I naute chu a damlo fo em? Hei hi immunodeficiency hmasa ber a ni thei.

I fa naupangte chu khawsik , flu, emaw beng na vangin a na fo em ? A chang chuan i fa chu naupang dang aiin a na zawk angin i inhria em? A châng chuan, khawsik pawh hi pneumonia ang chi thil pawi takah a chang a, ni tam tak damdawi ei a ngai a ni? Hetiang thil hi i ngaihtuah nasa hle a ni ngei ang. Dik tak chuan hei hi a chang chuan naupang taksa hriselna chak lohna vang pawh a ni thei. Vawiin hian hetiang dinhmun hi kan sawi a ni.

Primary Immunodeficiency Syndrome (PIDD) hi eng nge ni?

A awlsam zawngin, Primary Immunodeficiency Disease (PIDD) nei naupang chuan a taksa hriselna a tichak lo hle a ni . Kan immune system hi kan ram venghimtu sipai angin han ngaihtuah teh. Pawn lam atanga hrik lo chhuak lakah kan taksa a venghim a ni. Chuvângin, he “sipai” hi a chak loh chuan, natna hrik chu awlsam takin taksaah a lut thei a, natna a thlen thei a ni .

He thu i hriat hian, “Aw, ka fa hian heng natna zawng zawng hi a vei dawn em ni?” Mahse a tha ber chu, tunah chuan heng natnate control nan hian enkawlna tha tak tak a awm tawh a ni. Chutiang enkawlna hmang chuan naupang chu naupang dangte ang bawkin hrisel, active leh normal takin a nung thei a ni. Hei hi genetic a ni a, chu chu pian tirh atanga awm reng a ni tihna a ni a, mi pakhat atanga mi dang hnena kai theih natna a ni lo.

He natna chi hrang hrang hi engte nge ni?

Heng immunodeficiency natna chi hrang hrang 550 chuang a awm a ni. Ṭhenkhat chu a tam hle a, ṭhenkhat chu a tlem hle. A tam zawk hi naupan lai atanga hmuhchhuah a ni a, mahse a chang chuan natna lanchhuahna hi a hnu lamah a lang thei. A chi hrang hrang thenkhat han thlir ila.

Eng symptom nge i fimkhur tur?

I fain he natna hi a nei nia i rinhlelh chuan heng natna lanchhuahna te hi lo thlir reng ang che. Heng symptom pakhat emaw a aia tam emaw a awm reng chuan doctor pan ngei ngei tur a ni.

• Naupang thanna a tlai emaw, a thau lo emaw a ni.
• Hri kai fo thin . Entîr nân, beng natna, sinus natna, a nih loh leh pneumonia thla khatah vawi hnih emaw vawi thum emaw .
• Antibiotics hman tlanglawn tak takInfection chu a nasat em avangin intravenous (IV) antibiotics , pills aiin a mamawh zawk a ni.
• Diarrhea awm reng emaw, ei leh in lama harsatna dang emaw.
• Lymph node a lo hring chhuak.
• Spleen lian tak a awm.
• Vaccine nung pek avanga thil thleng na tak.

He natna hi engtin nge dik taka kan hriat theih ang?

Rinhlelhna i neih chuan i chhungkaw doctor pan hmasak ber tur a ni. I fa chu a enfiah ang a, hetiang zawhnate hi a zawt ang che:

Tichuan, thu belhchian dawl zawk hriat duh chuan heng test te hi i en thei ang:

• Thisen test: Naupang thisen sample lak a ni a, immune system cell leh antibodies level te enfiah a ni.
• Genetic test: Hei hian immune system tichhe thei gene-ah hian chhiatna a awm leh awm loh direct-in a hriat theih a ni.
• Flow Cytometry test: Hei hi tunlai technology a ni a, laser beam hmangin immune cells te thuk taka zirchian a ni.

Hetiang dinhmun enkawl tur hian clinical immunologist hmuh a pawimawh hle .

Enkawlnate chu engte nge ni?

Thu lawmawm tak chu tunah chuan heng natna te hi enkawlna tha tak tak a awm ta a ni. Enkawlna hian thil tum lian tak pahnih a nei a, chungte chu natna hrik lo awm lo tura ven leh a lo awm a nih chuan uluk taka enkawl.

1. Infection enkawl dan: I fain infection a neih chuan antibiotics hi a tam zawk leh a pangngai aia rei zawk ei a ngai mai thei. Infection na tak takah chuan damdawi inah dah a ngai thei a, IV (intravenous) damdawi pek a ngai thei bawk.

2. Immunity tichaktu enkawlna: 1.1.

• Immunoglobulin (Ig) replacement therapy: A awlsam zawngin sawi ila, hei hian naupang chu mi hrisel hnen atanga natna do thei antibodies IV hmanga pek a huam a ni. Pawn lam atanga "sipai" pek ang mai a ni. Hei hi kar tin emaw thla tin emaw tih thin a ni.
• Stem cell transplant: Hei hi nausen natna chi hrang hrang na ber berte tan a ni. Mi hrisel (a tam zawkah chuan chhungkaw member) atanga lak chhuah stem cells chu naupang chhungah dah luh a ni. Heng cell te hian immune cell hrisel tak tak an siam thei a ni.Hei hi PIDD chi thenkhat tidam kim thei damdawi a ni.
• Gene Therapy: Hei hi enkawlna hmanraw changkang tak a ni. Naupang stem cells te chu lak a ni a, gene chhia chu laboratory-ah "edited" a ni a, chu cell te chu naupang taksaah dah leh a ni.

I fa enkawltu tan tips tlemte

Hetiang dinhmun nena nunpui hian i fa chu naupang dangte ang bawka hlim leh active taka awm turin i pui thei ang.

• I fa tan thu sawi rawh: I fa chu sikul a kal a nih chuan zirtirtute nen inbia la, i fa dinhmun sawifiah rawh. Hun engemaw chen chu sikul an kal thei lo mai thei tih hrilh rawh.
• Faina fimkhur rawh: Kut sil fo tur a ni a, a bik takin chaw ei hma leh toilet hman zawhah. Hriselna laka inven a pawimawh hle.
• Ei leh in tha pe rawh: Thei, thlai, leh buh chi hrang hrang ei tur tha tak pek hian i fa chu chakna a pe ang.
• Mut tawk: Mut that hi taksa hriselna atan a pawimawh hle.
• Stress tihtlem: I fa chu inkhelh tir la, hobby-ah inhmang la, boruak hlimawm tak siam rawh.

Hetiang dinhmun hi a châng chuan tuar harsa i ti mai thei. Mahse, nangmah chauh i ni lo. Hemi chungchang hi i doctor, chhungte leh i thiante nen sawiho rawh. Hetiang fa nei nu leh pa dangte nena inbiakna neih hi i tan chakna nasa tak a ni thei bawk.

Primary Immunodeficiency, PIDD, immune system, hri kai tam, genetic disorder, SCID, CVID, immunoglobulin therapy te a awm bawk