Sickle Cell Crisis hi i hria em? He dinhmun hrehawm tak hi han sawi ila!

Sickle cell natna i neih chuan natna nasa tak a rawn thleng nghal tih i hre tawh emaw, i tawng tawh emaw pawh a ni thei. Hei hi sickle cell crisis kan tih chu a ni. Thil lungchhiatthlak leh hrehawm tak a ni thei tak zet a ni. Mahse, lungngai suh, vawiinah hian chipchiar takin kan sawi dawn a ni.

He sickle cell harsatna hi eng nge ni?

A awlsam zawngin, sickle cell natna chu i taksa ‘sickle cells’, a nih loh leh sickle ang maia thisen sen, thisen kalna kawng khata a tang a, thisen kal a tikhawtlai emaw, a titawp emaw a ni. I hria em, kan thisen sen (red blood cells) te hi taksa pum puia oxygen phurtu an ni. Chuvangin, sickle cell natna i neih hian i tissue leh organ te hian oxygen an hmu tlem hle. Hei hian natna nasa tak leh harsatna dang a thlen thei a ni .

Tui pipe-a bawlhhlawh tlem a tlak chuan tui luang chu a tlahniam ang maiin han ngaihtuah teh. Mahse hetah hian a tang tlat chu chu sickle ang maia thisen sen hringte chu a ni. Hengte hi thisen sen pangngai round angin an ben awlsam lo va, hmun tenau tak takah pawh an slip lo. Chuvang chuan an inkhung hran tum a ni.

A chang chuan he natna hi in lamah enkawl theih a ni a, mahse a natna lan chhuah dan a nasat chuan damdawi inah ni engemaw zat enkawl a ngai mai thei.

Sickle cell crisis chi hrang hrangte chu engte nge ni?

Sickle cell crisis hi chi li a awm a. Eng nge an nih hi han thlir ila:

• Vaso-occlusive crisis: Hei hi a tam ber chi a ni. Heta thil thleng hi sickle cells te chu i capillaries emaw thisen kalna kawng te tak te dang ah an tang a, chu chuan i tissue leh organs ah thisen kal a ti tlem a ni. Hei hian natna nasa tak thlentu chu a ni. A chi dangte chuan taksa hmun bik a nghawng a ni.

• Aplastic crisis: Hei hi i bone marrow (i ruh chhunga thisen cell siamna hmun)-in thisen sen (red blood cells) a siam chhuah loh thut a ni. Hei hi virus infection thenkhat, a bik takin parvovirus B19 avanga lo awm a ni tlangpui.

• Hyperhemolytic crisis: Hei hi i hemoglobin level (thisen sen chhunga protein, oxygen phurtu) a tlahniam nghal a ni. Hei hi i thisen sen (red blood cells) a chhe chak lutuk vang a ni. Hei hi thisen pek hnuah pawh a thleng thei a, hei hi sickle cell natna enkawlna tlanglawn tak a ni.

• Splenic sequestration: Hei hi i spleen (i pum veilam sir chunglama awm organ)-a sickle cells a tlakbuak a, chu chuan spleen chu a ti lian nghal a, na takin a lo hring chhuak ta a ni Hei hi naupang tê tê tan chuan a hlauhawm zual thei hle a, thisen tam tak chu kawchhungah a khawlkhawm thei a, chu chuan thisen volume a tihhniam phah a ni.

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Hei hi eng symptoms nge ni?

Sickle cell natna lanchhuah dan hi taksa chhunga khawi hmunah nge a nghawng dan azirin a danglam thei. A lan chhuah dan tlangpui chu:

• Luak chhuak thei.
• Chauhna nasa tak, hahna.
• Lu na.
• Jaundice (vun leh mit sen).
• Natna (hei hi a lan chhuah dan ber leh na ber a ni).
• Thâwk harsa.
• Chaklohna.

