Mi pakhat damlo a, taksa tui leh chi a tlem avangin damdawi inah dah a nih chuan doctor-te chuan a tlakchhamna phuhruk nan saline an pe ang. Chu chu thil pangngai a ni. Mahse, a chang chuan, taksaa sodium level hniam tak hi rang tak leh rang taka a pun chuan thluak a tichhe thei tih i hria em? Chu chu Central Pontine Myelinolysis an tih, natna hlauhawm tak, mahse na tak kan tih chu a ni. A hming hi a buaithlak deuh nachungin, a awlsam zawngin sawi ila.
A awlsam zawngin, hei hi eng ang dinhmun nge ni?
Hei hi nervous system nena inzawm natna a ni. Taksa mamawh electrical signal te hi kan thluaka nerve cell (neurons) kaltlangin a kal a. Heng nerve cell vel hi venhimna khuh a awm a. Myelin sheath kan ti a . Electric wire vel plastic sheath ang mai a ni. He myelin sheath hian electrical signal te chu rang tak leh engmah daltu awm lovin a kal thei a ni.
Central Pontine Myelinolysis (CPM) hi thluak hmun bik, a bik takin pons-a myelin sheaths te a chhiat chuan a thleng thin. He chhiatna hian taksa peng hrang hrang hnathawh a nghawng thei a ni.
A châng chuan 10% vêlah chuan he chhiatna hian pons chauh ni lovin, thluak hmun dang pawh a nghawng thei a ni. Chuvangin he dinhmun hi hming zau zawk dangin hriat a ni. Chu chu Osmotic Demyelination Syndrome (ODS) natna a ni.
Hetiang dinhmun hi a awm fo lo a, mahse intensive care unit (ICU)-a admit zinga 2.5% vel chu ODS vei theihna an nei tih hmuhchhuah a ni.
Hetiang dinhmun a lo awm chhan hi eng nge ni?
A chhan ber chu taksaa sodium level (chu chu kan ei chi (salt)-a awm) a hniam lutuk hian a pung thut a, a rang hle bawk . He hlauhawmna hi a bik takin taksaa sodium level ni hnih aia tam a tlahniam a, enkawlna pek a nih chuan a sang hle.
A pawimawh ber chu, hei hi kan ei leh in a ni lo. Hei hi damdawi inah thil thleng thei a ni a, sodium hi thisenah pek a nih chuan , chu chu saline hmangin, damdawi atan a ni.
Hetiang hian han ngaihtuah teh. Mi chu ni tam tak chhung chu a luak nasa hle a, a nih loh leh ril\am a nei bawk. Tichuan, tui chauh ni lo, sodium ang chi chi (salts) te pawh an taksa atangin a bo ta a ni. Damdawi ina an lo kal hian an sodium level a hniam hle. Tunah chuan doctor-te chuan an sodium level chu a pangngaia hruai kir leh tumin saline an pe ta a ni. Mahse, damloin risk factor dang a neihte an hriat loh chuan sodium level chu tlemin an tisang thuai thei a ni.
Chutiang a nih chuan thluak cell chhunga tui chu cell atang chuan a leak chhuak nghal a. Cell te chu grape vawt ang maiin an tlahniam ta a ni. He inthlak danglamna rang tak hi kan sawi tawh myelin sheaths tichhetu chu a ni.
Tute nge risk sang zawk?
Mi zawng zawng hian an sodium level a san lutuk chuan he natna hi an nei vek lo a, mahse mi thenkhat erawh chu an hlauhawm zawk thung.
| Risk group a ni | Hrilhfiahna |
|---|---|
| Zu ruih hmangte | Nutritional deficiency leh salt imbalances hi rei tak zu in thinte zingah a awm fo thin. |
| Liver transplant hmanga enkawl damlote | He risk hi a bik takin liver transplant surgery nei tawhte tan a sang hle. |
| Naupai laiin Hyperemesis a awm thin | Hyperemesis Gravidarum, naupai laia luak chhuak tawp lova awm hian taksaa chi (salt level) nasa takin a ti tlahniam thei a ni. |
| Hun rei tak damlohna | Hun rei tak chhunga damdawi lama harsatna dang, taksa tichak lo emaw, ei leh in lama harsatna thlentu emaw chuan a hlauhawmna a tipung a ni. |
He natna lan chhuah dan engte nge ni?
