a awm.
• Pum a hring chhuak.
• Luak chhuak.

Chuvangin, natna lan chhuah dan i hriat veleh damdawi lam pan vat a pawimawh hle.

Engtin nge Hirschsprung’s Disease hi hriat chhuah a nih?

Doctor hnena i naute i hruai hian i tih hmasak ber chu naute pum chu i hriat a ni. A hring, na leh bawlhhlawh a inkhar loh an enfiah thin. Tichuan, rectum an check a, stool buildup a awm em tih an enfiah thin.

Chu bâkah, doctor chuan heng test pakhat emaw, a aia tam emaw a ti thei bawk:

• X-ray: Pum chhunga X-ray hmanga intestine blockage awm leh awm loh enfiah theih a ni.
• Contrast enema: Hemiah hian doctor chuan naute hnute chhungah catheter an tih tube te tak te a thun a. Tube kaltlangin tui him tak contrast an tih chu intestine chhungah a thawn lut a. Tichuan, X-ray an la a, chu tui chu intestine kaltlangin engtin nge a kal tih an en a. Hei hian intestine chhungah blockage emaw narrowing emaw a awm em tih chiang taka hriat theih nan a pui thei a ni.
• Biopsy: Hei hi a natna hriat chian nan test pawimawh ber a ni. Doctor chuan hmanraw bik hmangin naute intestine lian (rectum) tawp lam atanga tissue te tak te chu a la chhuak thin. Tichuan pathologist pakhat chuan microscope hmangin tissue chu a en a, kan sawi tawh nerve cells te chu a awm em tih a en a. He test hi naute tan a na lo va, anesthesia pawh a ngai lo.

Hirschsprung’s Disease hi engtin nge enkawl leh enkawl a nih?

Hirschsprung natna hi damdawi a la awm lo. Mahse, surgery hmangin hlawhtling taka enkawl theih a ni. Surgery hi chi hnih a awm a, chungte chu pull-through procedure leh ostomy surgery te an ni.

Pull-through hmanga tih dan tur

Hei hi Hirschsprung natna atana surgery neih tam ber leh hman tlanglawn ber a ni. He surgery-ah hian surgeon chuan naute intestine lian tak atanga nerve cells awm lohna hmun chu a la chhuak a, intestine hrisel tak chu anus nen direct-in a thlunzawm a ni. He surgery hi laparoscopically (incision tenau tlemte hmangin) emaw, conventional emaw hmangin tih theih a ni. He surgery hnuah hian naute hi a dam thuai thin.

Ostomy operation tih a ni

Naute thenkhat chu pull-through procedure hma emaw, a ruala emaw ostomy surgery neih a ngai mai thei. Hei hi colostomy (intestine lian tana tih dan) emaw, ileostomy (intestine te tana tih dan) emaw pawh a ni thei.

Hetiang tihnaah hian surgeon-te chuan naute pum vunah hian intestine lian emaw, small intestine emaw a\anga a \hen an dah \hin a. Naute hnute ai chuan naute bawlhhlawh chu "stoma" an tih kawngkhar hmangin a chhuak thin. Naute taksaah hian "ostomy bag" an bun a, chu chuan a bawlhhlawh chu a la khawm a ni. Hei hi hun eng emaw chen atan a ni tlangpui. A hnuah chuan surgery dangah lakchhuah a ni a, "pull-through procedure" tih zawh a ni.

Enkawlna dang a awm bawk

Surgery bakah hian heng enkawlnate hi a \angkai thei bawk:

• Bowel management: Naute rilru hrisel tak neih theihna tura damdawi leh/ emaw enemas hmanga enkawl dan.
• Sacral nerve stimulation: Surgeon chuan a hnungzang hnuai lamah hmanraw te tak te a dah a, chu chuan bowel leh bladder control nan a pui thin.
• Biofeedback: Hei hi therapeutic technique a ni a, taksa hnathawh duh loh zawng, bowel movement ang chi control dan min zirtir a ni.

Pul-through surgery hnua harsatna emaw, side effect emaw awm thei te chu engte nge ni?

Hirschsprung's Disease vei naute chu pull-through surgery'' hnuah an dam nghal vat thin.Amaherawhchu, naute thenkhat chuan an dam hnuah pawh a hnuaia harsatna te hi an tawk thei a ni:

• Fecal incontinence a awm thei.
• Ek khal.
• Intestinal natna (Enterocolitis) a awm thei.

