Mena ka whakaritea koe, tētahi rānei o tō whānau mō te pokanga, e mōhio ana koe he wāhanga noa o te tikanga te rongoā whakamoe. Ko te tikanga, ka whakamoea koe kia kore ai koe e mamae. Heoi, he tino onge te uruparenga a ētahi tāngata ki ētahi rongoā whakamoe, ā, ka mate pea rātou. I Nirogi Lanka, e hiahia ana mātou ki te kōrero mō tēnei mate kino, engari ka taea te rongoā, e mōhiotia ana ko te malignant hyperthermia .
He aha te Matū Whakawera Kino?
He whakarāpopototanga noa iho, he mate ira te mate hyperthermia kino . Ka tukuna iho i roto i ngā whānau. Mena kei a koe tēnei mate, ka kaha te urupare a tō tinana ina pāngia koe e ngā rongoā whakangote motuhake i te wā e pokanga ana. He āhuatanga ohorere hauora tēnei ka mate pea mēnā kāore e whakahaerea tonutia.
Ko te mea nui kia maumahara , ehara i te mea ko ngā rongoā whakamoe katoa ka puta ai tēnei tauhohenga. Ko tētahi rōpū rongoā motuhake anake ka puta ai. Hei tāpiri, ki te kitea wawetia, ka tino taea te rongoā.
Ko te nuinga o te iwi kāore i te mōhio kei a rātou tēnei whakarerekētanga ira nā te mea kāore e kitea he tohu i roto i te oranga o ia rā. Ka puta noa te raruraru ina uru mai ngā rongoā whakamoe motuhake ki roto i tō tinana.
Ko wai kei te mōrearea nui ake?
Ko te mōrearea e pā ana ki te hītori o tō whānau.
- Hītori Whānau: Mena kua pāngia tētahi whanaunga tata — pērā i te mātua, teina, teina rānei, te tamaiti rānei — e te mate pāwera kino, kei roto koe i te mōrearea. Me whakamōhio atu koe ki tō tākuta whakamoe mō tēnei hītori whānau i mua i tētahi pokanga.
- Ētahi mate uaua : Ahakoa kāore he hītori whānau, he nui ake te mōrearea o te hunga whai mate uaua onge, tae atu ki:
- Te mate matua o te pokapū
- Mate maha-minicore
- Te mate King-Denborough
- Mate STAC3
He onge ēnei mate, engari ki te mea kua tautuhia koe, tētahi mema rānei o te whānau kua pāngia e tētahi, he mea nui kia kōrerohia tēnei ki tō tīma hauora.
He Pēhea te Noa o te Mea?
He onge te hyperthermia kino. E ai ki ngā tatauranga, tata ki te 1 i roto i te 100,000 pokanga pakeke ka puta. He nui ake te kitea i roto i ngā tamariki, ā, tata ki te 1 i roto i te 30,000 pokanga ka pāngia. He mea nui, ko te haurua o ngā take katoa kua tautuhia ka puta i roto i ngā tāngata kei raro iho i te 19 tau te pakeke.
Heoi, e whakapono ana ngā tohunga he tokomaha atu pea te hunga e mau ana i te mate ira me te kore e mōhio. Nā te mea ka noho puku tonu te mate mena kāore e whakamahia aua rongoā, he maha ngā kaikawe ka noho tonu i roto i ō rātou oranga katoa me te kore e pāngia e te tauhohenga.
He aha ngā tohu?
Ka puta pea ngā tohu i te wā pokanga, i muri tata mai rānei i te rūma whakaora. Nā te mea kei raro koe i te rongoā whakamoe, kāore koe e rongo i ēnei tohu. Heoi, ka kitea tonutia e tō tākuta whakamoe. Ka aro turukihia e rātou ō tohu ora puta noa i te tukanga katoa, ā, ka tīmata i te maimoatanga whakaora ora i te wā tonu ka puta mai ai ēnei tohu.
| Ngā Tohu Tūatahi | Ngā Tohu Kino o Muri Mai |
|---|---|
| Te pikinga ohorere o te tere o te ngakau (tachycardia) , kāore i te mārama. | Te pāmahana tinana tino tiketike. |
| Te pikinga ohorere o ngā taumata o te hauhā waro (CO2). | He mimi pouri (parauri, mangu rānei). |
| Te tere o te manawa (tachypnea) . | Ngā whakamātautau toto e whakaatu ana i ngā tohu o te pakaru o te uaua. |
| Te pakari o te uaua, te pūmau rānei. | Ngā rerekētanga o te manawa o te ngakau (arrhythmia) . |
| Te pikinga tere o te pāmahana tinana. | Te toto kore e taea te whakahaere. |
| Ngā hopukanga. |
He aha te take o tēnei?
