Kei te heke haere tō mahara me ō nekehanga? Me ako tātou mō tēnei (Corticobasal Degeneration)!

Ka wareware koe i ētahi mea i ētahi wā? Kāore rānei koe e kite ana he uaua ki te neke i ō ringaringa me ō waewae? Ka kōrero pōturi koe i a koe e kōrero ana? Ki te mea kei te piki haere ēnei mea, he mea nui pea kia mōhio koe ki tēnei āhuatanga e kōrerohia nei e tātou i tēnei rā, arā, ko te `(Corticobasal Degeneration)`. Kaua e manukanuka, me kōrero noa iho tātou mō tēnei.

He aha te "Corticobasal Degeneration"?

Ki te kī ngāwari, ko te `(Corticobasal Degeneration)` he mate pūnaha io e pā ana ki tō tātou roro. E kīia ana hoki e ētahi ko te `(Corticobasal Syndrome).` Ko te mea e tupu ana i roto i tēnei ko te pakaru o ētahi pūtau o tō tātou roro, ā, ka whakangaromia haeretia. Pērā i ētahi taputapu ka pirau haere i te roanga o te wā. Nā tēnei, ka taea e tō tātou kaha ki te kōrero, ki te horomi kai, ki te neke i ō tātou tinana, me te maumahara ki ngā mea te heke haere. Ko te mea pouri ko te piki haere o ēnei tohu (te ahu whakamua) i te roanga o te wā.

Ko te kupu "corticobasal" i roto i te ingoa e pā ana ki ngā wāhanga e rua o te roro e tino pakaru ana i te mate:

• Te cortex roro: Koinei te paparanga o waho rawa o te kiko io o tō tātou roro. He mea tino nui tēnei wāhanga mō ō tātou mahara, ako, nekehanga ā-ringa, me ngā kare ā-roto.
• Ngā pūtau io matua: He kohinga pūtau io tēnei kei roto i te roro. He mea nui mō te ako me ngā mahi nekeneke.

Ko te tikanga o te kupu "degeneration" ko te "whakahekenga" ko te "ngaronga rānei o te mahi." Nō reira, ko te mea e tupu ana i roto i tēnei mate ko te heke haere o te mahi a ēnei wāhanga e rua o te roro.

Ka taea e tēnei āhuatanga, e kiia nei ko te "Corticobasal Degeneration," te whakapoto i te roanga o te oranga o te tangata, ā, ka puta he raruraru mōrearea ki te ora. I te horapa haere o ngā tohu puta noa i te tinana, ka uaua pea te mahi takitahi.

He aha ngā tohu o te `(Corticobasal Degeneration)`?

Ka rerekē pea ngā tohu o tēnei mate i ia tangata, engari ko ngā āheinga ka pāngia whānuitia ko:

• Ngā uauatanga nekehanga (`Apraxia`): Ko te tikanga o tēnei ka uaua ngā mahi pēnei i te pātene i te pātene, te pupuri rānei i te pūnu hei kai. Ahakoa ka tukuna e te roro ngā karere ki ngā ringaringa, kāore e taea e rātou te mahi tika.
• Te ngoikore o te mahara: Ka uaua ki te maumahara ki ngā mea hou, ā, ka wareware haeretia ngā mea tawhito.
• Te ngoikore o te tirohanga: Tērā pea ka pāngia ētahi tāngata e ngā raruraru tirohanga.
• Ngā uauatanga kōrero (`Aphasia`): Te uaua ki te kimi kupu, te korekore o te kōrero, ā, i ētahi wā ka ngaro rawa te kōrero.
• Te uaua ki te horomi: Tērā pea ka rite koe ki te mea kei te kōkō koe ina horomi koe i te kai me te inu.

