A châng chuan i rilruah a tight deuh a, thawk harsa i ti em, a nih loh leh i thawhrimna tlem tê pawh i nei em? Hengte hi i thinlung chhunga kawngkhar te tak te ang maia thawk i pulmonary valve-a harsatna awm chhinchhiahna a ni thei. Ngaihtuah buai suh, vawiin hian he thu hi chipchiar tak leh awlsam takin kan sawi dawn a ni. Hei hi hriatthiamna chuan thlamuanna nasa tak a pe ang che.
Pulmonary Valve Disease hi eng nge ni?
A awlsam zawngin sawi ila, Pulmonary Valve Disease hi kan thinlunga valve pawimawh tak Pulmonary Valve hian hna a thawk tha lo tihna eng pawh a ni. Kawngkhar vengtu ang maiin han ngaihtuah teh. I thinlung dinglam sir hnuai lam, Right Ventricle , atanga thisen kal tir theitu a ni a, chu chu lung chhunga thisen phurtu thisen kalna kawng lian ber, Pulmonary Artery -ah a kal thei a ni. Thisen hian lung a thlen chuan oxygen thar a la chhuak thin. Tichuan, chu thisen oxygen khat chu taksa pum puiah a darh a, kan cell-te chu nunna a pe a ni.
Chuvangin, he pulmonary valve-ah hian harsatna a awm chuan i thisen chu i lung thleng a harsa thin. Chuti a nih chuan eng nge thleng? Taksa tissue, cell leh taksa peng hrang hrangte hian oxygen an dawng tlai hle. Hei hi tui pipe a inkhar a, tui luang chu a tlahniam ang mai a ni. Hei vang hian harsatna chi hrang hrang kan nei a ni.
Pulmonary Valve Disease chi hrang hrangte chu engte nge ni?
Pulmonary valve natna hi chi thum a awm a. Eng nge an nih i en ang u, awlsam takin:
1. Pulmonary Valve Regurgitation: Hei hi valve a khar tha lo a, thisen thenkhat hnunglam hawia a leak lai a ni. Tui faucet khar tha lo leh tui tla tlem te te a leak ang maiin han ngaihtuah teh. Tichuan chu thisen chu hmalam pan leh turin thinlung chuan nasa zawkin a thawk a ngai a ni.
2. Pulmonary Valve Stenosis: Hei hi valve a zim emaw, dik zawka sawi chuan a block emaw a ni. Hei hian thisen kalna kawng a ti zim a ni. Tui pipe hrual ang maiin ngaihtuah la, chu chuan tui luang tur kawng a ti tawi a ni. Hei hian thisen chu hmalam pan turin thinlungin nasa zawka hna a thawh a ngai thin.
3. Pulmonary Atresia: Hei hi natna khirh tak a ni. Hei hi naute chu valve siam lo emaw lo thanglian tha lo emaw neia piang a nih chuan a ni . Hei hi pianpui thinlung natna a ni.
Pulmonary Valve Disease hi engtiang chiahin nge a awm?
Heng natnate hi engtiang chiahin nge a hluar tih i lo en ang u.
Pulmonary valve regurgitation (valve kaltlangin hnunglam hawia thisen chhuak) hi a takah chuan a awm fo thin.. Mi thenkhat chu an pian tirh atangin valve structure danglam deuh deuh an ni. Heng taksa lama danglamna nei te hian pulmonary valve regurgitation an nei tam zawk. Mahse, a tam zawkah chuan a nêm hle. Chu chu hlauh tur emaw, enkawl tur emaw a ni tihna a ni lo. Mi tam zawk tan chuan harsatna lian tham a thlen lo.
Pulmonary valve stenosis (valve tihtlem) hi pianpui thinlung natna vei zinga 7% velin a awm thin.
United States-ah chuan naute 7,000 zinga pakhat vel chu pulmonary atresia (pian laiin valve awm lohna) neiin an piang a. Kan rama statistics hi a dik lo hle nachungin hei hi condition ngaihtuah ngai tak a ni.
He natna lan chhuah dan hi eng nge ni thei ang?
Pulmonary Valve Disease natna lan chhuah dan hi mi hrang hrangah a inang lo thei. Mi thenkhat chuan heng symptoms te hi an nei thei a:
- Chest pain: I rilru a hrual ang maiin a lang a, a chang chuan thawk lak lai pawhin.
