Aw, a chang chuan kan thil hriatte hian kan lungngai em em a, kan mangang em em thin a ni lawm ni? A bik takin he khawvela naute thar lo kal tur chungchang a nih chuan. Vawiin hian kan sawi dawn a, natna hlauhawm tak, a sensitive deuh a, mahse kan hriat chian a pawimawh hle. Hei hi Iniencephaly kan ti a.
Chuti a nih chuan, Iniencephaly chu eng nge ni?
A awlsam zawngin, Iniencephaly hi pianpui natna khirh tak a ni . Naute lu, kawr leh ruhro a nghawng ber a ni. Hetiang natna neia piang naute hian kawr a tawi hle thei a, a nih loh leh kawr pawh a nei lo thei bawk. Tin, an lu hnunglam (bent back head) leh ruhro (spinal deformities) an nei thei bawk. Hei hi a harsat zia han ngaihtuah teh. Vawi tam tak chu heng harsatna lian ber berte bakah hian naute taksa system dang, thinlung leh lungah te pawh thil dik lo engemaw zat a awm thei bawk.
A tam zawkah chuan he natna neia piang naute hi an pian hmain an thi a, chu chu nausen pum chhungah emaw, an pian hnu rei vak loah emaw an thi thin. A tlem hle a, naute natna khirh lo zawk nei chu rei tak a dam thei.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Iniencephaly hi a takah chuan natna hlauhawm tak a ni. Chu chu a thleng fo lo tihna a ni. Scientist-te chuan he natna hi kum 1836 daih tawh khan an lo report hmasa ber a, tuna data atanga a lan dan chuan he natna hi naute sang za zinga pakhat atanga za vel ah a awm niin an chhut. Mahse, heng chhut dan hi a inang lo. Thil dang pakhat chu he natna hi naute hmeichhiaah pawh a tam deuh niin an sawi bawk.
Engtin nge iniencephaly hi a lo awm?
He Iniencephaly hi engtin nge a lo awm tih i en ang u. Hei hi a takah chuan nervous system a piansualna a ni . Doctor te chuan hei hi ``Neural Tube Defect'' an ti a. Naupai hnu kar hmasa berte hi a pawimawh hle tih i hria em? Hetih lai hian ``neural tube'', chuta tang chuan naute thluak, ruhro leh ruhro (spinal cord kal tlanga nerve lian ber) te chu a lo piang tan thin. A tlangpuiin naupai kar thumna emaw kar linaah emaw he neural tube hi a khar vek tawh a, nervous system pawh a lo thang tha tur a ni. Mahse, Iniencephaly-ah chuan eng emaw chhan vangin he thil hi a titawp a, nervous system pawh a lo thang tha lo hle.
Iniencephaly hi engte nge ni?
A chhan dik tak sawi a har khawp mai . Doctor-te chuan genetic (i.e. inherited) leh environmental factors inzawmkhawm niin an ngai. A then phei chuan chromosomal abnormalities, `(Monosomy X)`, `(Trisomy 13)` leh `(Trisomy 18)` te hi a inzawm tih hmuhchhuah a ni.
Tin, naupai lai hian environment factor thenkhat pawhin he hlauhawmna hi a tipung thei bawk. Chung zingah chuan:
- Folic acid tlakchhamna: 1.1.Hei hi thil pawimawh tak a ni. Hemi chungchang hi kan sawi belh leh ang.
- Zu hman dan: Naupai laia zu in.
- Meizial zuk: Chu chu cigarette zuk ang chi thil tihna a ni.
- Diabetes Mellitus: Nu hian zunthlum thunun theih loh a nei a.
- Thau lutuk: Nu taksa rih zawng hi a rawt aia tam a ni.
- Damdawi thenkhat hman dan: Damdawi thenkhat hi hman a ni a, a bik takin naupai tirh lamah hman a ni. Entirnan, sulfa damdawi, antiseizure damdawi, diuretics, leh antihistamines te hi a ni.
A pawimawh ber chu i naute hian naupai hmasaah neural tube defect a nei a nih chuan i naupai leh hunah chuan a hlauhawmna chu a sang deuh hlek a ni.
Engtin nge Iniencephaly hi hriat chhuah a nih?
Naute a pian veleh doctor-te chuan naute lu ruh leh ruhro enin iniencephaly natna hi an hre thei a ni. Chu chu pawn lam chhinchhiahna hmangin an hre thei tihna a ni . Naute chu rei tak a dam chuan doctor chuan ultrasound, CT scan, leh MRI ang chi test hmangin a dinhmun a zir chiang thei a, eng enkawlna nge awm tih a rel thei bawk.
Hei hi naute pian hmain hriatchhuah theih a ni lo em ni?
Ni e, hei hi zawhna pawimawh tak a ni. Naute a pian hma pawh, chu chu naupai lai pawhin, neural tube chhiatna, iniencephaly ang chi, hriat theihna test engemaw zat a awm a ni . I doctor chuan heng test te hi routine checkup atan emaw, i naupai chu hlauhawma an ngaih chuan emaw a rawt thei ang.
- Prenatal ultrasound: Hei hi kan hriat chian vek scan a ni. Sound wave hmangin nausen pum chhunga thlalak a la thin. Doctor chuan he scan hmang hian naute lu, a kawr leh ruhro chu ngun takin a en a, a danglamna a awm leh awm loh a enfiah thin.
- Quad marker screen: Hei hi nu thisen test a ni. Hormone leh protein engemaw zat a zawng thin. Protein pawimawh tak pakhat chu alpha-fetoprotein (AFP) a ni. He AFP hi naute siam a ni. Chumi hnuah chuan nu thisenah a kal lut ta a ni. Nu thisenah AFP level a sang hle a nih chuan naute hian neural tube defect a nei thei tih a tilang thei a ni.
- Amniocentesis tih hi a ni.He test-ah hian doctor chuan naute chhehvel amniotic fluid tlemte chu needle te tak te hmangin a paih chhuak thin. Lab hian he amniotic fluid-a AFP level hi a teh a, chromosomal abnormalities awm leh awm loh enfiah nan ``Karyotype testing'' tih test pawh a ti bawk. Heng test pahnihte hian neural tube problem a awm leh awm loh leh a chhan chu eng nge ni tih hriat theihna a pe thei a ni.
- Fetal MRI: Hei pawh hi scan chi khat a ni. Radio wave leh magnetic field chak tak hmangin naute ruh leh tissue te thlalak chiang tak, chipchiar tak tak a siam chhuak thin. A tha ber chu MRI scan hian naute chu radiation a tawk lo tih hi a ni.
He natna hi a hma thei ang bera hriatchhuah a pawimawh hle . Doctor-te chu a hmaa hriat chhuah a nih chuan naute dinhmun chu chhungte hnenah an hrilhfiah thei a, nu leh pate hnenah rilru lam tanpuina tul tak tak an pe thei bawk. Naupai chhunzawm zel a nih chuan heng thil dik lote hian nau neih laiin nu tan pawh hlauhawmna engemaw zat a thlen thei bawk.
Iniencephaly hi eng enkawlna nge ni?
Dik tak chuan he natna, Iniencephaly hi enkawlna bik a awm lo . Hetiang natna vei naute tam zawk hi naupai lai emaw, nausen pum chhungah emaw, an pian atanga darkar tlemte chhungin an thi thin. Hei hi dinhmun lungchhiatthlak tak a ni. Doctor leh health worker-te chuan he lungngaihna tuar chhuak tur leh tuar chhuak tur hian chhungkaw tanpui nan a tul ang ang an pe a ni.
A tlem hle a, chu chu naute tlemte chauh hun rei tak an dam tihna a ni a, doctor-te chuan naute pakhat zel chu pakhat zelin an enkawl a, chutih laia natna lan chhuah dan azirin an enkawl a ni.
Folic acid hian hei hi a veng thei ang em?
Hei hi kan hriat tur pawimawh ber a ni . Neural tube defects, anencephaly telin, venna atana i tih theih pawimawh ber chu naupai hma leh naupai laiin folic acid ei hi a ni . Folic acid hi B vitamin a ni. Kan taksaa cell thar siam chhuahna atan a pawimawh hle.
Research atanga a lan dan chuan ni khata folic acid microgram 400 (mcg) ei hian neural tube defects awm theihna chu 70% velin a tihziaawm thei a ni . Nau neih kum tling hmeichhia zawng zawng tan nitin hetiang zat hi ei a pawimawh hle. Hei hi chhan pahnih a awm a, chungte chu:
- Naupai tam tak hi ruahman lawk a ni lo.
