Nu thar emaw, pa thar emaw i nih chuan i naupang tê i ngaihtuah nasat zia chu ka hria. A châng chuan i naute vun chu a sen vek tih i hmuh chuan i hlau mai thei. Hei hi jaundice an ti a. A tam zawkah chuan a pawi lo hle a, mahse a chang chuan, he jaundice hi a na zual chuan naute thluak a tichhe thei a ni. Chu chu tunlaia kan sawi tum chu a ni a, chu chu kernicterus an ti a ni.
Kernicterus chu eng nge ni?
A awlsam zawngin sawi ila, Kernicterus hi natna hlauhawm tak a ni a, i naute thisenah hian thil sen (yellow substance) bilirubin (hei hi hyperbilirubinemia kan ti a) a tam lutuk a, chu chuan naute thluak a tichhe thei a ni.
Tunah chuan he bilirubin hi eng nge a nih i ngaihtuah mai thei? Kan taksaa thisen sen (red blood cells) a chhiat avanga lo awm thin yellow waste product a ni. A tlangpuiin kan thin hian he bilirubin hi taksa atangin a paih chhuak thin. Mahse a chang chuan, a bikin nausen piang tharah chuan thin (liver) hian a paih chhuak tha thei lo. Tichuan bilirubin chu thisenah a pung khawm a, chu chuan naute vun, mit var, hmui leh lei hnuaia mucous membrane te chu a sen vek a ni. Chu chu jaundice kan tih chu a ni .
Kernicterus symptoms hi a lo lang zauh zauh thin. Jaundice bakah hian nau piang tharte hian thinrimna, hnute pek duh lohna leh seizure an nei thei bawk. A natna a nasat chuan naute chuan hriatna a hloh thei a, thluak pawh a tichhe vek thei bawk. Chuvangin i nausen piang tharte nungchang leh hmel lan danah danglamna i hmuh chuan Doctor i pan nghal tur a ni.
A chang chuan doctor-te chuan he natna hi ‘Bilirubin Encephalopathy’ tiin an sawi thin tih i hre tawh mai thei.
Kernicterus hi engtiang chiahin nge a awm?
Nausen piang tharah hian jaundice hi a tam hle. Mahse, doctor-te chuan nau piang thar jaundice chungchangah an fimkhur reng a, chu chuan kernicterus-a a lo awm theihna a ti tlem a ni. Chuvangin kernicterus hi a awm lo hle a ni.
Hei hian naute piang tharte a nghawng tam ber nachungin, puitlingah pawh a awm thei a, a tlem hle.
Kernicterus natna lan chhuah dan chu engte nge ni?
Kernicterus chhinchhiahna hmasa ber chu jaundice a ni . I naute hian jaundice a neih chuan a hnuaia hmunte hi a sen angin a lang ang:
- Naute vun a ni.
- Mit a var lai chu.
- Kawng chhunga membrane nalh tak tak (gums leh lei hnuai lam ang chi).
Doctor-te chuan naute pian hnu kar khat atanga kar thum chhungin he natna hi an hmuchhuak thei a ni.
Jaundice bakah hian kernicterus hian heng symptoms te hi a nei thei bawk:
- Lethargy , mut theih lohna.
- Khawsik.
- Luak chhuak.
- Duh loh vanga taksa ruh (muscle movement) te.
Heng symptoms te hi a natna nasat dan azirin a danglam thei a, chu chu kernicterus stage hrang hrang a ni.
Kernicterus-a stage hrang hrang
Kernicterus hi stage lian pathum a awm a. Stage tinah hian symptoms a inang lo vek.
- A tir lamah: Chaw ei leh hnute pek harsatna, mutthilh, taksa ruh (muscle tone) tlahniam, startle reflex tlahniam . Ngaihtuah teh, naute chu nunna nei lo mai mai a ni.
- Middle stage: thinrimna, au ri nasa tak, a chang chuan tap ri sang tak, taksa ruh (muscle tone) sang. Naute chu a rilru a hahdam lo mai mai niin a lang.
- Late stage: Duhthusamin hnute pek chu a tawp vek a, taksa ruhte chu a nghet lo va, taksa chu hnunglam hawiin a hnunglam hawiin a hnunglam hawiin a awm a, convulsions a awm bawk. Hei hi a hlauhawm ber leh nunna atana hlauhawm ber a ni .
I naute hian jaundice leh a chunga kan sawi tak symptom dangte a neih chuan doctor pan nghal vat tur a ni.
