I thinlung aortic valve hian flap pakhat a nei em? (Unicuspid Aortic Valve) - Hemi chungchang hi han sawi ila!

A chang chuan, ‘Aw, ka fa hian thinlung lam harsatna tenau a nei a, thinlung mur mur nen a piang’ tih kan hre fo thin? A nih loh leh, ṭhalai pakhatin thawk a harsat emaw, a rilru a na emaw chuan doctor-te chuan, ‘Heart valve-ah hian harsatna tlemte a awm’ an ti ṭhin. Chutiang chuan thinlung natna pakhat, a tlem hle a, mahse hriat a pawimawh em em chu kan sawi dawn a ni.

He aortic valve pakhat (`Unicuspid Aortic Valve`) hi eng nge ni?

A awlsam zawngin, i thinlunga aortic valve hian a tlangpuiin a neih ṭhin pathum aiin leaflet pakhat chauh a nei a ni. "Unicuspid" tih thumal hi "single-leaflet" tihna a ni. Kawngkhar pahnih ni lovin lock pakhat chauh nei angin ngaihtuah rawh.

Heng lehkhabu te hi kawngkhar te tak te ang mai a ni. An inhawng a, an khar a, chu chuan oxygen tamna, thisen thianghlim chu thinlung veilam ventricle - thinlung hnuai lama veilam chamber - atanga aorta -ah a kal thei a ni. Chumi hnuah chuan aorta hian taksa pum puiah thisen a pump chhuak ta a ni. Chuvangin, he valve-a leaflet awm zat a tlem chuan thisen kalna tur daltu tenau te a awm thei a ni.

Hetiang natna, Unicuspid Aortic Valve vei thenkhat hian thinlung lam harsatna dang an nei thei bawk. Entir nan:

• Aortopathy : Hei hian aorta bang a chak lohna a kawk a ni.
• Ventricular Septal Defect (VSD) : Thinlung hnuai lam chamber pahnih inkar bang chhunga khur awm.
• Patent Ductus Arteriosus (PDA) : Nau piang hnua khar tur thisen kalna kawng chu a inhawng reng a.
• Coronary Artery Anomalies : Thinlung thisen petu artery-a inthlak danglamna thenkhat.

Hei hi thil awm lo tak a ni. Mipui zahawm zinga 0.02% vel a nghawng a ni. Tin, mipaah ​​a tam zawk bawk.

Hei hi chi hrang hrang a awm em?

Ni e, ``Unicuspid Aortic Valve'' hi chi hnih lian tak a awm. Heng chi hnih inthlauhna chu leaflet (leaflet) pahnih te valve wall nena an inzawmna gap a ni a, chu chu ``Commissure'' an ti a ni. Hei hi hetiang hian i hrethiam thei ang. I hmui chu i hmaiah a innghat reng a, mahse an inzawm khawm thei a, an inthen thei ang tih han ngaihtuah teh, a dik em? Chu chu ``Commissure'' tih chu a ni.

Heng chi hnih hi:

1. Acommissural type: Hei hi a na ber chi a ni. Hetiang a nih chuan commissure a awm lo, chu chu gap a awm lo tihna a ni. Tin, aorta nen pawh a inzawm lo bawk. Leaflet te chu a inzawm khawm vek a, weld khawm ang mai a ni. Thisen chu khur te tak te, pinhole ang maia luang chhuak chauh a ni.

2. Unicommissural chi hrang hrang: 1.1.Hei hi a dang aiin a na lo deuh a, a tam ber chi a ni bawk. ``Commissure`` pakhat a nei a, chu chu gap pakhat a ni. Aorta nen pawh a inzawm bawk. Hetiang valve hi hawn a nih chuan line ang mai a ni. Mi thenkhat chuan sangha hmui nen an tehkhin a.

Eng symptom nge i hmuh theih?

Puitlingin he natna (Unicuspid Aortic Valve) a neih chuan a lan chhuah dan tlangpui chu:

• Thâwk lak tawi : Tlemte i hah chuan stairs i chhoh dawnin i muhil ang tih i hre mai thei.
• Luak chhuak : I ding chhuak thut chuan i luak chhuak thei.
• Angina : Hei hi rilru natna emaw, tightness emaw hriatna a ni. Mi thenkhat tan chuan hei hi hmui, kawr, a nih loh leh kutphah thlengin a darh thei a ni.
• Fainting/fainting : Vawikhatmah hriatna hloh.

Hetiang natna vei naupang tê tête hian left-sided heart failure ang chi natna an nei tlangpui . Tin, an kum rualpui naupang dang ang bawkin an thau an tlahniam duh hle bawk a, chu chu an thau tlem hle tihna a ni.

A hmaa kan sawi tawh ``Acommissural`` type, chu chu a nasat ber chi a ni a, naute naupang tak takah chuan symptoms a lang thin . Mahse ``Unicommissural`` type nei te chuan kum 20 emaw 30 emaw an tlin hma loh chuan symptom an nei lo thei a, chu chu puitling naupang an nih thlengin a ni.

