Kei te pōuriuri hoki tō tirohanga ina ara ake koe i te ata? Kei te ahua kino haere i te roanga o te rā? He uaua rānei ki a koe te kite i ngā rama i a koe e taraiwa ana i te pō? Ahakoa he āhua noa iho ēnei, tera pea he tīmatanga o tētahi raruraru kanohi iti. Koinei te momo mate ka kōrerohia e tātou i tēnei rā, ko te Fuchs' Dystrophy tēnā.
He aha te mate pukupuku a Fuchs?
Ki te whakarapopoto, ko te Fuchs' Dystrophy he mate e pā ana ki te cornea o ō kanohi e rua. E mōhio ana koe he aha te cornea? Ko te kiriuhi mārama, rite ki te karāhe e kapi ana i te mua o tō kanohi. Ko te wāhanga tae o tō kanohi, te iris , me te pupil, e kapi ana i tēnei cornea. E kiia ana hoki tēnei ko te 'Fuchs' corneal dystrophy' me te 'Fuchs' endothelial dystrophy'.
Nō reira, ina pāngia koe e te mate Fuchs' dystrophy, ka mate haere ngā pūtau i te paparanga o roto rawa o tō cornea, e kiia nei ko te corneal endothelium . He wāhanga tino nui tēnei endothelium. He rite tana mahi ki te papu wai iti. Ka āwhina ki te tango i te wai kore e hiahiatia mai i te cornea, kia mārama, kia ma hoki.
Whakaarohia, he aha te mea ka tupu ina mate ngā pūtau e mahi ana i roto i tēnei papu? Ka tīmata te wai ki te kohikohi i roto i te kornea. Kātahi ka pupuhi te kornea, ka rite ki te hautai kua kī tonu i te wai. Koinei te take ka tīmata te āhua pōuriuri o ngā kanohi, ā, i ētahi wā ka rite ki te kohu kua puta ki runga i te kanohi. I ngā wā tino kino, ka puta he pupuhi wai iti ki te mata o te kornea. Ka taea e ēnei pupuhi te whakararuraru me te whakararuraru i te kanohi.
He aha ngā wāhanga o te Fuchs' Dystrophy?
E rua ngā wāhanga matua o te mate pukupuku a Fuchs.
- Wāhanga tōmua: Ko te tohu matua ka pā ki a koe i tēnei wā ko te tirohanga pōuriuri i te ata . He rite ki te whakaata kua kohu i te oho ake. Heoi, i a koe e mahi ana i ō mahi o ia rā, i roto i ētahi haora, ka heke haere te pōuriuri, ā, ka mārama ake tō tirohanga. Tērā pea kāore he tohu nui o ētahi tāngata i tēnei wā.
- Wāhanga tōmuri: I te haere whakamua o te mate, ka tīmata te pōuriuri i kitea i te ata anake, ā, ka mau tonu i te roanga o te rā. Ka pūmau te pupuhi o te kornea. Ko te tikanga tēnei ka pōuriuri pea tō tirohanga i ngā wā katoa o te ao, o te pō, o te ata rānei.
He aha ngā tohu o te Fuchs' Dystrophy?
I ngā wāhanga tōmua, kāore pea koe e kite i tētahi tohu. Heoi, i te whanaketanga haere o te mate, ka kite pea koe i ngā tohu pēnei i:
- Te iti o te tirohanga pō: He rite tēnei ki te kitenga i te kanapa me ngā porowhita huri noa i ngā rama o mua i te wā e taraiwa ana i te pō.
- Te uaua ki te kite i ngā rā ua: Ina pōuri haere te taiao, he uaua ki te kite mārama i ngā mea.
- Te uaua ki te wehewehe i ngā mea (te kore e aro ki te rerekētanga): Hei tauira, tera pea he uaua ki te kimi i tētahi pana mā i runga i te pakitara mā.
- Te aro ki te mārama kanapa: Ka kikorangi rawa ngā kanohi, ā, kāore e taea te titiro atu ki te rā, ki ngā mārama kanapa rānei i te kāinga.
- He rite ki te onepu, ki te paru rānei kei roto i ō kanohi. He kare ā-roto whakarihariha, me te mea kei roto tetahi mea e mau ana.
- Ka pakū ngā mirumiru o te kornea, ā, ka mamae ngā kanohi. He tohu kino tēnei.
- Te whara: Ka puta tuatahi ēnei whara ki waenganui o te kornea. Ka taea e ēnei whara te whakararu i te tirohanga mō ake tonu atu.
He aha te take o te Fuchs' Dystrophy?
Ko te take matua mō te whanaketanga o te mate Fuchs dystrophy he mea tuku iho . Ko te tikanga, mēnā kei tō whaea, kei tō pāpā rānei te mate, tera pea ka pāngia koe e te mate. Ka kiia tēnei he tukunga iho autosomal dominant i roto i te pūtaiao hauora. Heoi, i ētahi wā ka pāngia te tangata e te mate i ētahi wā, ahakoa kāore he tangata o te whānau e pāngia ana e te mate.
