Sickle Cell natna avanga harsatna awm thei: I hriat tur

Sickle Cell Disease tih hi i hre tawh mai thei . A awlsam zawngin, kan taksain thisen sen a siam dan tichhe thei dinhmun a ni . I hria em, heng thisen sen (red blood cells) te hi kan taksa pum puia oxygen phurtu an ni. A tlangpuiin heng cell te hi flat, round, leh flexible disc an ni. Mahse sickle cell natna vei chuan thisen sen hring, sickle ang maia khauh tak a nei a. Chuvangin, he pianzia danglam tak hian hriselna lama harsatna engemaw zat, a nih loh leh ' complication ' a thlen thei a ni. Mahse, lungngai suh, i doctor hian heng harsatna tam tak hi a enkawl thei a, a then pawh a veng thei bawk. A pakhat zel chungchang hi han sawi ila.

Natna - harsatna awm tam ber

Sickle cell natna avanga harsatna awm fo leh ti thinrim ber chu natna hi a ni . Hei hi a chhan chu sickle ang chi cell-te chu thisen kalna kawng te tak teah an tang tlat a ni . Kawngpui zim takah car lian tak a tang a, eng nge thleng tih hi han ngaihtuah teh. Chu chu heng cell te hian thisen kalna kawng an block hian a thleng thin.

He natna hi hnungzang hnuai lam, ke, kut, pum emaw, rilruah emaw a awm fo thin. Attack na tak (crisis emaw episode emaw) angin a lo thleng nghal thei. Thalai leh kum upa zawkah chuan a chang chuan hun rei tak chhung hrehawmna a ni thei.

A tlangpuiin hetiang pain attack i neih hian Paracetamol emaw Ibuprofen ang chi painkillers hmangin hahdamna i hmu thei a ni. Mahse hre reng ang che, kum 19 hnuai lam tan aspirin pe suh , a chang chuan a natna a nasat chuan doctor chuan opioid group atanga natna tidamtu chak tak a pe thei bawk. Mi thenkhat phei chuan damdawi inah enkawl an ngai hial a ni.

I doctor chuan heng natna thlentu te hi ven emaw tihziaawm emaw nan a hnuaia mi hi a rawn rawt thei ang:

• Tui tam tak in thin ang che.
• Khua lum lutuk leh khaw vawt lutuk loh tur.
• Hmun sang, tlangram ang deuhah hun hmang tam lutuk suh.
• Damdawi pakhat Hydroxyurea tih hian naupang leh puitlingah heng natna thlen tam lohna hi a tiziaawm a ni.

Thisen tlakchhamna (Anaemia).

Hei hi sickle cell natna avanga harsatna awm fo dang a ni. Hei hi sickle ang maia red blood cells te chu cell pangngai aiin an thih chak zawkna hmun a ni.. Chuvangin taksa hian cell thar a siam thei lo a, chu chu an thih dan ang zat zat a ni. Chuvângin, taksa cell-a oxygen thlen zat chu a tlahniam a, i chau hle thei a, i chak lo hle a, i lu a buai thei bawk . Tin, thinlung thawk chak leh thawk harsa tih ang chi te pawh i tawng thei bawk. Naupangah chuan thisen tlakchhamna (anemia) hian a thang chak lo thei hial a ni.

Anemia a nasat chuan thisen pek a ngai mai thei. Mahse, thisen pek fo hian iron level a tisang a, thinlung, thin leh pancreas te a tichhe thei a ni. Chuvangin, i doctor chuan i iron level a enfiah fo ang a, chu chu a enkawl theih nan a pui ang. Puitling tan pawh damdawi Hydroxyurea hian thisen tlakchhamna a tidam thei bawk.

Infection leh emergency dangte

Infection laka invenna a tipung

Sickle cell natna vei te, a bik takin naupang te te hian hri kai an kai tam zawk. Hei hi natna hian spleen a tihchhiat vang a ni . I hria em, kan thisen atanga bacteria ang chi hrik te filter chhuaktu organ pawimawh tak chu spleen hi a ni. Chuvangin a thawh that loh chuan natna hrik hi awlsam takin taksaah a lut thei a ni.

Splenic Sequestration tih a ni

Hei hi nunna atana hlauhawm emergency a ni a, a bik takin naupang tê tête tan chuan a ni. Hei hi sickle cells ten thisen kalna tur a tihkhawtlai hian a thleng thin. Spleen chu a lo hring a, a na bawk. Naupang thenkhat chuan symptom lian tham an nei lo mai thei. Mahse, mi dangte chuan chak lohna, vun leh hmui dum, mut tam lutuk, pum veilam na, leh thinlung thawk chak ang chi natna lan chhuahna an nei thei a ni Heng symptoms te hi i neih chuan damdawi inah kal nghal rawh .

Acute Chest Syndrome a awm a, a rilru a hah hle

Hei pawh hi dinhmun pawi tak a ni. Hei hi sickle cell natnain lung chhunga thisen kalna kawng a block na hmun a ni. Khawsik, thawk harsa, rilru na, leh khuh ang chi symptoms i neih chuan damdawi inah kal nghal rawh. Doctor-te chuan oxygen, antibiotics, leh thisen pekna pawh an pe thei che a ni.

Hun rei tak chhunga harsatna dang awm thei

Sickle cell natna hian hun kal zelah harsatna a thlen tam thei hle.

• Ruh hloh (Avascular Necrosis): Ruh lian tak tak (hip ang chi)-a thisen kal chu tihtawp a nih chuan ruh tissue chu a thi tan thin. Hei hi tleirawl leh puitlingah pawh a awm fo. Painkiller hian a ti hahdam thei a, mahse mi thenkhat chuan zai an ngai mai thei.
• Organ dang chhiatna: Mit, thinlung, kal leh thin lama harsatna nei hian thisen zam leh stroke a thlen theihna a sang hle. Hei vang hian i doctor chuan heng taksa peng hrang hrangte hnathawh dan hi a enfiah fo ang.

Bone Marrow Transplant leh Tunlai Enkawlna

Harsatna nasa tak tawk fo thin tan chuan ruhro (bone marrow transplant) tih damdawi hi ngaihtuah theih a ni. Hei hian sickle-cell siamtu bone marrow cells te chu cell hrisel tak tak hmanga thlak a huam a ni. Hei hian natna chu a tidam vek thei a ni.

Mahse hei hi mi zawng zawng tih theih a ni lo. I tissue nena inmil tur donor hrisel tak i zawn a ngai a ni. Tin, thinlung emaw, kal emaw ang chi taksa peng hrang hranga harsatna i neih chuan he surgery hi a hlauhawm thei hle bawk. Damdawi inah rei tak i awm a ngai mai thei. A chang chuan he enkawlna hi a hlawhtling lo thei bawk. Chuvang chuan chhungkuain Doctor nen fimkhur takin an inbia a, he enkawlna hi an tan a tha em tih an rel a ngai a ni.

Tin, damdawi thar zawk, Crizanlizumab ang chi te pawh a awm a, chu chuan natna a tihziaawm thei a ni. Hengte pawh hi i doctor zawt la.