Nu emaw pa emaw chuan nausen piang thar an en hian an tih hmasak ber chu an kut leh ke te te kut zungtang leh ke ruhte chhiar hi a ni. Mahse, chu kut zungtang te tak te pahnih emaw, a aia tam emaw chu vun membrane hmanga inzawm ang maia inzawm khawm i hmuh chuan han ngaihtuah teh? Nu i nih angin i lungkham deuh mai thei. Mahse, lungngai suh, vawiinah hian nu tam takin an lo tawn tawh mai thei dinhmun hi kan sawi dawn a ni.
Syndactyly chu eng nge ni?
A awlsam zawngin, he natna hi damdawi lam tawng chuan syndactyly an ti a. Hei hi naute kut emaw ke emaw kut zungtang pahnih emaw a aia tam emaw vun hmanga inzawmkhawm a ni a, chu chu duck ke ruh inkar webbing ang chiah a ni. A châng chuan he inzawmna hi vun chhungah chauh a awm ṭhin. Hun dangah chuan a hnuaia ruh (spinals) leh soft tissue dangte pawh a inzawm thei bawk.
Hei hi piansualna a ni a, pian tirh atanga hriat theih a ni. A then phei chuan naute chu nausen pum chhunga a la awm laiin nau neih hmaa ultrasound screening neih lai pawhin hmuhchhuah theih a ni.
Engvangin nge naute chungah hetiang hi a thlen? Eng nge a chhan?
Hei hi hrethiam tur chuan nausen pum chhunga a lo thanlen dan hi tlem kan hriat a ngai a ni. Naute chu nau pai a, a pum chhunga a lo thanglian chuan a kut leh ke chu a tir lamah chuan flipper ang maia paddle ang maia siam a ni. Kut zungtang chu a inthen lo.
Naupai kar 10 vel ah chuan heng kut zungtang te hi an inthen tlangpui a, an sei a, an inkar a webbed structure chu an hloh thin. Syndactyly hi eng emaw chhan vanga chutih laia heng kut zungtang te hi an inthen tha lo a nih chuan a lo awm thin.
A tam zawkah chuan, isolated birth defect angin a thleng thin , damdawi lam harsatna lian dang awm lovin. Mahse a chang chuan genetic influence a nei thei bawk. Chumi awmzia chu chhungkaw zinga mi tu emaw, entirnan nangmah, i kawppui emaw, i nu leh pate emaw pawhin he natna hi an lo nei tawh a nih chuan i naute pawhin a vei theihna chance a awm tihna a ni. Zirna hrang hrangah syndactyly vei zinga 10% leh 40% inkar chuan chhungkaw history an nei tih hmuhchhuah a ni .
A tlem hle a, he finger-jointing hi genetic syndrome lian zawk dangte feature a ni thei. Entirnan, he natna hi Apert, Chotzen, leh Poland syndrome-ah te hmuh a ni. Mahse hengte hi a tlem hle.
Hetiang natna hi Syndactyly an tih hi chi hrang hrang a awm em?
Ni e, naute zawng zawng hi a nghawng dan inang vek lo. A natna nasat dan leh a natna tissue a zirin chi hrang hrangah then theih a ni. A chi lian ber berte chu eng nge ni tih i lo en ang u.
| Syndactyly chi hrang hrang | Hrilhfiahna awlsam tak |
|---|---|
| Syndactyly awlsam tak (type awlsam tak) . | Kut zungtang hi vun leh a hnuaia soft tissue chauhvin a inzawm khawm a ni. Ruh inzawm a awm lo. |
| Complex syndactyly (a chi hrang hrang) 1.1. | Vun hnuaia ruh (spinae) thenkhat pawh hi an inzawm khawm a, an inzawm khawm a ni. |
| Syndactyly buaithlak tak (a chi hrang hrang buaithlak ber) . | Hei hian ruh dang, ruh bo emaw, ruh lo thang tha lo te, chubakah tendon leh ligament pangngai lo te a huam thei bawk. |
| Syndactyly tling lo (type tling lo) 1.1. | Kut zungtangte hi a inzawm kim lo. Kut zungtang inkar vun thenkhat chauh hi membrane ang maia inzawm a ni. |
Tin, eng kut zungtang nge inzawm khawm tih a zirin chi dang engemaw zatah then a ni bawk.
