I fanu emaw, i fapa emaw chu an kum rualpui naupang dangte aiin tlemin a lo seilian chak zawk ang tih i hre ngai em? Nu leh pa ṭhenkhat chuan an ṭhan chhoh zelna, an aw inthlak danglam, leh puitling ang maia thawmhnaw rim pawh an hmuh hian tlem chuan hlauhna leh lungkhamna an neih hi thil pangngai a ni. Hei hi hlauh tur thil tak tak a ni em? Vawiin hian nu leh pa tam takin an ngaihtuah thin he thu hi kan sawi dawn a, chu chu naupangin kum pangngai a thlen hmaa a puitlin hun a ni.
A awlsam zawngin, precocious puberty chu eng nge ni?
Precocious puberty, damdawi lama
precocious puberty tia hriat chu naupangin kum pangngai aia hmaa puitlin chhinchhiahna a lantir hi a ni. Thil thleng tlangpui chu:
- Hmeichhe naupang chuan kum 8 leh 13 inkar a puitlin tan thin.
- Mipa naupang pakhat chuan kum 9 leh 14 inkarah puitlin hun a paltlang tan thin.
Chuvangin,
hmeichhe naupangin heng kum bithliah hmaa puitlin theihna chhinchhiahna a lantir a nih chuan, chu chu hmeichhe naupang tan kum 8 a tlin hma leh mipa tan kum 9 a tlin hmaa , chu dinhmun chu Precocious Puberty kan ti a ni.
Tlem han hrethiam ila, engtin nge he puitling nihna kalphung hi a lo awm?
Hei hi kan taksaa automatic system ang mai a ni. Ngaihtuah teh, kan thluaka control center lian ber
Hypothalamus . Kum dik tak a thlen chuan he control center hian gland te tak te dang,
Pituitary Gland -ah signal a thawn a ni. Chu signal chu a dawn meuh chuan Pituitary Gland chuan
Gonadotropins tih hormone a siam a, thisenah a chhuah tir ta a ni. Heng hormone te hi naupang gonads tichak turin direct-in an kal a ni.
Puitling laia taksa inthlak danglamna zawng zawng hi heng hormone te hnathawh vang a ni. Precocious puberty-a thil thleng chu he thil zawng zawng hi a hmain a intan a ni.
Hetiang dinhmun hi chi hnih a awm a.
He puitlin hma hi a lo awm dan a zirin chi hnih lian takah then theih a ni. He classification hi a chhan hriatthiam nan a pawimawh hle.
| Lampang | A awlsam zawngin... |
|---|
| Central Precocious Puberty (Central Type) a ni a, a nupui hian a fapa chu a hruai a. | Hei hi a tam ber chi a ni. Heta thil thleng chu thluaka control center (Hypothalamus) chu a hun hmain a thawk chhuak a ni. Thluak chhunga darkar a ri a, alarm a ri hma ang mai a ni. Tichuan kan sawi hormonal process zawng zawng chu a inthlak danglam vek a ni. |
| Peripheral Precocious Puberty (peripheral type) a ni a, a rilru a hah lutuk chuan a rilru a buai em em a. | Heta buaina hi thluak ah a awm lo. Puberty chhinchhiahna hi taksa hmun dang (e.g. ovaries, testicles, adrenal glands) atanga thluak atanga signal awm lovin hormone (estrogen emaw testosterone) siam chhuah vang a ni. |
Engvangin nge naupang chungah hetiang hian a thlen? A chhan engte nge ni?
A chhan chu kan sawi chi hrang hrang a zirin a inang lo.
Central Precocious Puberty (Central Type) awm chhan hrang hrang 1.1.
Hei hian thluak control center chu a hmaa a activate chhan zawn a huam a ni. Mahse
a tam zawkah chuan, a bik takin hmeichhe naupangah chuan a chhan chiang tak hmuh tur a awm lo. Mahse, a châng chuan hetiang thil hi a chhan a ni thei:
- Thluak hliam emaw accident emaw (Brain Trauma ) .
