He ngenge noa iho rānei koe i ētahi wā, he mamae te upoko, he ngoikore rānei? He maha ngā wā kāore tātou e aro nui ana ki ēnei mea iti, tika? Heoi, ki te piki ake te maha o ngā toto whero i roto i tō tinana ki tua atu i te taumata kua tohua, arā, ko te erythrocytosis , ko te polycythemia rānei, ka puta pea ēnei tohu. He mea tēnei me āwangawanga koe i ētahi wā. Nō reira, i tēnei rā ka kōrerohia e tātou he aha te erythrocytosis, he aha i puta ai, me ngā mea ka taea te mahi mōna.
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He aha tonu te erythrocytosis?
Ki te whakarapopoto, ko te Erythrocytosis te wā e nui ake ai te kukū o ngā Pūtau Toto Whero (Erythrocytes) i tō toto i te mea noa. E mōhio ana koe, e rua ngā wāhanga o roto o tō tātou toto. Ko tētahi ko te wāhanga totoka, arā, ko ngā pūtau toto whero, ko ngā pūtau toto mā, me ngā pereti toto. Ko tētahi atu ko te wāhanga wai, e kiia nei e tātou ko te plasma. I roto i te erythrocytosis, ka piki ake te maha o ngā pūtau toto whero i te wāhanga wai, arā, ko te plasma.
Ki te whakamātauhia tō toto, ka kite koe i ngā uara e rua i runga i te pūrongo: Hematocrit me Hemoglobin .
- Hematocrit (HCT): Mā tēnei ka mōhio koe ki te ōrau o ō toto e titoa ana i ngā toto whero.
- Te Hemoglobin (HB): He pūmua tino nui tēnei e kitea ana i roto i ngā toto whero e kawe ana i te hāora puta noa i ō tātou tinana.
I roto i te erythrocytosis, ka teitei ake pea i te tikanga tetahi, tetahi rānei o ēnei uara hematocrit me te hemoglobin.
He aha te pānga o tēnei pikinga o ngā pūtau toto whero ki te tinana?
He mea nui ngā toto whero mō ō tātou tinana. Ka haria e rātou te hāora mai i ngā pukahukahu ki ngā pūtau me ngā kiko katoa o te tinana. Koia te take e whāngaihia ai, e ora ai hoki ō tātou kiko.
Heoi, ki te nui rawa te pikinga o ēnei toto toto whero, ka puta pea ngā raruraru. Kei te take o te pikinga o ngā toto toto whero. He iti noa iho ētahi pānga. Tērā pea ka pāngia koe e ngā āhuatanga pēnei i te ānini me te ngenge. Heoi, ki te piki ake ngā toto toto whero mō ētahi take nui, ka tīmata te toto ki te matotoru. Kātahi ka tūpono te pāngia e ngā āhuatanga kino pēnei i te toto totoka, te mate manawa, te whiu rānei .
Koia te take, ki te pāngia koe e ēnei tohu, he mea nui kia toro atu koe ki te tākuta kia kitea ai te tino take. Mā reira anake ka taea ai e koe te whiwhi maimoatanga tika, te whakaiti i ngā tohu, te ārai rānei i ngā āhuatanga kino.
He aha ngā momo matua o te erythrocytosis?
E rua ngā momo o te erythrocytosis, i runga i te pikinga o ēnei toto whero:
1. Erythrocytosis Tino: Koinei te wā e nui ake ai te maha o ngā toto whero e hangaia ana i roto i tō tinana i te mea noa.
2. Erythrocytosis Whānui: Koinei te wā e noho noa ai te maha o ngā toto whero, engari ka heke te nui o te plasma i roto i te toto, nō reira te āhua nei kua piki ake te kukū o ngā toto whero. Hei tauira, ki te nui tō ruaki, ā, ka pāngia koe e te mate korere, ā, ka ngaro te nui o te wai i roto i tō tinana, ka heke te rere o tō toto. Ka puta pea tēnei āhuatanga i ngā wā pēnei.
