I in chhunga tui pipe pakhat chu thil pakhatin a lo dang ang tih han ngaihtuah teh. Tichuan tui chu a luang tha lo va, hmun khatah a tang a, buaina lian tak a siam a ni. Chu chu "Sickle Cell Crisis" lai hian kan taksa chhungah a thleng thin. Hei hi thil hrehawm tak a ni. Chuvangin vawiin hian he thu hi chiang takin sawi ila.
He sickle cell natna ( SCD ) leh ‘crisis’ hi eng nge ni?
A awlsam zawngin kan thisenah hian cell chi khat,
red blood cells . Mi hrisel takah chuan heng cell te hi a round a, a flexible bawk. Ball te tak te ang mai an ni. Hei hian taksa chhunga thisen kalna kawng te tak te tak te kal tlangin engmah tihbuai lohvin a kal thei a, taksa peng zawng zawngah oxygen a phur thei a ni. Mahse,
Sickle Cell Disease (SCD) vei tan chuan thisen sen thenkhat chu a pianzia a inang lo hle. An zungbun an ni lo va,
C-shape-ah an inher zawk a ni . Tin, heng cell te hi an khauh hle a, an sticky hle bawk. Chuvângin, heng sickle ang maia siam cell-te hi chu thisen kalna kawng te tak te kal tlanga an kal chuan hmun khatah an tang tlat mai a ni.
A hmaa kan sawi tawh ang khan pipe chhunga tui chu a tlakbuak ang bawkin heng cell te pawh hi an inzawm khawm a, thisen kalna kawng atanga thisen kal chu an titawp vek a ni.
Chutianga thisen kal chu a tawp chuan chu channel hmanga chawmtu taksa pengte chuan oxygen mamawh chu an dawng lo. Hei hi medical science-ah chuan
(Hypoxia) an ti a. He oxygen tlakchhamna hian tuar theih loh, natna nasa tak a thlen thin. Chu chu
"Sickle Cell Crisis" kan tih chu a ni. He natna hi darkar tlemte atanga kar tlemte thleng a awm thei. A bik takin rilru chhunga thisen kalna kawng te te a block avangin natna khirh tak
(Acute Chest Syndrome) an tih hi a lo awm thei a ni. Hei hian sickle cell vei zinga 50% aia tam a nghawng a ni.
‘Sickle cell crisis’ natna lan chhuahna chu engte nge ni?
Hetiang dinhmunah hian mi tin hian symptom hrang hrang an nei thei a ni. Mahse a lan chhuah dan tlangpui thenkhat a awm. Table pakhatah han en ila.
| Symptom a ni | A sawifiahna a ni |
|---|
| Tuar theih loh khawpa hrehawmna | Hei hi a symptom ber leh langsar ber a ni. Natna chu a lo thleng nghal thei a, a dull thei a, a hliam thei bawk a, a hrual thei bawk a, a hrual thei bawk. Kut leh ke, pum, rilru, leh hnungzang hnuai lam ah te a awm tam ber. Naupang tê têah chuan kutphah leh kephah a na zual thei. |
| Thâwk harsa | Thâwk hahna, rilru natna nena inzawm a awm thei. Hei hi symptom pawi zawk a ni. |
| Chauhna/chau lutuk | Nunna nei lo leh chau lutuk i ti mai thei. |
| Vun a sen (Jaundice) . | Mit leh vun var chu a sen thei. |
| Thil dang pawh a awm | Mipaah chuan luak chhuak, lu na, taksa peng thenkhat che harsa, leh erection na tak tak a awm thei. |
He ‘harsatna’ thlen chhan bik a awm em?
Hetiang dinhmun hi a chhan dik tak hriat a harsa fo a, mahse a thlentu ‘trigger’ tlanglawn engemaw zat hmuhchhuah a ni.
- Dehydration : Tui in tam loh.
- Temperature inthlak danglamna: Temperature inthlak danglam nghal awmna hmuna kal . Entîr nân, boruak ṭha tak awmna pindan aṭanga pawn lama ni lum takah chhuah thut.
- Infection: Khawsik ang chi infection tenau tak pawh hi a thlentu a ni thei.
- Stress: Stress lutuk hi a chhan lian tak a ni bawk.
- Hmun sang tak: Hmun sang tak tak, tlang chhip, oxygen tlemna hmuna kal.
‘Crisis’ a lo thlen hian eng nge i tih ang? Enkawlnate chu engte nge ni?
Hetiang dinhmun hi i neih chuan, .
