Ni a lo kal zel a, i mit a chau ang maiin, i tawng laiin i lei a hrual ang maiin, i taksa pengte chu a hring vek ang maiin i inhria em? Chungte chu hahna vang mai pawh a ni lo mai thei. Vawiin hian hetiang symptoms thlentu ‘ Myasthenia Gravis ’ tih hming pu condition bik leh a enkawlna thar hman tawh chungchang kan sawi dawn a ni. Hei hi hriat chian a pawimawh hle.
Myasthenia Gravis hi eng nge ni tak tak?
A awlsam zawngin sawi ila, myasthenia gravis hi kan taksa invenna system, immune system-in kan cell hrisel tak takte a rawn bei sual thinna natna rei tak a ni. Hei hi autoimmune disease an ti a.
Ngaihtuah teh, kan thluak a\anga thuchah rawn thawn chu nerve kal tlangin a kal a, taksa peng pakhatah a thleng a, chu chuan a thawk ta a ni. He natnaah hian nerve leh muscle inkar neuromuscular junction a chhia a. Kan immune system siam antibodies thenkhat chuan he junction hi an thleng a, message kal dan tur an tikhawlo thin. Chumi avang chuan zawi zawiin taksa ruh chu a chak lo tan ta a ni .
Hetiang harsatna thlentu antibody chi hnih lian ber chu anti- acetylcholine receptor (AChR) leh anti-muscle-specific tyrosine kinase (MuSK) te an ni. I doctor chuan hengte hi a hrilhfiah ang che.
He natna lan chhuah dan tlangpui engte nge ni?
Heng symptoms te hi mi hrang hrangah a inang lo thei. Tin, ruh i hman tam poh leh a chak lo zual sauh bawk. A hnuaia table-ah hian a lan chhuah dan tlangpui thenkhat tarlan a ni.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Mitmeng a tla thla | Mit pakhat emaw, mit pahnih emaw control loha tlak. Mi thenkhat phei chuan pahnih pawh an hmu mai thei. |
| Hmel lan dan inthlak danglam | Hmai leh hmui ruh chak lohna hian nuih leh thinrimna lantir ang chi thil a tidanglam thei a ni. |
| Kut, ke leh kut zungtang chak lohna | Nitin hna thawh harsat, thil pakhat chawi, sam hrual, emaw, kea kal te. |
| Chaw ei harsat | Chaw emaw in tur emaw i ei laiin i rilru a buai ang maia inhriatna. |
| Thusawi harsa | Thusawi laiin aw inthlak danglam te, i hnar hmanga i thusawi ang maia ri te, emaw, lei inzawmkhawma thusawi te. |
Engtin nge damdawi thar Rystiggo hian hna a thawh?
Rystiggo (Rozanolixizumab-noli) hi damdawi thar, myasthenia gravis enkawlna atana pawm a ni. Damdawi chi khat, neonatal Fc receptor (FcRn) blockers an tih zingah a tel a ni.
Tunah chuan hei hian engtin nge hna a thawh tih i en ang u. A hmaa ka sawi tawh ang khan he natna thlentu hi kan thisena antibody tha lo (AChR leh MuSK) te hi a ni. Rystiggo hian a tih tur chu heng antibody tha lo tak takte hi target a, kan taksa atanga lakchhuahna tikhawtlai a ni.
A awlsam zawngin sawi ila, he damdawi hian filter angin hna a thawk a, chu chuan kan thisen a tifai a, natna thlentu antibody tha lo a tihtlem phah bawk.
Heng antibody te hi a tlem chuan nerve leh muscle inkara signal transmission tibuaitu chu a tlahniam thin. Chuvang chuan taksa chakna a lo pung leh a, symptoms te chu control a ni.
He damdawi hi mi zawng zawng tan a tha em?
No. Rystigmo hi myasthenia gravis vei puitling, an thisenah AChR emaw MuSK emaw antibodies test tawhte tan chauh hman phal a ni. Heng antibody nei lote hian he damdawi hi an hlawkpui lo mai thei. Chuvangin he enkawlna hi i tan a tha em tih i doctor-in a rel ang.
Engtin nge enkawlna pek a nih a, a side effects te chu engte nge ni?