E rua ngā momo o te erythrocytosis tino, i runga i te take:
Eritrocytosis Tuatahi
Kei roto i tō tātou hinu wheua te raruraru. E mōhio ana koe, ko te hinu wheua te wheketere matua i roto i tō tātou tinana e hanga ana i ngā toto whero. Nō reira, i roto i tēnei erythrocytosis tuatahi, nā te hapa ira i roto i ngā pūtau take (ngā pūtau tūpuna) i roto i te hinu wheua, ka piki haere te hanga o ngā toto whero me te kore e taea te whakahaere. Ka taea te tuku iho i tēnei hapa ira (hei hapa whānau), ka taea rānei te puta i roto i te oranga.
- Te Erythrocytosis Tuatahi i Whiwhi: He tauira pai tēnei o te mate e kiia nei ko te Polycythemia Vera . He maha ngā tāngata e whakapoauau ana i te Erythrocytosis me te Polycythemia Vera hei mate kotahi. Heoi, ehara i te mea kotahi. Ko te Polycythemia Vera he mate motuhake, he tino kino hoki e puta ai te Erythrocytosis.
- Te Erythrocytosis Tuatahi Tuku Iho: I ētahi wā, ka nui rawa ngā toto whero e whakaputaina ana e te hinu wheua nā ngā hapa o ngā ira tuku iho mai i ngā mātua.
Eritrocytosis Tuarua
Ehara te raruraru i konei i te hinu wheua, engari i tētahi atu mea i waho o te hinu wheua. I te nuinga o te wā, ko te erythrocytosis tuarua ka puta mai i te nui rawa o te homoni e whakaputaina ana e tō tātou tinana e kiia nei ko te erythropoietin , ko te EPO rānei. He karere matū te 'EPO'. Koinei te mea e kī ana ki te hinu wheua kia "hanga ake i ngā pūtau whero."
Whakaarohia, he mate pūkahukahu, he mate ngākau rānei tōu. Kātahi ka iti te nui o te hāora e whiwhihia ana e te tinana. I taua wā, ka ngana te tinana ki te hanga i te homoni 'EPO', ā, mā roto i tēnā, ka whakaoho i te hinu wheua kia hanga i ngā pūtau whero. Nā te mea he hāora kei roto i ngā pūtau whero. Heoi, ki te nui rawa te hanga o ngā pūtau whero i tēnei ara, ka puta te erythrocytosis tuarua. Ka taea hoki te puta o tēnei erythrocytosis tuarua i ētahi āhuatanga ira, engari ehara aua hapa ira i ngā mea kei roto i te hinu wheua.
Me pēhea te tirotiro i ngā uara toto hei kite mēnā he erythrocytosis tōu?
Ina hoki, ka rerekē te taumata o te kukū o ngā toto whero e kiia ana he mea noa i ia tangata, i ia tangata. He maha ngā āhuatanga e pā ana ki tēnei, tae atu ki tō tau, ahakoa he tāne koe, he wahine rānei, me te teitei o te rohe e noho ana koe (ahakoa kei te taumata moana koe, kei te rohe maunga rānei).
Ko te erythrocytosis i roto i ngā pakeke ka kitea mā te pikinga o te hematocrit (HCT) me/ranei te hemoglobin (HB). Ka taea te ine i ēnei uara mā te whakamātautau toto e kiia nei ko te "Complete Blood Count (CBC)".
Mō ngā tāne:
- Hematocrit (HCT): Mena he nui ake i te 50%
- Hemoglobin (HB): Mena he nui ake i te 17.5 g/dL
Mō ngā wāhine kāore i te hapu:
- Hematocrit (HCT): Mena he nui ake i te 45%
- Hemoglobin (HB): Mena he nui ake i te 15.3 g/dL
He mea nui: He aratohu whānui noa iho ēnei uara. Mā tō tākuta e whakatau mēnā he erythrocytosis tōu i muri i te whakaaro ki tō hauora whānui.
He aha ngā take o te Erythrocytosis Whakawhanaunga?
