I naute hian pooping harsatna a nei em? Hirschsprung natna chungchang hi han sawi ila

Thil tenawm tak tak te bakah nau piang thar in lama hruai luh hlimna te pawh hi thil pangngai tak a ni lawm ni? Nu leh pate hian an naute ei leh in, inbual, leh ek chhuah (‘ peeing ’ kan ti) te hi an ngaihtuah ber a ni. Chuvangin, i naute hian ni hnih chhung, a nih loh leh darkar 48 vel a poop lo a nih chuan, emaw, a pum chu a danglamin a hring a, a khauh a nih chuan, hei hi i tan thil pawimawh tak a ni ang. Vawiin hian naute thenkhat piangsualna Hirschsprung’s Disease tih kan sawi dawn a ni.

Hirschsprung natna hi eng nge ni?

A awlsam zawngin, Hirschsprung’s Disease hi i naute pianpui (i.e., pianpui natna) a ni. I naute intestine lian (colon) hmun thenkhata bawlhhlawh kalna chu a ti hniam emaw, a titawp vek emaw a ni. A châng chuan doctor-te chuan ``congenital megacolon'' an ti ṭhin.

Ngaihtuah teh, chaw kan ei hian bawlhhlawh anga ei chhuah leh paih chhuah a ngai a ni. Hetiang kalphung hi a dik taka a awm theih nan kan intestines chhunga muscle te hi an inzawm khawm a, an relax a ngai a ni. Hei hi nerve cells hmanga signal a ni. Hirschsprung’s Disease vei nauteah chuan , a chhungril tawp lam, hnute bula nerve cell te chu a lo thang tha lo hle. Heng nerve cell bikte hi ``neural crest cells'' an ti a.

Chuvangin, ek chu naute intestines kal tlanga a kal a, nerve cells te hnathawh that lohna hmun a thlen chuan a block a, a kal tlang thei lo. Hei hi constipation a awm lai a ni. He natna hi enkawl nghal a nih loh chuan harsatna lian tak a thlen thei a ni . Chuvang chuan hei hi kan hriat chian a pawimawh hle a ni.

He natna hi engtiang chiahin nge a hluar?

Hirschsprung’s Disease hi a nasat vak lo. Nau piang 5,000 zinga pakhat vel a nghawng a ni . Tin, hmeichhia aiin mipaah ​​a let thum atanga a let liin a tam zawk bawk.

He natna lan chhuah dan engte nge ni?

Naute thenkhat chu an pian tirh lamah Hirschsprung’s Disease vangin bowel obstruction an nei thei a. If your naute hasn’t had a bowel movement within 48 hours of birth , chu chu he natna chhinchhiahna lian tak a ni thei. Chuvangin fimkhur a pawimawh hle.

Nausen piang tharte zingah hian symptom dang hmuh tur awm thei te chu:

• Abdominal bloating: Naute pum chu gas khat ang maiin a awm thei a, khawih harsa a ti thei bawk.
• Constipation: Ek chhuah hi a harsa hle a, a nih loh leh ni eng emaw zat a liam lo.
• Luak chhuak: A chang chuan luak chhuak chu sen emaw, sen emaw a ni thei.
• Diarrhea: Nausen thenkhat chuan constipation ai chuan diarrhea an nei thei.
• Chaw ei chakna hloh leh taksa rihna tlahniam: Naute hian bawnghnute a in duh lo mai thei a, chuvangin a thau tha lo thei bawk.
• Growth tihkhawtlai a ni.

I naute hian heng symptoms pakhat emaw, a aia tam emaw a neih chuan doctor lam pan nghal a tha ber.

Engvangin nge Hirschsprung natna hi a lo awm?

Nausen chu nausen pum chhunga a awm hian, a hmaa kan sawi tawh neural crest cells te chu naute intestine te tak te chung lam atanga a hnute thlengin a lo thang lian thin. Mahse, Hirschsprung’s Disease vei nauteah chuan heng nerve cells te hi intestine lian hmun dangah an lo thang lian tawh lo. Doctor-te chuan hetiang thil hi a thlen chhan chiang takin an la hre lo.

