He aha te mate Evans Syndrome? Me kōrero tātou mōna!

Kei te ngenge koe i ētahi wā? He uaua rānei ki a koe te aukati i te toto ahakoa i ngā mea iti rawa? Tērā pea nā te mea kei te mahi te pūnaha ārai mate o tō tinana ki a koe. I tēnei rā ka kōrero tātou mō tētahi mate onge engari he mea nui hei mōhio. Ko te Mate Evans tēnā. Kaua e manukanuka, ka kōrerohia e tātou ngā mea katoa i roto i ngā kupu māmā noa iho.

Nā, he aha te mate Evans?

Ki te kī ngāwari, he mate pūnaha ārai mate a Evans Syndrome. Ko te mea ka tupu, ko ngā hōia e tika ana kia tiaki i tō tātou tinana, te pūnaha ārai mate, ka tīmata hē ki te whakangaro i ētahi o ō tātou ake toto. He rite ki tā tātou ake ope taua e whakaeke ana i ō tātou ake iwi. Nō reira, ka ngaro i roto i tō tātou tinana te nui o ngā toto e tika ana. Ko tēnei hekenga rerekē o ngā toto ka kiia e tātou ko te cytopenia i roto i te rongoā.

Ko te nuinga o te hunga e pāngia ana e te mate Evans Syndrome ka pāngia tuatahitia e te iti o ngā toto whero (he āhuatanga e kiia nei ko te anemia ) me ngā platelets (he āhuatanga e kiia nei ko te thrombocytopenia ). Haunga ngā mea e rua, tera pea he iti anō hoki te maha o ngā momo toto ma e kiia nei ko te neutrophils (he āhuatanga e kiia nei ko te neutropenia ).

Ina iti iho ēnei momo toto, ka pāngia ngā mea nui o roto i tō tātou tinana, pērā i te whiwhi hāora, te toto totoka, me te whawhai ki ngā mate. Koia tātou ka ngoikore ai, ka ngenge ai, ka tīmata te toto tere, ā, ka maha ake te mate .

Ka pāngia pea ētahi tāngata e tēnei mate mā te ngawari noa iho, engari ka pāngia ētahi e te kino rawa atu. Kāore hoki ōna pānga e mau tonu i te roanga o te oranga. Ko te mea pai , ahakoa kāore he rongoā mōna, ka taea e te maimoatanga te āwhina i te whakahaere i ngā tohu me te whakaiti i ngā pānga .

He aha ngā tohu o te mate Evans Syndrome?

Ka rerekē rawa ngā tohu o te Evans Syndrome. Kei te momo cytopenia kei a koe me tōna kaha. He maha ngā wā ka puta tuatahi te anemia , te thrombocytopenia rānei, ā, muri iho ka puta mai ētahi atu.

Ngā tohu tōmua o te korenga o ngā toto whero ( anemia ):

Ahakoa te hikoi poto noa iho, kei te ngenge tonu koe? Kei te ngenge tonu koe, ā, kāore e taea e koe te mahi i ngā mea o mua? Tērā pea kei te mā te āhua o tō mata. Anei ētahi o ngā tohu tōmua o te mate toto iti :

• Tino ngenge noa iho.
• Kiri mā (kiri kōwhai) .
• Te māhunga , te whanoke rānei .
• Te uaua ki te manawa (dyspnea) .
• Te tere o te manawa o te ngakau (tachycardia) .
• Te āhua nei kei te pāorooro kē te ngākau (ngā tere o te pāorooro o te ngākau) .

Ngā tohu tōmua o te korenga o ngā pereti toto (thrombocytopenia):

Kua kite koe i ētahi wā ka puta mai ngā ira whero iti ki tō kiri? Kāore rānei, ka puta noa ngā marutanga ki tō tinana? Kei te ahua koe kei te toto nui atu ō kapia i te mea noa ina parai koe i ō niho? Koinei pea ngā tohu o te iti o ngā pereti toto:

• He iti noa ngā ira whero e toto ana (petechiae) i raro i te kiri.
• Ngā ira papura o te kiri (purpura) .
• He marō (ecchymosis) e puta ana kāore he take.
• Te toto nui mai i ngā kapia, i te ihu rānei.
• Te toto toto nui i roto i ngā wāhine i te wā paheketanga.
• Te toto me te tūtae, te mimi rānei.