He damdawi hi damdawi in emaw clinic emaw-ah vun hnuai lam tissue-ah injection angin pek thin a ni. Hei hi belly button hnuai lam hmunah pek a ni tlangpui.
- Enkawlna cycle: 1.1.He vaccine hi kar khatah vawi khat kar 6 chhung pek thin a ni tlangpui. Hei hi treatment cycle an ti a. Chumi hnuah chuan hun engemaw chen chu enkawl lovin i kal thei a, a tul chuan cycle thar i tan thei bawk. Hei hi i doctor-in a rel vek a ni.
- Fimkhur tur: Injection i pek hnuah minute 15 vel chu doctor enkawlna hnuaiah i awm ang a, allergy hi a chang chuan a awm thei a ni.
| Risk/side effect a awm thei | Eng nge tih tur leh hriat tur |
|---|---|
| I doctor hriattir nghal tur dinhmun | |
| Active Infection awm thei te | Khawsik, taksa na, khuh, phlegm, thawk harsa, ril\am ang chi symptom i neih chuan enkawl hma emaw, enkawl lai emaw chuan doctor hnenah hrilh nghal rawh. Infection a thianghlim hma loh chuan enkawl hun sawn a ngai mai thei. |
| Side effect awm fo thin | |
| Lu na | Hei hi thil tenawm tak a ni tlangpui. A nasat emaw, a awm reng emaw chuan doctor hnenah hrilh rawh. |
| Nausea leh luak chhuak | Hei hi enkawlna kar hmasa berah chuan a awm fo thin. Tui tam tak in la, ei tur hmin (buhfai, banana) ei bawk ang che. A awm reng chuan doctor hnenah hrilh rawh. |
| Injection site-a thil thlengte | Injection na hmunah hian a sen, a hring leh a hring a awm thei. Hei hi a vawi khatnaah hmun khata inject ai chuan injection hmun thlak danglam hian tihziaawm theih a ni. |
Damdawi dang leh vaccine dangah harsatna a awm thei ang em?
Ni e, chu chu thil pawimawh tak a ni.
- Vaccine: Vaccine thenkhat chu Rystiggo enkawl hma leh enkawl lai pawhin pek theih a ni lo. Chuvangin vaccine i dawn apiang chu i doctor hnenah hrilh lawk ang che.
- Damdawi dang: I ei mek damdawi dang, a bik takin immune-related treatment Intravenous Immunoglobulin (IVIg) , leh monoclonal antibodies , te hian Rystiggo nen an inzawm thei a ni.
Chuvangin i damdawi ei zawng zawng (vitamin leh herbal products telin) engmah thup lovin doctor hnenah hrilh vek a pawimawh.
Engtin nge damdawi hian hna a thawk em tih i hriat theih ang?
Rystiggo i tan atanga kar tlemte chhungin i taksa ruhte a chak chho zel tih i hre tan ang a, i natna lan chhuah dan pawh a lo tha chho zel ang. Amaherawhchu, i natna lan chhuah dan a lo tha leh a nih pawhin i doctor thurawn tel lo chuan damdawi ei kha bansan ngai suh. Chutianga i tih chuan i symptoms chu a lo lang leh thei a ni. I dinhmun chungchang hi doctor nen inbia fo ang che.
Take-Home Thuchah a ni
- Myasthenia Gravis natna a ni a, keimahni taksain kan taksa peng hrang hrangte a rawn bei a.
- Rystigmo hi he natna enkawlna thar a ni. Taksa atanga natna thlentu antibody tha lo tak tak te chu a paih chhuak thei a ni.
- He enkawlna hi mi zawng zawng tan a tha lo. I doctor chuan i thisenah AChR emaw MuSK antibodies emaw i neih leh neih loh enfiahin hei hi i tan a tha em tih a hre thei ang.
- Inenkawl laia khawsik leh khuh ang chi natna lanchhuahna i neih chuan doctor hnenah hriattir nghal tur a ni.
- Damdawi dang i ei tur zawng zawng doctor hnenah hrilh vek a pawimawh hle.
- Damdawi pek tawhte chu eng thil vang pawha doctor thurawn tel lova chawlhsan loh tur a ni.











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh