He nui ake tetahi taha o te tinana o tō pēpi i tetahi taha? (Hemihyperplasia) Me ako tātou mō tēnei!

Kua kite koe i tētahi taha o te tinana o tāu tamaiti, ahakoa he ringa, he waewae rānei, he taha rānei o tōna mata, he āhua nui ake i tētahi taha? I ētahi wā he iti rawa tēnei rerekētanga, kāore pea e kitea i te tīmatanga. Engari i te tipu haere o te tamaiti, ka kitea nuitia tēnei rerekētanga. I tēnei rā ka kōrero tātou mō tēnei āhuatanga.

He aha te Hemihyperplasia? Kia mārama tātou!

Ki te whakarapopoto, ko te hemihiperplasia te wā e tipu nui ake ai tetahi taha o te tinana i tetahi taha. I ētahi wā ka kiia tēnei ko te overgrowth syndrome , ā, i ētahi wā ko te hemihipertrophy . Ko te nuinga o te wā ka pā ki te mata, ki ngā ringa, ki ngā waewae rānei. Engari i ētahi wā ka pā hoki ki ngā whekau o roto i te puku. Whakaarohia he roa ake tetahi waewae i tetahi atu, he matotoru ake rānei tetahi ringa. I te tīmatanga, he tino ngawari pea tēnei rerekētanga, engari i te pakeke haere o te tamaiti, ka kitea nuitia.

Ko wai ka pāngia e tēnei mate? He pēhea te noa o tōna pānga?

He mate te hemihyperplasia e pā ana ki ngā tamariki . Ko tōna tikanga, kāore he rerekētanga i waenga i ngā tāne me ngā wāhine. He mate whānau mai tēnei, arā, ka whānau mai te tamaiti me tēnei mate. I ētahi wā ka kitea e ngā tākuta i te whānautanga mai. Engari i ētahi wā, kāore pea e kitea kia pakeke ake rā anō te tamaiti, kia kitea rā anō te rerekētanga i waenga i ngā taha e rua o te tinana.

He tino onge tēnei mate . Kua whakaatuhia e ngā rangahau ko te mate Beckwith-Wiedemann , te momo hemihyperplasia tino noa, ka puta i roto i te kotahi i roto i te 11,000 whānautanga. Nō reira, ka taea e koe te whakaaro he aha te onge o tēnei.

He aha te pānga o te hemihyperplasia ki te tamaiti?

Ko te pānga matua o tēnei mate ki te tamaiti ko te rerekētanga o te rahi o ngā wāhanga e rua o te tinana, e tika ana kia rite tonu. Hei tauira, tera pea tetahi taha o te mata e ahua nui ake ana i tetahi atu, arā, tera pea e ahua whanake ake ana.

Ko te mea nui, ko ngā tamariki he hemihyperplasia kei te nui ake te mōrearea ki te pāngia e te mate pukupuku . Ko tēnei mōrearea ko te Wilms tumor, he momo mate pukupuku tākihi, me te hepatoblastoma, he momo mate pukupuku ate o ngā tamariki. Ko te pikinga o te mōrearea o ēnei mate pukupuku nā te pānga o tēnei kore taurite o te tipu o te tinana ki ngā whekau o roto o te tamaiti.

Mena he hemihyperplasia tō tāu tamaiti, me tirotirohia ia mō te mate pukupuku mō te iti rawa i te 7 tau . Ko ēnei whakamātautau ko:

• Ngā tirotiro oro-oro o te puku: Ka tirohia e ēnei ngā tipu pēnei i te pukupuku.
• Ngā whakamātautau toto: Ka tirohia tēnei mō tētahi tohu pukupuku e kiia nei ko te alpha-fetoprotein . Ka taea e tēnei te whakaatu mēnā kei reira te mate pukupuku.

Tērā pea ka mataku koe ina rongo koe mō ēnei whakamātautau, engari ko te mōhio ki ēnei mea i mua i te wā, me te whakahaere tika i ngā whakamātautau, koinei te mea nui mō te hauora o tāu tamaiti.

He aha ngā tohu o te Hemihyperplasia?

Ko te tohu matua, ko te tohu tino kitea o tēnei mate, ko te nui haere o tētahi taha o te tinana i tētahi taha . I ētahi wā, he tino ngawari tēnei rerekētanga, engari ka kitea haere i roto i te wā.

Ko ētahi atu tohu (e pā ana ki te mate Beckwith-Wiedemann kua whakahuatia i mua) ko:

• He āhua kitakita kei ngā taringa.
• Ētahi hapa i roto i te pakitara o te puku.
• Te whakanui ake i ngā whekau o roto (ate, pancreas, whatukuhu).
• Arero nui.
• Te iti o te huka toto (hypoglycemia) .

Ahakoa kotahi, e rua rānei o ēnei tohu, ehara i te mea kei te pāngia tonutia te tamaiti, engari ki te pāngia ia e ēnei āhuatanga, he pai ake te toro atu ki te tākuta.

He aha te rerekētanga i waenga i te Hemihyperplasia me te Hemiatrophy?

Ka puta ngā panonitanga o te rahi o te tinana i ēnei āhuatanga e rua. Heoi, ko te hemiatrophy he āhuatanga kāore i te tino whanake tetahi taha o te tinana. Kotahi noa te wāhi o te tinana ka pā ki te hemiatrophy, pērā i ngā ringa. Ka pā pea te hemihyperplasia ki ngā wāhi maha o te tinana i te wā kotahi.

He aha ngā take o te hemihyperplasia?

I ētahi wā, ka puta te hemihyperplasia i te mate ira e kiia nei ko te mate Beckwith-Wiedemann . I ētahi atu wā, ka puta te mate me te kore he mate ira. I ēnei wā, kāore ngā tākuta e tino mōhio he aha te take. Mena kāore e pā ana ki te rerekētanga o te ira, he mate tūpono noa iho pea, arā, ka puta noa mai i te tūponotanga.

Me pēhea te tautuhi i te hemihyperplasia?

Kāore he whakamātautau motuhake hei tātaritanga i te hemihyperplasia. Mena ka kite te tākuta o tāu tamaiti i te tipu kore taurite i waenga i ngā wāhanga e rua o te tinana, ka whakahaerehia pea e ia he aromatawai tinana me te whakamātautau ira hei tirotiro mena kei a koe te mate Beckwith-Wiedemann . Ka taea e ēnei whakamātautau ira te āwhina i tō tākuta ki te whakatau mena he mate ira te take o te mate.

Waihoki, ka whakahaerehia pea e te tākuta o te tamaiti he ultrasound hei tirotiro i ngā āhuatanga rerekē, i ngā pukupuku rānei i roto i ngā whekau o roto.

He rongoā katoa tēnei mō tēnei? He aha ngā maimoatanga?

Kāore, kāore he rongoā mō te Hemihyperplasia. Kaua e manukanuka. Mā te tīma hauora o tāu tamaiti e whakawhanake he mahere maimoatanga e hāngai ana ki ōna hiahia, ā, e hangai ana ki ōna tohumate.

Ko te maimoatanga mō te hemihyperplasia i roto i te tamaiti e whakawhirinaki ana ki te whānuitanga o te rerekētanga i waenga i ngā taha e rua o te tinana. Tērā pea kei roto i te tīma hauora o tāu tamaiti ngā tohunga pēnei i:

• Tohunga mate ate: Mō ngā raruraru e pā ana ki te ate.
• Tohunga wheua: Mō ngā mea pēnei i te roa o te waewae.
• Tohunga Niho: Mō ngā raruraru e pā ana ki te whatukuhu.
• Kairangahau io: E pā ana ki te pūnaha io.
• Tākuta tamariki: Tirohia te hauora whānui me te whanaketanga o te tamaiti.
• Taote taote kirihou: I ētahi wā hei whakatika i ngā huringa o te āhua.

Ka mahi tahi ēnei tohunga katoa ki te whakawhanake i tētahi mahere maimoatanga mō tāu tamaiti, me te aroturuki hoki i ngā whekau i roto i te puku o tāu tamaiti. Nā te mea e hono ana te hemihyperplasia ki te pikinga ake o te mōrearea o te mate pukupuku, kei te rapu tonu ngā tākuta i ngā āhuatanga pēnei i te hepatoblastoma .

Me pokanga te tamaiti?

I ētahi wā ka taea e te pokanga te whakatika i ngā rerekētanga o te roa o ngā peka . He rerekē ngā momo pokanga mō tēnei. Mena ka tūtohu tō tīma hauora i te pokanga, kōrero ki a rātou mō te momo pokanga e pai ana mō tāu tamaiti. Tērā pea kei a tāu tamaiti ēnei:

• He pokanga hei whakaroa i te ringa/waewae poto.
• He pokanga e āta whakahaere ana i te tipu o te māhunga/ringa.

He raruraru, he pānga taha rānei kei te rongoā?

Mena ka pokangahia tāu tamaiti, tera pea ka ngenge ia mō ētahi wiki i a ia e ora ana. Tērā pea ka mamae anō hoki ia i te wāhi i tapahia ai. Pātai atu ki tō tākuta mō ētahi atu pānga taha o te pokanga motuhake a tāu tamaiti.

Kia pēhea te roa o te wā e ora ai i muri i te pokanga?

Ka rerekē te roa o te wā whakaora i runga i te momo pokanga kua mahia ki tāu tamaiti. Tērā pea ka pupuhi, ka mamae, ka ngoikore te tinana mō ētahi rā, wiki rānei i muri i te pokanga. Ki te kore koe e kite i tētahi whakapainga i roto i te wā, kōrero ki te tākuta o tāu tamaiti.

Ka taea te ārai i tēnei āhuatanga?

Kāore e taea te ārai i te hemihyperplasia, he āhuatanga e puta noa mai ana i te wā e hapu ana. Heoi, tera pea kei te pāngia tō pēpi e te mate Beckwith-Wiedemann.Nō reira, ki te mea he hemihyperplasia tōu, ā, e tumanako ana koe kia whānau mai anō he tamaiti, kōrero ki tō tākuta mō ngā whakamātautau ira . Ka taea e ēnei whakamātautau te āwhina ki te whakatau mēnā ka pāngia anō hoki ō tamariki e ēnei āhuatanga rerekē o te ira.

Mena he hītori tō kōrua, tō hoa rānei, o ngā mate ira, ā, kei te whakaaro koe kia whānau he tamaiti, he mea pai kia kōrero koe ki tētahi tākuta. Akene ka hiahia koe ki te whai whakaaro ki te tohutohu i mua i te haputanga .

He aha ngā mea ka tumanakohia e au mēnā he hemihyperplasia tāku tamaiti?

Mena kei a koe, kei tāu tamaiti rānei te hemihyperplasia, ka raru pea koe i te rahi koretake o ngā wāhanga tinana. Hei tauira, he uaua ki te kimi kākahu e tika ana te tau. Ko te rerekētanga o te roa o ngā waewae ka pā ki ngā mea pēnei i te ngokingoki, te hikoi, me te oma.

Waihoki, ki te kitea he hemihyperplasia, ko te tikanga me tirotiro tonu tāu tamaiti mō te mate pukupuku . Me tumanako ka mahia ēnei whakamātautau i ia torutoru marama tae noa ki te 7 tau te pakeke o tāu tamaiti.

He aha te tirohanga mō te hemihyperplasia?

He mate mō te wā roa te hemihyperplasia. Heoi, kua whakaatuhia e ngā rangahau mā te kitenga wawe me te tirotiro auau mō te mate pukupuku ka tino whakapai ake i te tirohanga . Ahakoa ka pāngia te tamaiti e te mate pukupuku mā te tirotiro auau, he nui ake te tūponotanga he pukupuku iti, ā, he wāhanga tōmua o te mate. Ko te tīmatanga o te maimoatanga wawe, ko te nui ake o te tūponotanga ka angitu.

Ka taea te noho roa i te roanga o te ora me te Hemihyperplasia?

He ora hauora te nuinga o ngā tamariki e pāngia ana e te hemihyperplasia, ā, he rite tonu te roa o te oranga ki ērā atu tamarikitanga. Ahakoa he mea nui kia tirotirohia mō te mate pukupuku i te wā tamarikitanga, ka heke haere te mōrearea o tēnei mate pukupuku i te taenga o te tamaiti ki te taiohitanga.

He aha ngā pātai me pātai atu e au ki te tākuta?

Mena he hemihyperplasia tō tāu tamaiti, tera pea he maha āu pātai. Mā te mōhio ki ngā whakautu ki ēnei pātai ka marino tō hinengaro, ā, ka āwhina i a koe ki te whakarite mō te heke mai. Pātai atu ki te tākuta, ki te nēhi rānei o tāu tamaiti pēnei i:

• He take ira te mate hemihyperplasia o taku tamaiti, he take tūpono rānei?
• He aha koe i tūtohu ai i tēnei maimoatanga, i tēnei pokanga rānei?
• Me aha ahau kia pai ai te noho o taku pēpi i mua atu, ā, i muri hoki i te pokanga?
• Kia pēhea te roa e noho ai te tamaiti ki te hōhipera?
• He aha te momo tapahi kei reira, mēnā he mea kei reira?
• Me whiwhi rongoā te tamaiti?
• He aha ngā mōrearea o te pokanga me te rongoā whakamoe mō te tamaiti?
• Kia pēhea te roa ka ora ai te tamaiti i muri i te pokanga?
• He aha ngā mea me tumanako atu ahau mō te hauora o taku tamaiti mō te wā roa?

Haunga ēnei pātai, kaua e wehi ki te pātai ki tō tākuta i ngā mea katoa kei roto i tō hinengaro.

Hei whakamutunga, he karere hei kawe ki te kāinga

Ko te hemihyperplasia, e mōhiotia ana ko te hemihipertrophy, ko te overgrowth syndrome rānei, he mate whānau e tipu ake ai tetahi taha o te tinana i tetahi taha. Kāore pea ēnei rerekētanga tipu e kitea i te whānautanga. Mēnā ka puta he kore taurite o te roa o ō rātou waewae, o te rahi rānei o te tinana o tāu tamaiti, kōrero ki tētahi tākuta tamariki. Nā te mea ka piki ake te mōrearea o te mate pukupuku i tēnei mate, he mea nui kia mōhio wawe koe ki te mate . Mā te kore e mataku, me te whiwhi i ngā tohutohu hauora me te maimoatanga e tika ana, ka taea e koe te āwhina i tāu tamaiti kia ora hauora.