- Chauhna: Chau tih mai mai, engmah tih theih loh khawpa chak lo anga inhriatna.
- Lightheadedness: Luak hah, a chang chuan muhil.
- Thâwk hahna: Thâwk harsa, thawk hah, tlem kal emaw, stairs-a chho emaw pawhin.
- Exercise tih theih loh: Ka tih thin angin tlan, zuang, exercise tih ka duh lo va, ka ti a nih pawhin ka chau nghal vat thin.
Mahse, stenosis na lo emaw, regurgitation na lo emaw nei te hian symptom an nei lo mai thei tih hre reng ang che. Chuvang chuan medical test neih a pawimawh.
Nausen Pulmonary Atresia a vei chuan thaw a harsat thei a, chaw pek a harsat thei a, mut a hah fo a, a chang chuan an vun rawng dum (Cyanosis) a nei bawk. Hei hi i ngaihven em em tur a ni. Nu leh pa kan nih angin heng symptoms te hi in hriat chian chuan doctor pan nghal tur a ni.
Pulmonary Valve Disease awm chhante chu engte nge ni?
He natna thlentu hi natna chi hrang hrang a zirin a inang lo. Engtin nge a thawh tih i lo en ang u.
- Pulmonary Stenosis awm chhan: A tam zawkah chuan hei hi a chhan chiang tak hmuh a harsa thin. Mahse, he natna hi genetic disorder thenkhat vang emaw, naupai laiin nuin rubella ang natna a vei a nih chuan a lo awm thei a ni. Rubella hi nausen a nghawng thei a, chuvangin naupai lai hian fimkhur a pawimawh hle.
- Pulmonary valve regurgitation awm chhan: 1.1.Hei hian chhan hrang hrang a nei thei. Entirnan, thisen sang (a bik takin pulmonary hypertension), endocarditis, rheumatic fever, etc. Congenital heart issues thenkhat emaw an enkawl dan emaw avanga lo awm thei a ni bawk. Hetiang dinhmun hi thinlung natna Tetralogy of Fallot an tih nei tawhte tan a tam hle.
- Pulmonary Atresia awm chhan: Thil tam takah chuan he natna hi a chhan dik tak hriat a ni lo. Mahse, nausen pianphung (gene) inthlak danglam vang te, naupai laia boruak tha lo (environmental toxins) a tawrh vang emaw, nuin a ei tur thil emaw avanga lo awm nia ngaih a ni.
He natna hian eng harsatna nge a thlen theih?
Pulmonary Valve Disease hian i thinlung ventricle dinglam chu i lung chhunga thisen pump turin nasa zawka hna a thawh a ngai thin. Hei hian i thinlung a tichhe thei a, a ti lian thei bawk. A tlem hle nachungin, he natna hi a nasat chuan thinlung chak lohna a thlen thei a ni . Chumi awmzia chu i thinlung hian i taksaah thisen a pump tling thei lo tihna a ni.
Pulmonary Atresia vei naupangte hian thin natna leh heart rhythm pangngai lo an nei thei a, chuvangin enkawl vat a pawimawh.
He natna hi engtin nge an hriat chhuah?
Doctor pan i kal hian i thinlung i ngaihthlak laiin thawm danglam tak a hriat chuan (stethoscope hmangin ) , chu chu Pulmonary Regurgitation emaw Pulmonary Stenosis emaw chhinchhiahna a ni thei. He murmur hi valve chhunga thisen luang chhuak avanga thawm danglam tak a ni.
He natna hi hriat theih nan eng test nge tih thin?
Doctor chuan pulmonary valve natna finfiah nan a hnuaia test te hi a ti thei ang:
- Fetal Echocardiogram: Hei hian naute pian hmain Pulmonary Atresia ang chi natna a hriat theih nan a pui a ni.
- Echocardiogram (Echo): Hei hian thil tam tak a en thei a, chu chu thinlung hnathawh dan leh valve awm dan te hi a ni. `Atresia`, `Stenosis` emaw `Regurgitation` emaw hriat theihna atan hman a ni. Aw hmanga thinlung thlalak lak ang a ni.
