I naupang tê hian thil mak tak tak a nei em? (West Syndrome) Hemi chungchang hi han sawi ila!

I naupang tê chu a rawn inher nghal vat a, lightning-in a rawn nuai ang maiin a rawn inher chhuak tih i hmu ngai em? A kut leh ke chu a inzawm nghal a, a nih loh leh hnunglam hawiin a inhnukdawk ta a ni. Hei hi second tlemte chauh a awm a nih pawhin, a zawnin vawi tam tak a thleng a nih chuan, a hmutu nu leh pa tu tan pawh a hlauhawm hle thei. Condition hlauhawm tak kan sawi dawn a, mahse hriat vat a pawimawh hle. Chu chu West Syndrome a ni.

A awlsam zawngin, West Syndrome hi eng nge ni?

West Syndrome hi epilepsy natna chi khat a ni a , naupang tê tê, a bik takin kum khat hnuai lamte chu a vei ṭhin . A hmuchhuaktu doctor hming chawia sak a ni.

Hei hian doctor zingah hming eng emaw zat a nei a. `Infantile Spasms (IS)` tih hming pawh i hre mai thei. Chu chu ``nausen spasms'' tihna a ni.``Epileptic Spasms'' an ti bawk.Hming tam tak awm mahse, damdawi lam dinhmun inang an sawi vek a ni.

Hetiang natna lan chhuah dan hi engte nge ni?

Hei hi a langsar ber chu a hmaa kan sawi tawh ang khan jerking hi a ni. Chungte chu `spasms` an ti a. Heng jerk te hian mizia bik engemaw zat an nei a:

• Contraction lo awm dan: Naute chu hmalam pan nghal (a pum na a neih lai ang chi) emaw, a hnunglam hawia a inthlak emaw. Kut leh ke chu a nghet nghal a, a inher nghal bawk.
• Hun: Stroke vawi khat chu second tlemte chauh a ni.
• Clusters: Heng contraction te hi vawi khat a lo kal a, a tawp lo. Anni chu a kal zel a, a inzawm khawm (clustered pattern) a ni . Contraction pakhat chu a zui leh a, chutah chuan a dang, a hnuah a dang, cluster pakhata contraction 150 thleng a awm leh a ni. Ni khatah hetiang cluster 60 thleng nei naute an awm.
• Hun: Naute mut atanga a harh veleh heng chetna te hi i hmu thei tlangpui.

Heng thawmhnaw bakah hian symptom dang pawh hmuh tur a awm thei bawk.

Engvangin nge naute chungah hetiang hi a thlen?

West Syndrome hi a tlem hle. Nausen 10,000 zinga 6 vel a nghawng a ni. Naute thla 4 leh thla 8 inkar a nghawng tam ber. A chhan dik tak chu hriat chian ni lo mah se, a chhan lian ber eng emaw zat hmuhchhuah a ni.

• Structural brain problems: Thluak lo thanglian emaw, a lo pian chhuah emaw chhunga thil danglam lo awm apiang.
• Genetic changes: He natna hi naute genes inthlak danglamna engemaw zat avanga lo awm thei a ni.
• Thluak chhiatna: Nau piang lai emaw, engtik lai emawa thluaka oxygen tlakchham vang, accident ang chi.
• Metabolic disorders: Taksa chemical process-a harsatna engemaw zat a awm vang a ni.
• Brain infections: Thluak natna hrik kai theihna.
• Tuberous Sclerosis Complex: Taksa leh thluaka cancer ni lo tumor lo awm thin, genetic condition a ni.

Engtin nge diagnosis hi siam a nih?

I naute hian hetiang chiah hian seizure a nei tih i hriat chuan a rang thei ang bera naupang enkawltu doctor i pan tur a ni .

Doctor hian heng test te hi a sawi ber a ni:

• EEG (Electroencephalogram): Hei hi test pawimawh ber a ni. A awlsam zawngin, thluaka electrical activity chu pattern angin a record a ni. Naute West Syndrome vei chuan EEG-ah hian `Hypsarrhythmia` tih hming pu pattern mumal lo tak a lantir ang. Hei hi he natna hmuhchhuahna atana clue ber a ni.
• MRI emaw CT scan emaw hmangin:Heng scan te hian thluak insiam danah harsatna, chhiatna emaw, thil danglam emaw a awm em tih hriat nan a pui thin.
• Thisen, zun leh cerebrospinal fluid (CSF) test: Heng test te hian khur chhan hi genetic emaw metabolic problem emaw a nih leh nih loh hriat nan a pui thin.

Hei hi eng enkawlna nge ni?

West Syndrome hmuhchhuah a nih hnuah a rang thei ang bera enkawl tan a pawimawh hle a, a chhan chu seizure control hian naute thluak thanna tihchhiatna a ti tlem thei a ni.

Damdawi ei tur

Hemi enkawlna atana hman tlanglawn ber chu damdawi a ni.

• ACTH: Hei hi hormone a ni. Injection angin pek a ni. Heartbeat control-na kawngah a thawk tha hle.
• Vigabatrin (Sabril): Hei hi epilepsy damdawi a ni bawk. A bik takin naute West Syndrome, Tuberous Sclerosis vanga natna vei te tan a tangkai hle.
• Steroids: `Prednisone` ang chi steroid te pawh hman a ni.

Heng damdawi te hian side effects a nei thei a, chu chu immunity tlahniam, thisen sang sang, leh mit lama harsatna te a ni. Chuvangin doctor chuan naute chu a enfiah fo thin a, a thatna leh a hlauhawm dan a zirin a enkawl thin.

Ketogenic Diet hmanga ei leh in

Nausen thenkhat tan chuan an riltam control nan damdawi a tawk lo a nih chuan doctor chuan he special diet hi a rawt thei a ni. Hei hi thau tamna, carbohydrate tlem tak eitur a ni.

Inzai

MRI scan-a stroke hi thluaka hliam bik avanga lo awm a nih thu chiang taka a lan chuan doctor chuan chu hmun chu surgery hmanga lak chhuah a rawt thei a ni. Hei hi mi zawng zawng tih theih a ni lo. Medical team-in an rel a ni.

Nakin hun chungchâng eng nge i sawi theih ang? (Hmuh dan tur) .

Hei hi zawhna zawh harsa tak a nih laiin, thudik hriat a pawimawh hle. West Syndrome hmalam hun tur chu thil pawimawh engemaw zatin a hril dawn a ni.

• A chhan: Seizure hi eng nge ni? Thluak hliam na tak avanga lo awm a nih chuan a result a tha lo thei hle. A chhan chiang tak awm lo (idiopathic) a nih chuan a result a tha tawk hle.
• Enkawl tan hun: Naute hmuhchhuah atanga thla khat chhunga enkawl tan theih a nih chuan naute thanlenna chu a pangngaia a lo kir leh theihna a sang hle.
• Enkawlna chhanna: Engtiang chiahin nge seizure hi control theih a ni.

He babbling hi kum 4 velah a tawp tlangpui a, mahse, .Naupang tam tak chuan a hnuah epilepsy chi dang an nei thei a ni.

Naupang tam tak chuan zirlai lama harsatna emaw, rilru lama hmasawnna lama harsatna emaw level engemaw chen an nei a. Mahse, a tir lama enkawlna tha ber a awm chuan naute 20%-25% vel chu finna pangngai nen nun pangngaiin an hmang thei a ni. Chuvangin hma lak hmasak hi a pawimawh a ni.