Nu naupai i nih chuan i scan lai khan ‘Ventriculomegaly’ tih thumal hi i hre tawh mai thei. Chu chu i hriat chuan hlauhna leh mangang nasa tak i nei ngei ang, a dik em? ‘Aw, ka naute chungah hian thil pawi tak a awm em?’ tiin i ngaihtuah ngei ang. Hetiang hunah hian nu tam takin chutianga an inhriat chu thil pangngai tak a ni. Chuvangin, sawi belh ngai lovin, tunlai hian he natna ‘Ventriculomegaly’ an tih hi awlsam tak, hriatthiam theih takin i sawi ang u.
Ventriculomegaly hi eng nge ni?
A awlsam zawngin, Ventriculomegaly chu i naute thluak chhunga tui (fluid-filled cavities) (hengte hi ‘ventricles’ kan ti) chu a tlangpui aia lian a nih chuan a ni. Hetiang hian han ngaihtuah teh: kan thluak hian a chhungah hian heng chamber te te hi a nei a. Heng chamber chhungah hian tui bik ‘cerebrospinal fluid’ emaw `(Cerebrospinal fluid - CSF)’ an tih a awm a.
He `(CSF)` fluid hi a pawimawh hle. Kan thluak leh kan ruhro (spinal cord) tana venhimna cushion ang mai a ni. Chu chu heng taksa pengte hi chhiatna laka a humhim a, a chawm a, bawlhhlawh a paih chhuak tihna a ni. A tlangpuiin he `(CSF)` fluid hi siam chhuah a ni a, thluak chhungah leh a chhehvelah a kal a, chutah chuan taksaah a lut leh thin. Hei hi thil thleng reng a ni a, cycle ang mai a ni.
Mahse, a châng chuan he `(CSF)` tui kalna kawngpuiah hian inkharkhip a awm a nih chuan, emaw, tui siam chhuah leh lakluhna inkara inthlauhna a awm chuan, he tui hi ventricles an tih cavities chhungah a tang a, a pung khawm tan ta a ni. Chu chu chutiang khur chu a lian zauh zauh a, balloon tuiin a khat ang maiin a lian chho ta a ni. Hei hi nausen lai, chu chu nausen pum chhunga a awm laiin `Ventriculomegaly` kan tih chu a ni.
‘Hydrocephalus’ tih thumal pawh i hre tawh mai thei. Hei hi cerebrospinal fluid (CSF) a awm khawm avanga ventricles lian thamna a ni bawk a, chu chuan thluak chungah pressure a tisang bawk. Doctor-te chuan naute pian hnuah ‘hydrocephalus’ natna hi an hmuchhuak tlangpui. Nausen pum chhunga ventricles a lo lian chuan ventriculomegaly an ti a.
Hei hi thil awm dan tlangpui a ni em?
United States atanga data atanga a lan dan chuan he natna hian nau piang nung 1,000 zinga pahnih vel a nghawng thei a ni. Mahse a pawimawh ber chu a tam zawkah chuan hei hi natna khirh tak a ni a, naute a pian hian harsatna a thlen lo. A tam zawkah chuan heng ventricles te hi an lo thang lian tawh lo va, a nih loh leh an size pangngaiah an tlahniam leh thin. Chuvangin he hming i hriat hian hlau lutuk a ngai lo.
Ventriculomegaly natna lan chhuah dan chu engte nge ni?
A tam zawkah chuan nausen pum chhunga ventriculomegaly chhinchhiahna hmuh tur a awm lo.I doctor chuan naupai laiin ultrasound pangngai tih laiin i naute ventricles a lian tih a hmu tlangpui ang. Naute ventriculomegaly na lo nei te hian an pian hnuah pawh symptom an nei lo tlangpui.
Mahse, a natna a nasat chuan naute hian a pian hnu ni engemaw zat hnuah hydrocephalus natna a lantir thei a ni. Heng chhinchhiahnate hi:
- Naute lu chu a danglam bik lo hle emaw, a lu lian zawng a lo pung thut emaw a ni.
- Naute lu chunglam (fontanel) hmun nalh tak chu a hring leh a bulh angin a lang.
- Mit chu a dinglam hawi thei lo va, hnuai lam hawi ang maiin a lang (downward gaze).
- Chauh lutuk emaw, rilru hah lutuk leh tap reng reng emaw.
- Luak chhuak fo thin.
- Bawnghnute in harsat emaw, in duh lohna emaw.
Eng thilin nge hei hi a thlen?
Ventriculomegaly hian chhan hrang hrang a nei thei. A châng chuan , a chhan chiang tak hmuh tur a awm lo. Hriat reng tur pawimawh tak chu he dinhmun hi a tlangpuiin thil thleng mai mai a ni a, nu leh pate gene atanga rochun emaw, boruak avanga lo awm emaw a ni lo
A chhan langsar ber pahnih chu:
- Kan sawi tawh ``CSF'' fluid zalen taka a kal theihna leh taksa chhunga a natural absorption-ah hian eng emaw zat tihkhawtlai emaw, inthlauhna emaw a awm a.
