I naute pum chu a hrual em? Prune Belly Syndrome a ni em? Hei hi i fimkhur ang u.

I naute piang thar i en hian a pum vun chu prune ang maiin a hrual tih i hmu em? A nih loh leh a pum chu a danglam bik takin a lian em? Nu leh pa tu pawhin heng thilte an hmuh hian an hlauthawng hi thil pangngai a ni. Mahse hei hi Prune Belly Syndrome tih hming pu, natna hlauhawm tak chhinchhiahna a ni thei. Lungngai suh, engkim chiang tak leh awlsam takin kan sawi dawn a ni.

Prune Belly Syndrome hi eng nge ni?

A awlsam zawngin sawi ila, Prune Belly Syndrome hi a awm lo hle a, nau piang (congenital) a awm thin. Heng naupangte pum chhunga vun hi a hring hring leh prune ang maia lang a nih vang a ni. Hei hi thil pawimawh pathum avanga lo awm a ni.

1. Pum ruh chak lo emaw awm lo emaw: Naute pum ruh chu a lo thang kim lo a, chu chuan pum chhunga vun chu a ti hrual a, a hrual bawk.

2. Undescended testicles: Mipa naupangah chuan an taksa atanga an awmna tur scrotum-ah an lo chhuk lo.

3. Urinary system problems: Naute zun kawng, chu chu kidney leh bladder siam danah harsatna a awm a.

Heng thil pawimawh pathum bakah hian he natna hian naute taksa peng dang pawh a nghawng thei bawk. Entîr nân, thinlung, lung, intestines, leh skeletal system a nghawng thei a ni. Hei hi Triad Syndrome emaw Eagle-Barrett Syndrome emaw an ti bawk.

Hetiang dinhmun hi engtiang chiahin nge a awm?

Hei hi thil awm lo tak a ni. Nau piang thar 30,000 atanga 40,000 zinga pakhat velin a vei a ni. Thil mak tak chu he natna vei zinga 95% chu mipa naupangah an awm tih hi a ni .

He natna lan chhuah dan berte chu engte nge ni?

Prune Belly Syndrome hi symptom 50 chuang a awm a. Mahse, heng symptoms te hi nausen hrang hrangah a inang lo thei. I doctor chuan i naute chu a enfiah ang a, a natna hriat chian nan a tul angin test a ti ang.

A langsar zual deuh deuhte hi han thlir ila.

Engvangin nge hetiang hi a lo awm? Eng nge a chhan?

Researcher-te chuan hei hi a chhan tak tak an la hmu lo a, mahse a chhan ni thei nia sawi theory engemaw zat a awm.

• Bladder lama harsatna: Mi thenkhat chuan he natna hi naute pum chhunga a lo seilian laia lo awm thin bladder-a thil dik lo awm vang niin an ngai. Zun a luang tha thei lo va, a pung khawm a, chu chuan bladder, ureters leh kidney te a ti hring chhuak thin. Bladder a lo seilian chuan pum ruhte chu pressure a siam a, chu chuan atrophy a tipung a ni.
• Muscle development problem: Mi dangte chuan a chhan ber chu naute pum ruhte a lo thang tha lo vang niin an ngai.
• Genetic Causes: He natna hian genetic influence a nei thei niin an ngai a, chu chu unau zingah hmuh a ni. Naupang genetic condition Trisomy 18 (Edwards syndrome) leh Down syndrome (Trisomy 21) te pawh Prune Belly Syndrome hi hmuh tur a awm bawk.

Hetiang dinhmun avang hian eng harsatna nge awm thei?

Prune Belly Syndrome hian side effect leh complication tam tak a nei a. Nausen hrang hrangah a inang lo. Hengte hi complication langsar ber berte chu an ni.

• Constipation: Pum ruh chak loh avangin ek chhuah harsa.
• Bone deformities: thil hip dislocation, kut, kut zungtang, ke ruh awm lo ang chi.
• Zun kawng natna: Zun kawng natna (UTIs) a awm fo thin.
• Nau pai theih lohna emaw cancer: Naupai theih lohna emaw, nakin lawkah cancer vei theihna emaw a thlen thei.
• Lung thanna a tlahniam: Lung a lo thang tha lo (pulmonary hypoplasia).
• Chronic kidney failure: Hei hi harsatna na ber a ni.

