Kāore pea koe i rongo i te kupu 'Medullary Sponge Kidney' i mua. Ahakoa he uaua ki te whakaahua, he mate whānau tonu tēnei e pā ana ki ngā whatukuhu. He māmā noa iho, koinei te wāhi e puta ai ngā mirumiru wai iti, e kiia nei ko ngā cysts, i roto i ō whatukuhu, inā koa i waenganui o ngā whatukuhu (medulla). Me kōrero taipitopito tātou mō tēnei i tēnei rā, e tika ana?
He aha rawa te Medullary Sponge Kidney?
Kia titiro tuatahi tātou ki ngā whatukuhu me ā rātou mahi. E mōhio ana koe, he wāhanga tino nui ngā whatukuhu o te pūnaha mimi i roto i tō tātou tinana. He wāhanga waenga kei ia whatukuhu, e kiia nei ko te medulla. He awa tino angiangi tēnei medulla e kiia nei ko ngā ngongo iti. Ka kohia e ēnei awa ngā para kua tātarihia mai i te toto, ā, ka hangaia he mimi. Kātahi ka honoa ēnei awa, ka hono atu ki ngā awa nui ake e kiia nei ko ngā awa kohikohi. Mai i ēnei, ka haere te mimi ki te pūwāhi kohikohi matua i waenganui o te whatukuhu, te pelvis whatukuhu. Mai i reira, ka haere te mimi mā roto i ngā ureter ki te pūkahukahu, kātahi mā roto i te urethra ki te wehe atu i te tinana.
Āe, ko te mea ka pā ki te tangata e pāngia ana e te 'Medullary Sponge Kidney', ko te whakawhanaketanga o ngā putunga kohi i kōrerotia e au he pūwero iti, ā, ka pupuhi aua putunga, ka nui haere. He rite ki te hautai te āhua. Koia i huaina ai ko te 'Sponge Kidney'. I te nuinga o te wā ka pā tēnei mate ki ngā whatukuhu e rua, engari i ētahi wā ka pā ki te whatukuhu kotahi anake.
Me pēhea te whanaketanga o tēnei mate whatukuhu hautai medullary?
He pātai tāu inaianei mō te aha ka puta ina puta ēnei pūwero. Ina puta ēnei pūwero, kāore e taea e aua awa pai (ngā ngongo) te mahi tika. Kātahi ka tīmata ngā mea pēnei i te konupūmā ki te whakatakoto ki roto i ēnei awa. Ka kiia tēnei ko te (nephrocalcinosis). Ehara i te mea ko te konupūmā anake, engari ko ētahi atu mea pēnei i te phosphate me te oxalate ka taea hoki te kohikohi pēnei. I roto i te wā, ka piri tahi ēnei mea kua kohikohia, ka hanga he kōhatu tākihi .
Ka ārai hoki ēnei whēte me ngā kōhatu i te rere o te mimi mā te ara mimi, ka piki ake te mōrearea o ngā mate urutā ara mimi (UTI) .
He aha te rerekētanga i waenga i tēnei me te Mate Tākihi Polycystic?
Kua rongo pea koe i te mate whatukuhu polycystic (PKD). He mate anō hoki tēnei e puta ai ngā pūkahukahu i roto i ngā whatukuhu. Nō reira, he aha te rerekētanga i waenganui i ngā mea e rua?
Ko te mate tākihi polycystic (PKD) he mate ira e tuku iho ana i te nuinga o te wā. Ka whakanuia ngā tākihi e ia, ka puta he maha ngā whēkau puta noa i te tinana. I ētahi wā ka arahi pea te PKD ki ngā raruraru nui.Ka pā mai pea ngā raruraru mō te wā roa. He maha ngā tāngata whai PKD ka pāngia e te ngoikore o te whatukuhu, ā, me whakamahi i te dialysis hei pure i ō rātou toto.
Heoi, he tino onge te ngoikore o te whatukuhu i roto i te hunga e pāngia ana e te medullary sponge kidney (MSK). Koinei te rerekētanga matua.
Ko wai te hunga e tino pāngia ana e tēnei mate? He pēhea te noa o tōna pānga?
E whakaarohia ana i tēnei wā ka puta noa mai tēnei mate "medullary sponge kidney (MSK)". Arā, kāore he take motuhake. Heoi, nā te mea kei roto i ētahi whānau, tera pea he tūponotanga o te tukunga iho. Heoi, kāore anō kia kitea he tauira ira mārama mōna.