- Pulse Oximetry: Hei hi `atresia` vei te thisen a oxygen level enfiah nan hman thin a ni. Test awlsam tak a ni a, kut zungtang chungah clip dahin tih a ni.
- Cardiac Catheterization: Hei hi `Atresia` emaw `Stenosis` emaw a awm chuan tih thin a ni. Thisen kalna kawng atanga thisen kalna kawng te tak te chu thinlung chhunga luhtir a, pressure tehna leh a tul chuan enkawl dan.
- Electrocardiogram (EKG/ECG): Hei hi `Atresia` emaw `Regurgitation` emaw a awm chuan thinlung electrical activity enfiah nan tih a ni.
- Heart MRI (Magnetic Resonance Imaging): Hei hian `Stenosis` emaw `Regurgitation` emaw a awm chuan thinlung chipchiar taka thlalak lak nan a pui a ni.
- Chest X-ray: Hei hian `regurgitation` a awm chuan thinlung lian leh te leh lung dinhmun a hriat theih nan a pui a ni.
Pulmonary Valve Disease hi engtin nge enkawl a nih?
Hei hi i dinhmun a zirin enkawl dan a inang lo. A chang chuan damdawi hmanga thunun theih a ni a, a chang chuan operation pawh a tel thei bawk.
Damdawi leh enkawlna bikte
Pulmonary valve natna hi enkawlna hrang hrang a awm a:
- Balloon Valvuloplasty: Hei hi pulmonary valve tawi te tihzauh nan tih a ni. Hei hi valve chhungah balloon ang chi thil te tak te dahin inflate-in tih a ni.
- Damdawi emaw stent dah (``Atresia`` tan): Hei hi naute pian hnua thisen kalna kawng khar nghal vat thin ``Ductus Arteriosus`` chu a inhawng reng theih nan tih a ni. He tube hi hawn reng hian lungah thisen a kal theih nan a pui thin.
- Diuretics: Heng damdawi te hi valve atanga thisen chhuak avanga heart failure avanga taksaa tui awm lohna tura pek thin a ni. Taksain tui tam lutuk chu zun kaltlangin a paih chhuak thin.
- Pulmonary Hypertension (lung chhunga thisen sang sang) emaw Endocarditis (thinlung natna) (Regurgitation atan): Heng natna te control nan damdawi pek thin a ni.
- Transcatheter procedure emaw open-heart surgery: Heng procedure te hi valve leak siamthat nan emaw, valve thar dah nan emaw hman a ni.
Enkawlna avanga harsatna/side effect awm thei
Nausen thenkhat chuan operation hnuah ei tur an harsat thei a, an hnar atanga tube te tak te hmanga chaw pek an ngai thei bawk (tube feeding).
Valve thlak hnuah i fain ha lam hna a thawh hunah antibiotics a ei a ngai dawn a ni. Heng damdawi te hian heart infection endocarditis an tih vei theihna a ti tlem a ni.
Pulmonary valve siam that hnuah a leak leh thei a, doctor-in a zau emaw, a thlak emaw a ngai mai thei.
Surgery dang ang bawkin natna kai leh thisen chhuah theihna chance tlemte a awm a, mahse chu chu doctor-te chuan an fimkhur hle.
Enkawlna atanga dam leh theih nan eng chen nge a duh?
`Pulmonary Atresia` avanga zai hnuah i fa chu kar khat emaw kar hnih emaw vel damdawi inah a awm ang. `Pulmonary Valve Regurgitation` avanga zai a nih hnuah dam lehna tur hian kar tam tak, thla tam tak pawh a ngai thei. `Pulmonary Stenosis` atan `Valvuloplasty` i tih zawh chuan kar khat vel chu hnathawh hahthlak tak tak i pumpelh a ngai dawn a ni.
Pulmonary Valve Disease i neih chuan eng nge i beisei theih ang?
He natna i tawn dan hi midang tawn dan nen a danglam thei. Mi thenkhat chuan symptoms an nei tlem hle a, operation pawh an ngai lo mai thei. Mi dangte chuan an dam chhungin pulmonary valve surgery vawi khat aia tam an mamawh thei bawk.
