I fate mit chu a tlangpui aia tlem a inthlau tih i hmu ngai em? A nih loh leh doctor in a hrilh che em? Damdawi lam hawi chuan he natna hi Orbital Hypertelorism kan ti a ni. A chang chuan Ocular Hypertelorism an ti bawk. Heng thute hi hlauhawm tak ni thei mah se, hei hi kan ngaihtuah angin a pawi lo hle. Vawiin hian he thu hi awlsam takin, in hriatthiam theih angin kan sawi dawn a ni.
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Orbital Hypertelorism hi eng nge ni tak tak?
A awlsam zawngin Orbital Hypertelorism hi natna hran a ni lo. Piansualna dang emaw, genetic disorder emaw chhinchhiahna angin a awm tlangpui.
Ngaihtuah teh, nausen pum chhunga a awm lai hian a hmai ruhte chu zawi zawiin a pianzia a lo chang ta a ni. Hetih lai hian a mit dahna mitmeng pahnih chu a tlangpui aia hla deuhah a awm a. Chuvang chuan naupang pangngai aiin mit inkar hi a lang tam zawk a ni. He hmun tihpun hi ruh dangin a khat a ni.
A pawimawh ber chu hetiang mit inhlat naupang tam zawk hian mit lamah harsatna an nei lovang. Mit a nghawng leh nghawng loh chu mit inhlat dan leh naupangin symptom dang a neih danah a innghat a ni.
Engtin nge doctor-te hian hei hi an hriat chian tak tak?
A tlangpuiin doctor chuan naute a pian veleh he natna hi a hmuchhuak nghal thin. A châng chuan, naute pum chhunga a la awm laiin ultrasound scan-ah pawh hriat theih a ni.
Mit inkar hlat zawng ruat a awm lo a, mahse doctor-te chuan hei hi tehna lian pahnih an hmang a ni.
| A tehna hmanrua | A awlsam zawngin sawifiah a ni |
|---|---|
| Canthal chhung lam hlat zawng | Mit pakhat hnar hnaih ber kil atanga mit dang hnar hnaih ber kil thlenga hlat zawng. |
| Pupillary atanga hlat zawng | Mit pakhat pupil lairil atanga mit dang pupil lairil thlenga hlat zawng. |
Heng tehna pahnih hi naupang orbital hypertelorism nei tan chuan a tlangpui aia sang a ni.
Engvangin nge hetiang hi a lo awm? A chhan berte chu engte nge ni?
Doctor-te chuan he natna dinna lungphum hi naute pian tirh atanga kar lina leh kar riat inkar inkarah an phum niin an ngai. Naute luruh ruhte chu three-dimensional (3D) puzzle chi hrang hrang inzawmkhawm angin ngaihtuah rawh. Heng piece hrang hrangte dahkhawmna atana step hrang hrang tihbuai emaw, inthlak danglamna emaw a awm chuan mitmeng pahnih chu a inmil lo thei a, a inhlat thei hle.
Hei hi a chhan lian ber pahnih chu:
1. Nau piangsualna
2. Genetic lama harsatna awm thei
1. Pianpui natna
Nausen pian tirh laia a taksa pianphung, chhungril lam emaw, chemical process-a thil awm dan dik lo, piansualna chu a ni. Chûngte chu:
- Genetic leh hereditary factors te a ni.
- Naupai laiin nuin a kai thin infection thenkhat.
- Radiation laka invenna.
- Naupai laia ruihhlo emaw zu emaw hman.
A châng chuan nau piangsualna hi chhan hriat lohvin a awm thei a, a lo thleng mai thei bawk. Chutiang piansualna pakhat chu Craniosynostosis hi a ni. Heta thil thleng chu naute luruh ruh inzawmkhawmtu suture te chu an fuse khawm a ni. Hei hian Orbital Hypertelorism a thlen thei bawk.