Ko te nuinga o te tangata ka mōhio kei a rātou te mate i muri i te putanga mai o ngā tohu, i te nuinga o te wā i roto i ō rātou tau 20. E kiia ana hoki he paku nui ake te mōrearea o ngā wāhine i ngā tāne .
He tino noa tēnei, ā, kotahi i roto i te 5,000 tāngata te toharite e pāngia ana e te MSK. Heoi, he nui ake te kitea i roto i te hunga he kōhatu tākihi tō rātou. Ko te tikanga tēnei kei waenganui i te 12% me te 20% o ēnei tāngata ka pāngia e te MSK.
Ka puta te toto toto tiketike i te whatukuhu hautai waenga?
Tērā pea ētahi e whakaaro ana mēnā ko tēnei "MSK" te take o te toto toto tiketike, te toto toto rānei. E ai ki ngā rangahau o nāianei, kāore he taunakitanga e kī ana ko te "takahiki hautai medullary" te take o te toto toto tiketike.
He aha te take o te whatukuhu hautai medullary?
Kāore anō kia tino mōhiotia e ngā tākuta he aha i pāngia ai ētahi tāngata e tēnei mate. E whakaarohia ana nā te raruraru o te whanaketanga o te whatukuhu i te wā e hapu ana, i te wā kei roto tonu te pēpi i te kōpū .
He aha ngā tohu o tēnei mate?
He mea whakamiharo, he tokomaha ngā tāngata e pāngia ana e te Medullary Sponge Kidney (MSK) kāore e pāngia e tetahi tohu . Ko te tikanga o tēnei ka ora tonu rātou me te kore e mōhio kei a rātou te mate. He iti noa iho te ōrau, tata ki te 10%, ka pāngia e ngā tohu.
Ki te puta ēnei tohu, he hononga tēnei ki ngā mate mimi (UTI) me ngā kōhatu tākihi. Koinei ngā tohu matua:
- Te toto i roto i te mimi (hematuria): Ko te tikanga ka whero pea te mimi, i ētahi wā ka rite ki te tae o te wai tī.
- Mamae taha: Ka puta te mamae i ngā taha e rua o tō tuara, i raro i tō rara.
- Mamae i te mimi (dysuria): Tērā pea ka pā te wera me te mamae i te mimi.
- Ngā kōhatu whatukuhu: He mea tēnei kua pā ki te tini o te tangata. Ka puta mai pea me te mamae nui o te tuara.
- Ngā mate urutā o te ara mimi: Tērā pea ka puta ngā tohu pēnei i te mimi pinepine me te kirika.
Me pēhea te tātaritanga o te whatukuhu hautai medullary?
Mena kei a koe ēnei tohu, ka tirotirohia e tō tākuta tō tinana i te tuatahi. Ka pātai atu rātou mō tō hītori hauora, tō hītori whānau, me ngā tohu katoa e pā ana ki a koe.
Ki te whakapae tō tākuta he mate tākihi tōu, tera pea ka tonoa e rātou ētahi whakamātautau toto me te mimi . Ka tirohia ēnei:
- He toto kei roto i te mimi?
- Me pēhea te mahi a ngā whatukuhu?
- He mate mimi kei te pā mai?
Hei tāpiritanga, ka taea te whakahaere i ngā whakamātautau whakaahua motuhake hei tirotiro i ngā whēkau i whakahuatia ake nei e au. Ko ngā momo matawai e tino kitea ana ko:
- Matawai CT: Ka whakamahia ngā hihi-X hei whakaputa i tētahi whakaahua toru-ahu (3D) o ngā whatukuhu.
- Pyelogram Ā-roto (IVP): Ko te werohanga i tētahi tae motuhake ki roto i tō uaua. Kātahi ka tangohia ētahi whakaahua hihi-X. Ka tātarihia te tae mā roto i te toto mai i ngā whatukuhu ki roto i te mimi, kia mārama ai te whakaatu a ngā whakaahua hihi-X i te ara o te mimi. Ka āwhina tēnei ki te kimi i ngā pūwero me ngā wāhi kua āraia te mimi.
- Matawai Ultrasound: Ka whakamahia ngā ngaru oro hei tango pikitia o ngā whatukuhu.
Me pēhea te rongoā i te whatukuhu hautai medullary?