Waihoki, ka taea e ētahi mea te whakakino ake i te mate pukupuku o Fuchs .
- Te kai hikareti: Ko te hunga e kai hikareti ana ka nui ake te tūponotanga ka pāngia rātou e tēnei mate.
- Te pānga ki te rā (te pānga ki ngā hihi UV): Kāore i te pai te pānga pinepine ki ngā hihi ultraviolet kaha.
- Te mate huka: Ka nui ake te kino o tēnei mate i roto i te hunga mate huka.
Ko wai kei te mōrearea nui ake ki te whakawhanake i te Fuchs' Dystrophy?
He nui ake te tūponotanga o ētahi tāngata ki te pāngia e te mate pukupuku o Fuchs i ētahi atu. Kia kite tātou ko wai tēnā.
- Tau: Tērā pea ka taea e te tākuta te kite i ngā tohu tuatahi o tēnei mate i waenga i te 30 me te 40 tau. Heoi, he maha ngā wā ka pāngia te tirohanga i muri i te 50 tau .
- Ira Tangata: He nui ake te tūponotanga o ngā wāhine ki te pāngia e tēnei mate i ngā tāne.
- Hītori whānau: E ai ki te kōrero i mua ake nei, mēnā kei te pāngia tētahi o te whānau e te mate pukupuku a Fuchs, ka tūpono pea ētahi atu ki te pāngia anō hoki.
Me pēhea te tautuhi a ngā tākuta i te Fuchs' Dystrophy?
Mena kei a koe ēnei tohu, ko te mea tuatahi me mahi e koe ko te toro atu ki tētahi tohunga tiaki kanohi . Ka pātai tuatahi ia ki a koe mō ō tohu, ka arotake i tō hītori hauora, kātahi ka whakahaere i tētahi whakamātautau kanohi hōhonu.
I tēnei whakamātautau kanohi, ka kite te tākuta i ētahi tohu e kī ana kei a ia te mate pukupuku a Fuchs.
- Ka kite koe kua matotoru ētahi o ngā paparanga o te kornea .
- NāuKa kitea ngā panoni ki te āhua o te endothelium.
- Tērā pea ka kite koe i ngā puku iti e kīia nei ko te guttae i te taha o roto o te cornea. He tohu ēnei nō te ngoikore o ngā pūtau endothelial.
Ngā whakamātautau hei whakaū i te Fuchs' Dystrophy
Hei whakaū i te mate, ka whakahaerehia pea e te tākuta ētahi whakamātautau, pēnei i:
- Te tirotiro i te kanohi mā te whakamahi i ngā karuārai kanohi motuhake. Hei tauira, ko te tirotiro rama kuiti me te tirotiro i te karuārai kanohi confocal/spectular . Mā ēnei ka taea e tātou te kite i te kornea i te taumata pūtau.
- Pachymetry: He whakamātautau kore mamae tēnei. Ka ine i te matotoru o tō cornea. Ki te pupuhi te cornea, he matotoru rawa, tika?
- Tomography Whārite Ātaahua (OCT): He matawai kanohi kore-whakaeke tēnei, kāore he mamae. Ka whakamahia te māramatanga hei tango pikitia mārama o roto o tō kanohi, inā koa te wāhanga whakawhiti o te cornea.
He aha ngā maimoatanga mō te Fuchs' Dystrophy?
I runga i ngā whanaketanga pūtaiao o nāianei, ka taea te rongoā i te mate pukupuku o Fuchs, engari kāore e taea te rongoā . I ngā wāhanga tōmua o te mate, ki te kore he tohu nui, ka tirotirohia pea koe e tō tākuta. Ko te tikanga o tēnei ka tonoa pea koe kia haere mai ki te tirotiro kanohi i ngā wā katoa.
Anei ētahi atu tikanga maimoatanga:
- Ngā hinu kakara me ngā pata kanohi: Ki te kore e tino kino ō tohu, ka tohua pea e tō tākuta he rongoā hei whakaiti i te pupuhi i roto i te kornea me te āwhina i te tango i te wai nui. He wā poto noa iho te whakaora mai i ēnei.
- Whakamaroke makawe ā-ringa: Kaua e miharo, he maimoatanga anō hoki tēnei! Hei whakaiti i te pupuhi o te ata, kua kitea ko te pupuhi i te hau matao ki tō mata mai i te whakamaroke makawe (mai i tawhiti me te āta) ka āwhina i te whakamaroke i te makuku nui i roto i te kornea. Me pātai atu koe ki tō tākuta mō te tikanga tika.