Hei tāpiritanga ki tēnei, ka kitea pea ētahi atu tohu pēnei i ēnei:

• Te māuiui o ngā uaua, te wiri, te pūkeke o ngā uaua, te wiri rānei.
• Te uaua ki te mahi i ngā mahi iti, ngāwari hoki (hei tauira, te pātene i te hāte, te tuhituhi ki te pene).
• Te mate ringa tangata kē: Te kore e taea te whakahaere i tētahi ringa, i tētahi waewae rānei e hiahia ana koe ('Te mate ringa tangata kē'). Whakaarohia kei te mahi tētahi o ō ringa i ngā mea kāore koe e hiahia kia mahia e ia, ā, e whakaaro ana koe kāore e taea e koe te whakahaere.
• He āhua ngoikore i tetahi taha o te tinana.
• He tino puhoi ngā nekehanga (`Bradykinesia`) te kore rānei e taea te neke i ngā peka me ngā waewae (`Akinesia`).
• Te ngoikore o te mahi hinengaro, arā, te ngoikore o te mātauranga (Dementia).
• Te uaua ki te hikoi me te kore he āwhina.
• Ngā panonitanga o te wairua me ngā whanonga (te kore aro, te riri ohorere, te kore aro).

Kāore tēnei mate e pā ki te katoa i te huarahi kotahi. He maha ngā wā ka āta haere. I ētahi wā ka tīmata ngā tohu i te ringa kotahi, kātahi ka horapa ki te ringa me ngā waewae kē. Tērā pea ka tīmata koe ki te whakaaro kei te tūtuki koe i a koe e hikoi ana, kātahi ka kore e taea e koe te hikoi me te kore āwhina. Tērā pea ka tīmata koe ki te kōrero pōturi, ā, i roto i te wā, tērā pea kāore e taea e koe te kōrero i tētahi rerenga kōrero whai tikanga.

I te mea ka pāngia e te mate ngā wāhanga maha o te roro, ka kino haere ngā tohu. Ka āta haere tēnei.

Āhea ka tīmata ngā tohu o te `(Corticobasal Degeneration)`?

Ko te tikanga ka tīmata ngā tohu i waenga i te 50 me te 70 tau te pakeke. Ko te nuinga o te tangata ka pāngia e ō rātou tohu i te 64 tau te pakeke. Ahakoa he onge te tīmatanga i te 40 tau te pakeke, kāore anō kia puta he pūrongo mō te whanaketanga o te mate i te wā o mua.

He aha ngā take o te `(Corticobasal Degeneration)`?

Ko te take matua mō tēnei, ko te pakaru haere o ngā pūtau me ngā kiko o te roro, ka mate haere. I te nuinga o te wā, ka tīmata tēnei kino i ngā wāhi i kōrerohia i mua ake nei, arā, ko te cerebral cortex me te basal ganglia. I te whanaketanga o te mate, ka pā pea ki ētahi atu wāhanga o te roro.

E whakapono ana ngā kairangahau kei roto i tēnei mate tētahi pūmua e kiia nei ko "Tau" . Kei roto i ngā pūtau roro tēnei pūmua i te nuinga o te wā. Engari i roto i tēnei mate, ka piri tahi tēnei pūmua, ka hanga he puranga. Ka kiia ēnei puranga ko ngā "neurofibrillar tangles". Ka meinga ēnei puranga kia pirau, kia mate hoki ngā pūtau roro. Nō reira, ka puta he raruraru ki te nekehanga, ki te kōrero, me te mahara.

Kāore anō kia mōhiotia te take tuturu e pupū ai te pūmua Tau. Kua kitea he maha ngā tāngata e pāngia ana e te Corticobasal Degeneration he momo ira (whakarerekētanga) e kiia nei ko te momo H1 i runga i te chromosome 17. Tērā pea ka nui rawa te whakaputanga o te pūmua Tau, ka pupū tahi, tērā pea he rōpū methyl kua piri ki te ira Tau, ka pā ki tana mahi.