Ngā tohu o te neutropenia (tērā pea ka puta, kāore rānei e puta i muri mai):

He mea noa te pāngia e te makariri kotahi, e rua rānei i te marama. Engari he maha tonu te pāngia e te kirika? He maha tonu ngā wā ka pāngia koe e te mate waha? He roa te wā e ora ai? Anei ētahi mea ka pā mai ina iti ō neutrophils:

• Te kirika.
• Ngā mate pukupuku o te waha.
• Te makariri pinepine, te kirika, me te mamae o te puku.
• Ngā mate taringa e hokihoki mai ana.
• Ngā mate harore mō te wā roa.
• Ngā mate urutā o te ara mimi (UTI) .

Ētahi atu tohu o te mate Evans (tērā pea ka puta i ētahi wā):

• Ngā kōpuku lymph pupuhi i te kaki.
• Te whēkau nui .
• Ate nui haere .
• Te kiriuhi .

He aha i puta ai te mate Evans Syndrome?

E ai ki tā mātou i kōrero ai i mua ake nei, he mate pūnaha ārai mate a Evans Syndrome. Ko te tikanga o tēnei ka hē te pūnaha ārai mate o tō tātou tinana ki te mōhio ki ētahi o ō tātou ake toto hei "hoariri" ka tīmata ki te whakaeke i a rātou.

Mā ngā pūtau-B tēnei mahi e mahi, he momo pūtau motuhake i roto i tō tātou pūnaha ārai mate. Ka hangaia e ēnei pūtau-B tētahi mea e kiia nei ko ngā paturopi . Ka haere ēnei paturopi ki te hopu i aua pūtau toto harakore, ka whakangaro i a rātou. I te nuinga o te wā, ka tīmata rātou ki te whakaeke i tētahi momo pūtau toto i te tuatahi, kātahi ka taea e rātou te tīmata ki te whakaeke i ētahi atu momo pūtau toto.

Ko tēnei tukanga te take e ngoikore ai koe i te iti rawa i ngā momo pūtau toto e rua (cytopenia), ā, i ētahi wā ko ngā momo e toru katoa. Ko te ngoikore o ngā momo e toru ka kiia ko te pancytopenia . Ko ngā āhuatanga matua e toru e iti ai ēnei pūtau toto ko:

• Te mate toto toto ā-aunoa (AIHA)Koinei te wā e whakaitihia ai ngā pūtau toto whero. Arā, ka tere ake te whakangaromanga i te mea ka taea e te tinana te hanga.
• Te toto toto ārai mate (ITP) : He āhuatanga tēnei e heke ai te nui o ngā pereti toto. Ka whakaekea e te pūnaha ārai mate ngā pereti toto mai i te toto, ā, ka tangohia atu.
• Te mate pūkahukahu ā-tinana (AI) : He āhuatanga tēnei e heke ai te maha o ngā neutrophils, he momo toto mā. Ka whakaekea, ka whakangaromia hoki e te pūnaha ārai mate ngā neutrophils.

Whakaarohia, he maha ngā take mō te iti o te maha o ngā pūtau toto (cytopenia). I ētahi wā, nā te mea kāore e nui ngā pūtau toto e hangaia ana e te hinu wheua. Heoi, i roto i te cytopenia autoimmune, ka whakangaromia e te pūnaha ārai mate ōna ake pūtau toto.

He aha ngā mea e pāngia ai te mate o Evans Syndrome?

Kāore anō kia tino mōhiotia e ngā kaipūtaiao he aha i puta ai ēnei mate ārai mate. Engari kua kitea e rātou he maha ngā wā ka tīmata ēnei mate i muri i tētahi mate kino, i tētahi āhuatanga rānei e tino pāngia ai te pūnaha ārai mate. Ka kiia ēnei he mea whakaoho .