- Type 1: Hei hi a tam ber a ni. Kut zungtang pathumna leh palina emaw, ke ruh pahnihna leh pathumna emaw a nghawng tlangpui. Kut pahnihah emaw, ke pahnihah emaw hmuh theih a ni fo.
- Type 2: Hei hian kut zungtang pathumna leh palina leh ke ruh pangana a nghawng a ni. Hetiang chi naupang thenkhat pawh hian kut zungtang extra an nei thei bawk.
- Type 3: Hei hian kut chauh a nghawng. Kut zungtang palina leh pangana hi a inrawlh tlangpui.
Hetiang chi dang pawh a awm. I doctor chuan i naute chu taksa a enfiah ang a, X-ray a ti ang a, a tul chuan eng chi nge a nih leh engtiang chiahin nge a nasat tih hriat tumin genetic testing a ti ang .
Hei hi eng enkawlna nge ni?
He thu i hriat hian i rilruah zawhna lo lang hmasa ber chu, "Tunah hian eng nge ka tih ang? Hemi atan hian operation ka neih a ngai em?"
A tha ber chu heng natna tam tak hi hlawhtling taka enkawl theih a ni.
- Enkawl ngai lo: Ke ruh ruh hi a te lutuk tihna a ni a, chu chu naute thanlenna emaw, kut hman dan emaw tichhe lo, natna na lo tak a nih chuan enkawl a ngai lo mai thei. A bik takin ke ruhte hi a tlangpuiin a inzawm tlat a, naupang kal dan emaw, thiltih danah emaw nghawng a neih loh avangin enkawl lohvin a awm fo thin.
- Surgery: Chi dang zawng zawng ang bawkin enkawlna chu kut zungtang surgery hmanga then hran a ni. He surgery hi naute kum 1 leh kum 2 inkar a nih chuan tih thin a ni . Hei hi a chhan chu chutiang kum chuan anesthesia vei theihna a hniam zawk vang a ni. Tin, kut zungtang te hi a inthen hma poh leh naute kut chu a thawk thei ang a, a lo thanglian zel bawk ang.
Surgery tih dan tur
Surgery an neih chhung hian doctor chuan uluk takin ke ruh inzawm (fused toes) inkar vun chu "zig-zag" pattern-in a tan a. Hei hi hliam a awm loh nan leh a hnua ke ruhte a inzawm leh loh nan tih a ni. A châng chuan, ke ruhte inthen hnua vun a awm tlem chuan naute taksa peng dang, a kutphah emaw, a ke ruh emaw aṭangin vun tê tê chu lak chhuah a ni a, vun hrualna atan hman a ni
Operation hnuah i naute kut chu kar engemaw zat chhung chu cast-ah a awm ang. A hnuah chuan kut zungtangte chu a inzawm leh tawh loh nan rubber spacer i hman a ngai mai thei. I naute hmasawnna enfiah tur leh zawhna zawt turin doctor i pan fo a ngai dawn a ni. Naupang thenkhat chuan an kut leh kut zungtang chet that nan physical therapy an mamawh mai thei.
A pawimawh ber chu he thil hi ngaihtuah buai lo, naute pian veleh Doctor nena inbiak vat hi a ni. I mamawh kaihhruaina zawng zawng a pe ang che.
Take-Home Thuchah a ni
- Syndactyly hi naute pian tirh atanga a kut zungtang inzawmkhawm (fuseed together) a ni. Hei hi piansualna a awm fo thin.
- Hei hi nausen pum chhunga a lo thanglian lai hian ke ruhte a inthen tha lo vang a ni.
- A tam zawkah chuan damdawi lam thil dang nen a inzawm lo va, mahse chhungkaw history emaw, genetic influence emaw a awm thei.
- Ke ruh emaw kut zungtang emaw inrawlhna tenau tak tak a awm chuan enkawl a ngai lo mai thei.
- Thil dang tam zawkah chuan operation hian he dinhmun hi a tidik vek thei a, hlawhtling takin a siam tha thei bawk.
- I naute hian he natna hi a neih chuan hlauthawng suh la, naupang enkawltu emaw plastic surgeon emaw hnenah thurawn dil rawh.











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