A pawimawh ber chu i doctor nen inbia a, ‘crisis’ a lo awm a nih chuan enkawl dan tur treatment plan siam hi a ni. In lama i tih theih thilte
Natna a lo tan meuh chuan in lama tih theih engemaw zat a awm.- Tui tam tak in rawh: I taksa hi tui a awm reng theih nan a pawimawh hle.
- Painkillers: Painkiller hman tlanglawn tak Paracetamol emaw Ibuprofen emaw i ei thei. Mahse i doctor hnenah eng damdawi nge tha ber tih zawt rawh. Entirnan, kal lama harsatna i neih chuan Paracetamol hi a tha zawk mai thei.
- Thil tih dan dang: Tui lum bottle hnawih te, tui lum taka inbual te, leh zawi zawia massage te hian natna a tiziaawm thei a ni.
- Rilru hriselna: Meditation ang chi method hmangin i rilru timuang rawh. Chhungte leh ṭhiante hnen aṭangin ṭanpuina zawng rawh.
Damdawi lam enkawlna
He ‘harsatna’ venna leh enkawl nan hian doctor-te’n damdawi bik engemaw zat an rawt a ni.- Hydroxyurea : He damdawi hian sickle ang maia thisen zam (red blood cells) siam a ti tlem a, hei hian natna khirh tak tak ‘crise’ awm fo thin chu a ti tlem a ni.
- L-glutamine oral powder (Endari): Hei hian 'crisis' a veng thei bawk a, damdawi ina dah ngai a ti tlem bawk.
- Crizanlizumab-tmca (Adakveo): He damdawi hian thisen cell inzawmkhawm leh thisen kalna kawng a tikhawlo thei lo.
- Thu pawimawh: Hemi atan hian a hmain damdawi pakhat Voxelotor (Oxbryta) an lo hmang tawh a. Mahse, himna tur ngaihtuahin September 2024 khan market atangin paih a ni a , tunah hian he damdawi hi i ei a nih chuan i doctor nen sawiho nghal a, enkawlna tha dang pan leh a pawimawh hle.
In lama inenkawlnain a natna a thunun loh chuan damdawi in emergency room (ETU)-ah rei vak lovah kal thin ang che. Chutah chuan natna tidamtu chak zawk pek i ni ang. Natna tihreh a nih hma chuan damdawi inah ni engemaw zat awm a ngai mai thei.
‘Crisis’ hi a veng thei ang em?
A tihtawp vek theih loh laiin, ‘harsatna’ awm theihna tur tihtlem nan thil tam tak i tih theih a awm . Nunphung tihdanglam tur:
- Khaw lum lakah inveng rawh:Tui lum-a inbual emaw, inbual emaw loh tur. Ni khaw vawt leh AC awmna hmuna kal hunah thawmhnaw lum ha thin ang che.
- Tui in tam: Nilengin tui tam tak in thin ang che.
- Zu khap: A theih ang anga zu in tlem.
- Air travel: Khualzin i nih chuan commercial aircraft-ah chauh thlawk la, pressurized cabin nei rawh.
- Stress enkawl rawh: I rilru tih hahdam theih dan tur zawng rawh.
A tlangpuiin hrisel taka awm theih nan, .
- Natna laka inthiarfihlim rawh: Damlote lakah a theih ang anga inthiarfihlim rawh. Kut sil fo thin ang che.
- Meizial zuk loh tur.
- Exercise: Exercise light hi a tha a, mahse exercise hahthlak lutuk (intensie weight training ang chi) erawh chu pumpelh tur a ni. Exercise i tih laiin tui tam tak in thin ang che.
- Natna dang thunun: Natna dang, zunthlum ang chi i neih chuan i Doctor thupek angin uluk takin thunun tur a ni.
- Vaccine lak: Vaccine mamawh zawng zawng chu a hun takah lak vek tur a ni.
- Naupai: Naupai emaw, naupai tum emaw i nih chuan damdawi lam thurawn la nghal tur a ni.
Take-Home Thuchah a ni
- Sickle cell crisis hi natna khirh tak a ni a, chu chu sickle ang maia thisen sen ten thisen kalna kawng te te an block avangin oxygen tlakchhamna a thlen thin.
- A lan chhuah dan ber chu natna nasa tak lo chhuak nghal, thawk harsa, leh hah lutuk te hi a ni.
- Hetiang dinhmun hi tui tlakchhamna, infection, stress, leh temperature inthlak danglamna ang chi thil vang a ni thei.
- I doctor enkawl dan tur chu zawm fo ang che. In lama natna hi thunun theih loh a nih chuan damdawi in Emergency Department (ETU)-ah kal nghal tur a ni.
- Tui tam tak in fo te, khawsik laka invenna te, nunphung hrisel tak vawn reng te hian ‘harsatna’ thlen theihna a tihziaawm thei a ni.
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