Sickle cell natna natna chu dull, sharp, stabbing, emaw stabbing emaw a ni thei . Darkar tam tak, ni tam tak, a nih loh leh kar tam tak pawh a daih thei. Natna hi taksa khawi hmunah pawh, hmun khatah emaw, hmun engemaw zatah emaw a awm thei. Entir nan:

• Kut emaw kutphah emaw ah.
• A rilruah.
• Ke emaw ke emaw ah.
• A hnungzang hnuai lamah.
• Pum chhungah.

Engvangin nge he sickle cell crisis hi a lo awm?

Sickle cell natna hi sickle ang maia thisen sen inzawmkhawm a, thisen kalna kawng pakhat a block hian a awm thin. Mahse, mithiamte chuan hei hi eng thil nge a lo intan tih chiang takin an hre ngai lo.

Mahse, he natna thlentu trigger thenkhat a awm a:

• Dehydration : Taksain tui a tlakchham chuan thisen a thim a, cell te chu a inkhar tam zawk thin.
• Hmun sang zawka kal (a chhan chu hmun sang zawkah oxygen a tlem avangin).
• Infection : Infection eng pawh, khawsik emaw flu emaw ang chi.
• Naupai lai.
• Meizial zu emaw Vaping emaw.
• Taksa tihchakna nasa lutuk.
• Stress : Lungngaihna leh hlauhna lutuk.
• Temperature nasa tak a inthlak nghal (e.g., boruak lum tak takah i awm hnua tui lum tak lak).
• Vitamin thenkhat, entirnan folate tlakchhamna.

Hei hian eng harsatna nge a thlen theih?

Sickle cell crisis nasat dan chu thisen kalna kawngkhar block awmnaah a innghat a ni. I tissue emaw organ emaw-a thisen kalna kawng a inkhar a nih chuan, harsatna hrang hrang:

• Acute chest syndrome : Hei hi natna khirh tak, nunna atana hlauhawm tak, rilru chhunga awm a ni. A lan chhuah dan chu khawsik, rilru na, leh thawk harsa te a ni.
• Thisen a chhuak thin.
• Chronic pain (natna kal zel).
• Spleen enlargement leh spleen nena inzawm natna dangte.
• Kea hliam dam lo.
• Liver natna.
• Lung natna, entirnan, pulmonary hypertension.
• Necrosis : Thisen kal chak loh vanga ruh emaw tissue (a bik takin hip ang hmunah) thi.
• Penis erection na tak (mipaah ​​chuan priapism an ti bawk).
• Stroke : Thluaka thisen petu thisen kalna kawng a block emaw, a rupture emaw avanga lo awm a ni.

Engtin nge hei hi i hriat chian?

Sickle cell natna i neih chuan thla 6 danah emaw kum khatah vawi khat emaw thisen test turin doctor i hmu tawh ngei ang. Mahse sickle cell crisis i neih chuan lab test full set i neih a ngai dawn a ni. Chûng zîngah chuan:

• Thisen chi test (thisen pek ngai i nih chuan).
• CBC (Complete Blood Count) : Hei hian hemoglobin level leh thisen sen leh var awm zat a teh a.
• CMP (Comprehensive Metabolic Panel) : Metabolic test hrang hrang, kal leh thin ang chi taksa peng hrang hrangte hnathawh dan enfiahna chi hrang hrang a ni.
• Liver hnathawh dan test a ni .
• Reticulocyte count : Hei hian thisen sen thar siam chhuah zat a teh a. Hei hian ruhro (bone marrow) hnathawh that dan tur ngaihtuahna a pe thei a ni.

Chu bakah, i doctor chuan taksa enfiahna kimchang leh imaging test te a ti thei bawk a, chungte chu:

• Doppler ultrasound : Thisen kal tlanga thisen kal dan en rawh.
• MRI : A bik takin stroke ang chi natna rinhlelhna a awm chuan.
• Ultrasound : Pum chhunga taksa peng hrang hrang leh pum chhunga thil awmte en nan.
• Chest X-ray : Acute chest syndrome ang chi natna enfiah nan.