Kernicterus natna chhante chu engte nge ni?
Kernicterus awm chhan ber chu hyperbilirubinemia , nausen piang thar liver-in bilirubin a paih chhuah dik loh vang a ni.
Hetianga bilirubin a pun theih chhan hi chhan hrang hrang a awm a:
- Polycythemia: Hei hian taksaa thisen sen (red blood cells) a pun lutuk tihna a ni.
- Hemolysis: Hei hi thisen sen (red blood cells) tihchhiatna a ni. Hei hi cell nun chhunga thil thleng pakhat angin a thleng tlangpui. Mahse, a châng chuan heng cell te hi a chhe rang lutuk emaw, a tam lutuk emaw pawh a ni thei.
- Nau piang laiin hliam: Naute a pian hian lu vun hnuaiah thisen a awm khawm thei (cephalohematoma) , vun leh luruh inkarah thisen a chhuak (subgaleal hemorrhage) , a awm thei bawk.
- Naute thisen cell tichhe thei damdawi lam dinhmun: Entirnan , Rh hemolytic disease , emaw, naute thin (liver) tichhe thei dinhmun, Crigler-Najjar syndrome ang chi emaw.
Liver-in bilirubin chu bawlhhlawh a paih chhuah theih loh chuan thisenah a pungkhawm a, chumi hnuah thluak tissue-ah a kal leh thin. Hetiang hian bilirubin hi thluaka a thleng a nih chuan harsatna lian tak a thlen thei a ni.
Kernicterus hian hun rei tak chhunga nghawng leh harsatna a neihte chu engte nge ni?
Kernicterus vanga harsatna awmte hi a chang chuan nunna atana hlauhawm tak a ni thei a, hun rei tak chhung nghawng a nei thei bawk. Chung zingah chuan:
- Hriatna hloh.
- Cerebral palsy natna a niThil awmdan chu.
- Cognitive development lama harsatna awm thei .
- Thluak a tichhe vek.
- Coma ah a awm.
Hengte hi hriat tur hlauhawm tak tak a ni. Mahse, heng natna khirh tak takte hi a hmaa hriatchhuah leh enkawl a nih chuan ven theih a ni tih hre reng ang che.
Tute nge Kernicterus vei theihna hlauhawm zawk?
I naute piang thar chu kernicterus vei theihna a sang zawk thei a, chu chu:
- Nausen piang tharin jaundice a neih chuan.
- Naute vun rawng hi a dum deuh a nih chuan a vun sen (hetiang natna chhinchhiahna hmasa ber a ni) hriat a harsa mai thei. Hei hi a bik takin i fimkhur tur a ni.
- Kar 37 hmaa naute piang chu preterm baby an ti a.
- Chaw i ei \ha lo a nih chuan i ek chhuah \ha thei lo ang (bilirubin hi ek nen taksa atangin a chhuak \hin).
- Chhungkaw zinga mi pakhatin nausen laiin jaundice a vei a nih chuan (biological family history).
Nausen hrisel tak tak pawhin jaundice an nei thei. Mahse, jaundice hi a nasat chuan kernicterus a thlen thei a ni.
Engtin nge Kernicterus hi an hriat theih?
Doctor chuan naute hian kernicterus a nei em tih chu taksa enfiahna leh test thenkhat hmangin a hre tlangpui. Test lian pahnih neih a ni a, chungte chu:
- Light meter test: Hei hian i naute vunah êng pakhat chu hmanraw bik hmangin a ti eng a ni. Naute vun atanga light a rawn bounce dan leh device-a a kir leh dan hi bilirubin level chhiar nan hman a ni. Hei hi test hrehawm lo leh awlsam tak a ni.
- Bilirubin thisen test: A natna hriat chian nan doctor chuan i naute kekawr atanga thisen sample te tak te a la ang a, lab-ah a thawn ang a, bilirubin awm zat a teh ang.
A châng chuan, lu ultrasound scan, CT scan , emaw MRI scan ang chi thilte pawh tih theih a ni. Mahse an tul lo. Chutiang symptom nei condition dang a awm loh nan chauh an ni.
Kernicterus thlentu bilirubin level hi engzat nge ni?
