Me ako tātou mō te Mate Budd-Chiari, he mate kino e aukatia ai ngā oko toto i roto i te ate.

Ko te ate tētahi o ngā okana tino nui o tō tātou tinana. Pērā i tētahi wheketere nui, he pūnaha nui tō te ate o ngā oko toto e tango ana i ngā poke mai i te toto. Whakaarohia, he aha ka puta mēnā ka āraia, ka whaiti rānei tētahi, ētahi rānei o ēnei oko toto? I roto i te rongoā, he mate onge tēnei engari he tino kino nā te ārainga o ngā uaua e kawe ana i te toto i waho o te ate . He mea tino nui kia mōhio ki tēnei. Me kōrero māmā noa iho.

He aha te tikanga o te Budd-Chiari Syndrome?

Ko te huarahi pai ki te mārama ki tēnei ko te whakaaro ki te mea ka puta ina aukatia te waikeri i roto i tō tātou whare. Pērā i te paipa kua aukatia e te wai, ina aukatia ngā uaua ate, ka tīmata te toto ki te kohi i roto i te ate. Tērā pea nā te toto totoka, te pupuhi i roto i te uaua, te pēhanga rānei mai i waho.

Ina kohia te toto pēnei, ka pupuhi te ate, ka nui haere. Ehara i te mea koinā anake, engari ka taea hoki te whakanui ake i te whēkau nā tēnei pēhanga. Ki te haere tonu tēnei āhuatanga, tera pea ka puta he maha atu ngā pānga kino kino.

• Te toto toto tiketike o te tomokanga: Te pēhanga nui rawa atu i roto i te uaua matua e kawe ana i te toto ki te ate (te 'uaua tomokanga').
• Varices: Nā te pēhanga nui nei, ka nui haere ngā uaua toto i ngā wāhi pēnei i te korokoro me te puku, ā, ka pakū, ka toto hoki.
• Te ascites: He āhuatanga e whakakīia ai te puku e te wai, pērā i te wai, ka pupuhi. Ka kiia tēnei ko te "ascites".
• Te mate ate: He kino roa ki te ate, ka mate ngā pūtau ate, ka whara hoki te ate. He mate kino tēnei e kore e taea te whakaora.

He rerekē ngā momo o tēnei mate?

Āe, ka taea te wehewehe ki ētahi momo matua i runga i te tere me te kaha o ngā tohu. Waihoki, e rua ngā momo i runga i te pūtake.

I runga i te take, e rua ngā momo matua:

1. Te Mate Budd-Chiari Tuatahi: I tēnei wā, kei roto i te uaua toto tonu te raruraru. Tērā pea ka puta mai i te toto totoka (thrombus) te pupuhi rānei i roto i te uaua.

2. Te Mate Budd-Chiari Tuarua: I konei ka puta te raruraru mai i waho o te uaua toto. Hei tauira, ka taea e te pukupuku matepukupuku, te pukupuku rānei kāore i te matepukupuku e tata ana ki te ate te aukati i te uaua toto.

He aha ngā tohu o tēnei?

Ka rerekē pea ngā tohu o tēnei mate i ia tangata, i ia tangata. Ka rerekē anō hoki i runga i te momo mate. Heoi, he iti noa ngā tohu e kitea ana.

He aha te take e puta ai te mate Budd-Chiari? He aha ngā take?

He maha ngā wā, ka puta tēnei i tētahi āhuatanga hauora e whakanui ana i te hiahia o te tinana ki te hanga i ngā toto totoka.

• Ngā mate toto (Myeloproliferative neoplasms - MPNs): He momo matepukupuku toto onge ēnei. Ka nui rawa ngā pūtau toto ka puta i te tinana, ka nui ake te tūponotanga o te toto totoka.
• Ngā mate toto totoka tere rawa: Ngā āhuatanga e tere rawa ai te toto totoka nā ngā take ira, nā ētahi atu mate rānei. Hei tauira, ngā āhuatanga pēnei i te 'Protein C', te 'S' ngoikore rānei, te 'Antiphospholipid antibody syndrome'.
• Ngā pukupuku ate, ngā pukupuku tākihi rānei: Ka taea e ngā pukupuku matepukupuku, ngā pukupuku pai rānei te pēhi i ngā oko toto mai i waho.
• Te Hapūtanga: He nui ake te mōrearea o ngā wāhine ki te toto totoka i te wā e hapū ana.
• Pire ārai whānau: Mā te whakamahi i ētahi momo pire ārai whānau ka nui ake te tūponotanga o te toto totoka.
• Ētahi atu mate: Ka taea hoki tēnei te puta mai i ngā mate pēnei i te 'mate pūtau marino' me te 'mate whekau mumura (IBD)'.

Heoi, i ētahi wā kāore e kitea te tino take . Ka kiia tēnā he 'idiopathic'.

Me pēhea te kitenga a te tākuta i tēnei?

Ina kite koe i tētahi tākuta, ka whakarongo pai ia ki ō tohumate, ka tirotiro i a koe, kātahi ka whakahau i ētahi whakamātautau hei whakaū i te mate.

1. Ngā whakamātautau toto: Ka āwhina ēnei ki te tirotiro i ngā taumata whākōkī ate me te whakatau mēnā he mōrearea kei te puta he toto totoka.

2. Ngā whakamātautau whakaahua:

• Matawai Ultrasound Doppler: Koinei te matawai tuatahi, te matawai māmā rawa, me te mea nui rawa. Ka whakamahia ngā ngaru oro hei tirotiro i te rere o te toto i roto i ngā oko toto o te ate. Ka taea e tēnei te whakaatu mēnā he aukati kei roto.
• Matawai CT, Matawai MRI rānei: Ka taea e ēnei momo matawai te tango pikitia mārama ake o te ate me ngā whekau e karapoti ana. I ētahi wā ka werohia he wai motuhake ('rauemi whakawhiti') ki roto i te tinana kia kitea pai ai ngā oko toto.
• Venography (venogram): Ka mahia tēnei whakamātautau mēnā kāore i te tino kitea he hua o ētahi atu matawai. I tēnei whakamātautau, ka werohia he wai motuhake ki roto i te uaua toto, ā, ka tangohia he whakaahua hihi-X hei tirotiro i te rere o te toto.

3. Kohikohi Ate: Hei whakatau i te nui o te kino kua pā ki te ate, me te mōhio kua whanake te mate ate cirrhosis, ka tangohia he wāhanga iti rawa o te ate mā te whakamahi i te ngira iti, ā, ka tirohia i raro i te karu hiko.

He aha ngā maimoatanga mō tēnei?

E rua ngā whāinga matua o te maimoatanga. Ko tētahi he whakatuwhera anō i te oko toto kua āraia, he waihanga rānei i tētahi ara rerekē mō te rere o te toto. Ko tētahi he rongoā i te pūtake o te mate.

Te maimoatanga me te rongoā

I te tīmatanga, ka hoatu ngā rongoā pēnei i ngā rongoā whakakore toto (ngā rongoā whakangawari toto ) hei whakarewa i ngā toto totoka me te ārai i te hanganga o ngā totoka hou. Hei tauira, ko ngā rongoā pēnei i te heparin, te warfarin rānei.

Ngā maimoatanga motuhake kāore i te pokanga

Mena kāore e taea e te rongoā anake te whakahaere i te āhua, he maha ngā tikanga maimoatanga e whakahaerehia ana e ngā tākuta tohunga.

• Te Huringa Portosystemic Intrahepatic Transjugular (TIPS): He tikanga uaua ake tēnei. He māmā noa iho, ka hangaia he "takahi" ki roto i te ate. Ka whakauruhia he ngongo iti (he stent) ki waenganui i te uaua tomokanga pēhanga-teitei me te uaua ate, e tango ana i te toto mai i te ate. Ka hangaia he ara hou mō te rere o te toto me te kore e aukatia.
• Angioplasty Transluminal Percutaneous: Ko tēnei he pupuhi i tētahi oko toto kua āraia, kua whaiti rānei ki tētahi poihau. I ētahi wā ka whakauruhia he ngongo iti rite ki te mata (he 'stent') hei ārai i te whaiti anō o te oko toto.

Te Whakatō Ate

Ki te kore e angitu ngā maimoatanga katoa, ki te kore rānei e angitu te ate (te ngoikore o te ate) kua pāngia rānei e te cirrhosis, ko te huarahi whakamutunga ko te whakawhitinga ate hauora.

He aha te heke mai mō tēnei mate?

He maha ngā āhuatanga e whakawhirinaki ana ki te matapae o te mate. He mea nui te wawe o te kitenga o te mate, te whānuitanga o te kino, me te pai o tana urupare ki te maimoatanga.

Ki te kore e rongoatia, ka mate pea te tūroro kua aukati katoatia ōna oko toto i te ngoikore o te ate i roto i te toru tau pea. Heoi, mā te maimoatanga tika, inā koa te whakawhitinga ate, ka roa pea te ora. Nō reira, ko ngā kōrero pai rawa atu mō tēnei mea nō tō tākuta. Māna e whakamārama atu ki a koe kia rite ki tō āhuatanga.