Khawsik , khuh, leh flu natna nei reng reng chu i chau em? A chang chuan, “Aw, ka taksa a chak lo,” tiin kan ngaihtuah thin. Mahse chu chu a chhan a ni ngai lo. A châng chuan, chutianga kan tih chhan chu kan taksa invenna, chu chu immune system chak lohna a ni thei bawk. Vawiin hian hetiang dinhmun, CVID an tih, kan nitin nun nasa taka nghawng thei natna chungchang kan sawi dawn a ni.
CVID chu eng nge ni?
A awlsam zawngin sawi ila, CVID (Common Variable Immunodeficiency) hi kan taksa invenna (immune system) nena inzawm, genetic disease a ni. Natna chi hrang hrang `primary immunodeficiency disease (PIDD)` tih zingah a tel a ni.
Kulhpui ang maiin han ngaihtuah teh. He kulhpui hian hmêlma hrik an tih laka humhim turin sipai a nei a . Heng sipaite hi damdawi lama antibody kan tih chu an ni. CVID vei chuan heng antibodies te hi a level hniam hlein a siam chhuak thin. Chuti a nih chuan, kan kulh chhunga sipai an tlem chuan eng nge thleng? Ram dang hmelma, chu chu natna hrik te chu awlsam takin taksaah an lut thei a, natna an thlen thei a ni .
Chumi avang chuan CVID vei te hian beng natna , sinus infection, leh lung infection te an nei fo thin. He natna hian natna khirh zawk, intestinal problem, thisen leh autoimmune natna, leh cancer te pawh a tipung bawk .
Tute nge CVID vei theihna sang zawk?
Immunodeficiency natna dang nena khaikhin chuan CVID hi a awm fo thin. A vaiin mi 25,000 zinga pakhat velin a nghawng a ni.
Tu pawh a nghawng thei a, mahse puitlingah a tam ber. CVID hian naupang leh tleirawl puitlingte a nghawng thei a, mahse puitlingah hmuhchhuah a ni fo. He natna hi kum 20 leh 50 inkar vel a ni tlangpui .
Mahse, survey-ah chuan CVID vei mi 10 zinga 2 vel chu naupan laiin immunodeficiency an nei tih hmuhchhuah a ni.
Eng thilin nge CVID a thlen?
Dik tak chuan doctor-te hian CVID vei tam zawkin he natna hi an neih chhan hi eng nge ni tih chiang takin an la hre lo.
Amaherawhchu, CVID vei mi 10 zinga pakhat vel tan chuan a chhan hi rochun a ni. Chumi awmzia chu i DNA a genetic mutation a awm vang a ni thei tihna a ni . A awlsam zawngin, i nu, i pa, a nih loh leh i chhûngkaw member dang aṭangin he natna hi i rochun a ni mai thei.
CVID hi immune system-a genetic defects vang pawh a ni thei. Heng chhiatnate hian taksaah hian immunoglobulins, natna hrik dotu protein chi khat, a bik takin antibodies immunoglobulin G (IgG) an tih chu a siam chhuak tlem hle a ni. Hei hian immune system a tichak lo hle. A châng chuan, he natna hi nakin lawkah a lo awm thei bawk.
CVID natna lan chhuah dan engte nge ni?
CVID symptoms hi mi hrang hrangah a inang lo thei. Mi thenkhat chuan symptoms na lo tak tak an nei a, thenkhat erawh chuan na tak tak an nei thei thung. I immune system a chak loh danah a innghat.
A hnuaia table-ah hian CVID natna lan chhuah dan langsar zual thenkhat tarlan a ni.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Thluak lam natna (respiratory system) natna | Khuh tam leh rei tak, thawk harsa, leh lung natna (chu chuan bronchitis emaw pneumonia ang chi natna a thlen thei). |
| Beng leh sinus natna | Beng natna leh sinus natna a awm fo thin. |
| Digestive system lama harsatna awm thei | Diarrhea, luak chhuak, luak chhuak, leh sawifiah theih loha taksa rihna tlahniam. |
| Joints leh spleen te | Khup, kutphah, leh kutphah ang chi ruhkawrte a hring leh a na. Spleen lian tak a awm. |
| Thil dang pawh a awm | Liver function lama harsatna, thisen platelet tlahniam, leh vaccine pek avanga thil danglam emaw, na tak emaw a awm. |
Engtin nge CVID hi hmuhchhuah a nih?