Doctor chuan i naute thisenah Total Serum Bilirubin (TSB) level a teh ang a, kernicterus a awm leh awm loh a enfiah ang. A tlangpuiin TSB level hi 0.1 leh 1.2 mg/dL (deciliter khatah milligram) inkar a ni tur a ni. Jaundice symptoms hi TSB level 2.0 mg/dL vel a nih chuan a lang tan thin. TSB level 25 mg/dL aia sang chu a sang hle nia ngaih a ni a, kernicterus anga ngaih a ni. Test result chungchangah harsatna i neih chuan doctor zawt rawh.
Kernicterus hi engtin nge enkawl a nih?
Kernicterus hi enkawlna hrang hrang a awm a. Doctor chuan naute dinhmun a zirin enkawl dan tur dik ber a ruat ang.
- Phototherapy: Hei hian naute vunah ultraviolet light eng tak tak eng chhuak a ni. Heng light te hi damdawi lamah a him a, naute a tichhe lo. Naute chu khumah dahin, a eng chu naute vun lam a hawi a ni. Enkawl lai hian naute mit chu a khuh vek a. He light hian bilirubin chu taksa atanga awlsam taka paih chhuah theih turin a thlak danglam thin.
- Thisen inthlengna: Hei hian naute thisen ngei lakchhuah a, a aiah thisen petu thisen leh/ emaw plasma hmanga thlak a huam a ni. Doctor chuan naute kut chhunga vein pakhatah tube te tak te emaw, umbilical stump chhunga catheter emaw a dah lut a. Hei hi thisen a bilirubin awm zat tihtlem thuai nan tih a ni.
- Intravenous Immunoglobulins (IVIG): I naute hian Rh natna ang chi natna avanga bilirubin level sang tak a neih chuan doctor chuan IVIG a pe thei ang. Hei hi antibody therapy a ni. I naute kut chhunga vein pakhatah saline solution angin pek a ni.
Heng enkawlnate hi a hlauhawm deuhin a lang thei a, mahse naute chu natna khirh tak atanga chhanchhuahna atana tih a nih thu hriat reng a pawimawh.
Naute enkawl hnua a dam leh theih nan eng chen nge a mamawh?
Naute a dam leh theih nan kar hnih vel a la ngai thei. Amaherawhchu, naute dinhmun hi a tawp lam a nih a, thluak a chhiat tawh chuan a chhiatna chu a let leh thei lo mai thei. Chutiang a nih chuan, naute chu a lo puitlin chhoh zêl a, chu natna chu a tuar theih nân enkawlna leh ṭanpuina a awm a ni.
I naute chu chaw tha tak pein a dam thuai theih nan i pui thei ang. Naute kernicterus nei chuan hnute pek harsatna a nei thei. I doctor chuan naute hnena ei tur mamawh pek dan tur a hrilh ang che. I naute chu a poop dik theih nan chaw tha pek a ngai a ni. Pooping hmang hian bawlhhlawh bilirubin ang chi chu taksa atanga paih chhuah a ni.
Kernicterus-a hmalam hun chu eng nge ni?
I naute hi kernicterus natna hmasa ber emaw, a laiah emaw enkawl a nih chuan a dam kim thei a ni. Mahse, naute kernicterus natna hnuhnung zawkte chuan nunna atana hlauhawm harsatna an nei thei a ni. I naute dinhmun hriat belh duh chuan i doctor nen inbia ang che.
A tam zawkah chuan nau piang tharte jaundice hi a nasat a, kernicterus-ah a chan hmain doctor-te chuan an hmuchhuak a, an enkawl thin. Chuvangin kernicterus hi a awm lo hle a ni.
Naute chu kernicterus atang hian a dam kim thei ang em?
Awle,Naute chu a hmaa hriatchhuah leh enkawl a nih chuan kernicterus natna atang hian a dam kim thei a ni. Mahse, naute dam lehna rate chu a natna stage leh a chhan hrang hrangah a innghat a ni.
Kernicterus hi a veng thei ang em?
Kernicterus thlentu zawng zawng hi ven theih a ni lo. Mahse i nautein kernicterus a vei theihna tur chu a hnuaia mi ang hian i tih hian i ti tlem thei ang:
- I naute pian hnuah jaundice a awm leh awm loh fimkhur reng ang che. I naute taksa khawi hmunah pawh rawng sen (yellow discoloration) i hmuh chuan doctor pan nghal tur a ni.
- I nau piang thar enkawlna tur appointment te chu lo thlir ve suh. Hengte hi i naute hi a hun hmaa piang a nih chuan a pawimawh hle.