- Te whakawhitinga kōnea: Ina tīmata te whakawhāiti nui o tō tirohanga e te mate pukupuku a Fuchs, ko te pokanga te maimoatanga pai rawa atu. Tērā pea ka taea e koe te whai i tētahi tikanga endothelial keratoplasty (EK) , e whakawhitinga ana i tētahi wāhanga noa iho o te kōnea. Tērā pea ka taea e koe te whai kōnea hou. He tino angitu te pokanga EK ināianei nā te mea ko te tango noa i te paparanga mate o te endothelium ka whakakapia ki tētahi paparanga hauora.
- Te Tangohanga Anake a Descemet (DSO):He maimoatanga hou tēnei. Ko te tikanga he waru i tētahi porowhita o ngā pūtau mate i waenganui o te kornea. Mā tēnei ka taea e ngā pūtau hauora huri noa i te kornea te tipu ki roto, ka whakakī i ngā āputa. Kāore pea tēnei e mahi mō te katoa, ā, kei te tākuta te whakatau.
He aha ngā pātai me pātai atu ahau ki taku tākuta mō te Fuchs' Dystrophy?
He mea nui kia hanga he whanaungatanga pai ki tō tākuta kanohi. Kia mahara ki te haere ki ō whakamātautau kanohi i runga i te wā kua whakaritea. Me kōrero tonu atu ki tō tākuta mēnā ka puta he tohu hou, mēnā rānei ka kino haere ō tohu.
Ka taea e koe te pātai atu ki te tākuta i ngā pātai pēnei:
- He aha ngā tohu e tika ana kia kite ahau i a koe i te wā e taea ai?
- He aha te maimoatanga e taunaki ana koe māku? He aha ngā painga me ngā huakore?
- He whakamātautau haumanu kei reira ka taea e au te whakauru atu?
- Mena he kino taku tirohanga, he aha ētahi taputapu āwhina mō te tirohanga iti hei āwhina i ahau?
Ka taea te ārai i te mate pukupuku a Fuchs?
Ina hoki, kāore he huarahi i tēnei wā hei ārai i te mate pukupuku o Fuchs. Heoi, ki te mea he kaipaipa koe, ka taea e te whakamutu te āwhina. Mena he mate huka koe, he mea nui hoki kia mahi tahi koe me tō tākuta ki te whakahaere i ō taumata huka toto.
He aha ngā mea ka tumanakohia e au mēnā kei a au te Fuchs' Dystrophy?
I runga i te kaha o te mate pukupuku a Fuchs, ki te kore koe e whiwhi maimoatanga tika, ka pāngia pea koe e te mamae nui, te ngaro o te tirohanga, me te matapo pea .
Engari mā te maimoatanga tika, ka tino pai ake tō āhua. Whai muri i ētahi pokanga (tae atu ki ngā mōhiti), ka taea e tō tirohanga te hoki ki te 20/20, pērā i te tangata hauora, i roto i ētahi rā. Koia te mea nui kia mahi tahi koe me tō tākuta ki te kimi i te maimoatanga e tika ana māu.
He mea whakamataku te pāngia e ngā tohu o tētahi mate kanohi, ā, kāore te mate kanohi o Fuchs i te rerekē. Mena kei a koe ngā tohu pēnei i te mamae o ngā kanohi, te tirohanga pōuri rānei, me toro atu ki te tākuta i te wā e taea ai. Kia maumahara, ko te tātaritanga wawe me te maimoatanga ka hua ake ngā hua pai rawa atu. Kei te whakawhanake tonu ngā kairangahau i ngā huarahi hou hei whakahaere me te rongoā i te mate kanohi o Fuchs me ētahi atu mate kanohi.
Karere Tangohia ki te Kāinga
Āe, ko tāku tumanako kua mārama ake koe ki te mate Fuchs' Dystrophy, i kōrerohia e tātou i tēnei rā.
- He mate tuku iho tēnei e pā ana ki te kornea o te kanohi.
- Ko ngā tohu matua ko te pōuri o te tirohanga i te ata , te pōuri o te tirohanga puta noa i te rā, te kitenga i ngā mowhiti ina titiro ki ngā rama, me te mamae o ngā kanohi.
- Ka taea e ngā mea pēnei i te momi hikareti, te hihi UV kaha, me te mate huka te whakararuraru i te mate.
- Ka taea e te tākuta kanohi te tātaritanga i tēnei me te tohu i te maimoatanga tika māu.
- Kei reira ngā maimoatanga pēnei i te rongoā me ngā pokanga motuhake (te whakawhitinga kiriuhi, DSO).
- He mea tino nui kia tere te kite me te rongoā i te mate.
Ki te pā mai ēnei tohu ki a koe, kaua e wehi ki te toro atu ki te tākuta. He mea utu nui ngā kanohi, nō reira ko tā tātou kawenga te tiaki i a rātou.
Te Mate Kore o Fuchs, Te Kornea, Te Mate Kanohi, Te Tirohanga Pōuri, Te Whara Kanohi, Te Whakatō Kornea











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