- Hliam emaw, harsatna dang emaw chuan naute thluak hmasawnna a nghawng thei a ni.
Hei hi genetic thil a ni em?
No. Ventriculomegaly hi thlahtute atanga lo piang a ni lo. Hei hian random occurrence a ni tihna a ni a, nu atanga naute hnena kal zel thil a ni lo tihna a ni.
Risk factors te chu engte nge ni?
Ventriculomegaly hi thil thleng mai mai a ni fo thin. Naupai laiin amah chauhin emaw, harsatna dang nen emaw a awm thei bawk. Zirna thenkhatah chuan a hnuaia thil awmte hian naute ventriculomegaly vei theihna a tipung deuh thei tih hmuhchhuah a ni:
- Spina bifida (nau piangsual, ruhro (spinal cord) inrawlhna).
- Agenesis of the corpus callosum (ACC) (thluak chanve pahnih inzawmkhawmtu structure a lo thanglian tha lo).
- Nu naupaiah natna kai, entirnan, syphilis emaw cytomegalovirus (CMV) emaw.
- Chromosomal dik lo, entirnan, Down syndrome.
Eng harsatna nge awm thei?
Ventriculomegaly vei naute hmalam hun chu a nasat dan leh a chhan bulpuiah a innghat a ni. A tlangpuiin ventricles te hi a lian deuh chauh a, ultrasound-ah thil danglam dang a awm lo a nih chuan a tlangpuiin a rah chhuah chu a tha hle.
Mahse, naute ventricles lian tak tak nei, emaw, naute hriselna lama harsatna dang nei, nausen pian tirh atanga ventricles lian zawk nei te chu harsatna a thlen theihna a sang zawk. A tlem hle nachungin, naute ventriculomegaly na tak neia piangte hian thluak lam harsatna emaw, an thanlenna lama harsatna emaw an nei thei a ni.
Ventriculomegaly vei naute chu a dam thei ang em?
Ni e, a dik tak zet. Ventriculomegaly hi enkawl theih a ni.
Engtin nge Ventriculomegaly hi an hriat theih?
Doctor-te chuan he natna hi nausen taksa (fetal anatomy scan)-ah an hmuchhuak tlangpui a, naupai kar 18 leh kar 22 inkarah an ti thin. A châng chuan naupai hnu lamah hriat theih a ni. He ultrasound neih chhung hian doctor chuan naute thluak hmun thenkhat a teh thin. A tehna chu a tlangpuiin a lian a nih chuan naute hian ventriculomegaly a nei tihna a ni thei.
Tichuan, i doctor chuan imaging test tam zawk a order thei a, chu chu nausen MRI (fetal Magnetic Resonance Imaging - MRI) te hi a ni. Hei hian naute thluak thlalak chiang tak tak a la thei a, chuvangin doctor chuan naute ventricles chu chipchiar zawkin a hmu thei a ni. MRI hi a him vek a ni.
I doctor chuan naute thluak ventricle-a tui awm zat enfiah turin i naupai chhung zawngin ultrasound tam zawk a order mai thei.
A then phei chuan amniocentesis an tih test pawh tih theih a ni. Hei hian doctor chuan naute chhehvel amniotic fluid sample tlemte lak nan needle te tak te a hmang a ni. He tui hi test theih a ni a, natna hrik a awm leh awm loh enfiah theih a ni a, chu chu cytomegalovirus ang chi hi a ni.
Naute a pian hnuah naute thluak ultrasound emaw MRI emaw tih leh a ni a, naute hian hydrocephalus a nei em tih leh surgery a ngai em tih hriat a ni.
Ventriculomegaly hriat theihna tur tehfung
Nausen ventriculomegaly nasat dan hi ventricle zau zawng atanga teh a ni. Nausen pangngaiah chuan thluak ventricles hi millimeter 10 (mm) aia zau lo – pea ang vel a zau a ni.
- Mild: Ventricles 10 leh 12 mm inkar a ni.
- Moderate: Ventricles 13 leh 15 mm inkar a ni.
- Na tak: Ventricles hi 15 mm aia zau a ni.
Engtin nge enkawl a nih?
Ventriculomegaly hi i naute pian hnuah enkawl a ni a, a tlangpuiin i naute hian hydrocephalus chhinchhiahna a neih chauhvin a mamawh thin.
Doctor chuan naute ultrasound emaw MRI emaw a ti ang. Naute ventricles-ah hian tui him lo tak a la awm chuan thluak surgery neih a ngai mai thei a, chu chuan tui awm zat leh thluaka pressure tihziaawmna tur a ni.
Surgery chi khat chu naute thluaka shunt dahin a tui chu paih chhuah a ni (ventriculoperitoneal shunt surgery). Shunt hi flexible tube a ni a, chu chuan extra cerebrospinal fluid (CSF) chu taksa peng dang (riltam ang chi)-ah a luang lut thei a ni.