- Brain Tumor chi hrang hrang
- Thluak natna a awm
- Congenital brain abnormalities thenkhat
- Radiation hmanga enkawl mek a ni
Peripheral Precocious Puberty awm chhan te
Hetah hian thluak inrawlhna a awm loh avangin a chhan chu taksa hmun dangah a awm a ni.
- Ovary, testicles , emaw adrenal glands-a lo awm tumor te.
- Genetic condition thenkhat (e.g. McCune-Albright syndrome) a awm bawk.
- Hypothyroidism na tak a awm.
- Adrenal gland natna (e.g. Congenital Adrenal Hyperplasia) a awm thei.
- Pawn lam atanga taksa chhunga hormone lut: 1.1.Hei hi a pawimawh hle. Puitling pakhatin estrogen emaw testosterone emaw awmna cream emaw damdawi emaw a hman a, naupang tê tê chungah a hnawih fo chuan hetiang dinhmun hi a thlen thei bawk tih han ngaihtuah teh.
Eng chhinchhiahna nge kan hmuh?
Heng mizia te hi hmeichhia leh mipa tan pawh a awm ve tho a, pakhat zel tana bik tak tak pawh a awm bawk.
An pahnih a mizia hmuh theih chu:- Acne a awm
- Puitling thawmhnaw rimtui ang maia rimtui
- Taksa than chakna rate sang nghal (Growth Spurt) .
Heng mize tlanglawn tak tak bakah hian mipat hmeichhiatna lam zia te pawh hmuh theih a ni.
| Hmeichhia tan | Tlangval tan |
|---|
| - Hnute hmasawnna | - Aw thuk zawk, tihchhiat |
| - Thlasik tan tirh | - Hmai leh kawrfual sam a lo thang lian |
| - Armpit leh genital area-ah sam a lo thang lian | - Mipat hmeichhiatna hmuna sam sei |
| - Testicles leh penis tihzauh |
| - Taksa thang lian zel |
Hemi a\ang hian harsatna dang lo chhuak thei a awm em?
Ni e, he dinhmun hian naupang chu taksa leh rilru lama harsatna engemaw zat a tawk thei a ni. 1.
A tâwpah a tawi ta: Hei hi nu leh pa tam takin an hriat loh thil a ni. Naupang puitlin hma te chuan a tir lamah chuan an sang chho zel a, mahse an ruh thanna chu a tawp thuai thin. Chumi awmzia chu puitlin hun a tawp meuh chuan an san zawng pawh a pung tawh lo tihna a ni. Chuvangin, a tawpah chuan an kum rualpui naupang dangte aiin an tawi zawk a ni. 2.
Rilru leh khawtlang harsatna: 1.1.Hei pawh hi a pawimawh hle. Naupang pakhatin class-a mi zawng zawng hmaa a taksa a danglam a, naupang dangte aiin a danglamin a inhriat chuan engtin nge a awm ang tih han ngaihtuah teh?
- Mualphona leh mualphona
- Naupang dangte nuihzatthlak taka awm
- Lungkhamna leh lungngaihna ang chi dinhmun
- Mahni kum nena inmil lo taka awm duhna
Chuvang chuan naupang taksa inthlak danglamna bakah a rilrua thil thlengte hi kan fimkhur hle a ngai a ni.
Engtin nge hei hi i hmuh theih, Doctor?
I fa chu doctor hnena i hruai hunah chuan a dinhmun dik tak
hriat theih nan test tlemte a nei ang. Lungngai suh, hengte hi naupang tan chuan a hrehawm lo.
- Taksa enfiahna: A hmasa berin Doctor chuan naupang chu uluk takin a enfiah ang a, i fa hriselna chanchin a zawt ang che.
- Bone Age X-ray: Naupang kut leh ke ruh X-ray te tak te lak a ni. Hei hi naupang ruhte chu an kum tak tak nena khaikhin chuan eng chen nge a puitlin tih hriat nan a ni. Naupang puitlin hma chuan an kum tak tak aiin ruh kum a sang zawk.
- Thisen test: Thisen tlem te chu hormone level (a bik takin pituitary hormone LH leh FSH ang chi) enfiah nan lak a ni.
