Doctor chuan i fate hian Sickle Cell Disease (SCD) a vei tih a hrilh che a ni mai thei. Nang, nu leh pa angin, he thu i hriat hian hlauhna leh lungkhamna nasa tak i neih hi thil pangngai a ni. He natna nena kan nun hian thil tam takah kan fimkhur a ngai a ni. Chuvang chuan a bik takin kan ngaihven a ngai a, vawiinah hian harsatna hlauhawm tak, nunna atana hlauhawm pawh ni thei kan sawi ta a ni. Hei hi ‘Splenic Sequestration’ an ti a. He hming hi a mak deuh viau nachungin, a chungchang i hriat chian chuan i fa chu i humhim thei a ni.
Splenic Sequestration hi eng nge ni tak tak?
Hei hi hrethiam tur chuan sickle cell disease (SCD) chungchang tlem han hrechhuak hmasa ila. A tlangpuiin mi hrisel takah hian thisen sen (red blood cells) hi a zungbun leh a hring (flat) a ni. Disc te tak te ang maiin. Thisen kalna kawng hrang hrangah awlsam takin an kal kual a, an tlu lo. Mahse, SCD vei naupang thisen sen (red blood cells) -a hemoglobin inthlak danglamna avang hian heng cell te hi a nghet a, sickle ang maiin a awm ta a ni.
Tunah chuan han ngaihtuah teh, heng sickle ang maia siam cell te hi thisen kalna kawng hrang hrangah hian cell round pangngai angin awlsam takin an inbual em? Ni lo, a dik em? An inzawm khawm a, thisen kalna kawng te tak te chhungah chuan tang turin an bei thin.
Chuta tang chuan buaina chu a intan ta a ni. Kan taksaah hian kan pum veilam ah hian ‘ spleen ’ an tih organ a awm a. Hei hi kan taksaa security guard ang mai a ni. A hna ber chu thisen chhunga hrik leh thisen cell hlui te paih chhuakin thisen tihfai hi a ni. Mahse SCD vei naupangah chuan chu sickle ang cell te chu a rilru chhunga thisen kalna kawng nalh tak takah chuan a tang tlat thin. Kawngpuiah traffic jam ang mai a ni.
Chutiang a nih chuan thisen chhuak tur chu a chhuak thei lo va, a chhungah a khawl khawm ta a ni. Zawi zawiin ril chu thisenin a khat a, a lo hring a, a lian chho zel bawk. Chu dinhmun hlauhawm tak chu ‘Splenic Sequestration’ an ti a.
Taksa chhunga thisen kal kual ngai tam tak chu riltam-ah a tlakbuak chuan taksa peng dang zawng zawnga oxygen phurtu thisen sen (red blood cells) chu hlauhawm takin a tlahniam nghal a ni. Hei hi severe anemia an ti a . Hei hian naupang chu a tichak lo hle thei a, a ti sen thei bawk.
Hetiang natna lan chhuah dan hi engte nge ni? Nu leh pa anga i hriat chian ngai thilte
Hei hi a pawimawh ber a ni. Heng symptoms te hi i hriat chian chuan rang takin hma i la thei a, naupang nunna i chhanhim thei bawk. Hetiang dinhmun hi naupang tê têah a tam ber a, mahse SCD vei kum eng pawhah a awm thei.
| Symptom a ni | I fimkhur tur chu |
|---|---|
| Pum veilam a na | Hei hi a lan chhuah dan tlangpui leh pawimawh ber a ni. I fain a spleen awmna hmunah a na tih a complain chuan ngaihtuah rawh. |
| Spleen lian tham (swelling) . | I doctor zawt la, i fate spleen palpate dan zir rawh. A pangngai aia lian leh khauh zawka a hriat chuan chu chu vaukhânna chhinchhiahna a ni. |
| Chak lohna leh hah lutuk | I fa, infiam that lai kha a chau lutuk a, a chak lo lutuk a, ke pawh a kal thei lo a nih chuan fimkhur rawh. |
| Vun dum (pale skin) a ni | I fa hmui, a hmui leh a kutphah chhung lam a rawn sen chuan thisen tlakchhamna chhinchhiahna a ni. |
| Thâwk rang emaw thinlung na emaw | Taksain oxygen a hmuh tlem chuan thinlung leh lung hian compensate turin hna a thawk rang zawk a ni. |
| Sawifiah theih loh thinrimna leh thinrimna | Naupang chu a na avângin, a thinrim a, thil tenawm ber berte avângin a ṭap thei a ni. |
| Mutthilh lohna danglam tak | Naupang chu kaihthawh theih loh khawpa a muhil a nih chuan chu pawh chu chhinchhiahna pawi tak a ni. |
A pawimawh ber: A chang chuan symptom dang langsar lo mahse, spleen a hring hian thisen sen (red blood cell count) hlauhawm takin a tihhniam thei a ni. Chuvangin heng chhinchhiahnate hi i hmuh chuan i fa chu damdawi in Emergency Department (ETU)-ah hruai nghal rawh. Hei hi in lama enkawl theih a ni lo.