2. Genetic lama harsatna awm thei
Genes hi DNA unit te tak te, kan taksa chhunga cell awmte hnena thupek pe thin a ni. Heng genes-a mutations hian genetic disease a thlen thei a ni. Orbital hypertelorism thlen thei genetic natna thenkhat chu:
- Apert natna a ni
- DiGeorge natna a ni
- Edwards natna a ni
- Crouzon natna (Crouzon syndrome) a ni
- Noonan syndrome a ni
- Neurofibromatosis chi khat a ni
I fain he natna hi a neih chuan i doctor chuan genetic counseling atan a refer thei che a, chu chuan i chhungte’n genetic disease an vei theihna tur an hriatthiam theih nan a pui thei che a ni.
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Hetiang natna nei naupangte hian an mit chu operation hmangin an inzawm khawm leh thei a ni. Hei hi reconstructive surgery an ti a . He surgery hi naupang kum 5 leh kum 7 inkar a nih chuan tih a ni tlangpui. He surgery hian naupang chu a lan dan pangngai zawk a pe a, mit inkar hlat zawng a ti tlem bawk.
I fa chu operation hma leh operation hnuah mit enfiahna neih fo a ngai ang a, chu chuan mit leh mit hmuhna lama inthlak danglamna a enfiah ang.
Chumi atan chuan surgeon-te chuan surgical technique pahnih an hmang ber a ni.
| Surgery chi hrang hrang | Eng thil nge thleng? |
|---|---|
| Box Osteotomy tih a ni | Hetah hian surgeon chuan hnar chunga ruh leh vun tam lutuk chu a paih chhuak a, chu hmuna awm turin mitmeng chu a siam thar leh thin. Mitmeng leh hnar chung lamah square ang chi section pakhat chu cut la, chu square chhungah chuan mitmeng chu i rawn luhtir ang tih han ngaihtuah teh. |
| Hmai lam Bipartition | Hei hi surgery buaithlak deuh a ni. Naupang orbital hypertelorism leh hmai ruh lama harsatna dang (e.g., jawbone, cheekbones) nei te chungah tih a ni. Mit inhnaih zawka siam turin mit zungbun, hnar leh hmui ruhte siam thar a ngai a, chutih rualin hmui leh ha lama harsatna awmte pawh siamthat a ni bawk. |
Operation hnua harsatna awm thei
Surgery dang ang bawkin, risk tlemte chauh a awm. Chung zingah chuan:
- Thisen chhuak
- Infection awm thei te
- Scarring a awm
- Mitmeng tla ( Ptosis ) .
- Diplopia (mihring pahnih) 1.1.
- Mitdel emaw mitdel emaw (hei hi a tlem hle) .
I surgeon chuan heng hlauhawmnate hi chipchiar takin a hrilhfiah ang che.
Engtikah nge doctor i hmuh ang?
I fa mit emaw, mit hmuh danah emaw danglamna i hmuh chuan doctor pan nghal rawh.
Tin, i fain a hnuaia symptoms te hi a neih chuan damdawi in hnai ber Emergency Department (ETU) ah kal nghal rawh.
- Mit hmuhna hloh emaw tlahniam nghal emaw.
- Mit natna nasa tak.
- Mit hmaa flash emaw floater thar emaw hmuh.
Naute chu Orbital Hypertelorism neia piang a nih vang mai mai chuan naupang dang angin hrisel leh tha takin an seilian dawn lo tihna a ni lo tih hre reng ang che. A chhan bulpui (underlying condition) a zirin i naute hian hun engemaw chen chu enkawlna a mamawh thei a ni. Chumi chungchang chu i doctor nen sawiho rawh.
Take-Home Thuchah a ni
- Orbital Hypertelorism hi natna hran a ni lo. Piansualna dang emaw, genetic condition dang emaw chhinchhiahna a ni.
- Hetiang natna vei naupang tam tak hian mit lamah harsatna an nei lo.
- Naupang kum 5-7 vel a nih chuan mit chu a inthlauhna pangngaiah hruai kir leh turin operation tih theih a ni.
- I fa hian he natna hi a nei a nih chuan i doctor nen zalen taka inbiakna neih hi hlau suh la, a tul anga thurawn leh enkawlna dawng rawh.
- A hun taka Doctor hmuh leh mit enfiah a pawimawh hle.
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