- Neural tube defects hi naupai kar hmasa lamah a awm a, chutih lai chuan mi tam takin nau an pai tih pawh an hre lo.
Chuvangin, naute i beisei a nih chuan, emaw, fa neih theih kum i nih chuan, i doctor nen folic acid chungchang hi sawipui ngei ang che. Naupai i tum a nih chuan i doctor hnenah naupai hmaa vitamin bik siam, folic acid awmna chu rawn rawt turin hrilh rawh.
Hmeichhia naute hmasa neural tube defect nei tawh, naute dang beisei mekte chuan folic acid tam zawk an mamawh mai thei. U.S. Centers for Disease Control and Prevention (CDC) chuan nitin folic acid microgram 4,000 (milligram 4) ei tur a rawt a, naupai hma thla khat atanga tan a, naupai atanga thla thum hmasa ber thleng chhunzawm zel tur a ni. Mahse, folic acid ei tam lutuk hi a tha lo . Chuvangin folic acid ei tam hmain doctor rawn hmasa phawt ang che.
A hlauhawmna tihtlem nan eng thil dang nge tih theih ang?
Folic acid ei bakah hian anencephaly vei theihna tihziaawmna tur thil dang engemaw zat a awm a:
- Neural tube tichhe thei nia hriat damdawi thenkhat ei loh . (Hemi chungchang hi i doctor nen inbia ang che.)
- Zu in hi tihtawp vek.
- I tan taksa rihna hrisel tak vawn reng.
- Zunthlum i vei a nih chuan uluk taka control a pawimawh.
- Meizial i zu a nih chuan bansan rawh.
Iniencephaly hi eng nge a hmalam hun?
Iniencephaly hi genetic condition buaithlak tak a ni. Chuvangin, he dinhmun atanga lo chhuak hi a tha vak lo fo thin . Naupai tam tak chu nau pai emaw, nau piang thi emaw-ah a tawp thin. Nausen chu nung chungin lo piang mah se, darkar tlemte chhungin a thih theihna chance a sang hle.
Kum 2019 thleng khan khawvela naute pariat chauh hi he natna iniencephaly nen hian hun rei tak an dam chhuak tawh a ni. Chung zinga pali chu zai an ni tawh a, an enkawl dan pawh a hlawhtling hle nia sawi a ni. Mahse, hei hi thil thleng tlem tak a ni.
Engtin nge naupai hrisel tak ruahman ang?
Nau neih kum i nih chuan nitin folic acid microgram 400 ei a pawimawh a, nau pai tum lo pawh nise. Naupai zawng zawng zinga a chanve vel chu ruahman lawk loh a nih avangin, mi tam takin nau an pai tih an hriat hma pawhin neural tube defects, anencephaly telin a awm thin a, folic acid hian hengte hi a veng thei a ni.
Naupai tumte chuan doctor an pan ngei tur a ni a , preconception counseling an la ngei tur a ni . He appointment chhung hian i doctor chuan i risk factor zawng zawng a enfiah vek ang a, naupai hrisel tak neih theihna tura i tih theih turte a rawn rawt ang che.
He thawnthu a\anga kan hriat reng tur pawimawh tak takte chu
Okay, chuvangin kan sawi tawh Iniencephaly chungchangah hian ngaihdan i neih kan beisei. Hei hi thil awm lo leh buaithlak tak ni mah se, kan hriat chian a pawimawh hle.
Hriat reng tur chu nau nei tura beisei hmeichhia zawng zawng tan naupai hma leh naupai thla thum chhungin folic acid tha tawk an ei hi a pawimawh hle.
Hei hian neural tube defects iniencephaly ang chi te chu nasa takin a tihziaawm thei a ni. Tin, nunphung hrisel neih te, zu leh zu in loh te, zunthlum ang chi natna te control a pawimawh hle bawk. Zawhna emaw rinhlelhna emaw i neih chuan doctor nen inbia ngei ang che. A tul angin thurawn an pe ang che.
` Iniencephaly, nau piangsual, neural tube chhiatna, folic acid, naupai, pianpui











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