Hemophilia chungchanga hriat tur thilte

Cut te tak te i hmuh chuan rei vak lo hnuah thisen chhuak chu a reh ta a ni lawm ni? Hei hi kan taksaa mechanism mak tak avang a ni. Mahse mi thenkhat tan chuan thisen chhuah hian hei hi awlsam takin a titawp thei lo. Cut tlemte pawh hian thisen a chhuah chhunzawm thei. Vawiin hian hemophilia tih hi kan sawi dawn a, chu chu mi tam takin an hre tawh a, mahse an hre chiang lo hle. Kan hlauh hmain eng nge a nih tak tak i hrethiam ang u.

Engtin nge hemophilia i vei tih i hriat theih ang?

A awlsam zawngin kan taksaa thisen chhuahna hmun apiangah ‘plug’ ang chi thil a lo awm a, chu chuan thisen chhuah chu a titawp a ni. Hei hi fibrin clot kan ti a. He clot siam tur hian kan thisena protein bik tam tak chu an thawk ho a ngai a ni. Hengte hi "clotting factors" kan tih te hi an ni.

Hemophilia hi heng clotting factors zinga pakhat, a bik takin factor VIII emaw factor IX emaw hi pian tirh atanga a awm loh emaw, a tlahniam emaw a ni. Tichuan, thisen zam chu a lo insiam tha lo va, thisen chhuah chu chawlhsan lovin a chhunzawm zel a ni.

I doctor-in he natna hi i neih a rinhlelh chuan i thisenah test eng emaw zat an ti ang.

• Step hmasa ber: I thisen sample lak a ni a, lab-ah chuan a clot theih nan eng chen nge a rei tih a test thin.
• Step 2: Chu test-ah chuan thil dik lo a awm a nih chuan, i thisenah factor VIII leh factor IX engzat nge awm tih hriat nan test chiang zawk neih a ni ang.

Hemophilia hi eng enkawlna nge ni?

Hemophilia enkawl dan hi i natna chi leh nasat dan azirin a inang lo. Entîr nân, hemophilia na lo tak i neih chuan, hliam i neih hnuah emaw, operation hma emaw chauhvin enkawl i mamawh mai thei.

Mahse, thisen chhuahna hmuna hemophilia na tak i neih chuan, thisen chhuah loh nan leh i ruhte a chhiat leh chak lohna tur venna atan enkawlna mumal i neih chhunzawm zel a ngai ang.

Enkawl dan tlangpui engemaw zat a awm a:

• Clotting factor tlakchham tawh thlak danglam (Replacement therapy) .
• Damdawi bik dang
• Side effects awm thei, ruh chhunga thisen chhuak te enkawlna

Clotting factor tlakchhamna pe chhuak

Hei hi a enkawlna ber a ni. Hei hian i taksaah clotting factor awm lo dose chu vein (intravenously emaw IV emaw) kaltlangin pek a huam a ni.

• Factor VIII hi hemophilia A vei tan a niPe.
• Factor IX hi hemophilia B vei te hnenah pek thin a ni.

Heng thilte hi kawng hnih a siam a ni. Pakhat chu thisen plasma pek atanga lak a ni . A dang chu laboratory a siam synthetic emaw recombinant DNA factors emaw a ni . Tunlaia factor chi thar awmte hi taksaa rei zawk awm thei tura duan a ni. Chuvang chuan tun hma angin inject fo a ngai tawh lo.

Damdawi bik dang

Clotting factor therapy bakah hian tunlai damdawi dang, thisen chhuahna control thei tur a awm bawk. I doctor chuan hengte hi a hrilhfiah ang che.

Ruh chhunga thisen chhuak leh harsatna dang awm thei te fimkhur rawh.

Hemophilia chhinchhiahna tlanglawn tak chu ruhkawr chhunga thisen chhuak hi a ni . Hei hi khup, khup, leh ke ruh ang chi hmunah te a thleng thei a ni. Chutiang a nih chuan ruh chu a lo hring a, a na bawk.

• Enkawlna: I factor treatment lak nghal a pawimawh. Chutiang a nih loh chuan ruh chu a tichhia reng thei a ni. Chu bâkah, i doctor chuan i ruh chu chawlh hahdam la, ice hnawih tûrin a fuih bawk ang che . Hei hian natna leh hliam a tiziaawm ang.
• Chumi hnuah: Natna a reh hnuah, ruh inzawmna leh chakna siam\hatna tura pui turin physical therapy pawh a rawt thei bawk.

Tin, taksa tihchaknaah i fimkhur a ngai bawk. Hemophilia vei tan chuan infiamna zawng zawng hi a tha vek lo. Hlauhawm, contact sports hian chhungril thisen a chhuah tir thei. I doctor nen inbia la, eng exercise leh sports nge i tan a tha leh tha lo tih rel rawh.

Enkawlna hian harsatna a thlen thei em?

Tunlai hian enkawlna hi a him hle nachungin, i hriat tur thil pahnih a awm.

1. Thisen atanga kai theih natna

Tun hma, kum 1980 chho vel khan thisen atanga thil thleng avanga HIV leh hepatitis ang chi virus kai theihna a sang hle. Mahse tunah chuan chutiang lam chu i ngaihtuah a ngai tawh lo. Tunlai hian thisen petute chu uluk takin screening an nei a, thisen pek zawng zawng chu virus awm leh awm loh endik a, hmanraw bik hmanga tihthianghlim vek a ni. Chuvangin tunah chuan enkawlna atanga natna kai theihna a tlem hle. Mahse, doctor-te chuan hepatitis A leh B laka vaccine lak hi an rawt a ni.

2. Immune system inthlak danglamna (Inhibitors) .

Hei hi a buaithlak deuh a, mahse hriatthiam a pawimawh. A chang chuan kan taksa immune system, kan taksa invenna system hian he clotting factor kan pek hi ‘hmêlma’ anga kan pek hi a hre chiang hle. Tichuan, chu factor chu a tichhe tan ta a ni. Hei hi "inhibitors" siamna kan ti a ni. Chutiang a nih chuan i enkawlna chu a thawk tha lo mai thei. Chuvangin, i doctor chuan i thisen a test fo ang a, hetiang hi a thleng em tih a enfiah ang.