A châng chuan chhan awm lovin i chau a, i chau bawk em? A nih loh leh doctor-in i thisen test report a en a, "I thisen sen (red blood cells) pianzia a danglam deuh a?" Chutiang hunah chuan thumal kan hriat zinga pakhat chu (Poikilocytosis) (a lam tur: poi-ki-lo-say-to-sis) a ni. He hming i hriat hian hlau lutuk suh. Hei hi natna a ni lova, kan taksa chhungah thil dang a awm tih chhinchhiahna a ni thei. Chuvangin, hei hi hriat chian a pawimawh hle.
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(Poikilocytosis) tih hi eng nge ni tak tak?
A awlsam zawngin Poikilocytosis tih hian kan thisena thisen sen (red blood cells) tam tak (chu chu 10% aia tam) chu a pianzia danglam tak a ni tihna a ni. Tunah chuan, "Chuti a nih chuan engvangin nge thisen sen (red blood cells) pianzia hi a pawimawh?"
Ngaihtuah teh, kan taksa chhunga cell, tissue leh organ dang zawng zawng hian nung leh hnathawh theihna turin chakna an mamawh vek a ni. Chu chakna chu oxygen-in a pe a ni. Tuin nge hria ang, he oxygen hi gas cylinder in lama hruai ang mai hian taksa pum puiah a phur lut vek a ni? Chu chu kan thisen sen (red blood cells) a ni. A tlangpuiin thisen sen hrisel tak i ei chuan an lian leh te, an pianzia inang vek an ni. Pawisa zungbun (disk ang chi) a sir lehlamah a hrual deuh ang mai.
Chuvangin, heng thisen sen hringte pianzia a inthlak ((Poikilocytosis)) emaw, a lian leh te a inthlak ((Anisocytosis) tih hming pu dang a awm) emaw chuan oxygen an phur tha thei lo. Chu chu anemia (thisen chhunga thisen awm lohna) ang chi condition kan neih hun a ni. Chumi awmzia chu taksa cell-te hian oxygen an hmu tling lo tihna a ni a, chu chu chakna tihna a ni.
Thisen sen (red blood cells) pianzia dik lo chu engte nge ni? (Poikilocytes) te hi a awm a.
Doctor-te chuan heng thisen sen hring (Poikilocytes tia koh bawk) te hi an pianzia a\angin an thliar hrang \hin. Thisen sample-a (Poikilocytosis) i neih chuan a hnuaia mi pakhat emaw a aia tam emaw i hmu thei ang:
- Acanthocytes / Spur cells : Hengte hi hling hnah ang mai an ni. Cell membrane atanga chhuak, spike ang chi protrusions sei tak, zau tak tak an nei a.
- Codocytes / Target cells : Hengte hi target board ang maia lang. A laiah chuan dark circle a awm a.
- Dacrocytes / Mittui tla cell : Mittui tla ang chi. Cell sir khat chu a hring a, a hrual bawk.
- Drepanocytes / Sickle cells : Hei hi cell te tak te, sickle ang maia lian, sickle cell natna vei te zingah hmuh theih a ni.
- Echinocytes : Tuipui urchin ang bawkin a cell hi a chhung zawngah a hlat zawng inang vek, ruhroin a khuh a.
- Elliptocytes / Ovalocytes emaw Cigar cells : Hengte hi oval ang maia sei leh sei danglam tak an ni. Egg ang atanga cigar ang thlengin an lian thei hle.
- Schistocytes : Hei hi thisen zam (red blood cells) chi hrang hrang (fragments) a ni. An hmel chu rough, broken appearance an nei fo a, mahse eng ang chi pawh an ni thei.
- Spherocytes: A zungpui (Spherocyte) a ni. Ball te tak te ang maiin.
Heng chi hrang hrangte hi damdawi lam dinhmun bik nen a inzawm thei a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
Poikilocytosis natna lan chhuah dan hi a chhan a zirin a inang lo. Amaherawhchu, a lan chhuah fo te hi thisen tlakchham vanga a lan chhuah dan nen a inang reng a ni.
Thisen tlakchhamna chhinchhiahna thenkhat chu hetiang hi a ni:
- Chak lohna emaw, hah lutuk emaw (chau tih hriat mai mai).
- Thâwk harsa (dyspnea) – hna tê tê thawk pawha thawk harsa.
- Thinlung thawk chak emaw, mumal lo emaw (arrhythmia).
- A chang chuan i beng bulah "whooshing" ri (pulsatile tinnitus) i hre thin.
- Lu na .
- Luak chhuak .
- Vun dum hring .
- A rilru a na .
Heng symptoms pakhat emaw a aia tam emaw i neih chuan doctor thurawn lak a tha ber.
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Heng thisen sen hring pianzia dik lo awm chhan hi chi hnih ah then theih a ni: inherited leh acquired . Condition thenkhat, Myelodysplastic Syndrome te hian a pahnih hi a thlen thei a ni.