Pulmonary valve natna awm thei tur thlirletna
Naupang pulmonary valve stenosis vanga valvuloplasty nei te tan chuan hmalam hun a tha hle . Naupang cardiologist hnena check-up neih fo mai loh chu engmah an mamawh lo tlangpui. Mi thenkhat chuan kum 15 vel hnuah an valve tihzauh leh a ngai mai thei.
Pulmonary atresia hi enkawl loh chuan thihna thlen thei a ni a, mahse naupang tam tak chu operation hnuah puitling thlengin an dam thei.
Pulmonary valve regurgitation na lo emaw, na lo emaw nei tan chuan outlook a tha hle. Natna khirh tak nei tan chuan a hmalam hun chu enkawlna an dawn thuai danah a innghat a ni.
Engtin nge risk hi ka tihtlem theih ang?
I naute hian a chhan hriat loha awm, Pulmonary Valve Disease a vei theihna tur i tihtlem thei lo. Mahse naupai i tum a nih chuan Rubella Vaccine i dawng tawh tih hria ang che.
Pulmonary Valve Regurgitation vei theihna tur i tihziaawm theih nan a thlentu dinhmun, Pulmonary Hypertension, Endocarditis, leh Rheumatic Fever te hi i pumpelh thei a ni.
Engtin nge ka in enkawl ang?
I thunun theih thilte enkawl la, i thinlung hrisel takin vawng reng rawh.
- I thisen sang leh cholesterol level control rawh.
- Zuk leh hmuam thil siam hi pumpelh vek rawh.
- Exercise neih fo thin ang che. Ni khata minute 30 chauh kal pawh hi a tha.
- Thei, thlai leh ei tur saturated fat tlem emaw, thau nei lo emaw ei thin ang che. Hemi atan hian kan local diet hi a tha hle.
Engtikah nge ka doctor ka hmuh ang?
I cardiologist nena i follow-up appointment te chu lo thlir ve suh. I valve a la thawk tha em tih a enfiah thei bawk. A hmasa berah chuan i natna hriat theihna atana hman test ṭhenkhat chu tih nawn leh a duh mai thei bawk. Entir nan:
- Echocardiogram (Echo) hmanga tih a ni.
- CT scan (Computed Tomography - CT scan) hmanga tihchhuah a ni.
- Lung lam MRI
- EKG (Electrocardiogram - EKG) tih hi a tha hle.
Engtikah nge Emergency Department (ETU) ah ka kal ang ?
Heng symptoms te hi i neih chuan emergency room-ah kal nghal rawh:
- Fainting episode awm fo thin.
- Thâwk harsa na tak.
- I thinlung a thawk chak ang maia inhriatna (Heart Palpitations).
- Infection emaw thisen chhuak emaw chhinchhiahna, khawsik leh ek chhunga thisen, zai hnuah.
Doctor hnenah eng zawhna nge ka zawh ang?
Doctor hnenah hetiang zawhna hi i zawt thei ang:
- Kei (a nih loh leh ka fa) tan eng nge enkawlna tha ber?
- Ka (or ka fa) Pulmonary Valve Disease hi a chhan i hria em?
- Eng chen nge kei (a nih loh leh ka fa) hian nangmah hmu tura lo kal ka mamawh?
- Naupang thinlung natna nei nu leh pate tan support group a awm em?
A tawp berah chuan take-home message
I fa (a nih loh leh nangmah ngei pawhin) Pulmonary Valve Disease a vei tih i hriat chuan tlem a lungawi lo deuh hi thil pangngai a ni. Mahse, lungngai suh. Cardiologist te hian heng valve problem chi hrang hrang hi an buaipui fo thin. An thil tawn hmangin nangmah emaw, i fa emaw enkawlna tha ber tur chu an ruat thei a ni.
I hriatthiam loh zawng zawng zawhna zawh hreh suh. I doctor-in a tih test zawng zawngah kal la, damdawi pek zawng zawng chu a hun takah ei vek rawh. Nangmah chauh i ni lo va, he zinkawng zawh tura pui turin doctor, nurse leh i chhungte an awm bawk. Dam chakna atan pawh positive taka awm hi a pawimawh hle.
` Pulmonary Valve Disease, Heart Valve, Heart Disease, Thâwk harsa, Chhung na, Congenital Heart Disease, Heart Valve Problem, Pulmonary Stenosis, Pulmonary Regurgitation, Pulmonary Atresia











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