Waihoki, ki te mea he mate pūnaha ārai mate tōu, he nui ake te tūponotanga ka pāngia koe e tētahi atu mate. Me te mea nei ka horapa tēnei mate pūnaha ārai mate mai i tētahi wāhanga o te tinana ki tētahi atu.

Ka puta ko te mate Evans anake (ka kiia tēnei ko te mate Evans tuatahi ), ka puta rānei hei mate tuarua e pā ana ki tētahi atu mate (ka kiia tēnei ko te mate Evans tuarua) . Ko ētahi o ngā mate ka taea te hono atu i tēnei ara ko:

• Lupus pūnaha (systemic lupus erythematosus)
• Te ngoikore o te ārai mate taurangi noa
• Te ngoikore o te IgA whiriwhiri
• Te mate a Sjögren
• Te mate pukupuku kore-Hodgkin
• Te mate pukupuku toto mau tonu
• He mate hepatitis C mau tonu
• Te mate HIV mau tonu

Mena kei a koe te mate Evans tuatahi, tera pea i puta mai i muri i tētahi mate rangitahi, kāore rānei i te mārama te pūtake o te mate. E whakarōpūtia ana e ngā kaipūtaiao te mate Evans hei mate idiopathic . Ko te tikanga tēnei kāore anō kia kitea he pūtake tika.

He aha ngā raruraru pea ka pā mai i te Evans Syndrome?

Ehara i te mea ka pāngia te katoa e te mate Evans Syndrome e ngā raruraru. He tino ngawari noa iho ngā tohu o ētahi tāngata. Heoi, i ngā wā tino kino, ka taea e ēnei ngoikoretanga o ngā pūtau toto (cytopenias) te whakararu i te ora. Hei tauira:

• Ina kore e ranea ngā toto whero hei kawe i te hāora ki te tinana, kāore hoki e ranea te hāora i roto i te toto (hypoxemia) . He tino uaua tēnei ki te ngākau, ā, ka arahi pea ki te mate ngākau me te ngoikore o te ngākau.
• Ki te kore e ranea ngā pereti toto , e āwhina ana i te toto kia totoka, kāore e totoka tika. Ka tere te toto ka tere. Ka tere te arahi ki te anemia kino.
• Ina ngaro ngā neutrophils i roto i tō tinana , e āwhina ana ki te whawhai ki te mate, ka nui ake te tūponotanga ka pāngia koe e ngā mate, ā, ka kino haere, ka horapa puta noa i tō tinana. Ka arahi pea tēnei ki tētahi mate kino e kiia nei ko te sepsis .

Me pēhea te tautuhi a ngā tākuta i te mate Evans Syndrome?

Ka kitea te mate Evans Syndrome mā roto i ngā whakamātautau toto . Tērā pea ka kitea mēnā ka puta he tohu o te cytopenia, i te wā rānei e tirohia ana te nui o ngā pūtau toto i te wā o te tirotiro hauora o ia rā.

Mena ka whakaatuhia e tō Tatau Toto Katoa (CBC) he iti ō toto whero, ō pereti toto, ō neutrophils rānei, ka whakahaerehia e tō rōpū hauora ētahi atu whakamātautau. Hei tauira, ka tirohia e rātou tō toto mō ngā taumata teitei o ngā paturopi e pā ana ki te Evans Syndrome. Ka tirohia hoki e rātou ētahi atu āhuatanga ka puta ai te cytopenia, pērā i ētahi mate pukupuku, i te mate pukupuku rānei.

Ka whakaū ngā tākuta i te mate Evans Syndrome mā te whakakore i ngā take katoa. I ētahi wā, me mahi pea rātou i tētahi matawai CT (matawai tomography rorohiko) i tētahi koiora wheua rānei hei whakakore i ētahi atu mate.

He rongoā katoa kei te mate a Evans Syndrome? Me pēhea te rongoā?