Mō te hunga e pāngia ana e te hyperthermia kino, ka puta he whakarerekētanga ira e pā ana ki ētahi pūmua i roto i ngā pūtau uaua.
Whakaarohia ō pūtau uaua he "kūaha" e whakahaere ana i te tukunga o te konupūmā kua rongoatia. Mō te nuinga o te tangata, ka taea e ngā rongoā whakamoe te mahi i tēnei kūaha kia rite ki te tikanga.
Heoi, mō te hunga whai whakarerekētanga ira pēnei, ka mahi ngā rongoā whakamoe motuhake pērā i te kēti pakaru, ka puta he waipuke ohorere, kore whakahaere o te konupūmā ki roto i ngā pūtau uaua.
Ka pāngia ngā uaua e te uaua kore e taea te whakahaere, ka whakapakeke, ka tere haere te pākia o te tinana, ā, ka piki ake te pāmahana o te tinana. Ā tōna wā, ka pakaru ngā pūtau uaua, ka tukuna ngā matū pēnei i te pāhare pāporo ki roto i te toto, ka puta ai ngā tohu kino kua whakahuatia ake nei.
Ko ēhea rongoā ka whakaoho i tēnei tauhohenga?
E rua ngā momo rongoā matua e whakaoho ana i tēnei tauhohenga:
- Ngā hau rongoā whakangā:
- Halothane
- Te waikura
- Sevoflurane
- Isoflurane
- Ngā rongoā ā-roto-uaua:
- Succinylcholine (he rongoā whakangāwari uaua tere)
Me pēhea te tautuhi me te whakaū?
Te tautuhi i te wā o te pokanga
He maha ngā wā, ka kitea noa tēnei āhuatanga i te wā pokanga. Mēnā kāore koe i te mōhio kei a koe tēnei āhuatanga, ka mōhio anō hoki tō tākuta whakamoe. Heoi, nā te mea ka aroturuki tonu rātou i a koe puta noa i te tukanga, kua whakangungua rātou ki te whakapae tonu i te Malignant Hyperthermia mēnā ka kite rātou i ēnei tohu e whai ake nei:
- He pikinga ake o te tere o te manawa kāore i te māramahia.
- Te pikinga tere o te pāmahana tinana .
- Te pikinga ake o te hauhā waro e tukuna ana.
- Te pakari o te uaua.
Kua whakangungua ngā tohunga whakamoe kia kite wawe i ēnei huringa, kia taea ai e rātou te tīmata tonu i te maimoatanga whakaora ora.
Ka taea e au te kimi mēnā kei roto ahau i te mōrearea i mua?
Mena kei te whakapae koe kei roto koe i te mōrearea nā te hītori hauora o tō whānau, kei reira ngā whakamātautau motuhake hei whakaū i tēnei.
- Whakamātautau Whakawhanaungatanga Kawheine-Halothane (CHCT): Ko te tikanga o tēnei ko te tango i tētahi tauira iti o tō uaua (koiora uaua) ka whakaaturia ki te hau halothane me te kawheine i roto i te taiwhanga. Mā te tirotiro i te tauhohenga o te kiko uaua, ka taea e ngā tākuta te whakatau mēnā he mate pāwera koe ki tēnei mate.
- Whakamātautau Ira: Ka taea e te whakamātautau toto te tautuhi i ngā whakarerekētanga ira motuhake e hono ana ki te Malignant Hyperthermia (pēnei i a RYR1, STAC3, CACNA1S rānei).
Heoi, he nui te utu mō ēnei whakamātautau, ā, kāore e wātea ana i ngā whare hauora katoa. Mena kei a koe tētahi hītori whānau mō tēnei mate, e kore ngā tākuta e tatari mō ngā hua o te whakamātautau; engari, ka whakamahia e rātou ngā rongoā whakangote haumaru e kore e whakaoho i tēnei tauhohenga .