Nā te hekenga o te nui o te wai i roto i te tinana tēnei, ka heke te rere o te toto (plasma) me te pikinga o te kukū o ngā pūtau toto whero. Nō reira, ko te tino take o tēnei ko te matewai .
- Ruaki nui
- Korere
- Ko ētahi rongoā, hei tauira, ngā diuretics (ngā rongoā hei tango i te wai mai i te tinana) (Ka hoatu ēnei mō te toto toto tiketike, te pupuri wai rānei).
Nā ēnei take, ka heke te nui o te wai i roto i te tinana, ā, ka puta te erythrocytosis whanaunga.
He aha ngā take o te Erythrocytosis Tuturu?
E rua ngā take motuhake mō tēnei: te take tuatahi me te take tuarua.
Ngā take o te erythrocytosis tuatahi:
He maha ngā wā ka puta tēnei i te hapa ira e pā ana ki te hinu wheua.
- Te Polycythemia Vera me Ētahi Atu Pūngāwerewere Myeloproliferative: Koinei ngā āhuatanga e nui rawa ai te whakaputanga o ngā toto whero me ētahi atu toto i roto i te hinu wheua. Ko te Polycythemia Vera te mea tino noa o ēnei.
- Ngā hapa whānautanga: Tērā pea ka whānau mai ētahi tāngata me te hapa ira e hua ai te nui rawa o ngā toto whero e whakaputaina ana e te hinu wheua.
Ngā take o te erythrocytosis tuarua:
Ko te nuinga o te wā ka puta tēnei i te pikinga o te homoni EPO.
- Ngā āhuatanga e whakaiti ana i te hāora ki ngā kiko:
- Ngā mate pūkahukahu (hei tauira, te bronchitis mau tonu, te emphysema)
- Mate Manawa (hei tauira, ngā mate manawa whānau)
- Te moe pōrearea
- Hemoglobinopathy: Koinei ngā āhuatanga e kore ai e taea e te pūmua hemoglobin i roto i ngā toto whero te kawe tika i te hāora nā te mea he hapa.
- Ngā mate whatukuhu me ngā whakawhitinga tākihi:
- Te whakawhāiti o ngā oko toto e tuku ana i ngā whatukuhu (te stenosis o te uaua o te uaua o te whatukuhu)
- Hydronephrosis (te pupuhi o ngā whatukuhu nā te nui o te mimi)
- Ka puta pea tēnei āhuatanga i ētahi wā ahakoa i muri i te whakawhitinga whatukuhu.
- Ngā pukupuku: Ka taea e ētahi pukupuku matepukupuku me ētahi pukupuku kore-matepukupuku te whakaputa i te homoni EPO nui rawa.
- Ngā pukupuku matepukupuku: Te Matepukupuku Pūtau Whatu, Te Hemangioblastoma, Te Matepukupuku Pūtau Hepato, Te Matepukupuku Parathyroid.
- Ngā pukupuku kore-matepukupuku: Ngā Fibroids Kōpū, Pheochromocytoma, Meningioma.
- Te paihana waro haukini me te kai hikareti: Ka pāngia te tinana e te paihana nui e te paihana waro haukini, ka whakaiti i te hāora ki ngā kiko.
- Ko ētahi rongoā me ngā rongoā:
- Ngā Steroid Anabolic (e tangohia ana e ngā kaitākaro hei whakanui i te kaha)
- Te tango i te homoni testosterone.
He aha ngā tohu ka pā ki te tangata e pāngia ana e te erythrocytosis?
Ko ngā tohu e pā ana ki a koe (me tōna kaha) ka whakawhirinaki ki te pūtake o tō erythrocytosis. Hei tauira, ko te tangata whai erythrocytosis tuarua ka pāngia pea e ngā tohu pēnei i:
- Ānini
- He āhua pōhēhē, he āhua uaua ki te arotahi
- Te uaua ki te moe
- Te ngoikore, te ngenge
Tērā pea ka pāngia te tangata whai erythrocytosis tuatahi (ina koa ko te polycythemia vera) e ngā tohu kino ake:
- Te toto toto tiketike
- Te werawera nui i te pō
- Te ngaronga taumaha mō te kore take
- Te mamae nui, te pupuhi, me te whero o ngā hononga (e kiia ana ko te kauti )
- Ngā raruraru toto (te toto pinepine o te ihu, te toto, te maru rānei mai i tētahi whara iti noa iho)
- Kiri mākūkū (tērā pea ka nui ake te mākūkū, ina koa i muri i te kaukau wera)
- Te ngoikore o ngā waewae, te āhua e oma haere ana ngā pōpokorua
- Te whero me te mumura i te mata, i ngā ringa me ngā waewae.