Kāore he rongoā motuhake mō te mate e mōhiotia ana ko te medullary sponge kidney (MSK) i tēnei wā . Ko te whāinga matua o te rongoā ko te whakahaere me te rongoā i ngā mate mimi (UTI) me ngā kōhatu tākihi.
Ko te rongoā matua mō ngā mate mimi ko ngā paturopi .
Ko te maimoatanga mō ngā kōhatu whatukuhu e whakawhirinaki ana ki te rahi o te kōhatu. Ko ngā kōhatu iti ka puta noa i te mimi. Tērā pea ka kī atu tō tākuta kia nui ake te wai e inumia e koe hei āwhina i te kōhatu kia tere ake te puta. Tērā pea ka tohua e ia he rongoā whakamamae me ngā rongoā hei whakangāwari i ngā uaua o ō ureter.
Tērā pea me nui ake te maimoatanga mō ngā kōhatu nunui . Anei ētahi tauira:
- Te Whakaora Ngaru Whakaoho: He maimoatanga kore-whakaeke tēnei e whakamahi ana i ngā ngaru whakaoho kaha-nui hei wawahi i ngā kōhatu whatukuhu. Kātahi ka tukuna ngā wahi pakaru ki waho o te tinana i roto i te mimi.
- Ureteroscopy: Ko te whakamahi i tētahi ngongo roa, angiangi e kiia nei ko te ureteroscope hei tirotiro i te wāhi kei reira te kōhatu. Ka taea te whakamahi i tēnei taputapu hei tango i ngā kōhatu iti, ka taea rānei te whakamahi i te laser hei wawahi i ngā kōhatu nunui.
- Te Nephrolithotomy ā-kiri:Ka whakamahia tēnei tikanga e ngā tākuta ina kore e angitu ētahi atu tikanga. Ko te tikanga o tēnei ko te tapahi i te tuara, te kuru i te kōhatu whatukuhu mā roto, kātahi ka tangohia mai. He pokanga iti rawa te whakaekenga tēnei.
Ka taea te ārai i te whatukuhu hautai medullary?
He mate whānau te whatukuhu pūkahukahu (MSK) kāore e mōhiotia te pūtake, nō reira kāore e taea te ārai . Heoi, ka taea e koe te mahi i ngā mahi hei ārai i ngā mate mimi (UTI) me ngā kōhatu whatukuhu ka puta mai i tēnei.
Ka tohua pea e tō tākuta ngā rongoā pēnei i ēnei:
- Ngā paturopi horopeta iti hei ārai i ngā mate urutā mimi e hokihoki mai ana.
- Ka taea e ngā rongoā pēnei i te potassium citrate , te thiazide rānei (e mōhiotia ana ko ngā pire wai) te whakaiti i ngā taumata konupūmā i roto i te mimi me te ārai i te hanganga o ngā kōhatu tākihi.
Mā te whakarerekē i tō kai ka āwhina i te ārai i ngā mate mimi me ngā kohatu tākihi:
- Konupūmā: Mā te kai i te nui o te konupūmā ka āwhina i te whakaiti i te mōrearea o ngā kōhatu whatukuhu. (Tērā pea ka whakaaro ētahi tāngata mā te nui rawa o te konupūmā ka piki ake te mōrearea o ngā kōhatu, engari ehara i te mea pērā. Me kai noa iho. Whakawhitiwhiti kōrero ki tō tākuta.)
- Wai: He mea tino nui te inu i te nui o te wai . Ka waimeha te mimi, ka whakaiti hoki i te tūponotanga o te hanganga kōhatu. Ka āwhina hoki ki te tango i ngā huakita i roto i ngā whatukuhu. Ngana ki te inu i te iti rawa 2-3 rita wai i te rā.
- Ngā kai pūmua nui: Mā te whakawhāiti i ngā kai pūmua nui pērā i te mīti, te ika, me ngā hua manu ka āwhina i te ārai i ngā kōhatu tākihi.
- Tote: He mea nui anō hoki te whakaiti i te tote i roto i tāu kai. Mā te kai nui rawa i te tote ka nui ake te tūponotanga o te mate kōhatu whatukuhu. Nō reira, kia tūpato ki te nui o te tote ka tāpirihia e koe ki tāu kai. He nui te tote i roto i ngā mea pēnei i ngā kai kēne me ngā nūru inamata.
He mea nui: Me kōrero tonu ki tō tākuta, ki te tohunga kai rānei i mua i te whakarerekē i tō kai.