Engtin nge enkawl a nih?

Sickle cell crisis i neih chuan a natna lan chhuahna (symptoms) nuam lo tak takte control-na atana pui turin painkiller i mamawh mai thei. A nasat loh chuan in lamah damdawi lei theih loh, acetaminophen (e.g. Panadol®, Tylenol®) emaw ibuprofen (e.g. Advil®, Brufen®) emaw hmangin i enkawl thei a ni.

Amaherawhchu, natna khirh tak a neih chuan damdawi inah ni engemaw zat awm a ngai mai thei. Chumi hnuah chuan doctor-te chuan natna tidamtu chak tak (morphine ang chi), IV fluid (i thisen a kal ṭhat theih nan), leh a tul chuan oxygen an pe thei che a ni.

Tin, sickle cell natna enkawl dan pawh taksa peng hrang hrang a nghawng dan leh a lan chhuah dan nasat dan azirin a inang lo bawk. Doctor-te chuan damdawi te, thisen pek te, ruh ruh thlak te, a nih loh leh heng enkawlna inkawp te hi an hmang thei a ni.

Hun rei tak chhunga enkawl dan tur damdawi

Doctor-te’n sickle cell crise hun rei tak chhunga an enkawlna leh a lo awm tam lohna tihtlem nan damdawi chi hrang hrang an hmang a:

• Hydroxyurea: He damdawi hian i thisen sen (red blood cells) a ti lian a, an fold theihna a tipung a, hemoglobin chi khat fetal hemoglobin an tih chu a tipung bawk. Hei hian cell te clotting a ti tlem a ni.
• Crizanlizumab (Crizanlizumab) tih hi a awm lo.Hei hi monoclonal antibody chi khat a ni. I thisen zam (red blood cells) te chu i thisen kalna kawng bang ah a innghah loh nan a veng thei a ni.
• L-glutamine: Hei hi amino acid a ni a, thisen sen (red blood cells) tihchhiatna tihziaawm nan a pui a ni.
• Voxelotor: He damdawi hian i thisen sen (red blood cells) te chu a sickled a, a inzawm khawm loh nan a veng a ni.

Thisen pek a ni

Doctor-te chuan thisen pek hi aplastic emaw hyperhemolytic sickle cell crise emaw enkawlna atan an hmang thei a ni. He enkawlna hian i thisen sen hrisel tak takte chu a tikhat thei a, sickle cell complication i neih theihna a ti tlem thei bawk. Mi thenkhat chuan thisen pek tam a ngai mai thei.

Transplant te pawh a awm

Bone marrow transplant emaw stem cell transplant emaw hi a then phei chuan sickle cell natna tihdamna awmchhun a ni thei. Mahse, matching donor (unau ang chi) hmuh chu hun engemaw chen a la ngai thei. Tin, bone marrow transplant hian harsatna lian tham dang a thlen thei bawk a, chu chu graft vs. host disease (GvHD) te hi a ni. Hemi avang hian doctor-te chuan sickle cell crise an enkawl hian bone marrow transplant an ti tlem hle. Chu ai chuan a tum ber chu i natna lan chhuah dan enkawl leh i natna tihziaawm hi a ni.

Hei hi ven theih a ni em?

