Ko te ate tētahi o ngā okana tino nui o te tinana. He rite ki tētahi wheketere nui. He maha ngā mahi nui e mahia ana e ia, pērā i te tango i ngā paitini mai i ngā kai e kainga ana e tātou, te penapena pūngao, me te hanga au, e āwhina ana i a tātou ki te nakunaku i te kai. Nō reira, he mea tino nui te pupuri i tēnei wheketere kia mahi tika mō te hauora o tō tātou tinana katoa. Engari i ētahi wā ka pā puku mai ngā mate ki te ate, arā, ngā mate kāore e tino rangona ana e tātou. I tēnei rā ka kōrero tātou mō tētahi o aua mate. Ko te Primary Biliary Cholangitis, ko te PBC rānei te ingoa poto.
He aha te PBC?
Āe, kia māmā noa iho tēnei. E ai ki taku kōrero i mua ake nei, ka puta he wai e kiia nei ko te au o te ate. Koinei te mea e āwhina ana i a tātou ki te nakunaku i ngā ngako i roto i te kai e kainga ana e tātou, ki te mimiti i ētahi huaora, me te tango atu i te cholesterol me ngā paitini kāore e hiahiatia ana mai i te tinana.
Whakaarohia, kei roto i te ate he whatunga o ngā awaawa au, he rite ki te pūnaha ngongo iti. Ko te au e hangaia ana e te ate ka haere i roto i ēnei ngongo iti, ā, ka rongoa ki reira, hei āwhina i te nakunaku kai ina hiahiatia. Ko te mea e tupu ana i roto i te PBC ko te pakaru o ēnei awaawa au.
Ina pakaru ēnei awaawa, kāore e taea e te au te rere tika, ā, ka tīmata te kohikohi ki roto i te ate. He rite ki te paipa wai pakaru e whakakī ana i te whare ki te wai. Ko te au e kohikohi ana i tēnei ara ka tīmata te kino i ngā pūtau ate. Ina puta tēnei kino i roto i te wā, ka tīmata te hanga kiko whara , kaua ki ngā pūtau ate hauora. Ka kiia tēnei mate ko te cirrhosis . Ina whara te ate i tēnei ara, ka tata kore e mahi noa.
Ngā wāhanga e whā o te mate PBC
Kāore te PBC e kino haere i te wā kotahi. Ka whanake haere mārire, mā roto i ētahi wāhanga. E whā ngā wāhanga matua i te nuinga o te wā.
| Atamira | He aha te mea ka tupu |
|---|---|
| Wāhanga 1 (Wāhanga Kūaha) | Koinei te wāhanga tuatahi. Ko te mea e tupu ana i konei ko te mumura, te pupuhi rānei, huri noa i ngā awaawa au. Ka tīmata tēnei huringa i te rohe tomokanga o te ate, te wāhi e hono ai ngā oko toto me ngā awaawa au. |
| Wāhanga 2 (Wāhanga Periportal) | Kua horapa haere te mumura, ā, kua tīmata te puta mai ki te taha o ngā awaawa o te ate. I tēnei wā ka tīmata te hanga o ngā kiko whara iti (fibrosis). |
| Wāhanga 3 (Wāhanga Hepatum) | I nāianei, kua horapa atu taua kiko whara, ka hanga hononga i waenga i ngā wāhanga o te ate. He rite ki te whatunga whara, he rite ki te tukutuku pungawerewere, e horapa ana puta noa i te ate. |
| Wāhanga 4 (Atiroto Piripiri) | Koinei te wāhanga tino kino, te wāhanga whakamutunga hoki o te mate. I tēnei wā, kua horapa te kiko whara puta noa i te ate, kua matotoru te ate, ā, kua puta he puku. Ka kiia tēnei mate ko te cirrhosis. I tēnei wāhanga, kua tino ngoikore te mahi a te ate. |
He aha te tino take o te PBC?
He raruraru tēnei e pā ana ki te tini o te tangata. Ina hoki, kāore anō kia kitea e ngā tākuta te tino pūtake o te PBC. Heoi, ko te whakaaro whānui o nāianei he mate pūnaha ārai mate tēnei e hua mai ana i te huinga o ngā āhuatanga ira me te taiao .
Āe, he aha tēnei mate pūnaha ārai mate?
He kupu ngāwari tēnei, he hapa kei roto i te pūnaha ārai mate o tō tātou tinana. I te nuinga o te wā, ka whawhai ā tātou pūtau toto mā (ina koa ko ngā pūtau-T) ki ngā iroriki e puta ai te mate. Engari i roto i te PBC, ka huri kino ēnei pūtau ārai mate ka tīmata ki te whakaeke i ngā pūtau awaawa aukume hauora i roto i te ate. He rite ki tā tātou ake ope taua e whakaeke hē ana i ō tātou ake iwi.
Ko te wā e whakaeke tonu ai ō tātou ake pūtau i ngā awaawa au i tēnei ara, ka tīmata te kino i kōrerotia e au i mua ake nei.