Engvangin nge hetiang hi a lo awm? Eng nge a chhan?

Hetiang dinhmun, ``Unicuspid Aortic Valve'' tia koh hi naute chu a pum chhunga a la awm laiin a tlangpuiin a lo piang tur hnah pathumte chu a lo piang tan a, chutah chuan a inthen ai chuan an inzawm khawm a, pakhat an lo ni ta a ni. Hei hi naute pian hma pawhin a thleng thin .

Researcher-te chuan chiang takin an la finfiah thei lo nain, hei hi ``inherited condition'' a ni thei niin an ring.Chu chu genetic influence a awm thei tihna a ni.

Hei hian eng harsatna nge a thlen theih?

Unicuspid aortic valve nei chuan hun kal zelah harsatna hrang hrang a nei thei a. A bulpui berte chu:

• Aortic valve stenosis : Hei hi valve a inhawng tha lo a, thisen kalna a tikhawlo a ni. Hei hian thinlungin thisen pump turin hna a thawk nasa zawk a ni.
• Aortic valve regurgitation : Valve hi a khar tha lo va, thisen pump chhuah thenkhat chu thinlungah a leak leh thin.
• Infective Endocarditis : Thinlung lining, a bik takin valve-a natna hrik a ni. Valve pangngai lo nei te chu an hlauhawm zawk.
• Aortic Dissection vei theihna a sang : Hei hi aorta wall chu a chhung atanga a inthen nghal mai a, a na tak a ni.

Pawimawh: Natna hi a hun taka hriatchhuah leh enkawl a pawimawh hle a, heng harsatnate hi a lo thlen hma hian.

Engtin nge hei hi i hmuh?

Doctor hmu tura i kal chuan i taksa enfiahnaah stethoscope hmangin i thinlung chu a ngaithla ang . Doctor chuan i aorta bulah thinlung ri danglam tak (``heart murmur``) a hriat chuan hei hi a ringhlel mai thei. Tichuan, test dang engemaw zat neih belh leh a rawt mai thei.

Eng test nge tih a nih?

He ``Unicuspid Aortic Valve'' natna hi a awm leh awm loh dik taka finfiah nan test lian ber berte chu:

• Transthoracic Echocardiogram (TTE) : Hei hi thinlung ultrasound scan ang a ni. A rilru chhungril lamah tih a ni. Thinlung pianzia leh a valve hnathawh dan a teh thiam zawk.
• Transesophageal Echocardiogram (TEE) : Hei hi echocardiogram a ni bawk. Mahse, tube te tak te chu kawchhung atang hian thun a ni a, thinlung chu chaw kawng kaltlangin a thlir a ni. Hei hian TTE aiin image chiang zawk a siam thei a ni.
• Cardiac Computed Tomography (CT) scan : Hei hian thinlung leh aorta cross-sectional 3D image a siam thei a.
• Heart MRI (Magnetic Resonance Imaging) : Hei hian thinlung insiam dan leh hnathawh dan chipchiar takin a hriattir thei bawk.

Engtin nge enkawl a nih?

Hei hi enkawl dan hi kum leh a natna lan chhuah dan nasat dan azirin a inang lo.

Naupang tê tête enkawlna kawng hman tlanglawn tak takte chu:

• Surgical Valvotomy : Hei hian valve tissue inzawmkhawm chu tihtlak a, lehkhabu thar siam a ni.
• Valvuloplasty : Hei hi balloon ang chi thil hmanga valve hawn a ni.
• Commissurotomy : Mitmeng inzawmkhawmna hmun ``Commissures'' an tih te chu surgery hmanga then hran.
• Ross Procedure : Hei hi surgery buaithlak deuh a ni. Hemi chungchang hi a hnuah kan sawi belh leh ang.

Puitling tan chuan aortic valve siamthat (Unicuspid Aortic Valve repair) emaw, valve thar (replacement) emaw hmanga thlak emaw nan operation neih a ngai tlangpui .

Enkawlna hian side effect/complication a nei em?

Surgery dang ang bawkin, he enkawlna hian harsatna awm thei engemaw zat a nei a ni. Mahse hengte hi mi zawng zawngin an tawng vek dawn lo. Lungngai suh, i doctor chuan hengte hi uluk takin a hriattir ang che.

Harsatna awm thei tlangpui thenkhat chu:

• Kaichhawng
• Thisen a chhuak thin
• Thisen chhuah tam lutuk (`Bleeding`) .
• Endocarditis (valve natna a awm) .
• Valve siamthatna atana hman thin patch-a harsatna awm.
• Complete Heart Block : Thinlung electrical signal thawn chhuahna titawp.
• Lung natna
• Valve atanga thisen chhuak chu a sir dik lo lamah a chhuak.
• Lungphun (Heart Rhythm) pangngai lo

Eng chen nge tihdam a ngaih?

