Me ako tātou mō te Malignant Hyperthermia, he tauhohenga morearea ki te rongoā whakamoe i te wā e pokanga ana.

Ki te mea me pokanga koe, tetahi rānei o tō whānau, ka hoatu he rongoā whakamoe i mua i te pokanga, tika? He kupu ngāwari, ka meinga tātou kia moe rawa. Engari mō ētahi tāngata, ko ētahi o ngā rongoā e whakamahia ana mō tēnei rongoā whakamoe ka puta he tauhohenga kino rawa atu, tae atu ki te mate. I tēnei rā kei te kōrero tātou mō te mate wera nui , he mate morearea engari ka taea te rongoā mēnā ka kitea wawe.

He aha te Matū Whakawera Kino?

He kupu ngāwari noa iho, he mate ira te Malignant Hyperthermia. Ko te tikanga he mate tuku iho. Ina pāngia te tangata whai mate nei e ētahi momo rongoā whakamoe i te wā pokanga, ka tino kaha te tauhohenga a tōna tinana. He āhuatanga ohorere tēnei e morearea ana ki te ora. Engari ko te mea nui i konei , kāore tēnei e tupu ki ngā rongoā katoa e whakamahia ana mō te rongoā whakamoe i te wā pokanga. He iti noa iho ngā rongoā ka puta ai tēnei tauhohenga. Heoi anō, ki te kitea, ka taea te rongoā wawe. I te nuinga o te wā, kāore te tangata e mōhio kei a ia he whakarerekētanga ira e pā ana ki tēnei i roto i tōna tinana. Nā te mea kāore rātou e whakaatu i ngā tohu i te oranga noa. Ka puta noa te raruraru ina uru taua rongoā whakamoe ki te tinana.

Ko wai te mea nui ake te mōrearea?

Ka kitea tēnei mōrearea mēnā he mate tēnei kei tētahi o te whānau.

• Hītori whānau: Mena kua pāngia tētahi o ō whanaunga tata - he whaea, he pāpā, he tungāne, he tuahine, he tamaiti rānei - e te mate pāwera kino, ka nui ake tō tūponotanga. Nō reira, ki te pokanga koe, he mea nui kia kōrero koe ki te tohunga whakamoe mō tēnei hītori whānau .
• Ngā mate uaua : Ahakoa kāore tētahi o tō whānau i pāngia e tēnei raruraru, he nui ake te mōrearea o te hunga whai mate uaua onge. Hei tauira:
• Te mate matua o te pokapū
• Mate maha-minicore
• Te mate King-Denborough
• Mate STAC3

He tino onge ēnei mate, engari ki te pāngia koe, tētahi rānei o tō whānau e tētahi, he mea nui kia mōhio koe ki tō tākuta.

He pēhea te noa o tēnei āhuatanga?

Ehara tēnei i te mate tino noa. E ai ki ngā tatauranga, ka puta tēnei mate i roto i te kotahi i roto i te 100,000 pokanga i roto i ngā pakeke. I roto i ngā tamariki nohinohi, he paku teitei ake tēnei tau, arā, kotahi i roto i te 30,000 pokanga. He mea nui hoki kia mōhiotia ko te haurua o ngā tūroro kua tautuhia kei raro iho i te 19 tau te pakeke. Heoi, e whakaaro ana ngā kaipūtaiao he nui ake te kitea o te hunga whai ira ki tēnei mate i roto i te hapori. Nā te mea, ahakoa kei a rātou te ira, ki te kore rātou e pāngia e ngā rongoā whakangote e puta ai taua tauhohenga puta noa i ō rātou oranga, e kore rawa tēnei mate e puta.

He aha ngā tohu o tēnei?

Ka puta pea ēnei tohu i te wā pokanga, i muri tata mai rānei i te pokanga i a koe e ora ana. Mena kei a koe ēnei tohu i a koe e moe ana, ā, kei raro i te mate whakamoe, kāore koe e rongo i aua tohu. Engari ka kitea e tō tākuta whakamoe. Ka aro turukihia e rātou ō tohu ora puta noa i te pokanga. Nō reira, ka tīmata tonu rātou i te maimoatanga ina kite rātou i ēnei tohu.

He aha tēnei e tupu nei? He aha te take?

Ko te hunga e pāngia ana e te Malignant Hyperthermia, he huringa ira kei roto i ētahi pūmua o ō rātou pūtau uaua. Whakaarohia kei roto i ō tātou pūtau uaua he konupūmā kei roto. Ko te tukunga o tēnei konupūmā ka whakahaeretia e tētahi mea pērā i te kēti. Ina hoatu he rongoā whakangote ki te tangata noa, ka mahi tēnei kēti i roto i te āhua whakahaeretia. Ka pāngia, ka whakawhāitihia hoki ngā uaua e tēnei, ka tere ake te pākia o te tinana, ā, ka piki kino te pāmahana o te tinana. Ā tōna wā, ka mate ngā pūtau uaua, ā, ka kohia he nui ngā matū pēnei i te pāhare pāporo ki roto i te toto. Ka puta mai ētahi atu tohu kino nā ēnei take.

He aha ngā rongoā ka puta ai tēnei tauhohenga?

E rua ngā rōpū rongoā te nuinga o te wā e hua mai ai tēnei āhuatanga.

• Ngā rongoā whakangote manawa:
• Halothane
• Te waikura
• Sevoflurane
• Isoflurane
• Ngā rongoā ā-roto-uaua:
• Succinylcholine (he rongoā whakangāwari uaua tere tēnei)

Me pēhea e tautuhi ai, e whakaū ai hoki i tēnei?