He aha te heke mai mō te tangata e pāngia ana e te whatukuhu hautai medullary?
He tokomaha pea e mataku ana ki te rongo i tēnei, engari ko te nuinga o te hunga whai Medullary Sponge Kidney (MSK) ka taea tonu te pupuri i te mahi pai o te whatukuhu puta noa i ō rātou oranga .
Heoi, he iti noa te ōrau o te tangata, tata ki te 10%, ka pāngia pea e te ngoikore o te whatukuhu. Ko ngā tino take ko ngā mate mimi auau, me ngā kōhatu whatukuhu.
Ko te mamae mau tonu tētahi atu raruraru onge ka pā ki te hunga e whakawhanake pinepine ana i ngā kohatu tākihi. Ka taea te whakahaere i tēnei āhuatanga mā te mahi i ngā mahi hei ārai i ngā kohatu tākihi.
Ka taea e te whatukuhu hautai medullary (MSK) te whakaiti i te taumata o te konupūmā i roto i te toto. Ka taea e tēnei te ngoikore i ngā wheua . Ka piki ake te mōrearea o ngā mate e pā ana ki te wheua. Hei tauira:
- Osteoporosis (he mate e angiangi ai, e pakarukaru ai hoki ngā wheua)
- Te hyperparathyroidism tuarua (te nui rawa o te hunanga o ngā homoni e ngā repe parathyroid)
Hei ārai i tēnei momo kino o te wheua mō te wā roa, ka tohua pea e tō tākuta he rongoā pēnei i te potassium citrate.
Me pēhea te ora me te whatukuhu hautai medullary?
Ka aroturukihia e tō tākuta te mahi a tō whatukuhu i ia wā, ā, ka whakaratohia he tiaki tautoko ina hiahiatia. He mea nui kia tangohia ō rongoā kia rite ki te whakahaunga, kia whai i tō kai, me te pupuri i ō wā tirotiro . Ka taea e ēnei mea te āwhina i te ārai i ngā mate mimi me ngā kōhatu whatukuhu.
Kāore he rongoā mō te Medullary Sponge Kidney (MSK). Engari e ai ki taku kōrero i mua, he maha ngā tāngata e pāngia ana e tēnei mate kāore he tohu, ā, ko ētahi kāore e mōhio kei a rātou. Ina puta ngā tohu, ko te nuinga o te wā ka puta mai i te mate mimi, i te kohatu tākihi rānei. He tino ngāwari te rongoā i ēnei e rua. Ka taea hoki e koe te ārai i ngā mate mimi me ngā kohatu tākihi mā te whakarerekē i tō kai me tō momo noho. Mena he pātai, he āwangawanga rānei āu, kaua e mangere ki te kōrero ki tō tākuta .
Karere Tangohia ki te Kāinga
Āe, ko tāku tumanako kua mārama pai koe ki te 'Medullary Sponge Kidney' i kōrerohia e tātou. Me whakamahara anō tātou ki ngā kōrero tino nui:
- He mate whānau tēnei e puta ai ngā pūwero iti i waenganui o ngā whatukuhu (medulla).
- Ko te nuinga o te tangata kāore he tohu . Mena he tohu, nā te mate mimi (UTI) te take, nā te kōhatu tākihi rānei.
- Kāore he rongoā motuhake mō tēnei, engari ka taea te rongoā pai i ngā tohu me ngā raruraru.
- He mea tino nui te ārai i ngā kōhatu whatukuhu me ngā mate mimi. Hei mahi i tēnei, inuhia he nui te wai, kia tūpato ki tāu e kai ana, ā, whai i ngā tohutohu a tō tākuta.
- Ka taea e te nuinga o te tangata te pupuri i te mahi pai o ō rātou whatukuhu puta noa i ō rātou oranga . He onge te ngoikore o te whatukuhu.
- Mena he pātai āu mō tēnei, me tino toro atu ki te tākuta .
Kaua e manukanuka, he tokomaha te hunga ka taea te noho ora noa me tēnei mate!
`Te whatukuhu hautai Medullary, te mate Cacchi-Ricci, te mate whatukuhu, ngā kōhatu whatukuhu, ngā mate mimi, ngā whēkau whatukuhu, te mate whatukuhu whānau, ngā whēkau whatukuhu, te nephrocalcinosis, te toto toto tiketike, te hauora whatukuhu Sinhala











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