Engtin nge he natna hi kan hriat theih ang?

A tam zawkah chuan he natna hi i naupai lai scan (fetal ultrasound) i neih laiin a hmain hriat theih a ni. Scan hmang hian doctor chuan naute:

• Ruh emaw ruh emaw a dik lo
• Lung lam harsatna a awm
• Lung thanna hniam
• Digestive system lama harsatna awm thei
• Bladder chu a lo hring vek tawh.
• Kal (kidney) a lian a.

Naute a pian hnuah doctor chuan a en mai mai chuan naute hian he natna hi a nei tih a ringhlel thei a ni. Chu rinhlelhna chu nemnghet turin test eng emaw zat tih theih a ni a, chungte chu:

• Thisen test a ni
• Ultrasound hmanga scan a ni
• X-ray hmanga tih a ni
• CT scan a ni
• MRI scan a ni
• Voiding cystourethrogram (VCUG) - Hei hi bladder-ah tui bik inject a, naute zun laiin X-ray lak a, urinary system hnathawh dan enfiah a ni.

Engtin nge enkawl a nih?

Hemi enkawl dan hi naupang hrang hrangah a inang lo. Specialist team chuan naupang enkawlna tur ruahmanna felfai ber siam turin an thawk ho ang. Hei hian thil tam tak a ngaihtuah ang a, chung zingah chuan naupang kum, hriselna dinhmun, natna nasat dan, leh nu leh pate duh dan te pawh a tel ang.

• Mild cases: Naupang thenkhat, an natna lan chhuah dan a nasat loh chuan zun kawng infection venna emaw enkawlna emaw atan antibiotics chauh hmangin hlawkna an hmu thei.
• Surgery: Mahse, naupang tam tak chuan an pum bang, mipat hmeichhiatna, zunthlum leh zun kawng dang siamthat nan vawi tam tak operation an mamawh dawn a ni.

Hengte hi surgery chi hrang hrang tih thin thenkhat chu an ni:

• Vesicostomy: Pum kaltlangin zunthlum chhungah kawngkhar te tak te siam a ni a, chuta tang chuan zun a chhuak thei a ni.
• Orchiopexy: Testicles chu surgery hmangin an rawn hruai thla a, scrotum-ah an dah a.
• Cystoplasty tih a ni: 1.1.Surgery buaithlak zawk, bladder siam thar leh vek.

Thil na tak ṭhenkhatah chuan naupang chu kal thlak (kidney transplant) a ngai thei bawk .

Chung naupangte hmalam hun chu eng ang nge ni ang?

Heng naupangte dam rei zawng hi natna nasat danah a innghat a ni. Lungchhiatthlak takin, he natna vei naupang piang zinga 10% leh 25% vel chu an dam chhung kar hmasa berah hian nausen pum chhungah an thi emaw, harsatna vangin an thi emaw a ni.

Mahse, Prune Belly Syndrome vei naupang 40% vel chuan kal hnathawh dan pangngai an nei a, nun pangngai tak an hmang thei a ni.

30% dang chuan an dam chhungin engtik lai pawhin kidney transplant an mamawh dawn a ni.

Doctor hmuh hun tha ber berte chu engte nge ni?

Naupang Prune Belly Syndrome vei te hi zun kawng infection (UTI) vei an hlauhawm hle a, chuvangin zun kawng infection chhinchhiahna i hmuh chuan doctor ko nghal rawh.

Chu bâkah, i fain zun harsatna dang a neih emaw, a lan dân danglam tak a lantîr emaw chuan doctor thurâwn la rawh. Kum khatah vawi khat tal i fa chu medical check-up neihpui a pawimawh hle bawk .

Hetiang natna neia piang naute enkawl hi thil harsa tak a ni thei. Mahse, nangmah chauh i ni lo tih hre reng ang che. He natna chungchanga hriatna nei doctor leh specialist team te nena thawhhona hian nang leh i naute tan chakna leh kaihhruaina a pe thei a ni.