Amaherawhchu, 20% aia tlem loah chuan he natna hi chhungkaw tinah thlah khat atanga thlah dangah a darh zel tih hmuh theih a ni. Hei hian a awmzia chu genetic mutation vang a ni thei tihna a ni .

He natna vei theihna tur risk factors te chu engte nge ni?

Chhungkaw zinga mi tu emaw, nu leh pa emaw, unau emaw pawhin he natna hi a vei a nih chuan naute pawhin a vei theihna tur hlauhawm tak a awm a ni. Tin, naute a hnuaia natna nei te pawh hi Hirschsprung’s Disease vei theihna a sang zawk a ni:

• Congenital heart disease i neih chuan .
• Down syndrome i neih chuan .

He natna hian eng harsatna nge a thlen theih?

Hirschsprung natna vei naute zinga 40% vel chuan enterocolitis an tih natna an nei a. Hei hian naute intestines te leh lian te chu a ti na a, a infect a ni. Hei hi naute thenkhatah chuan a na lo hle laiin, thenkhatah chuan nunna atana hlauhawm thei khawpin a na thei bawk. Enterocolitis na tak a lo awm chuan naute chu khawsik a nei thei a, rang takin riltam na tak a nei thei bawk.

Pawimawh: Hirschsprung’s Disease hi enkawl tha a nih loh chuan natna khirh tak, nunna atana hlauhawm tak tak a thlen thei a, chungte chu:

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* Large bowel obstruction: Hemiah hian naute intestine lian tak kal tlanga chaw kalna chu a tawp vek a ni.

* Toxic megacolon: Hei hi a awm lo hle a, mahse nunna atana hlauhawm tak a ni. Naute intestine lian tak chu a hring nasa hle a, a lian hle bawk. Gas leh bawlhhlawh chu intestine hring dup chhungah a kal thei lo va, a block thei lo. Hei hian intestine chhungah pressure a tisang a, thisenah bacteria a lut thei a ni. Hei hian nunna atana hlauhawm tak `Enterocolitis` leh `Sepsis` tih te a thlen thei a ni. A nasat deuh thenkhatah chuan intestine-ah khur (`perforation`) a awm thei.

Harsatna dang hmuh theihte chu:

• Duh loh vanga chaw ei fo thin.
• Kawthalo.
• Khawsik.
• Ei leh in lama harsatna (malnutrition) a awm.
• Constipation na tak a awm.
• Pum a hring chhuak.
• Luak chhuak.

Chuvangin, natna lan chhuah dan i hriat veleh damdawi lam pan vat a pawimawh hle.

Engtin nge Hirschsprung’s Disease hi hriat chhuah a nih?

Doctor hnena i naute i hruai hian i tih hmasak ber chu naute pum chu i hriat a ni. A hring, na leh bawlhhlawh a inkhar loh an enfiah thin. Tichuan, rectum an check a, stool buildup a awm em tih an enfiah thin.

Chu bâkah, doctor chuan heng test pakhat emaw, a aia tam emaw a ti thei bawk:

• X-ray: Pum chhunga X-ray hmanga intestine blockage awm leh awm loh enfiah theih a ni.
• Contrast enema: Hemiah hian doctor chuan naute hnute chhungah catheter an tih tube te tak te a thun a. Tube kaltlangin tui him tak contrast an tih chu intestine chhungah a thawn lut a. Tichuan, X-ray an la a, chu tui chu intestine kaltlangin engtin nge a kal tih an en a. Hei hian intestine chhungah blockage emaw narrowing emaw a awm em tih chiang taka hriat theih nan a pui thei a ni.
• Biopsy: Hei hi a natna hriat chian nan test pawimawh ber a ni. Doctor chuan hmanraw bik hmangin naute intestine lian (rectum) tawp lam atanga tissue te tak te chu a la chhuak thin. Tichuan pathologist pakhat chuan microscope hmangin tissue chu a en a, kan sawi tawh nerve cells te chu a awm em tih a en a. He test hi naute tan a na lo va, anesthesia pawh a ngai lo.