Rochun Conditions te
A tam zawkah chuan congenital causes hi thisen sen pakhatin a lo thang lian a, a thawk tha a, a dam theih nan a mamawh genetic information (DNA) a dik lo vang a ni. Chutianga insiam dan pangngai lo nei thisen sen (red blood cells) te chu taksain cell thar a siam hmain an chhe nghal vat thin. Hei hi hemolytic anemia an ti a .
(Poikilocytosis) thlentu pianpui natna thenkhat:
- (Hereditary Elliptocytosis) tih a ni
- (Hereditary Spherocytosis) tih a ni
- (McLeod Syndrome) tih a ni
- (Pyruvate Kinase tlakchhamna)
- (Sickle Cell Natna) (Sickle Cell Natna) .
- (Thalassemia) tih a ni
Chûngte chu thlah kal zelah an lo inthlâkthleng fo ṭhîn.
Acquired Conditions te chu a ni
Hun a kal zel a, damdawi lam dinhmun thenkhat chuan thisen sen (red blood cells) pianzia a tidanglam thei bawk. Entirnan, taksain thisen zam hrisel siamna atana a mamawh nutrients, vitamin B12, folate, leh iron te a hmuh loh chuan thisen tlakchhamna chi hrang hrang a awm thei a ni. Poikilocytosis hi heng ei leh in lama tlakchhamna chhinchhiahna tlanglawn tak a ni. Natna, cancer thenkhat ang chi, thisen zam (red blood cell) siam chhuah tibuaitu vang pawh a ni thei bawk.
A hnu lama (Poikilocytosis) thlentu thenkhat chu:
- Autoimmune Hemolytic Anemia atanga lo chhuak a ni
- Kang (a zau a nih chuan) .
- (Celiac Natna)
- Infection chi hrang hrang
- Iron tlakchhamna avanga thisen tlakchhamna
- Kidney Natna a awm
- Leukemia (thisen cancer) 1.1.
- Liver Natna a awm
- Megaloblastic anemia (vitamin B12 emaw folate tlakchham vang emaw) .
- (Myelofibrosis natna) tih a ni
- Poisoning (e.g. lead) a awm thei.
- Thisen pek a nih chuan a chhân lêtna
- Splenectomy tih a nih chuan a chhanna
- Rul seh a ni
Hei hian eng harsatna nge a thlen theih?
Poikilocytosis thlentu dinhmun tam tak chu enkawlna hmangin enkawl theih a ni a, thenkhat chu tihdam vek theih a ni bawk. Mahse, enkawl loh chuan natna ṭhenkhat chu a nasat phah thei a, nunna atana hlauhawm pawh a ni thei. Entirnan, thisen tlakchhamna (anemia) i neih chuan i chau lutuk a, nitin hna i thawh theih loh khawpin i chau mai thei. Hun kal zelah thisen sen hrisel tak tak i hloh chuan organ failure ang chi dinhmun a thlen thei a ni .
A bik takin naupang tê têteah chuan thisen tlakchhamna enkawl loh a awm chuan an thanlenna leh an thanlenna a nghawng thei a ni.
Chuvangin, i doctor chuan i Poikilocytosis awm chhan dik tak a hriat chian hnuah, heng ang harsatna lo thleng tur venna tur hian a tul ang ang chu a pe ang.
Engtin nge hetiang chiah hian i diagnose? (Diagnosis) tih a ni.
Doctor-in poikilocytosis a hriat theihna atana a hman theih test ber chu peripheral blood smear (PBS) a ni. Hei hian lab technician pakhatin i thisen sample drop khat a la a, microscope hmangin a en a ngai a ni. Chumi hnuah chuan i thisen sen (red blood cells) engzat nge a pianzia danglam tak tih leh eng ang chi nge an nih tih an hmu thei ang.
Cell chi thenkhat chu natna chi hrang hrangah a tam zawk. Mahse, natna dinhmun inang chhungah pawh cell chi hrang hrang a awm thei. Entirnan, (Hemolytic Anemia), (Megaloblastic Anemia), (Myelofibrosis), (Thalassemia) ang chi dinhmunah chuan cell chi hrang hrang pangngai lo engemaw zat hmuh theih a ni.
I doctor-te chuan i poikilocytosis thlentu dik tak hriat tumin test engemaw zat an tih belh a ngai mai thei.
(Poikilocytosis) awm chhan hriat nan test dang neih belh a ni
Thisen chhiar kimchang (CBC) hi PBS nen an ti fo thin. CBC hian i thisena cell awmte chungchang tam tak a pe thei a, an level leh size te pawh a pe thei bawk. CBC-a value thenkhat hian thisen sen chungchang hi a hriat belh theih a, hei hian Poikilocytosis awm chhan hriat theihna kawngah a pui thei a ni. Heng hlutnate hi a hnuaia mite hi a ni:
- Mean Corpuscular Volume (MCV) : I thisen sen zat zat zat.
- Mean Corpuscular Hemoglobin (MCH) : I thisen sen chhunga hemoglobin awm zat zatve.
- Corpuscular Hemoglobin Concentration (MCHC) awm zat zat''.: I thisen sen (red blood cells)-a hemoglobin awm zat zat (average value).
- Red Cell Distribution Width (RDW) : I thisen sen (red blood cells) te hi engtiang chiahin nge a lian dan a inang lo.