Me pēhea te rongoā?
Ko te rongoā whakaora ora matua e whakamahia ana hei rongoā i te mate wera nui ko te dantrolene .
Ina whakapae te tohunga whakamoe i tēnei mate, ka tukuna e rātou tēnei rongoā mā te uaua. I te wā kotahi, ka:
- Kati tonu te hoatutanga o te rongoā whakamoe.
- Whakamōhio atu ki te taote pokanga, ā, kia tere tonu te whakamutu i te pokanga.
- Hoatu he wai matao ki roto i te uaua o te tinana , ā, whakamahia ngā tikanga whakamatao o waho pērā i ngā putea hukapapa hei whakaheke i te pāmahana o roto o tō tinana.
- Whakaratohia he tautoko hāora.
- Whakaorahia ngā arrhythmias o te ngākau.
Kia tau te āhua, ka tirotirohia koe i te Wāhanga Tiaki Kaha (ICU) mō te 24 hāora te iti rawa, ka whakahaerehia e te tīma hauora ngā whakamātautau toto me te whakarato i ngā tiaki whai muri e tika ana.
He aha te tirohanga whakamua, ā, he aha ngā raruraru ka puta?
Ki te kitea wawetia e te tīma hauora te mate, ā, ka tukuna he maimoatanga tika, he tino tūponotanga ka ora katoa.
Heoi, ahakoa te tere o te maimoatanga, he mate kino tonu tēnei, ā, ka taea pea te arahi atu ki te ngoikore o ngā okana maha, te mate rānei.
Ko ngā raruraru pea ko:
- Te pakaru o te uaua.
- Te ngoikore o te whatukuhu.
- Te ngoikore o te ate.
- Ngā mate toto.
- Te hopukanga o te ngākau.
- Ngā hopukanga.
- Koma.
- Te mate.
Ki te kore e rongoatia, ka mate te tangata i te mate kino (Malignant Hyperthermia). Ahakoa te maimoatanga pai rawa atu, e kiia ana ko te reiti mate kei waenga i te 3% me te 5%.
Ka taea te ārai?
Ae, ka taea! Ko te huarahi tino whai hua ki te ārai i tēnei mate ko te whakarite kia mōhio katoa koe me tō tīma hauora ki tō āhua mōrearea.
Ki te mōhio koe kei a koe tētahi whakarerekētanga ira e tika ana, ki te mea rānei kua pāngia tētahi mema o te whānau e tēnei mate, me whakamōhio koe ki tō tākuta whakamoe i mua i te pokanga. Kātahi ka whakamahia e rātou ngā rongoā haumaru, rerekē hoki kāore e whakaoho i te tauhohenga , ā, ka ārai i te raruraru kei puta.
He tokomaha ngā tāngata ka kitea kei roto rātou i te mōrearea i muri i te pāngia e tētahi tauhohenga. Koia te take he mea nui kia mārama ki tō hītori hauora whānau.
Karere Tangohia ki te Kāinga
- He tauhohenga onge, tuku iho, ā, he kino te hyperthermia kino ki ētahi rongoā whakangā.
- Ehara i te mate pāwera; he mate ira.
- Ko te mahi tino nui ka taea e koe te mahi ko te whakamōhio atu ki tō tākuta me te tohunga whakamoe i mua i te pokanga mēnā kua pāngia tētahi o te whānau e tētahi raruraru e pā ana ki te whakamoe.
- Ina mōhio ngā tohunga hauora ki tō mōrearea, ka taea e rātou te whakamahi i ngā rongoā haumaru hei ārai katoa i tēnei tauhohenga.
- Ahakoa he mate kino tēnei, he tino ngāwari te rongoā mēnā ka tere te tautuhi. Kia mōhio, kia kaha hoki, kaua e mataku.
Te Hiperthermia Kino, te rongoā whakamoe, te pokanga, te tauhohenga rongoā whakamoe, te mate ira, te dantrolene, te hītori whānau, te haumaru o te pokanga, ngā raruraru rongoā whakamoe, ngā mate ira