- I naute hian jaundice a vei a nih chuan doctor kaihhruaina hnuaiah enkawlna zawng rawh. Doctor chuan a tul chuan enkawl dan tur thurawn a pe ang.
A pawimawh ber chu i naute pianhmang emaw nungchang emaw a danglamna tlemte pawh i hmuh chuan, ngaihthah lovin, doctor hnenah hrilh mai tur a ni.
Engtikah nge ka naute hi doctor hnenah ka hruai ang?
I naute piang thar vun, a mit var emaw, a ka chhung lam emaw a sen a nih chuan a pian tirh atanga kar hmasa berah doctor pan a pawimawh. Nausen piang thar zingah jaundice hi a awm fo a, mahse bilirubin level sang chuan nunna a tichhe thei a ni. Doctor chuan i naute chu a enfiah ang a, a bilirubin level a enfiah ang a, a hrisel em tih a enfiah ang.
Engtikah nge ka naute hi emergency treatment unit (ETU) ah ka hruai ang ?
I naute hian jaundice leh kernicterus symptom dang, seizures ang chi a neih chuan 911 call nghal la, emaw, i naute chu emergency room hnai berah hruai rawh. Emergency-a fimkhur tur chhinchhiahna dangte chu:
- Naute chuan a taksa chu thal ang maiin a ben a, a lu chu hnunglam a hawi a, a taksa nen "C" angin a siam a nih chuan.
- Non-stop-a i tap a nih chuan, emaw aw sang taka i au chuan.
- Meatballs chu a danglam bik taka khauh a nih chuan, a nih loh leh meatballs chu a chak lo ang tih a hriat chuan.
Hetiang hunah hian hmalak vat a pawimawh a, hlauhthawn loh a pawimawh.
Ka naute doctor hnenah eng zawhna nge ka zawh ang?
I naute chungchanga i rilruah eng thil pawh i doctor zawh hlau ngai suh. Zawhna i zawh theih ṭhenkhat chu hetiang hi a ni:
- Nausen piang thar hian engzat nge medical checkup a neih ang?
- Ka naute hian eng stage nge kernicterus a neih?
- Enkawlna hian side effect a nei em?
- Ka naute hian engzat nge phototherapy a mamawh?
- Kernicterus hian ka naute thluak a nghawng em, hun rei tak chhung harsatna a thlen em?
Nausen piang thar nu leh pa i nih angin i naute vun leh mit a sen a nih chuan hlauhna i neih hi thil pangngai a ni. I naute hian i control theih loh leh i siam that theih loh symptoms a lantir lai pawh en a harsa hle. Jaundice hi a hluar hle laiin, kernicterus – naute thisena bilirubin tam lutuk avanga jaundice natna khirh tak – chu chutiang chuan a awm lo. Thil dik lo nia i hriat chuan i naute doctor hmu la, i naute tan thu sawi rawh. Kernicterus hnuah harsatna a awm thei a, mahse i naute chu a thanlen theih nan dam chhung zawnga tanpuitu a awm. A hmaa hriatchhuah leh enkawl a nih chuan i nausen piang thar chu a dam leh thei a ni.
Thu tawite hriat reng tur
Okay, chuvangin Kernicterus chungchanga kan sawi tawh pawimawh ber berte kha han thlir let leh ila.
- Kernicterus hi natna awm lo mahse hlauhawm tak a ni a, nausen piang thar thisena bilirubin level a san lutuk chuan thluak a tichhe thei a ni.
- Hei hi a lan hmasak ber chu jaundice - vun leh mit sen (yellowing) a ni .
- Jaundice bakah hian i naute chu a muhil a, a hnute a pe duh lo a, a thinrim a, a taksa a khauh a, a seizure a nei a nih chuan doctor pan nghal tur a ni.
- A hmaa hmuhchhuah a, enkawl a nih chuan (phototherapy leh exchange transfusion ang chi) naute chu a dam vek thei a ni. A tlai lutuk chuan thluak a tichhe reng thei a ni.
- Naute pian hnuah jaundice lakah fimkhur rawh. Doctor thupek zawm rawh.
- Ringhlelna i neih chuan doctor biak hreh ngai suh. I naute venghimtu tha ber i ni.
He thu hi i tan a tangkai ngei ka beisei. Nang leh i fate hriselna tha kan duhsak a che!
` Kernicterus, Bilirubin, Jaundice, Nau piang thar, Thluak chhiatna, Hyperbilirubinemia, Naute hriselna











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