Me pēhea te tautuhi a ngā tākuta i te erythrocytosis?
Ka whakamātau tuatahi tō tākuta ki te whakatau i te take o te nui o ngā toto toto whero i roto i tō tinana, mā te whakamahi i ngā momo whakamātautau me ngā tikanga.
Tuatahi, ka pātai atu rātou mō tō hītori hauora, ngā rongoā e tangohia ana e koe, tō āhua noho (hei tauira, he momi hikareti koe), me ō tohumate, ā, ka tirohia mēnā he erythrocytosis whanaunga (nā te hekenga o te toto toto i roto i te toto) te take. Ka whakahaerehia hoki e rātou he whakamātautau tinana.
Ko te mea e whai ake nei hei tirotiro ko te mea kei a koe te mate tuatahi, te mate tuarua rānei . Ka taea hoki e koe te whakahaere i ētahi atu whakamātautau me ngā mōhiohio kua whakahuatia i runga ake nei.
He aha ngā whakamātautau e mahia ana?
- Tatau Toto Katoa (CBC): Ka taea e tēnei te tirotiro i te tatau toto whero, te hemoglobin (HB), me te taumata hematocrit (HCT).
- Te Whakamātautau Toto Āpiti (PBS): Ko te tango i tētahi pata toto ka tirohia ngā pūtau i raro i te karuārai hei tirotiro mēnā he rerekē te āhua, te rahi rānei. Mēnā he mate tōu pērā i te Polycythemia Vera, tera pea ka kitea e koe ngā pūtau rerekē.
- Ngā Whakamātautau Mahi a te Tākihi me te Ate: Mā tēnei ka taea te whakaatu mēnā he mate tākihi, he pukupuku rānei e nui rawa ana te EPO.
- Ine i te hāora i roto i te toto mā te whakamahi i tētahi pūoko iti e whakanohoia ana ki te matimati . Mā tēnei ka āwhina ki te whakatau mēnā nā te mate manawa, te mate pūkahukahu rānei i puta ai te mate.
- Te tirotiro i te taumata o te erythropoietin (EPO): Mena he iti te taumata o te EPO, tera pea ko te erythrocytosis tuatahi, mena he teitei te taumata o te EPO, tera pea ko te erythrocytosis tuarua.
- Te tātaritanga mimi: Ka tangohia he tauira mimi hei tirotiro mō ngā āhuatanga rerekē. Mena he toto whero kei roto i te mimi, tera pea nā te mate tākihi.
Mena kei te whakapae te tākuta kei a koe tētahi āhuatanga motuhake, pērā i te polycythemia vera, ka taea e ia te mahi i ētahi atu whakamātautau, pērā i te koiora wheua .
Me pēhea te rongoā i te erythrocytosis?
I te nuinga o te wā, kāore e taea te whakaora katoa i te pūtake o te erythrocytosis. Heoi, ka taea e te maimoatanga te whakahaere me te whakaiti i ngā tohu. Mēnā he erythrocytosis i puta mai i ngā take nui, ka whakamahia hoki te maimoatanga hei ārai i ngā āhuatanga morearea pēnei i te toto totoka.
- Te tango toto, te tango kiri rānei:
Koinei te rongoā tino noa mō te polycythemia vera. He rite ki te tuku toto, engari ko te tango i tētahi toto iti mai i tētahi uaua me te whakaiti i te maha o ngā toto whero me te nui o te toto e nui rawa ana. Ko te erythrocytosis tuarua kāore e hiahiatia tēnei rongoā.