I beng, sinus emaw, lung natna emaw i vei reng a nih chuan, emaw, vaccine pek dan tlangpui avanga thil danglam tak i neih chuan i doctor hnenah hriattir ngei ang che.
Heng symptoms te hi doctor i hrilh hian CVID a ringhlel mai thei. Diagnosis tih chian nan i medical history leh i chhungte medical history a zawt ang. Tichuan, thisen test engemaw zat an order ang. Heng thisen test te hian i taksa antibody a hniam zia leh i immune system a thawk tha em tih a enfiah thei a ni.
A chang chuan, i doctor chuan natna dang vaccine a pe thei che a, a chhanna atan i taksa antibody level chu a pangngaiin a sang em tih test a ni thei bawk.
CVID enkawl dan tur a awm em?
CVID hi damdawi a la awm lo. Mahse, lungngai suh. He natna hi i enkawl tha thei a, natna hrik lakah i inveng thei a, nun pangngai leh hrisel tak i hmang thei bawk.
Enkawlna ber chu immunoglobulin (IgG) thlak danglamna therapy a ni . Hei hian damlo hnenah IgG antibodies pek a huam a, thisen petu hrisel tak takte hnen atanga lak chhuah a ni. Hei hian i taksaa antibodies level a tisang a, immune system a tichak bawk.
He enkawlna hi kawng hnih in kan hmu thei a:
1. IV method: Saline solution angin thla khatah vawi khat vein (IV)-ah pek thin a ni.
2. Subcutaneous method: Kar khatah vawi khat emaw, kar hnih danah emaw vun hnuaia injection angin.
A pawimawh ber chu he enkawlna hi dam chhung atan ei a ngai a ni.
Mi tam zawk chuan he enkawlna atang hian side effect lian tham an tawk lo. Mahse, ṭhenkhat chuan lu na emaw, allergy emaw an nei thei. I doctor nen inbia la, i tan eng enkawlna nge tha ber tih hriat chian rawh.
Tin, infection i neih chuan i doctor chuan a enkawl nan antibiotics emaw antiviral damdawi emaw a pe bawk ang.
CVID vanga harsatna dang lo awm thei te
Immune system a thawh that loh avangin CVID vei te hian damdawi lam natna khirh tak dang an neih theihna chance a sang hle.
- Autoimmune diseases: Hei hi taksa immune system-in mahni cell hrisel tak takte a beih sual hian a ni. Hengte hian `autoimmune hemolytic anemia` (thisen sen hrisel tihchhiat), `rheumatoid arthritis` (arthritis), leh `thrombocytopenia` (thisen platelet hniam) te ang chi dinhmun a thlen thei a ni.
- Cancer: CVID hian cancer chi hrang hrang, lymphoma emaw, pum cancer emaw a vei theihna a tipung a ni.
- Bronchiectasis: Lung infection fo hian lung chhunga thawkna kawng a tichhe thei a, a tizau reng thei bawk. Hei hian khuh reng reng a thlen thei a, mucus pawh a tifai a harsa thei bawk.
- Granulomas: Hei hi thisen var (white blood cells) pungkhawm atanga lo piang chhuak te tak te a ni. Lung, vun emaw, taksa peng dangah emaw hmuh tur a tam ber.
Take-Home Thuchah a ni
- CVID hi genetic condition a ni a, taksain antibody a siam chhuah tlem avangin immune system a tichak lo hle.
- Beng, sinus, leh lung infection tam lutuk hi a lan chhuah dan ber a ni.
- Nangmah emaw, i hriat miin emaw heng symptoms te hi i neih chuan doctor pan vat la, thurawn la rawh.
- CVID hi tihdam kim theih ni lo mah se, dam chhung zawnga antibody enkawlna (IgG therapy) hmangin uluk taka enkawl theih a ni.
- CVID i vei a nih chuan hrik laka inven nan faina tha, kut sil fo ang chi te vawng reng a pawimawh hle.
CVID, Common Variable Immunodeficiency, immunity, natna tam tak, hri kai, antibody, IgG therapy











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