Kāore e taea te kī he mate tēnei e tukuna iho ana i tētahi whakatipuranga ki tētahi whakatipuranga mā roto i ngā ira. Arā, kāore he ture e kī ana nā te mea kei te whaea tēnei mate, ka pāngia anō hoki tana tamāhine e tēnei mate. Heoi, ki te pāngia tētahi o te whānau, inā koa he whanaunga tata (whaea, tuahine, tungāne rānei), he paku teitei ake te tūponotanga ka pāngia ētahi atu e tēnei mate i te tangata noa. Nō reira, ka taea te kī he hononga ira kei reira.
Ko wai kei te nui ake te mōrearea ki te whakawhanake i te PBC?
Ahakoa ka taea e te tangata katoa te pāngia e te PBC, he nui ake te mōrearea o ētahi tāngata. Me titiro tātou ko wai rātou.
| Tauwehenga Mōrearea | Ētahi atu taipitopito |
|---|---|
| Ira Tangata (Ira Tangata) | He mea miharo tēnei. He nui ake te kitea o te PBC i roto i ngā wāhine. E 9 ki te 10 ngā wā ka nui ake te tūponotanga o ngā wāhine ki te pāngia e te mate i ngā tāne. |
| Tau | Ko te nuinga o te hunga kua pāngia e tēnei mate kei waenga i te 30 me te 60 tau te pakeke , engari ka pā anō hoki ki te hunga rangatahi, pakeke ake rānei i taua wā. |
| Hītori Whānau | E ai ki taku kōrero i mua, mēnā he PBC tō tētahi o tō whānau (ina koa ko tō whaea, ko tō tuahine rānei), he nui ake tō tūponotanga ki te pāngia e te mate i tērā o te taupori whānui. |
| Papamuri Ira | Ao whānui, ko te nuinga o ngā pūrongo mō tēnei mate ko te hunga nō te Raki o Ūropi (pērā i a Kōtirana me ngā whenua o Scandinavia). Heoi, ka taea te pā ki tētahi whenua, ki tētahi iwi rānei o te ao. |
He aha ngā tohu?
Koinei te mea tino nui. Ko te mea whakamataku mō te PBC ko te kore e whakaatuhia e te nuinga o te tangata tetahi tohu i ngā wāhanga tōmua. I ētahi wā ka kitea noa iho i te wā e mahia ana he whakamātautau toto mō tētahi atu mate.
Engari i te whanaketanga o te mate, ka puta pea ēnei tohu:
- Ngenge: Ko tētahi tohu nui ko te tino ngenge, ahakoa te kore take e kitea ana.
- Kiri Mākūkū: Tērā pea ka pāngia koe e te mākūkū e kore e taea te tohe puta noa i tō tinana, inā koa i ō nikau me ō kapu waewae.
- Ngā kanohi me te waha maroke: Ka heke te hanga roimata i roto i ngā kanohi me te huware i roto i te mangai, ka puta te maroke.
- Te mamae o ngā hononga me ngā wheua.
- He mamae ngawari, he koretake rānei i te taha matau o runga o te puku.
I te haere whakamua o te mate (ki te wāhanga o te cirrhosis), ka puta pea ngā tohu pēnei i te pupuhi o ngā waewae, te wai i roto i te puku, me te kōwhai o ngā kanohi me te kiri (jaundice).
Āhea koe me toro atu ki te tākuta?
Ki te mea kei te pāngia koe e ngā tohu pēnei i te ngenge tonu me te mākūkū o te kiri, kāore he take e kitea ana, kaua e kīia he "kaumātuatanga noa iho" he "nui rawa te mahi" rānei. Haere tonu ki te kōrero ki tō tākuta.
Ka tirohia koe e te tākuta, ā, ki te tika, ka tonoa e ia ētahi whakamātautau toto. Ka taea te tautuhi ngāwari i tēnei mate mā te tirotiro i ngā whākōkī ate me ngā paturopi motuhake (AMA - Antimitochondrial Antibodies). Nō reira kaua e warewarehia ngā tohu. Ko te wawe o te tautuhi, ko te nui ake o te tūponotanga ka rongoatia, ka whakahaeretia hoki.
Karere Tangohia ki te Kāinga
- He mate mau tonu te PBC e kino ai ngā awaawa aukume iti i roto i te ate.
- Ehara tēnei i te mate hopuhopu. He maha ngā wā ka puta mai i te hapa o te pūnaha ārai mate o tō tātou tinana (autoimmune).
- I ngā wāhanga tōmua, kāore pea he tohu e kitea ana. Ko ngā tohu tōmua e tino kitea ana ko te ngenge me te mākūkū o te kiri.
- Ko tēnei mate te mea tino noa i waenga i ngā wāhine, inā koa ko te hunga i waenga i te 30 me te 60 tau te pakeke.
- Ki te mea he ruarua, he tohu rānei āu mō tēnei, me tātaritanga e koe anō (Taria, he hapa reo Tai tēnā. He hapa tāpae taku i roto i taku whakaaro. Me tūpato). Kaua e tātaritanga e koe anō, engari me toro atu ki tētahi tākuta whai tohu, me rapu tohutohu.











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