- Ngā rongoā:
- Mō te hunga e nui ana te mōrearea o te toto totoka, ka tūtohu pea te tākuta kia tangohia he aspirin iti te horopeta i ia rā.
- Kei reira anō ngā rongoā hei whakaiti i te maha o ngā toto toto whero:
- Hydroxycarbamide (Hydroxycarbamide)
- Hydroxyurea (Hydroxyurea)
- Busulfan
- Interferon alfa (Interferon alfa)
- Ruxolitinib
Ka tohua e tō tākuta ngā rongoā e tika ana mō tō āhua. Ka tohua hoki e ia he maimoatanga mō te āhua taketake, i runga i te pūtake o tō erythrocytosis.
Mena kei a au tēnei āhuatanga, he aha taku e tumanako ai?
Ka whakawhirinaki tō wheako ki te pūtake o tō erythrocytosis me tōna kaha. Hei tauira, ko ētahi āhuatanga tuku iho o te erythrocytosis tuatahi ka puta he tohu ngawari noa iho, ā, kāore e morearea ki te ora. Heoi, ko ngā āhuatanga kino ake, pērā i te polycythemia vera, me rongoā mō te wā katoa.
Me pēhea taku tiaki i ahau anō?
Ko te mea nui ko te whai i ngā tohutohu a tō tākuta kia tika. I tēnei wā, tera pea ētahi huringa āhua noho hei āwhina i a koe:
- Ki te kai hikareti koe, kati.
- Kia mau tonu te taumaha tinana hauora.
- Ki te mea he toto toto tiketike tōu, me whakahaere.
- Kia kaua e haere mai i te taumata o te moana ki ngā wāhi teitei rawa (ngā wāhi maunga) i ngā wā katoa e taea ana.
Āhea ahau me haere ki te hōhipera tere (ETU) ?
Mena he mate tōu e pā ana ki te erythrocytosis e tūpono ai koe ki te toto totoka, he mea nui kia mōhio koe ki ngā tohu o te toto totoka. Mena ka pāngia koe e tētahi o ngā tohu e whai ake nei, rapua tonutia te awhina hauora:
- Te Thrombosis Utauta Hōhonu (DVT): Te pupuhi, te mamae, me te whero i te waewae kotahi.
- Te toto totoka i roto i ngā pukahukahu (Pulmonary Embolism - PE): Te mamae o te uma, te uaua ki te manawa, te pōuri.
- Whiu: Te ngaronga ohorere o te taurite, te taunga o ngā hononga, te ngoikore o ngā uaua, te ngoikore rānei o te taha kotahi o te tinana.
- Te whakaekenga o te manawa: Te mamae o te uma, te poto o te manawa, te ānini, te werawera.
Ki te pā mai tētahi o ēnei tohu ki a koe, me toro atu ki te tākuta tonu atu, kaua e whakaroa.
Hei whakamutunga, ngā mea hei maumahara (Karere hei tango ki te kāinga)
Ko te erythrocytosis he pikinga o te maha o ngā toto whero i roto i tō toto. He āhuatanga iti noa iho tēnei, he tohu rānei i ētahi wā mō tētahi āhuatanga kino.
- Mena ka pā mai ētahi tohu rerekē ki a koe (ina koa te ngenge tonu, te ānini, te ponana kiri, te uaua ki te manawa), tirohia he tākuta.
- Mā te tākuta e whakatau te tino take o te nui o ngā toto whero i roto i tō toto.
- I ētahi wā, mā ngā whakarerekētanga ngāwari o te āhua noho (hei tauira, te whakaiti i te nui o te rongoā e tangohia ana e koe, te rongoā i te matewai) ka taea te whakatau i tēnei raruraru.
- Mena he mate kino ake te take o te erythrocytosis, ka tirotirohia koe e tō tākuta i ia wā, ā, ka hoatu ki a koe te maimoatanga e tika ana.
He mea tino nui te tiaki i tō hauora, nō reira, ki te mea he āwangawanga āu, kaua e wehi ki te kōrero ki te tākuta.
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