Whakaarohia kei te titiro koe ki te whakaata, ka kite i tētahi rārangi tika i waenganui o tō mata, he whero rawa tetahi taha, he werawera, ā, ko tetahi taha he noa, he mā pea... Kāore ianei tēnā i te whakamataku, i te miharo hoki? Mēnā rānei ka kite koe i tētahi taha o te tinana o tō pēpi hou kua huri whero, ā, ko tetahi taha he noa? Koinei te mea e kiia nei e mātou ko te rongoā Harlequin Sign in. Nā te mea he ahua rerekē te ingoa, me rapu atu tātou mō tēnei mea, me te mea he mea tēnei hei wehi mā tātou.
He aha rawa tēnei Tohu Harlequin?
Ki te whakarāpopototanga, ko te Tohu Harlequin te wā e rerekē ai te tae o te kiri i tētahi taha o tō tinana, o tō mata rānei (ka whero, ka pōuri rānei), ko tētahi taha ia ka noho tonu, ka mā tonu i ētahi wā. Ko te āhua nei kua wehea ēnei taha e rua e tētahi rārangi tika, i waenganui tonu o te tinana.
Haunga tēnei rerekētanga o te tae kiri, ka kitea anō hoki ētahi atu āhuatanga i ngā taha e rua.
- Whero: Tērā pea he hyperhidrosis (he nui rawa te werawera) tēnei wāhi. Tērā pea ka paku mahana te kiri o taua wāhi ina pā atu.
- Taha Mā/Noa: Kāore tēnei taha e werawera. Ka mātao hoki te kiri ina pā atu.
Ahakoa he tohu pea tēnei Tohu Harlequin mō tētahi mate hauora pēnei i te 'Harlequin syndrome', i te nuinga o te wā he pai noa iho, ā, ka memeha noa iho.
He aha ngā take matua mō tēnei?
Kāore e taea te kimi i tētahi take motuhake mō tēnei. Ko te take matua mō tēnei he raruraru whakawhitiwhiti kōrero i roto i te pūnaha io motuhake o tō tātou tinana. Whakaarohia tēnei hei pūnaha "aunoa-pairati" o tō tātou tinana. Mā tēnei pūnaha e whakahaere ngā mea kāore tātou e mōhio kei a tātou, pērā i tō tātou manawa, te tere o te ngakau, me te werawera.
Nō reira, ki te mea he aukati, he hapa rānei kei roto i te ara io e tuku karere ana mai i te roro (hypothalamus) mā te taurakira ki te mata me te tinana o runga, tērā pea kāore te karere e tukuna tika ki te taha kotahi o te tinana. Koinei te take e whānui ai ngā oko toto i tetahi taha, e whero ai, engari kāore tetahi taha e whiwhi i te karere, ā, e noho noa ana.
Ka pā anō hoki tēnei ki ngā pēpi whānau hou?
Ae, he mea tēnei e kitea ana i roto i ngā pēpi whānau hou. E ai ki ngā rangahau, tata ki te 10% o ngā pēpi hauora ka pāngia pea e tēnei Tohu Harlequin. Nō reira, kaua e manukanuka mēnā kei tō pēpi tēnei.
I te nuinga o te wā ka puta tēnei i waenga i ngā rā e rua me te rima i muri i te whānautanga o te pēpi, engari i ētahi wā ka puta mai i te toru wiki pea te roa.
Ko te mea tino nui ko tēnei Tohu Harlequin kei ngā pēpi whānau hou.Kāore he kino. Ka ngaro atu tēnei panoni tae i roto i te 30 hēkona noa iho. I ētahi wā ka roa pea ki te 20 meneti. Tērā pea ka puta anō ina whakatakotoria te pēpi ki tōna taha.
He mea tino nui: Kaua e whakapoauautia tēnei āhuatanga e kiia nei ko te Harlequin Sign ki te 'Harlequin ichthyosis', he āhuatanga ira tino morearea, he mea morearea ki te ora, ā, he tino onge. Ko te 'Harlequin ichthyosis' he āhuatanga e kapi katoa ana te tinana o te pēpi i ngā unahi matotoru, rite ki te pereti, me ngā kapiti hohonu i waenganui. He mea tino rerekē.
Ētahi atu mate e pā ana
I ētahi wā ka puta te Tohu Harlequin hei tohu mō ētahi atu mate hauora.
Te Mate Harlequin
He āhuatanga tēnei e pā ana ki tō tātou pūnaha io aroha. Mā tēnei pūnaha io tātou e whakahaere te urupare "whawhai-ā-rere", arā, ko ngā huringa e puta ana i roto i te tinana ina harikoa tātou, ina mataku, ina whakakorikori tinana rānei. Ina whakahohehia tēnei pūnaha i roto i te tangata whai mate Harlequin Syndrome (hei tauira, i te wā e whakakorikori tinana ana), ka whero tetahi taha o te mata me te tinana, engari kāore tetahi taha.
Te Mate Horner
He mate pūnaha io onge anō hoki tēnei. Ka pā ki te kanohi me ngā kiko e karapoti ana i te taha kotahi o te mata. Ka kiia hoki ko te 'oculosympathetic palsy'. Ka puta mai i te aukati i te ara io mai i te roro ki te kanohi me te mata. I konei anō hoki, ka whero pea te taha o te mata e pāngia ana.
| Tūnga | Ko wai ka pāngia? | Ngā āhuatanga matua | He pono? |
|---|---|---|---|
| Tohu Harlequin (i roto i ngā pēpi hou) | Ngā pēpi whānau hou hauora (tata ki te 10%) | He whero rangitahi i tetahi taha o te tinana. | Kāo. Kāore he kino, ā, ka memeha noa iho. |
| Te Mate Harlequin | Mō te tangata o ngā tau katoa | Te whero me te werawera i tetahi taha i te wā e whakakorikori tinana ana, e harikoa ana rānei. | Kei te pūtake o te take. I te nuinga o te wā kāore he kino. |
| Te Mate Horner | Mō te tangata o ngā tau katoa | He kamo o raro i te taha kotahi o te mata, he kanohi mangu iti, he iti te werawera, me te whero o te mata. | Tērā pea he tino kino te tino take (hei tauira, he pukupuku). He mea nui kia tirohia te hauora. |
Me pēhea te rongoā?
Ko te maimoatanga e whakawhirinaki ana ki te take o te Tohu Harlequin.
- Mō ngā pēpi hou: Kāore he maimoatanga e hiahiatia ana. Ka memeha noa iho i roto i ētahi hēkona, i ētahi meneti rānei.
- Mō te Mate Harlequin: Kāore e hiahiatia he maimoatanga i ngā wā katoa. I ētahi wā ka pai ake tēnei mate i a ia anō. Heoi, ki te whakaaro tō tākuta he mea tika te maimoatanga, ka tohua e ia he maimoatanga i runga i te take. Kei roto i ēnei ko:
- Ka whakamahia he kano ārai mate e kiia nei ko te 'Stellate ganglion block' hei whakahaere i te rerekētanga o te tae o te kiri.
- Ngā werohanga paitini botulinum hei whakahaere i te werawera.
- Mena he pukupuku kei raro, ka taea te tango mā te pokanga, mā te rongoā irahiko rānei.
- He tohutohu mō te manukanuka hinengaro i puta mai i tēnei āhua.
- Mō te Horner Syndrome: Ki te kore he mamae, kāore pea e hiahiatia he maimoatanga. I tēnei wā, ka rongoatia e te tākuta te take matua.
Āhea koe me toro atu ki te tākuta?
Ki te kite koe, tetahi rānei o tō whānau i te Tohu Harlequin, he whero, he werawera, he werawera hoki i te taha kotahi o te tinana, ko te mea pai ko te toro atu ki te tākuta me te tirotiro i a koe anō.
Ka tirotirohia koe e tō tākuta, ka pātai atu mō ō tohumate, ā, ki te tika, ka whakahaerehia ētahi whakamātautau hei whakakore i ētahi atu mate. Ahakoa he onge, he mea nui kia whakakorea he pukupuku, he mate rānei, nā te mea koinei pea te take.
Ki te puta ohorere mai ēnei tohu me ētahi atu tohu kino (hei tauira, te ānini nui, te panoni o te tirohanga, te ngaronga o te māramatanga), he mea nui kia haere tonu ki te Tari Whawhati Tata (ETU) o te hōhipera tata .
Karere Tangohia ki te Kāinga
- Ko te Tohu Harlequin he āhua e whero ana tetahi taha o te tinana, o te mata rānei, ā, he mā tetahi taha. Kāore tēnei i te kino i te nuinga o te wā.
- He mea noa tēnei i roto i ngā pēpi whānau hou. Ka memeha noa iho, i roto i ētahi meneti, kāore he maimoatanga, ā, kāore he mea hei manukanuka. Kia maumahara ehara tēnei i te mate kino 'Harlequin ichthyosis'.
- Ki te puta tēnei i roto i ngā pakeke, he tohu pea nō tētahi mate pūnaha io pērā i te 'Harlequin syndrome' me te 'Horner syndrome' rānei.
- Ki te pāngia koe, tō pēpi rānei e tēnei tohu, he mea whakaaro nui kia kaua e mataku, engari me toro atu ki tō tākuta kia kitea ai te tino take, kia kore ai hoki he mate kino kē atu.
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