Sickle cell crise hi a veng thei ngai lo. Mahse, a hlauhawmna tihziaawmna tur thil engemaw zat a awm a:

• Meizial zuk loh vek tur a ni.
• Khaw vawt hmuna i awm chuan incheina lum takin inchei thin ang che. Khawsik hian thisen kalna kawng a tikhawlo thei a, harsatna a thlen thei bawk.
• Zu in hi tihtlem emaw tihtawp vek emaw . Zu hian tui a tikhawlo thei a ni.
• Ni khatah tui glass 8-10 tal in thin ang che (stay hydrated).
• Nitin folic acid tablet ei thin la, hei hian thisen zam (red blood cell) a tipung a (hei hi doctor thurawn angin tih tur a ni).
• I kut chu sahbawn hmanga sil fo la, chu chuan hri kai theihna a ti tlem ang.
• Vaccine mamawh zawng zawng chu a hun takah (e.g. flu vaccine, pneumonia vaccine) lak vek tur a ni .
• Exercise hahthlak lutuk hi pumpelh la, mahse exercise tlem lutuk hi a tha.
• Stress tihtlem dan tur zawng rawh (e.g. yoga, meditation).

Engtin nge ka in enkawl ang (harsatna a lo thlen hian)?

Nangmah emaw, i hnaih ber tu emaw chuan sickle cell crisis i neih chuan heng thilte hi tih hian symptoms te chu a tiziaawm thei ang:

• In lum reng tur a ni. Inbual lum emaw, natna hmunah heating pad dah emaw hian i thisen kalna kawng a tizau ang a, thisen kal pawh a ti tha ang. A lumna hian taksa ruh natna te pawh a ti reh thei bawk ang.(Ice pack hnawih suh. Khawsik hian natna khirh tak a thlen thei. Chuvangin a lum thei ang bera awm a tha ber.)
• Tui tam tak in thin ang che. Tui i in tam chuan i thisen sen (red blood cells) te chu an inzawm khawm tlem a, chu chuan channel kaltlangin awlsam zawkin an kal thei a ni.
• Massage la rawh. Zawi zawia massage hian thisen kal a tipung thei a, taksa ruh a ti hahdam thei a, natna a tiziaawm thei bawk.
• Mindfulness tih hi practice rawh. Research atanga a lan dan chuan hun rei lote chhunga thil tum pakhata i rilru dah hian i thluak a tibuaitu a ni a, sickle cell natna nena inzawm natna pawh a tiziaawm thei bawk. I thawk lam ngaihtuah ang chi thil awlsam tak pawh hian a pui thei a ni.
• Over-the-counter painkillers ei thin ang che. Chung zingah chuan paracetamol, ibuprofen, emaw naproxen (e.g. Aleve®) te pawh a tel. Mahse i doctor-in a tih aia tam ei suh.

Engtikah nge Emergency Treatment Unit (ETU) ah i kal ang ?

Heng symptoms te hi i neih chuan Emergency Department (ETU) hnai ber ah kal nghal rawh :

* In lama damdawi hmanga thunun theih loh natna rang tak, na tak i neih chuan.

* Thâwk harsa emaw, rilru na emaw.

* Khawsik sang (101°F aia sang emaw 38.3°C aia sang).

* Chak lo thut, tawng harsa, hmai sir khat tlak (stroke symptoms).

* Pum natna nasa tak emaw, pum puar emaw.

* Jaundice a pun chuan.

* Mipa tan chuan erection na tak darkar 4 aia rei.

Tikhawtlai suh. Enkawl tan hma chuan hun rei tak chhunga harsatna awm theihna a ti tlem thei a ni.

I hriat reng tur pawimawh ber berte

Sickle cell natna i neih chuan harsatna ngaihtuah hian a ti buai deuh thei. Heng dinhmunte hian natna lan chhuah dan duhawm lo tak tak leh dam chhung zawnga harsatna a thlen thei a ni. Sickle cell crisis i tawk tawh a nih chuan hun hi a hlut zia i hria ang.

Over-the-counter pain reliever emaw, in lama i hman thin damdawi emaw hmanga i symptoms a ṭhat loh chuan doctor pan a hun tawh. Anni hi tanpui turin an rawn kal a ni. I dinhmun chungchang hi doctor hnenah sawipui hlau suh. Inenkawl hmasak hi a tha ber. I doctor nen thawk ho la, i tana tha tur pain management plan siam rawh.