- MRI emaw Ultrasound Scan emaw: A chang chuan doctor-in a chhan chhui chian belh a duh chuan thluak MRI emaw, pum ultrasound emaw tih a rawt thei bawk. Chûngte chu thluaka tumor awm thei, thluak, ovary, adrenal glands-a tumor awm thei te chu paih chhuah nâna tih a ni. Naupang zawng zawng hian hengte hi an mamawh vek lo.
Heng test neih zawh hian a tul chuan
pediatric endocrinologist hnenah refer i ni thei bawk .
Hei hi eng enkawlna nge ni?
Vanneihthlak takin he natna hi control nan hian enkawlna tha tak tak a awm a. Enkawlna chu a hmaa kan sawi tawh chi (Central emaw Peripheral emaw) leh a chhanah a innghat a ni.
- Central Precocious Puberty tan: Hetah hian thil tum ber chu thluak atanga ‘grow up’ tura signal lo lut chu hun eng emaw chen tihtawp a ni. Chumi atan chuan damdawi chi khat GnRH agonist an tih chu hman a ni. Hei hi thla khatah vawi khat emaw, thla thum danah emaw injection a ni. Darkar-a alarm snooze ang mai a ni. Hetiang enkawlna hi a tan veleh chuan puitlin hun chhinchhiahna chu a tlahniam zauh zauh thin. Naupangin kum dik tak (a tlangpuiin 11-12) a thlen chuan he damdawi hi tihtawp a ni a, chutah chuan a pangngai angin puitlin tan leh a ni. Hei hian naupang chu a san zawng pangngai a neih theihna tur leh rilru lama inbuatsaih theihna hun remchang a siamsak a ni.
- Peripheral Precocious Puberty tan chuan:Hetah hian enkawl dan chu a chhanah a innghat a ni. Hormone siamtu tumor a nih chuan surgery hmanga lakchhuah a ngai dawn a ni. External cream ang chi a nih chuan vawi khat i hman tawh loh chuan a buaina chu a bo vek ang. Enkawl dan tur chu a chhan a zirin thutlukna siam a ni ang.
Engtikah nge Doctor ka hmuh ang?
Hei hi a pawimawh hle. I fain a hnuaia thilte hi a tawk a nih chuan
doctor, a bik takin naupang enkawltu doctor pan ngei ngei tur a ni .
I fanu hian kum 8 a tlin hmaa kan sawi tawh puberty chhinchhiahna eng emaw tal a lantir emaw, i fapain kum 9 a tlin hmaa emaw a lantir chuan ngaihthah suh.
Damdawi lam thurawn lak hma chuan a chhan dik tak hriat theih nan a ṭanpui thei a, a ṭûl chuan enkawl ṭan theih a ni a, naupangin taksa leh rilru lama harsatna a tawh theihte chu a ti tlem thei a ni.
Take-Home Thuchah a ni
- I fanu hian kum 8 a tlin hmaa puitlin theihna chhinchhiahna a lantir emaw, i fapain kum 9 a tlin hma emaw a nih chuan lungngai suh.Mahse, naupang enkawltu doctor hmu ngei ang che.
- Hetiang dinhmun hi natna khirh tak chhinchhiahna a ni lo fo thin a, mahse a chhan dik tak hriat chian a pawimawh hle.
- He natna hi control nan hian enkawlna tha tak tak leh him tak tak a awm a, chu chuan naupangte hmasawnna pangngai a awm theih nan a pui thei a ni.
- I fa taksa inthlak danglamnaah fimkhur hle ang che, chubakah a rilru hriselnaah pawh fimkhur hle ang che. Hetih hun lai hian i fa tan i hmangaihna, i hriatthiamna leh i thlawpna hi a pawimawh hle.
- I fa rihna control leh ei leh in hrisel tak zirtirna hian heng natna te hi a tihziaawm thei a ni.
Precocious puberty, premature puberty, precocious puberty sinhala, naupang hormone, naupan lai natna, puitlin hun, hormone lama harsatna nei te
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