Hirschsprung’s Disease hi engtin nge enkawl leh enkawl a nih?

Hirschsprung natna hi damdawi a la awm lo. Mahse, surgery hmangin hlawhtling taka enkawl theih a ni. Surgery hi chi hnih a awm a, chungte chu pull-through procedure leh ostomy surgery te an ni.

Pull-through hmanga tih dan tur

Hei hi Hirschsprung natna atana surgery neih tam ber leh hman tlanglawn ber a ni. He surgery-ah hian surgeon chuan naute intestine lian tak atanga nerve cells awm lohna hmun chu a la chhuak a, intestine hrisel tak chu anus nen direct-in a thlunzawm a ni. He surgery hi laparoscopically (incision tenau tlemte hmangin) emaw, conventional emaw hmangin tih theih a ni. He surgery hnuah hian naute hi a dam thuai thin.

Ostomy operation tih a ni

Naute thenkhat chu pull-through procedure hma emaw, a ruala emaw ostomy surgery neih a ngai mai thei. Hei hi colostomy (intestine lian tana tih dan) emaw, ileostomy (intestine te tana tih dan) emaw pawh a ni thei.

Hetiang tihnaah hian surgeon-te chuan naute pum vunah hian intestine lian emaw, small intestine emaw a\anga a \hen an dah \hin a. Naute hnute ai chuan naute bawlhhlawh chu "stoma" an tih kawngkhar hmangin a chhuak thin. Naute taksaah hian "ostomy bag" an bun a, chu chuan a bawlhhlawh chu a la khawm a ni. Hei hi hun eng emaw chen atan a ni tlangpui. A hnuah chuan surgery dangah lakchhuah a ni a, "pull-through procedure" tih zawh a ni.

Enkawlna dang a awm bawk

Surgery bakah hian heng enkawlnate hi a \angkai thei bawk:

• Bowel management: Naute rilru hrisel tak neih theihna tura damdawi leh/ emaw enemas hmanga enkawl dan.
• Sacral nerve stimulation: Surgeon chuan a hnungzang hnuai lamah hmanraw te tak te a dah a, chu chuan bowel leh bladder control nan a pui thin.
• Biofeedback: Hei hi therapeutic technique a ni a, taksa hnathawh duh loh zawng, bowel movement ang chi control dan min zirtir a ni.

Pul-through surgery hnua harsatna emaw, side effect emaw awm thei te chu engte nge ni?

Hirschsprung's Disease vei naute chu ``pull-through surgery'' hnuah an dam nghal vat thin.Amaherawhchu, naute thenkhat chuan an dam hnuah pawh a hnuaia harsatna te hi an tawk thei a ni:

• Fecal incontinence a awm thei.
• Ek khal.
• Intestinal natna (Enterocolitis) a awm thei.

Heng harsatnate hi a lo awm a nih chuan i naute surgeon leh a nih loh leh gastroenterologist te pawhin an enkawl theih nan an pui ang che.

Naute hi enkawl hnuah engtiang chiahin nge a dam thuai ang?

Engkim a kal tha a nih chuan naute chu operation a nih atanga ni engemaw zat chhungin a dam leh tan dawn a ni. Hirschsprung’s Disease hi tihdam kim theih ni lo mah se, surgery hian result hlawhtling tak a nei thei tih hre reng ang che.

Surgery zawh hnua thil awmdan chu engtin nge a awm?