Hei hi i tih dan chi hrang hrang a zirin a danglam ang. A dam leh theih nan kar khat atanga thla engemaw zat chhung a ngai thei. I doctor chuan eng chen nge i chawlh a ngaih tih leh engtikah nge hna pangngai i thawh leh theih ang tih chiang takin a hrilh ang che.

Hetiang dinhmun nen hian nun chu eng ang nge ni ang?

Unicuspid Aortic Valve i neih chuan operation i mamawh ngei ang . Dik tak chuan i dam chhungin vawi khat aia tam i valve siamthat emaw thlak emaw i mamawh mai thei. Lung lam harsatna dang i nei thei bawk. Operation hnuah pawh thisen tithianghlimtu (anticoagulants) i ei chhunzawm a ngai thei bawk a, hei hi valve i neih chi hrang hrang a zirin a ni.

Mahse hei hi sawi tur a ni bawk he ``Unicuspid Aortic Valve'' hi automatic in a tha lehzual tur thil a ni lo . A dinhmun chu siamthat tura operation i neih hma loh chuan a awm reng a ni.

Chanchin tha a awm. Zirna pakhatah chuan ``Unicuspid Aortic Valve'' tih natna avanga aortic valve surgery nei zinga 97% chu kum 10 hnuah pawh an la dam tih hmuhchhuah a ni

Mahse, he natna avang hian kum 65 hnuai lam chu prosthetic aortic valve pek a nih chuan kum 10 aia dam rei zawng a tihniam thei tih ngaihdan a awm bawk. Chuvang chuan zirchiangtute chuan Ross Procedure hi thalai, thawkrim tan a tha ber an ti. He ``Ross procedure`` ah hian nangmah ngeiin pulmonary valve i la a, natna nei aortic valve awmna hmunah i transplant thin. Tichuan, mi thi atanga pulmonary homograft chu pulmonary valve lakchhuah tawhna hmunah dah a ni. Hei hi a buaithlak deuh a, mahse a result a tha hle niin an sawi.

Nangmah lam atanga eng nge tih i duh?

Operation hnuah i incision/cut enkawl dan tur chungchangah i doctor thupek uluk takin i zawm tur a ni . Eng chen nge i chawlh a ngaih tih leh engtikah nge lirthei khalh leh nitin thil dang i tih tan theih ang tih a hrilh bawk ang che.

I theihnghilh suh: Damdawi ei tur chu a hun taka ei a pawimawh hle a, doctor-in a sawi angin, ni ruat saah clinic-ah kal a pawimawh hle.

A châng chuan, "Aw, lung natna vei tur khawpin ka la upa lo," tiin i ngaihtuah ṭhin a, mahse i rilru a na a, thawk harsa i la nei tho.A hnuaia mi hi i neih chuan doctor pan ngei ngei tur a ni. Unicuspid Aortic Valve operation i neih hnuah pawh i doctor nen follow-up appointment i nei chhunzawm zel ang. Operation hnua harsatna (infection ang chi) a awm chuan emergency treatment i mamawh mai thei.

Doctor hnenah eng zawhna nge i zawh tur?

Doctor hmu tura i kal dawnin zawhna i neih apiang zawh hlau suh. Zawhna i zawh theih ṭhenkhat chu hetiang hi a ni:

• Ka tan enge inenkawlna tha ber?
• Valve thlak danglamna chi hrang hrangte hi eng nge an danglamna? (i.e., artificial valve leh biovalve hmanga siam)
• Engtiang chiahin nge operation ka neih vat a ngaih?
• Valve dah thar hian eng chen nge a daih?

I thinlunga thil pakhatin hna a thawk tha lo tih i hriat hian thil awlsam a ni lo. Mahse, hun kal zelah doctor-te chuan he natna hi enkawlna tha zawk an siam chhuak ta a ni. I tana tha ber tur chu i doctor nen sawiho rawh. Since this is a rare condition , i tan a tha ber tur chu doctor pakhat, a tawnhriat nei tawh zawng rawh. Entirnan, zirchiangtute chuan surgeon pakhatin kum khatah Ross procedure 15 tal a tih tur a ni an ti.

A tawp berah chuan hriat reng tur pawimawh ber (Take-Home Message) .

Okay, chuvangin tunah chuan he thinlung natna `(Unicuspid Aortic Valve)` tih hi vawiin a kan sawi tawh hi in hriatthiam ka beisei. Hei hi pianpui leh hmuh tur awm lo thil a ni tih hre reng ang che. Mahse, dik taka hriat chhuah a nih a, a hun taka enkawl a nih chuan nun ṭha tak i hmang thei a ni . Nangmah emaw, i hriat miin emaw heng symptoms te hi an neih chuan doctor pan a, thurawn lak hlau suh. A bik takin, hetiang natna hlauhawm tak enkawl hian medical team tawnhriat ngah tak takte puihna lak a pawimawh hle. I thinlung kha enkawl rawh. I nunah thil hlu ber a ni!

` Lung natna, Aortic Valve, Unicuspid Aortic Valve, Lung Surgery, Pianpui Lung Natna, Thâwk Tawt, Chhung Na