Taksa sodium level siamthat atanga ni hnih atanga ni thum chhungin symptoms hi a lang tan tlangpui. Symptoms lang hmasa ber a awm a, chubakah kar tam tak hnua symptoms lo lang te pawh a awm bawk.
| CPM natna lan chhuah dan | |
|---|---|
| A lan chhuah hmasak (ni 2-3 chhung) . | |
| |
| Nakin lawka (kar engemaw zat emaw thla engemaw zat hnuah) lo lang thei symptoms . | |
|
Mahse, hlau suh. A tirah chuan thihna rate hi a sang hle nia ngaih ni mah se, chu chu autopsy hmangin an chhut a ni. Data thar atanga a lan dan chuan he natna vei zinga 94% chu an damchhuak . Tin, 25% leh 40% inkar chu an dam chhuak vek bawk . Mahse, 25% leh 30% inkar chu permanent disability engemaw zat neiin an awm thei.
Doctor-te hian engtin nge hei hi an hmuh?
He natna hi hriat theih dan tha ber chu MRI (Magnetic Resonance Imaging) scan hmangin a ni . I doctor chuan i thluak MRI image te chu a en ang a, myelin sheaths tihchhiatna tilangtu thil danglam bik a awm leh awm loh a enfiah ang.
A châng chuan he chhiatna hi MRI-ah a lang nghal lo va, chuvangin i doctor chuan kar khat emaw kar hnih emaw hnuah MRI dang neih leh turin a ti thei che a ni.
CPM hi MRI image-ah hian condition dang engemaw zat angin a lang thei. Chuvangin, he natna hi a hnuaia natna hrang hrang nen hian inthlunzawm lo turin doctor-te an fimkhur hle a ni.
- Multiple Sclerosis natna a ni
- Autoimmune emaw infectious encephalitis (thluak natna) .
- Central nervous system natna (vasculitis) a awm
- Cancer chi hrang hrang
MRI ringawt pawh hian a chhiatna chu chiang taka a lan theih loh chuan doctor chuan neurological exam thui zawk a nei ang. Hei hian thluaka electrical signal tehna test, EEG (electroencephalography) te pawh a huam thei.
Engtin nge enkawl ang? Invenna hi a tha ber!
Dik tak chuan Central Pontine Myelinolysis enkawlna ber chu he natna hi a lo awm loh nan a ni .
I risk factor i neih apiang (entir nan, zu i in a nih chuan, damdawi dang i neih chuan) i medical team-te hriattir a pawimawh hle a, chutiang chuan him tak leh zawi zawiin i sodium level a tisang thei ang.
Hetiang dinhmun hi i neih chuan enkawlna chu i natna lan chhuah danah a innghat ang. Thil tam takah chuan thla tam tak chhung physical therapy leh rehabilitation treatment dangte a ngai dawn a ni.
Parkinson natna ang chi, khur ang chi i neih chuan i doctor chuan dopaminergic damdawi a pe thei ang .
Damdawi ina i awm chhung hian secondary complication dang lo awm tur venna pawh hi enkawlna atana thil pawimawh tak a ni. Medical team hian hetiang thil hi an enfiah reng dawn a ni:
- Ventilator hmanga innghahna
- Zun kawng natna a awm
- Pneumonia natna (Pneumonia) a ni
- Thisen zam chu thisen zam (Deep vein thrombosis) .
- Muscle atrophy a awm
He natna hi clinical trial pawh kalpui mek a ni a, i doctor pawhin pakhat a rawt mai thei.
Take-Home Thuchah a ni
- Central Pontine Myelinolysis (CPM) hi taksaa sodium (salt) level hniam tak tak leh rang taka a san avangin thluaka myelin sheaths te a chhiat avangin natna khirh tak a ni.
- Hei hi enkawlna tha ber chu invenna hi a ni . Eng enkawlna pawh i dawn hmain i doctor hnenah i medical history kimchang hrilh la, a bik takin zu in chungchang emaw, natna dang emaw chungchang sawi rawh.
- Hetiang dinhmun hi a lo awm a nih chuan damchhuah theihna chance a sang hle a, mahse a dam kim theih nan hun rei tak a ngai thei a, physical therapy pawh a ngai thei.
- Nangmah emaw i hriat miin emaw heng symptoms te hi i neih chuan, a bik takin damdawi inah sodium replacement therapy i neih hnuah doctor hnenah hriattir nghal rawh.











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