Engari e mōhio ana ngā kairangahau ehara i te mea ko tēnei ira anake te take o tēnei. Nā te mea he maha ngā tāngata o te taupori whānui kei a rātou tēnei ira, kāore rātou e pāngia e ngā tohu o te "Corticobasal Degeneration." Nō reira kei te haere tonu ngā rangahau hei kimi i te tino take o tēnei āhuatanga.

He whakapapa tuku iho te `(Corticobasal Degeneration)`?

Kāore anō kia mōhiotia e ngā tohunga hauora he aha i pāngia ai ētahi tāngata e te Corticobasal Degeneration. He tino onge te pāngia o ngā mema o te whānau kotahi e te mate. Arā , he uaua ki te kī he mate tuku iho.

He aha ngā raruraru ka pā mai?

I te whanaketanga o te mate, ka piki ake te tuponotanga o ngā raruraru kino pēnei i te:

• Ngā mate pāwera huakita
• Ngā toto totoka me ngā embolism pūkahukahu
• Ngā aituā tinana (pērā i te hinganga)
• Pūkahukahu
• Sepsis (he mate kino e puta mai ana i ngā huakita e uru ana ki te toto)

Me pēhea te tautuhi a ngā tākuta i tēnei mate? (`Tautoko`)

Ko te āhuatanga motuhake o te tātaritanga o te `(Corticobasal Degeneration)` ko te mea ka taea anake te whakaū mā te tirotiro i te roro i muri i te matenga. Ko reira anake ka taea e te tākuta, e te tohunga mate rānei te whakatau tika i te whānuitanga o te pirau o te roro.

Heoi, i a koe e ora ana, ka karanga pea tō tākuta i tēnei mate ko te "Corticobasal Syndrome" i runga i ō tohumate.

Hei whakatau i te mate, ka tirohia tuatahitia e tō tākuta ō tohumate.

Nā te mea he rite ngā tohu o te maha o ngā mate, ka whakahaerehia pea e tō tākuta he maha ngā whakamātautau hei whakatau i te tino take. Kei roto i ēnei ko:

• Ngā whakamātautau toto
• Ngā whakamātautau whakaahua roro (`Matawai Whakaahua`) - hei tauira `(MRI)` `(Matawai CT` rānei)
• He whakamātautau neuropsychological hei aromatawai i te mahi a te roro me te mahara

Hei tāpiritanga, ka taea hoki e te tākuta te tono i ngā matawai rongoā karihi pēnei i te `(FDG-PET (Fluorodeoxyglucose Positron Emission Tomography))` me te `(DAT (Dopamine Transporter))`. I ētahi wā, ka taea hoki e te `koiora kiri` te āwhina i te tautuhi mate.

He aha ngā maimoatanga mō te `(Corticobasal Degeneration)`?

Tērā pea ka tohua e tō tākuta ngā rongoā rerekē hei whakahaere i ngā tohu rerekē o tēnei mate.

Kia maumahara, kāore he rongoā mō tēnei mate i tēnei wā, kāore hoki he rongoā hei aukati i te haere tonu o ngā tohu. Heoi anō, kei reira ētahi mea hei āwhina i te whakaiti i te mamae i puta mai i ngā tohu.

Ko ngā rongoā mō ngā tohu e pā ana ki te uaua ka uru atu ki:

• Ngā nekehanga puhoi, te pakari rānei o te uaua: `(Levodopa)`
• Mō ngā mamae o te uaua: Clonazepam (Benzodiazepines)
• Mō te pakari o te uaua, te whakahaere nekehanga rānei: `(Paitini Botulinum)` (ngā werohanga Botox)
• Mō te pakari o te uaua: `(Cyclobenzaprine)`, `(Levetiracetam)` rānei `(Baclofen)`

Mō ngā raruraru mahara, ka tohua pea e tō tākuta tētahi o ēnei momo rongoā e kiia nei ko ngā "Cholinesterase inhibitors":

• `(Donepezil)`
• `(Rivastigmine)`
• `(Karanamine)`

Kāore ētahi rongoā e pai te mahi mō ngā tohumate o te katoa, nō reira ka whakamātau pea tō tākuta i ngā momo rerekē hei kimi i te mea e tino pai ana mōu.