Te kitenga i te wā o te pokanga

He maha ngā wā ka kitea tēnei mate i te wā pokanga. Mēnā kāore koe i te mōhio kei a koe tēnei mate, kāore hoki tō tākuta whakamoe e mōhio. Engari ka aroturukihia koe e ia puta noa i te pokanga, ā, ka whakapae pea ia kei te pāngia koe e te mate pāwera kino mēnā ka kite ia i ēnei huringa e whai ake nei:

• Te pikinga ake o te tere o te ngakau , kāore he take.
• Te pikinga tere o te pāmahana tinana .
• Te nui haere o te hauhā waro e tukuna ana.
• Te pakari o te uaua.

Kua whakangungua ngā tohunga whakamoe kia tere te kite i ēnei huringa, kia taea ai e rātou te tīmata wawe i te maimoatanga.

Ka taea te mōhio i mua i te wā mēnā he mōrearea kei reira?

Mena kei te whakapae koe kei a koe tēnei mōrearea nā te hītori o tō whānau, he maha ngā whakamātautau motuhake hei whakaū.

• Whakamātautau Whakawhanaungatanga Halothane Kawheine (CHCT): Ko te tikanga o tēnei ko te tango i tētahi wāhanga iti rawa o tō uaua (koiora uaua) ka whakaaturia ki te hau halothane me te kawheine i roto i te taiwhanga. Ka taea te whakamahi i te āhua o te tauhohenga o te wāhanga uaua hei whakatau mēnā kei te pāngia koe e tēnei mate.
• Whakamātautau ira: Mā tēnei whakamātautau, e tangohia ai he tauira toto, ka taea te kite i ngā whakarerekētanga ira (hei tauira, RYR1, STAC3, CACNA1S) e pā ana ki te Malignant Hyperthermia.

Engari he utu nui ēnei whakamātautau, ā, kāore e wātea ana i ngā wāhi katoa o Sri Lanka. Nō reira, ki te hiahia koe ki te pokanga ohorere, ā, kei roto i tō whānau tēnei mate, e kore ngā tākuta e tatari mō ngā whakamātautau , ā, ka whakamahia noa e rātou ngā rongoā whakamoe haumaru e kore e puta ai tēnei tauhohenga ki a koe.

Me pēhea te rongoā?

Ko te rongoā matua, me te rongoā whakaora ora e hoatu ana mēnā ka pāngia koe e te hyperthermia kino, ko te dantrolene . Ina whakapae te tohunga whakamoe i tēnei āhuatanga, ka tukuna tonutia tēnei rongoā mā te uaua. I taua wā anō,

• Ka mutu tonu te rongoā whakamoe e hua ai te tauhohenga.
• Ka whakamōhiotia te taote pokanga, ā, ka oti wawe tonu te pokanga.
• Hei whakaiti i te pāmahana tinana tiketike , ka tukuna he wai matao IV ki roto i ngā uaua, ā, ka whakamataohia te tinana ki ngā mea pēnei i ngā kete hukapapa.
• E whakarato ana i te hāora.
• He rongoā mō ngā mate manawa o te ngākau.

Kia oti te āhua te whakahaere, ka puritia koe ki te wāhanga tiaki nui (ICU) mō te iti rawa i te rā kotahi, ka tirotirohia koe e te tīma hauora. I tēnei wā, ka whakahaerehia e rātou ētahi atu whakamātautau toto, ā, ka tukuna atu he maimoatanga tāpiri mēnā e tika ana.

Ka pēhea te āhua o te āhuatanga? He aha ngā raruraru?

Ki te tere te tātaritanga a te tīma hauora i tēnei mate, ā, ki te tika hoki te rongoā, ka taea te ora katoa. Ko ngā raruraru ka puta mai i tēnei ko:

• Te pakaru o te uaua.
• Te ngoikore o te whatukuhu.
• Te ngoikore o te ate.
• Te toto.
• Te hopukanga o te ngākau.
• Ngā hopukanga.
• E taka ana ki te koma.
• Te mate.

He mate te mate wera nui kino e mate ai te tangata mēnā kāore e rongoatia. Ahakoa te maimoatanga tika, kei waenga i te 3% me te 5% te auau mate.

Ka taea te ārai i tēnei?

Āe, ka taea te ārai! Ko te huarahi pai ki te mahi i tēnei ko te mōhio ki tō mōrearea ki a koe anō me tō tākuta. Mena kei te mōhio koe he whakarerekētanga ira tōu e pā ana ki tēnei, ki te mōhio rānei koe kei te pāngia tētahi o tō whānau e tēnei mate, me kōrero koe ki te tohunga whakamoe i mua i te pokanga. Kātahi ka hoatu e ia he whakamoe ki a koe, ka whakamahia e ia ngā rongoā tino haumaru hei utu mō aua rongoā mōrearea. Kātahi ka kore taua tauhohenga mōrearea e puta. He tokomaha te hunga ka kitea kei a rātou tēnei mōrearea i muri i te pānga ki a rātou. Koia te mea nui kia mōhio koe ki tō hītori hauora whānau. Te Hiperthermia Kino, te rongoā whakamoe, te pokanga, te tauhohenga rongoā whakamoe, te mate ira, te dantrolene, te hītori whānau, te haumaru o te pokanga, ngā raruraru rongoā whakamoe, ngā mate ira