Heng harsatnate hi a lo awm a nih chuan i naute surgeon leh a nih loh leh gastroenterologist te pawhin an enkawl theih nan an pui ang che.

Naute hi enkawl hnuah engtiang chiahin nge a dam thuai ang?

Engkim a kal tha a nih chuan naute chu operation a nih atanga ni engemaw zat chhungin a dam leh tan dawn a ni. Hirschsprung’s Disease hi tihdam kim theih ni lo mah se, surgery hian result hlawhtling tak a nei thei tih hre reng ang che.

Surgery zawh hnua thil awmdan chu engtin nge a awm?

Operation an neih hnuah pawh naute thenkhat chu chaw ei kham, insum theih lohna leh intestinal infection te an nei chhunzawm thei a ni. Mahse, hun rei tak chhung damdawi lam enkawlna leh enkawl dan dik a nih chuan naupang tam zawk chu chaw ei kham na tak leh an riltam thunun harsa lovin nun pangngaiin an hmang thei a ni.

Hirschsprung natna hi ka veng thei ang em?

Vanduaithlak takin Hirschsprung natna hi tumahin an veng thei lo. He natna hi i vei a nih chuan, emaw, i chhungkuaa mi tu emaw chuan a lo vei tawh a nih chuan chhungkaw din hmain genetic counselor i hmuh hmasak phawt a tha mai thei.

Engtin nge ka fa hi Hirschsprung’s Disease a tuar theih nan ka puih theih ang?

Operation hnuah chuan i fain a natna a enkawl theih nan enkawlna engemaw zat a awm a:

• Nutritional guidance: I fa tana ei tur tha tur leh constipation venna atana tih tur chungchangah nutritionist hnen atangin thurawn i la thei ang.
• Specialist leh nurse te hnen atanga enkawl reng: Gastroenterologist leh hemi kawnga trained nurse enkawl hi a pawimawh hle.
• Biofeedback / pelvic floor rehabilitation: Hengte hian bowel control a tichak hle.
• Psychologist emaw social worker emaw atanga tanpuina: Naupang leh chhungkua chuan he harsatna hi an hmachhawn theih nan psychological support an dawng thei a ni.

I fa doctor te nen inbia fo ang che. I fate tana ei leh in leh enkawlna tha ber thlang turin an pui ang che.

Engtikah nge ka naute Hirschsprung’s Disease chungchang hi doctor hnenah ka hrilh ang?

Operation hnuah, a bik takin kum khatna chhungin naute hian intestinal infection (enterocolitis) an nei thei a ni. I naute hian heng symptoms te hi a lan chhuah chuan doctor hnenah hriattir nghal rawh:

• Rectal atanga thisen chhuak.
• Kawthalo.
• Khawsik.
• Pum a hring chhuak.
• Luak chhuak.

I naute hi Hirschsprung’s Disease neia a pian vang mai mai chuan nun hlim tak, hrisel tak a hmang thei lo tihna a ni lo tih hre reng ang che. He natna hi operation hmanga enkawl theih a ni. Mahse, operation hma hun chu i tan chuan a buaithlak hle thei a ni. Nausen piang thar nena kan inkawp hian lungngaihna leh hlauhna neih hi thil pangngai tak a ni. I chhungte leh i thiante hnenah tanpuina dil rawh. Inchhung hna leh chaw siamah te tanpui rawh se. Tichuan i naute nen hun i hmang thei a, chawlh hahdam i nei thei bawk.

Take-Home Thuchah a ni

• Hirschsprung’s Disease hi nausen thenkhat pianpui an ni a, intestine lian chhunga nerve cells te tha taka an lo thanglian loh avangin ek chhuah harsa an ti thin.
• I naute hian a pian atanga darkar 48 chhunga a zun chhuah loh, a pum a hring, a luak chhuak ang chi natna lanchhuahna a neih chuan doctor pan nghal rawh.
• He natna hi biopsy hmanga finfiah theih a ni.
• Pull-through procedure hi a enkawlna ber a ni. A châng chuan ostomy surgery pawh hun eng emaw chen tih theih a ni.
• Enkawl zawhah nausen tam zawk chu nun pangngai, hrisel takin an khawsa thei a ni. Mahse, damdawi lam enkawlna chhunzawm zel a ngai a ni.
• He zinkawngah hian nangmah chauh i ni lo. Doctor leh chhungte hnen atangin tanpuina dawng rawh.

I naute chu a dam thuai theih nan duhsakna hlanin!