Waihoki, pērā i ngā rongoā katoa, tera pea ngā pānga taha. Ka kōrero tō tākuta ki a koe mō tēnei. Ka tirotirohia koe e ia i ia wā kia mōhio ai kei te pai te mahi a te rongoā, ā, mēnā he raruraru kei te pā mai. Mēnā ka pāngia koe e ngā pānga taha, me kōrero tonu atu koe ki tō tākuta.

Ko te mea nui, kāore he maimoatanga i tēnei wā hei aukati i te haere whakamua o ēnei tohu, hei whakaora katoa rānei i te mate.

Me pēhea te whakahaere i ngā tohu?

I te wā e noho tahi ana koe me ngā tohu o te "Corticobasal Syndrome", ka āwhina pea ēnei rongoā ki te whakahaere i aua tohu:

• Whakaora mahi: Ka taea e tēnei te āwhina i a koe ki te ako i ngā huarahi hou hei mahi i ngā mahi o ia rā, me te pupuri i tō mana motuhake mō te wā roa. Mena e tika ana, ka taea hoki e koe te ako me pēhea te whakamahi i ngā taputapu āwhina nekenekehanga.
• Whakaora tinana: Ka āwhina tēnei ki te pupuri i te nekehanga o te tinana me te whakaiti i te mamae i puta mai i ngā tohu e pā ana ki te uaua. Ka āwhina te whakakori tinana ki te whakapakari i ngā uaua me te pupuri i te ngāwari.
• Whakaora kōrero: He āwhina tēnei mō ngā uauatanga o te kōrero me te horomi. Ka taea e ia te āwhina i ngā mea pēnei i te whakaatu whakaaro, te whakahua kupu, me te horomitanga haumaru o te kai.

Ka mahi tahi tō tākuta me koe ki te kimi i ngā rautaki whakahaere pai rawa atu mō ō tohumate. Tērā pea ka rerekē ēnei rautaki i ia tangata, i ia tangata, ā, me whakarerekē pea i te huringa o tō āhua i roto i te wā.

Āhea koe me toro atu ki te tākuta?

Mena kei a koe, kei tētahi rānei o tō whānau, ētahi o ēnei tohu o te `(Corticobasal Degeneration)`, me toro atu ki te tākuta tonu:

• Mena he uaua ki a koe te hikoi, te whakahaere rānei i ō waewae me ō waewae.
• Mena kei te pāngia koe e ngā raruraru mahara, e ngā tohu rānei o te mate wareware.
• Mena he uaua ki te kōrero, ki te horomi, ki te manawa rānei.
• Mena he wiri.

He aha te matapae mō te `(Corticobasal Degeneration)`?

Ki te pono, kāore i te tino pai te tirohanga mō te Corticobasal Degeneration. He mate haere tonu tēnei, arā, ka kino haere ngā tohu i te roanga o te wā.Engari he maha ngā wā ka puta mārire tēnei, i roto i ngā tau. Ka hoatu e tō tākuta he maimoatanga hei āwhina i a koe ki te aro atu me te whakahaere i ō tohumate. Ahakoa ka taea e ēnei maimoatanga te whakaiti i te kaha o ō tohumate, kāore e taea te aukati i te kino haere. I te kino haere o ō tohumate, ka uaua ake te whakahaere i a rātou ko koe anake.

Nā te mea ka puhoi te whanaketanga o tēnei mate, he wā tōu ki te whakamahere mō tō heke mai. Kāore koe e hiahia ki te mahi i ēnei mea i te wā tonu ina whiwhi koe i te tātaritanga. Me whai wā koe ki te whakaaro mō te mea pai mōu. Me mahi tahi koe me ō tākuta me te hunga e whakawhirinaki ana koe ki te whakarite i ō hiahia me te tiaki e hiahiatia ana e koe.