Operation an neih hnuah pawh naute thenkhat chu chaw ei kham, insum theih lohna leh intestinal infection te an nei chhunzawm thei a ni. Mahse, hun rei tak chhung damdawi lam enkawlna leh enkawl dan dik a nih chuan naupang tam zawk chu chaw ei kham na tak leh an riltam thunun harsa lovin nun pangngaiin an hmang thei a ni.

Hirschsprung natna hi ka veng thei ang em?

Vanduaithlak takin Hirschsprung natna hi tumahin an veng thei lo. He natna hi i vei a nih chuan, emaw, i chhungkuaa mi tu emaw chuan a lo vei tawh a nih chuan chhungkaw din hmain genetic counselor i hmuh hmasak phawt a tha mai thei.

Engtin nge ka fa hi Hirschsprung’s Disease a tuar theih nan ka puih theih ang?

Operation hnuah chuan i fain a natna a enkawl theih nan enkawlna engemaw zat a awm a:

• Nutritional guidance: I fa tana ei tur tha tur leh constipation venna atana tih tur chungchangah nutritionist hnen atangin thurawn i la thei ang.
• Specialist leh nurse te hnen atanga enkawl reng: Gastroenterologist leh hemi kawnga trained nurse enkawl hi a pawimawh hle.
• Biofeedback / pelvic floor rehabilitation: Hengte hian bowel control a tichak hle.
• Psychologist emaw social worker emaw atanga tanpuina: Naupang leh chhungkua chuan he harsatna hi an hmachhawn theih nan psychological support an dawng thei a ni.

I fa doctor te nen inbia fo ang che. I fate tana ei leh in leh enkawlna tha ber thlang turin an pui ang che.

Engtikah nge ka naute Hirschsprung’s Disease chungchang hi doctor hnenah ka hrilh ang?

Operation hnuah, a bik takin kum khatna chhungin naute hian intestinal infection (enterocolitis) an nei thei a ni. I naute hian heng symptoms te hi a lan chhuah chuan doctor hnenah hriattir nghal rawh:

• Rectal atanga thisen chhuak.
• Kawthalo.
• Khawsik.
• Pum a hring chhuak.
• Luak chhuak.

I naute hi Hirschsprung’s Disease neia a pian vang mai mai chuan nun hlim tak, hrisel tak a hmang thei lo tihna a ni lo tih hre reng ang che. He natna hi operation hmanga enkawl theih a ni. Mahse, operation hma hun chu i tan chuan a buaithlak hle thei a ni. Nausen piang thar nena kan inkawp hian lungngaihna leh hlauhna neih hi thil pangngai tak a ni. I chhungte leh i thiante hnenah tanpuina dil rawh. Inchhung hna leh chaw siamah te tanpui rawh se. Tichuan i naute nen hun i hmang thei a, chawlh hahdam i nei thei bawk.

Take-Home Thuchah a ni

• Hirschsprung’s Disease hi nausen thenkhat pianpui an ni a, intestine lian chhunga nerve cells te tha taka an lo thanglian loh avangin ek chhuah harsa an ti thin.
• I naute hian a pian atanga darkar 48 chhunga a zun chhuah loh, a pum a hring, a luak chhuak ang chi natna lanchhuahna a neih chuan doctor pan nghal rawh.
• He natna hi biopsy hmanga finfiah theih a ni.
• Pull-through procedure hi a enkawlna ber a ni. A châng chuan ostomy surgery pawh hun eng emaw chen tih theih a ni.
• Enkawl zawhah nausen tam zawk chu nun pangngai, hrisel takin an khawsa thei a ni. Mahse, damdawi lam enkawlna chhunzawm zel a ngai a ni.
• He zinkawngah hian nangmah chauh i ni lo. Doctor leh chhungte hnen atangin tanpuina dawng rawh.

I naute chu a dam thuai theih nan duhsakna hlanin!

` Hirschsprung natna, Hirschsprung natna, nausen riltam, pianpui megacolon, intestinal surgery, naupang enkawlna, pull-through procedure, ostomy