Engtin nge doctor hian he natna hi a hriat theih?
I fa chu damdawi inah i hruai hunah chuan doctor chuan he natna hi a finfiah theih nan hma engemaw zat a la ang.
1. Taksa endik : A hmasa berin doctor chuan naupang pum chu a palpate ang a, a ril chu a hring emaw a lian em tih a enfiah ang.
2. Thisen test: Hei hi test pawimawh tak a ni. Naupang thisen sample lak a ni a, hemoglobin level endik a, red blood cell count a hniam zia hriat a ni. Thisen var leh platelet level inthlak danglamna an zawng bawk.
3. Test dang: A then phei chuan X-ray emaw CT scan emaw hmangin kan zung (spleen) dinhmun chiang zawka en theih a ni.
Engtin nge enkawl ang? Hlau suh.
Hei hi emergency ni mahse, damdawi ina dah vat chuan hlawhtling taka enkawl theih a ni.
Enkawlna ber chu thisen pek a ni . Chumi awmzia chu naupang thisen sen (red blood cell count) chu a inmil thei ang bera thisen pekna pek a nih chuan a lo awm leh tihna a ni. Hei hian taksain a mamawh oxygen a hmuh theih nan a pui a, naupang dinhmun pawh a \ha thuai \hin. A châng chuan rilṭâm a thisen a tam lutuk chuan Doctor-in thisen a pêk laiin naupang taksa aṭanga thisen ṭhenkhat a lak chhuah a ngai mai thei.
A lo lang leh a nih chuan engtin nge kan tih ang?
Splenic sequestration chungchanga harsatna pakhat chu vawi khat a lo awm tawh chuan a lo awm leh a rinawm hle . Naupang thenkhat chuan an dam chhungin vawi tam tak he natna hi an hmachhawn a ngai dawn a ni.
Hetiang harsatna hi a awm chhunzawm zel a nih chuan doctor-te chuan surgery hmanga spleen lakchhuah (splenectomy) an rawt thei a ni. Spleen lakchhuah hian he dinhmun hlauhawm tak hi a lo awm leh tawh loh nan a veng vek thei a ni. Amaherawhchu, ril (spleen) lakchhuah a nih hnuah chuan taksain natna a do theihna (immunity) chu tlem a tlahniam a, chuvangin naupang chuan natna hrik thenkhat laka inven nan antibiotics leh vaccine bik a ei a ngai dawn a ni. I doctor chuan hei hi chiang takin a hrilhfiah ang che.
Take-Home Thuchah a ni
- Naupang sickle cell natna vei zingah splenic sequestration hi natna khirh tak, nunna atana hlauhawm tak a ni a, emergency medical treatment a ngai a ni.
- I pum veilam na, vun rawng, hah lutuk, leh ril a hring te ang chi symptoms te chu fimkhur reng ang che.
- I fate rilru natna palpate dan tur doctor hnen atangin zir rawh. I fa nunna chhanhimna kawngah a pui thei a ni.
- A chunga kan sawi tak symptoms i hmuh veleh hun khawhral suh la, i fa chu damdawi in hnai ber Emergency Treatment Unit (ETU) ah hruai rawh .
- Hetiang natna hi lo awm leh theihna a sang hle a, i doctor nen inbiak reng la, chutiang chuan thupek pekte chu zawm rawh.











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