He aha te roanga o te oranga o te tangata e pāngia ana e te `(Corticobasal Degeneration)`?

I te toharite, ko te nuinga o te tangata ka ora i te ono ki te waru tau i muri i te putanga mai o ngā tohu tuatahi o te Corticobasal Degeneration. Heoi, kāore tēnei e rite mō te katoa, ā, ko ētahi tāngata ka roa ake te ora. Tērā pea kāore tō āhuatanga e rite ki ngā tatauranga, nō reira ko te tangata pai hei kōrero atu mō tēnei ko tō tākuta.

He aha atu ngā āhuatanga he rite ngā tohu?

Tērā pea he rite ētahi o ngā tohu o te `(Corticobasal Degeneration)` ki ngā tohu o ētahi atu mate, pēnei i:

• Matepukupuku roro ('Matepukupuku roro / pukupuku roro')
• `(Te mate wareware o te taha mua o te wā)`
• Te mate a Alzheimer
• `(Te ngoikore o te pūnaha maha)`
• Te mate a Parkinson
• `(Parūtanga supranuclear ahu whakamua)`
• Whiu

Nō reira, he mea tino nui kia toro atu ki te tākuta tonu mēnā ka pāngia koe e tētahi tohu, nā te mea ka taea e te maimoatanga wawe te whakaora i te ora, inā koa i ngā take pēnei i te pararutiki.

He uaua pea te whakahaere i ngā kare ā-roto e puta mai ana i te tātaritanga pēnei i te `(Corticobasal Degeneration)`. Tērā pea ka mataku koe, ka manukanuka hoki mō te heke mai. I te whanaketanga o ngā tohu i roto i ngā tau, tērā pea ka whakaaro koe me pēhea te whakamahi pai i ia wā. He uaua pea te whakahaere i ēnei mea katoa i te wā kotahi. Tērā pea ka hiahia koe ki te kōrero ki tētahi tohunga hauora hinengaro mō te tautoko i tēnei wā uaua.

Kia maumahara, ehara i te mea ko koe anake i roto i tēnei āhuatanga katoa. Ki te hiahia āwhina koe, kaua e mangere ki te whakapā atu ki tō rōpū hauora.

Hei whakamutunga, ngā mea hei maumahara

Āe, anei ētahi o ngā mea kua kōrerohia e tātou mō te `(Corticobasal Degeneration)` e whakaaro ana ahau he mea nui ki a koe:

• He āhuatanga tēnei e pā ana ki te roro, ā, ka piki haere ngā tohu i te roanga o te wā.
• Kāore anō kia kitea te tino take o tēnei, engari e whakaarohia ana he hononga ki tētahi pūmua e kiia nei ko `(Tau)`.
• Kāore he rongoā i tēnei wā hei whakaora katoa i te mate.
• Heoi anō, kei reira ngā maimoatanga hei whakahaere i ngā tohumate, hei whakamāmā ake hoki i te oranga.(Pērā i te rongoā, te whakaora tinana, te whakaora mahi, te whakaora kōrero).
• He mea nui kia rapu wawe tonu i te tohutohu hauora.
• Whakamaherehia mō te heke mai, kia whiwhi ai koe i te tautoko e hiahiatia ana e koe.
• Kāore koe i te mokemoke. He mea nui anō hoki kia kaha tonu tō hinengaro. Rapua he āwhina mai i ngā tākuta, i te whānau, me ngā hoa.

Ko tāku tumanako he whai hua ēnei mōhiohio ki a koe. Mēnā he pātai āu, kaua e mangere ki te kōrero ki tō tākuta.

Te Hekenga o te Corticobasal, Ngā Mate Roro, Ngā Mate Pūnaha Io, Ngā Mate Nekehanga, Te Ngaronga o te Mahara, Ngā Mate Kōrero, Te Pūmua Tau, CBS, Te Ngaronga o te Roro, Apraxia, Aphasia, Te Mate Pōuri