A then phei chuan surgery chi dang endoscopic third ventriculostomy (ETV) an tih chu a ngai thei bawk. Hetiang tih danah hian surgeon chuan naute lu chunglam (fontanel) kaltlangin endoscope a dah lut thin. Hei hian cerebrospinal fluid (CSF) chu thluak chhung leh a chhehvela luang lut turin kawng dang a siam leh a ni.
Ventriculomegaly hi a mah chauhin a tha thei em?
Ni e, a chang chuan ventriculomegaly hi enkawl ngai lovin a dam thei bawk. A nih loh leh chutiang chuan a awm reng thei a, naute a pian hmain a mah chauhin a kal bo thei bawk. I doctor chuan i naupai chhung zawngin naute thluak ventricles lian leh te a enfiah ang.
Ka naute hian ventriculomegaly a vei a nih chuan eng nge thleng ang?
Naupai laiin he natna hi i vei tih hmuhchhuah a nih chuan i doctor chuan i naute thluak chu uluk takin a enfiah ang. I naute a pian hnuah naute ventricles a lian em tih an enfiah ang. Ventricles lian zawk emaw thluaka pressure emaw a awm loh chuan i naute chu a pian hnuah operation a ngai lo mai thei. Naute natna khirh tak nei tam zawk hian hun rei tak chhung hriselnaah nghawng an nei lo.
Ventriculomegaly vei naupang piangte chuan a hnuah hydrocephalus an nei thei a ni. Chutiang hunah chuan zai a ngai mai thei. Naute chu operation hnuah kum engemaw zat enfiah a ngai dawn bawk a, chu chuan naute thluaka pressure chu a pangngai reng em tih enfiah a ngai dawn a ni.
Ventriculomegaly chungchangah hian i buai tur em ni?
Nausen pakhatin ventriculomegaly na lo tak a neih a, hriselna lama harsatna dang a neih loh chuan ventriculomegaly hian hun rei tak chhunga nghawng a neih loh theihna chance 90% vel a awm.
I naute hi damdawi lam harsatna neia piang a nih thu i hriat hian lungkhamna i neih hi thil pangngai a ni. Zawhna i neih chuan doctor zawt rawh. I naute chu a hrisel dawn em tih i hlauhthawnna tihziaawmna turin an pui ang che. An theihtawp chhuahin an thlawp ang che.
Hei hian nau neih a nghawng em?
A tlangpuiin a ni lo. Naute lu a lian hle a nih loh chuan vaginal delivery pangngai neih theih a ni.Damdawi lam harsatna dang a awm emaw, naute lu a lian a nih chuan cesarean section (C-section) neih a ngai mai thei. I doctor chuan i naute chu mamawh bik nei naute enkawlna lama tui bik damdawi inah i hrinsak turin a rawt thei bawk. Hei hi a chhan chu specialist doctor leh Neonatal Intensive Care Unit (NICU) ang chi facility a awm vang a ni.
Ventriculomegaly hi ven theih a ni em?
No. Ventriculomegaly venna tur hian engmah tih theih a awm lo. I sualna a ni lo.
Ventriculomegaly hian naute hian Down syndrome a nei tihna em ni?
Hei hi a dik hauh lo. Ventriculomegaly leh Down syndrome hi inzawmna a awm a. Ventricles lian zawk nei nausen chu Down syndrome ang chi chromosomal disorder vei theihna chance a sang deuh thei a ni. Mahse, ventriculomegaly i neih chuan i naute hian Down syndrome a nei dawn tihna a ni hauh lo.
Doctor hnenah eng zawhna nge i zawh tur?
Ventriculomegaly hmuhchhuah dan tur zawhna neih hi thil pangngai tak a ni. I doctor hnenah heng zawhnate hi i zawt thei ang:
- Test tam zawk tih ka ngai em?
- He diagnosis avang hian thil danglam ka tih tur a awm em?
- Ventriculomegaly hi enkawlna tur a awm em?
- Ka naute hian cognitive emaw developmental delays a nei ang em?
- Ka naute a pian hnuah operation ka mamawh dawn em?
A tawi zawngin (Take-Home Message) .
Naupai laiin Ventriculomegaly natna hmuhchhuah a nih chuan thil mak tak a ni thei. "Ka naupai lai hian thil dik lo a awm em?" emaw, "Thil dik lo ka ti em?" Khawngaihin hre reng ang che, thil dik lo i ti lo va, a tam zawkah chuan i naute chu hrisel takin a piang ang. He diagnosis hian eng nge a awmzia leh i pian hnua eng enkawlna nge i mamawh dawn tih chu i obstetrician nen sawiho rawh. I zawhnate chhang tur leh i naupai leh naute hrisel taka awm theihna tura a tul zawng zawng la turin a awm reng a ni. Hlauthawng suh la, i doctor thurawn zawm rawh.
` Ventriculomegaly, nausen thluak, CSF, hydrocephalus, naupai scan, naute hriselna, thluak kawng hrang hrang











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh