Kua kite koe i tētahi wāhi pōuri, rite ki te mowhiti e karapoti ana i te karu o te kanohi o tētahi? Tērā pea kua kōrerotia tēnei e tētahi tākuta ki a koe. Tērā pea ētahi tāngata e mataku ana kei kino te tirohanga. Engari ehara tēnei i te mea e kino ai te kanohi. Heoi anō, he tohu nui pea tēnei mō tētahi atu mate kino kei roto i tō tātou tinana. I tēnei rā, me kōrero māmā noa iho tātou mō tēnei.
He aha ngā Mowhiti Kayser-Fleischer (mowhiti KF)?
He whakarāpopototanga noa iho, ko ngā mowhiti Kayser-Fleischer he mowhiti pouri e hangai ana ki te wāhanga tae o ō tātou kanohi, arā, te iris. Nā te nui rawa o te parahi i roto i ō tātou tinana e kohia ana i roto i te kanohi te take o ēnei mowhiti. Ka kitea pea he kakariki, he koura, he parauri rānei.
Ko te mea pai rawa atu, kāore ēnei mowhiti e kino ki tō tirohanga .
Ka tīmata tēnei mowhiti hei pewa i te taha whakarunga o te kanohi. Kātahi ka horapa haere, ka huri hei mowhiti kī tonu. Kei te hononga o te taha mā o te kanohi (sclera) me te taha mārama i runga ake i te taha tae o te kanohi (cornea) ēnei mowhiti.
Ko te mea nui, mō ngā tāngata o Sri Lanka he parauri pouri ō rātou kanohi, kāore e tino kitea ana ēnei mowhiti Kayser-Fleischer. Mō ngā tāngata he mārama ō rātou kanohi, he māmā ake te tautuhi i ēnei.
He aha te rerekētanga o ēnei i ētahi atu puku kanohi?
Tērā atu anō ngā āhuatanga ka puta ai ēnei momo porowhita kanohi. Nō reira, he mea tino nui kia wehewehea, kia mōhiotia hoki ēnei i a rātou anō. Kia tirohia tātou he aha ngā rerekētanga matua.
| Āhuatanga | Ngā Mowhiti Kayser-Fleischer | Ākau tawhito | Ngā Mowhiti Fleischer |
|---|---|---|---|
| Tae | Kakariki, koura, parauri (ngā tae pouri) | Tae mā-hina (tae mārama) | Tae kōwhai-parauri |
| Take | Te whakatakotoranga parahi | Te whakatakoto lipids | Te whakatakoto rino |
| Ngā mate e pā ana | Te mate a Wilson, te mate ate | Te nui o te cholesterol, te koroheketanga | Keratoconus - he kokiritanga o te kanohi he āhua kōne |
| Te tautuhi | Me whakahaere e te tākuta kanohi he whakamātautau rama-whiti. | E kitea ana e te kanohi tahanga. | Me tirotirohia ki tētahi karuārai motuhake (whakamātautau rama-pōturi). |
Hei tirotiro i ēnei mowhiti KF, ka whakamahia e te tākuta kanohi tētahi karuārai motuhake e kiia nei ko te whakamātautau rama-whiti . I ētahi wā, me whai whakamātautau hōhonu ake e kiia nei ko te gonioscopy . Ko te tikanga o tēnei ko te whakangoioi i te kanohi me te whakatakoto i tētahi karāhe motuhake ki runga i te kanohi.
He aha te tino take o ngā mowhiti Kayser-Fleischer?
Ko te mate a Wilson te tino take, ā, ko te tino take e kitea whānuitia ana mō tēnei .
He mate ira te mate a Wilson e nui ake ai te parahi i roto i te tinana i te mea e hiahiatia ana. I te nuinga o te wā, ka tangohia e te ate te parahi nui. Engari i roto i te tangata e pangia ana e te mate a Wilson, kāore taua tukanga e mahi tika. Kātahi ka tīmata te hanga o tēnei parahi i roto i te ate, te roro, ngā kanohi, me ētahi atu okana.
- Mate ate: Ka taea e te hanga parahi te kino i te ate, ā, ka pāngia hoki te ate e te mate ate.
- Ngā raruraru o te pūnaha io me te hinengaro: Ina tīmata te kohi o te parahi i roto i te roro, ka puta ake ngā tohu neurological me ngā raruraru hinengaro. Hei tauira:
- Ngā mate nekehanga pērā i te wiri o ngā peka me te uaua ki te hikoi
- Te uaua ki te kōrero
- Te manukanuka me te pouri
- Ngā huringa o te whanonga me te tuakiri
Whakaarohia, mai i te hunga whai tohu mate io nā te mate a WilsonKa kitea ēnei mowhiti KF i roto i te 95 o roto i te 100 tāngata. Ka kitea tēnei i roto i te 50% o te hunga he tohumate ate anake.
Ētahi atu take
Haunga te mate a Wilson, he maha atu anō ngā take o ngā mowhiti KF. He mate anō hoki ēnei e pā ana ki te ate.
- Te mate pūkahukahu tuatahi (PBC): He mate mau tonu tēnei e kino ai ngā awa pūkahukahu i roto i te ate.
- Te kōrekoretanga o te pēpi hou: Te ngoikore o te rere o te au i roto i te ate o ngā pēpi hou.
Me pēhea te rongoā mō tēnei?
Ko te mea nui me mārama tātou katoa ki konei , kāore ngā tākuta e rongoā i te mate pukupuku. Ka rongoā rātou i te mate hauora taketake i puta ai te mate pukupuku.
Te rongoā mō te mate a Wilson
E rua ngā whāinga matua o te maimoatanga.
1. Te tango i te parahi nui rawa atu i te tinana: Ka kiia tēnei ko te rongoā chelation parahi . Ko te tikanga ka hoatu he rongoā motuhake (ngā kaihoko chelating) hei here ki te parahi i roto i te tinana, ā, ka tangohia mā te mimi. Hei tauira, ko ngā rongoā pēnei i te penicillamine me te trientine.
2. Te whakaiti i te mimiti o te parahi mai i te kai: Ka mahia tēnei mā te hoatu i ngā tāpiringa konutea . Ka ārai te konutea i te mimiti o te parahi mai i ngā whekau ki roto i te tinana.
Te maimoatanga mō ētahi atu mate ate
Kāore e taea te whakaora katoa i ngā mate pēnei i te mate kōroke biliary tuatahi (PBC). Heoi, ka hoatu he rongoā hei whakahaere i ngā tohu me te ārai i te haere tonu o te mate. Mō te kōroke i roto i ngā pēpi hou, ka hoatu he miraka pēpi motuhake, he rongoā ārai-mākūkū, ā, i ngā wā tino kino, me mahi pea he pokanga whakawhitinga ate .
Kāore e taea e tātou te aukati i te hanganga o ēnei Mowhiti Kayser-Fleischer?
Kāore he huarahi hei ārai tika i te hanganga o ēnei mowhiti, nā te mea he tuku iho ngā mate pēnei i te mate a Wilson e hua ai ēnei, ā, kāore e taea te ārai.
Engari, ko te mea pai rawa atu ka taea e koe ko te tautuhi i te mate i te wā wawe .
Mena kei te pāngia tetahi o tō whānau tata, pērā i te whaea, te pāpā, teina rānei, e te mate a Wilson, he mea tino nui kia kōrero koe ki tō tākuta mō tēnei mea, kia whakamātauria hoki . Mā te kitenga wawe i a koe e āwhina ki te tīmata maimoatanga i mua i te puta mai o ngā tohu, me te ārai i ngā raruraru nui.
He mowhiti pumau ēnei?
Kāo, koinei te rongo pai rawa atu. Kāore ngā mowhiti Kayser-Fleischer e pumau . Ina rongoatia tika te mate pūtake, hei tauira te mate a Wilson, ka tangohia te parahi nui i roto i te tinana. Kātahi ka memeha haere ēnei mowhiti i roto i ngā kanohi, ka ngaro rawa atu .
Nō reira, kāore he take e wehi ai koe ki te kite i tēnei. Ko te mea nui ko te mōhio he tohumate tēnei, ā, ka tīmata wawe te rongoā i te mate taketake. Mēnā ka whakahuatia tēnei e te tākuta kanohi i a koe e tirotiro ana i tō kanohi, ka tukuna koe e ia ki tētahi tohunga tika mō ētahi atu maimoatanga.
Karere Tangohia ki te Kāinga
- Ehara ngā mowhiti Kayser-Fleischer i te mate kanohi, engari he tohu ā-waho o tētahi mate e takoto ana i raro (ko te mate a Wilson te nuinga) i puta mai i te nui rawa o te parahi i roto i te tinana.
- E kore ēnei mowhiti e kino ki ō tirohanga.
- Ka kitea tuatahitia ēnei ina tirohia ngā kanohi e te tākuta kanohi ki tētahi karuārai motuhake.
- Ka taea te whakakore katoa i ēnei mowhiti mā te maimoatanga tika o te mate pūtake.
- Mena kei te pāngia tetahi o tō whānau e te mate a Wilson, ahakoa kāore he tohu, he mea tino nui kia kite koe i tētahi tākuta me te kōrero mōna.











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