Ina hoki, kāore he rongoā katoa mō te Evans Syndrome, me tētahi atu mate pūnaha ārai mate. Ka rongoāhia e ngā tākuta ēnei mate pūnaha ārai mate mā te hoatu rongoā hei whakaiti i te mahi a tō pūnaha ārai mate.

Hei tāpiritanga, ka taea te rongoā motuhake i ō tohumate. Hei tauira, ki te tino iti te maha o ngā pūtau toto, ka taea pea e tō tākuta te whakatika i tēnei mā te whakawhiti toto i ētahi wā.

Pērā i te maha o ngā mate pūnaha ārai mate roa, ka taea e te Evans Syndrome te pai haere, te kino haere rānei i roto i te wā. I ētahi wā, ka ahua memeha haere ngā tohu (e kiia ana ko te remission) , engari ka hoki mai anō, ka kino haere rānei (e kiia ana ko te relapse ).

Me whakamātau pea koe i ngā maimoatanga rerekē puta noa i tō oranga, nā te mea ka rerekē pea te angitu i roto i te wā. Ka ngana tō tākuta ki te tiaki i a koe mai i ngā raruraru tino kino o te Evans Syndrome.

He aha ngā maimoatanga?

Ko te rongoā paerewa mō te Evans Syndrome ko ngā rongoā ārai mate , ā, ki te tika, ko ngā whakawhiti toto. Ka mahi ēnei ārai mate mā te whakaiti i te whakaekenga hē a tō pūnaha ārai mate.

Ngā momo rongoā matua e tukuna ana:

• Ngā corticosteroids , pērā i te prednisone . Koinei te maimoatanga tuatahi e hoatu ana.
• Ko te rongoā immunoglobulin ā-roto-uaua (IVIg) ko te hoatu i tētahi otinga kei roto ngā paturopi tangata mā roto i tētahi uaua. Ka taea e ēnei paturopi hou te here ki ngā paturopi ārai mate hapa, ā, ka whakakore i a rātou.

Ki te kore koe e pai ki ngā maimoatanga paerewa, ka whakamātau pea tō tākuta i ētahi atu maimoatanga. Kei roto i ēnei:

• Ngā paturopi monoclonal , pērā i te rituximab . He paturopi ēnei i hangaia i roto i te taiwhanga. I ētahi wā ka taea e ēnei te aukati i te urupare ārai mate. Tērā pea ka tūtohu mai tō tākuta i ēnei mēnā kāore ētahi atu rongoā e whai hua.
• Te tango i te whēkau . I ngā wā tino kino, ka tūtohu pea tō tākuta i tētahi pokanga hei tango i tō whēkau. Kei roto i tō whēkau te wāhi e tangohia ai ngā pūtau toto tawhito. Nō reira, ina tangohia te whēkau, ka pōturi ake te tukanga.

He raruraru, he pānga taha rānei kei te rongoā?

Ina tango koe i ngā rongoā ārai mate, ka heke te urupare a tō pūnaha ārai mate ki tō mate pūnaha ārai mate. Heoi, ka heke anō hoki tō ārai mate ki ngā mate urutā . Nō reira me mahi koe i ngā mahi whakatūpato motuhake kia kore ai e pāngia e te mate.

Tērā pea ka tūtohu tō tākuta i ētahi atu kano ārai mate hei tāpiri atu ki ērā kua riro kē i a koe. Ina ngoikore tō pūnaha ārai mate (he ngoikore te pūnaha ārai mate), tera pea ka ngāwari ake koe ki te pāngia e ngā mate kāore i te nuinga o te wā.

Ka pāngia te roanga o te oranga e te mate Evans Syndrome?

Kāore te mate Evans e pā ki tō roanga o te ora. He iti noa ngā tohu o ētahi tāngata, ā, he wā poto noa iho. Heoi, ko ētahi raruraru, pērā i te toto, te mate ngākau, me te mate pāwera, ka mōrearea pea ki te ora.

Mena kei a koe te mate Evans tuarua, arā, kei a koe tēnei mate me tētahi atu mate mau tonu, ka pā pea tēnei ki tō roanga o te ora. Tērā pea ka pāngia koe e ngā raruraru morearea e pā mai ana me tō mate kē atu.

