Sickle Cell Disease natna hi i tuar em? He natna hi engtin nge kan enkawl ang tih hi han sawi ila.

Sickle Cell Disease ( SCD ) vei tan chuan natna hi harsatna awm reng a ni. A awlsam zawngin sawi ila, i thisena thisen sen (red blood cells) te chu a zungbun atanga sickle ang maiah a inthlak a ni. Hêng sickle ang chi cell-te hi i taksaa thisen kalna kawng tê ber berteah an tang a, thisen kalna chu a tikhawlo . Chutah chuan natna nasa tak i tawng thut mai a ni. Hei hi "pain crisis" kan ti a ni. He natna hi a tam zawk chu hnungzang hnuai lam, kut, ke, rilru leh pum chhungah a awm thin. Mi thenkhat tan chuan natna avanga hriselna lama harsatna dang avang hian natna hi a awm reng thei a, a rei thei bawk. Hetianga hrehawmna i neih hian, lungngaihna , lungkhamna, leh lungkhamna i nei tam zawk a ni.

Mahse eng ang hrehawmna pawh nei mah la, hahdamna i hmuh theih nan kawng tam tak a awm. A pawimawh ber chu i natna enkawl dan tur ruahmanna tha tak siam turin doctor nen inbiakna neih hi a ni.

Engtin nge pain crisis i enkawl ang?

A tam zawkah chuan a natna chu a lo intan veleh in lamah i enkawl thei a ni. Over-the-counter painkiller Paracetamol emaw Ibuprofen emaw hmangin hahdamna i hmu thei tlangpui. ( Mahse, kum 19 hnuai lam tan aspirin hi hman a tha lo tih hre reng ang che .) Chu bâkah, ṭanpui tûrin thil dang tlemte i tih theih a awm bawk.

In lama tih theihte chiang taka hrethiam turin hetiang hian han thlir ila.

Mahse, a chang chuan heng thilte hian a puih loh chuan, emaw, a na lutuk a nih chuan nangmah emaw, i fa emaw damdawi inah dah a ngai mai thei. Chutah chuan doctor chuan IV fluid leh painkiller chak zawk a pe thei che a ni. Natna chu tuar theih loh a nih chuan in lama awm mai mai suh. Damdawi in hnai ber emergency room (ETU) ah a rang thei ang bera kal rawh.

Doctor tam tak chuan sickle cell natna vei te chu natna an hmachhawn theih nan pain management plan an pe thin. I natna chu nangmah chauha i enkawl theihna tura i tih theih turte a tarlang a ni. Doctor, nurse, ambulance hnathawk dangte’n emergency-a an ṭanpui theih dan tur pawh a hrilh bawk. Chuvangin, i natna i hriat tan hmain i doctor nen inbia la, ruahmanna siam rawh.

Natna tihziaawmna tur leh venna tur damdawi engte nge awm?

Damdawi bik engemaw zat a awm a, chu chuan natna thlen tam lohna a ti tlem thei a ni.

• Hydroxyurea awm zat:He damdawi hi nitin ei hian puitling leh naupangte zingah natna vei tamna a ti tlem thei a ni.
• L-glutamine (L-glutamine - Endari): Hman a nih chuan natna avanga damdawi ina i awm rei zawng a ti tlem thei a, damdawi ina admission a ti tlem thei bawk.
• Crizanlizumab-tmca (Adakveo): Hei hi sickle cell natna atana damdawi pawm thar ber zinga mi a ni. Target therapy a ni. Hei hian a awmzia chu he damdawi hian thisen sen (red blood cells) te chu a bik takin a target a, an inzawm khawm loh nan a thawk tihna a ni. Hei hian vaso-occlusive crises (VOCs) a ti tlem a, chu chuan natna a ti tlem thei a, chhungril taksa peng a tichhe thei bawk.

Heng damdawi te hi nangmah emaw i fa emaw tan a tha em tih hriat tumin i doctor nen inbia ngei tur a ni.

Natna rei tak tan eng nge tih theih ang?

Sickle cell natnain hun rei tak chhung nghawng a neih hian hun rei tak chhung harsatna hrehawm tak a thlen thei a, a bik takin kum upa lam tan chuan harsatna a thlen thei a ni. Entirnan, taksa pum puia thisen kal tlem chuan ruh leh ruhkawr a tichhe thei a, natna rei tak a thlen thei a ni.

Hetiang natna khirh tak hi enkawl tur hian i doctor chuan nitin ei tur painkiller a pe thei ang. I hnungzang leh ke ruhte thlawp turin physical therapy emaw, orthopaedic device emaw pawh an rawt thei bawk. Thil na tak ṭhenkhatah chuan, doctor-te chuan natna thlentu buaina siam ṭhat nân operation emaw, natna tihziaawm nân nerve pakhat chu rei lo tê chhûnga tihlum emaw a rawt thei a ni.

Engtin nge he natna hi rilru lamah i chak reng theih?

Sickle cell natna nena nun hi a harsa thei hle a, a bik takin naupang tan chuan a harsa hle. Natna nei reng rengte hian rilru lam harsatna, lungkhamna leh lungngaihna te an nei tam zawk. An dinhmun avângin mi dangte hlimawm thilte aṭangin hnawhchhuah niin an inhria thei a ni. Heng rilru put hmang hian natna avanga harsatna dang awmte chu a tizual thei a ni.

Nang pawhin i rilru a hah a, i lungngai a, beiseina i nei lo a nih chuan counseling emaw, psychotherapy emaw hi a ṭanpui thei hle. Rilru lam hriselna lama counselor a niI harsatnate i doctor nena in sawi dun hian he natna nena lo awm natna leh harsatna dangte nen hlawhtling tak leh hrisel taka nun dan tur i zawng thei ang.

Tin, i doctor emaw nurse emaw hnenah sickle cell natna vei midang leh chhungkaw inkhawm theihna tur support group chungchang zawt bawk ang che. Heng pawlte hian natna nena nun dan tur chungchangah midangte hnena thil tawn sawiho theihna hun remchang an siamsak thei che a, natna leh harsatna dangte hmachhawn dan tur thurawn pawh an dawng thei bawk.