Chu bâkah, i doctor chuan i vitamin B12, folate, leh iron level a enfiah thei a, liver function test pawh a ti thei bawk.
Hei hi eng enkawlna nge ni?
Enkawlna chu i poikilocytosis awm chhan leh i natna lan chhuah dan a nasat danah a innghat a ni.
Hetiang dinhmun lo awm chhan hi ei leh in lama harsatna (e.g. iron, vitamin B12 tlakchhamna) a nih chuan, ei leh in lama a kaihhnawih ei emaw, vitamin B12 emaw folate emaw tamna ei leh in lama inthlak emaw hian he (Poikilocytosis) dinhmun hi a titawp thei fo tih hre reng ang che.
Congenital condition tam tak hi uluk taka enkawl a ngai a ni . Thisen sen hrisel tak tak i neih theih nan thisen pek fo i mamawh mai thei. A nih loh leh symptoms i neih leh neih loh a zirin enkawlna chauh i mamawh mai thei bawk.
Hetiang dinhmun hi ven theih a ni em?
Poikilocytosis hi pianpui atanga lo awm thei chu kan veng thei lo.Mahse, a hnu lama lo awm thei thenkhat chu kan tihtlem thei a ni.
I thisen sen (red blood cells) enkawl dan tha ber pakhat chu i taksain a siam chhuah theihna tura a mamawh nutrients te i hmuh hi a ni. B vitamin, folate, leh iron te i ei tlem em tih enfiah rawh . Hengte hi i taksain thisen sen hrisel tak siamna atana a mamawh thil pawimawh tak takte an ni. Zu in tam lutuk tihtlem nan a pui bawk . Zu in tam lutuk hian i taksain heng nutrients te hi a hip harsa zawk thei a ni.
Nakin hun chu eng nge ni ang? (Hmuh dan tur) .
A tlangpuiin (Poikilocytosis) awm chhan hi a hnu lama lo awm a nih chuan prognosis a tha tlangpui. Congenital causes a nih chuan a hnuaia condition a zirin prognosis a inang lo. Entirnan, (Sickle Cell Disease) vei te dam rei zawng hi a tlangpuiin rei lo teah ngaih ni mahse, tunah chuan enkawlna thar hmangin kum 50 chuang dam theih a ni tawh a, chutih rualin a natna lan chhuah dan chu control theih a ni ta.
Engtikah nge Doctor i hmuh ang?
Anemia symptoms (kan sawi tawh, hahna leh chak lohna ang chi) i neih chuan doctor pan ngei ngei tur a ni.
Hrisel taka i inhriat a, symptom nei lo mah la, kum tin check-up neih a pawimawh. I doctor pawhin i thisen cell a check thei bawk. Thisen test awlsam tak, complete blood count (CBC) ang chi hian hriselna lama harsatna a nasat hmain hriatchhuah leh enkawl a pui thei a ni.
Hei hi Poikilocytosis'' hi natna khirh tak a ni em?
(Poikilocytosis) ngei pawh hi a pawi lo. Mahse, a niDamdawi lam dinhmun hnuaia awm chhinchhiahna a ni thei a, enkawl loh chuan harsatna a thlen thei a ni. Chuvang chuan (Poikilocytosis) thlentu dik tak hriat chian a, a tul chuan enkawlna zawn a pawimawh.
Poikilocytosis hi natna khirh tak angin a lang thei a, mahse chutiang chu a ni lo. Doctor ten i hriselna tehna atana an hman thin i thisen sen (red blood cells) ziarang mai a ni. I thisen sen (red blood cells) a dik lo tih i hriat chuan i doctor hnenah zawh hreh suh. I hriselna a nghawng em tih leh, a nghawng a nih chuan, chu natna tihbo emaw, a hnuaia dinhmun enkawl emaw tura i tih theih dan tur chu a hrilh thei che a ni.
💡 Kan hriat reng tur pawimawh ber berte (Take-Home Message) .
Okay, chuti a nih chuan, kan sawi tawh atanga hriat reng tur pawimawh tak takte chu hengte hi a ni:
- Poikilocytosis chu i thisen sen 10% aia tam a pianzia dik lo a nih chuan a ni.
- Hei hi natna a ni lo va, mahse a hnuaia awmte chhinchhiahna a ni thei.
- Hetiang a nih chuan thisen tlakchhamna (chau, chak lohna, vun rawng) symptoms pawh hmuh theih a ni.
- A chhan chu pianpui emaw, acquired emaw (nutritional deficiencies, natna thenkhat) a ni thei.
- Hei hi thisen test awlsam tak (PBS, CBC) hmanga hriat theih a ni.
- Enkawlna chu a chhanah a innghat a, mahse enkawl theih a ni fo.
- Ei leh in hrisel neih hian a hnu lama lo awm chhan thenkhat chu a veng thei a ni.
- Symptoms i neih emaw, rinhlelhna i neih emaw chuan doctor pan a, thurawn lak a tha ber.
Chuvangin, he thu hi i tan a tangkai ngei ka beisei. Hrisel takin awm rawh!
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