He aha te tirohanga mō te tangata e pāngia ana e te Evans Syndrome?

He rerekē ngā wheako o te hunga e pāngia ana e te Matepukupuku Evans. Ka taea e ngā tohu te ngawari, te kino rānei. E whakaaro ana ētahi tāngata kua memeha rawatia ā rātou tohu (whakamāmātanga). Ko ētahi ka pāngia anō i muri mai (ka hoki anō).

He tokomaha te hunga e hiahia ana ki tētahi momo maimoatanga me ngā tirotiro hauora auau. He maha ngā wā ka pai te mahi a ngā maimoatanga, engari kāore i te katoa. I ētahi wā, ka ahua heke te whai huatanga o ngā maimoatanga i roto i te wā. Me whakamātau pea koe i ētahi atu maimoatanga.

Me pēhea taku tiaki i ahau anō i a au e noho tahi ana me te mate Evans?

Mena kei a koe te mate Evans Syndrome, he mea nui kia mau tonu ō tirotiro hauora . Ahakoa kei te pai koe, ka hiahia tonu tō tākuta ki te aroturuki i tō āhua, me te kite wawe tonu mēnā ka kino haere.

Me aro tonu koe ki a koe anō, me te tirotiro hoki mō ngā tohu hou. Mēnā he makariri tōu, kāore e pai ake, he toto toto rānei kāore e taea te whakahaere, waea atu ki tō tākuta tonu .

He aha ngā pātai me pātai atu e au ki taku tākuta?

Akene he pai ki a koe te pātai atu ki tō tākuta i ēnei pātai:

• He aha ngā momo pūtau toto kāore i a au?
• E hia te nui o tā rātou hekenga?
• He aha ngā tohu, ngā tohu whakatūpato rānei me tirotiro e au?
• Me pēhea taku mōhio kei te whai hua te maimoatanga, kāore rānei?
• Ka aha mēnā kāore te maimoatanga e whai hua?
• Āhea ahau me whakarite i taku wā tirotiro ki te tākuta e whai ake nei?

He mate onge te mate Evans, kāore pea koe i rongo i mua. He rerekē, he whakararuraru hoki ngā tohu. He mahi uaua te mārama ki te āhua o te mate me tōna tikanga.

Ahakoa he mate mō te wā roa te mate Evans Syndrome, kāore e rite tonu i ngā wā katoa. Kia mau tonu te tumanako ka pai ake tō āhua, i ētahi wā. Ahakoa te āhua o ō kare ā-roto, kei reira tonu tō tīma hauora hei whakarato i te tiaki e hiahiatia ana e koe.

Karere Whakamutunga mō te Tango ki te Kāinga

Āe, me whakamahara atu tātou ki a koe ētahi o ngā mea tino nui kua kōrerohia e tātou.

• He aha te mate Evans?He mate onge e whakaekea ai e tō ake pūnaha ārai mate ō ake pūtau toto.
• Ka taea e tēnei te heke i te maha o ngā toto whero ( anemia ), ngā pereti toto (thrombocytopenia), me te iti pea o ngā neutrophils (neutropenia) .
• Tērā pea ka puta ngā tohu pēnei i te ngenge rawa, te kiri mā, te ngawari o te marō, te toto pinepine, me te mate urutā pinepine .
• Ahakoa kāore he rongoā katoa mō tēnei, ka taea te whakahaere i ngā tohu mā te rongoā .
• He mea tino nui te whai i ngā tohutohu a te tākuta i ia wā, me te aro ki ngā tohu.
• Kāore koe i te mokemoke. Mā ō tākuta me ō whanaunga koe e āwhina. He mea nui anō hoki kia noho pai.

Ko tāku tumanako ka whai hua ēnei mōhiohio ki a koe. Mēnā he pātai āu, kaua e mangere ki te kōrero ki tō tākuta.

Te mate Evans , te mate pūnaha ārai mate, te cytopenia, te anemia, te thrombocytopenia, te neutropenia, ngā mate toto