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Kei te mōhio koe ki te PBC, he mate puku e pā ana ki te ate? (Te Korokorotanga o te Waipiro Matua)

Kei te mōhio koe ki te PBC, he mate puku e pā ana ki te ate? (Te Korokorotanga o te Waipiro Matua)

Ko te ate tētahi o ngā okana tino nui o te tinana. He rite ki tētahi wheketere nui. He maha ngā mahi nui e mahia ana e ia, pērā i te tango i ngā paitini mai i ngā kai e kainga ana e tātou, te penapena pūngao, me te hanga au, e āwhina ana i a tātou ki te nakunaku i te kai. Nō reira, he mea tino nui te pupuri i tēnei wheketere kia mahi tika mō te hauora o tō tātou tinana katoa. Engari i ētahi wā ka pā puku mai ngā mate ki te ate, arā, ngā mate kāore e tino rangona ana e tātou. I tēnei rā ka kōrero tātou mō tētahi o aua mate. Ko te Primary Biliary Cholangitis, ko te PBC rānei te ingoa poto.

He aha te PBC?

Āe, kia māmā noa iho tēnei. E ai ki taku kōrero i mua ake nei, ka puta he wai e kiia nei ko te au o te ate. Koinei te mea e āwhina ana i a tātou ki te nakunaku i ngā ngako i roto i te kai e kainga ana e tātou, ki te mimiti i ētahi huaora, me te tango atu i te cholesterol me ngā paitini kāore e hiahiatia ana mai i te tinana.

Whakaarohia, kei roto i te ate he whatunga o ngā awaawa au, he rite ki te pūnaha ngongo iti. Ko te au e hangaia ana e te ate ka haere i roto i ēnei ngongo iti, ā, ka rongoa ki reira, hei āwhina i te nakunaku kai ina hiahiatia. Ko te mea e tupu ana i roto i te PBC ko te pakaru o ēnei awaawa au.

Ina pakaru ēnei awaawa, kāore e taea e te au te rere tika, ā, ka tīmata te kohikohi ki roto i te ate. He rite ki te paipa wai pakaru e whakakī ana i te whare ki te wai. Ko te au e kohikohi ana i tēnei ara ka tīmata te kino i ngā pūtau ate. Ina puta tēnei kino i roto i te wā, ka tīmata te hanga kiko whara , kaua ki ngā pūtau ate hauora. Ka kiia tēnei mate ko te cirrhosis . Ina whara te ate i tēnei ara, ka tata kore e mahi noa.

Ngā wāhanga e whā o te mate PBC

Kāore te PBC e kino haere i te wā kotahi. Ka whanake haere mārire, mā roto i ētahi wāhanga. E whā ngā wāhanga matua i te nuinga o te wā.

Atamira He aha te mea ka tupu
Wāhanga 1 (Wāhanga Kūaha) Koinei te wāhanga tuatahi. Ko te mea e tupu ana i konei ko te mumura, te pupuhi rānei, huri noa i ngā awaawa au. Ka tīmata tēnei huringa i te rohe tomokanga o te ate, te wāhi e hono ai ngā oko toto me ngā awaawa au.
Wāhanga 2 (Wāhanga Periportal) Kua horapa haere te mumura, ā, kua tīmata te puta mai ki te taha o ngā awaawa o te ate. I tēnei wā ka tīmata te hanga o ngā kiko whara iti (fibrosis).
Wāhanga 3 (Wāhanga Hepatum) I nāianei, kua horapa atu taua kiko whara, ka hanga hononga i waenga i ngā wāhanga o te ate. He rite ki te whatunga whara, he rite ki te tukutuku pungawerewere, e horapa ana puta noa i te ate.
Wāhanga 4 (Atiroto Piripiri) Koinei te wāhanga tino kino, te wāhanga whakamutunga hoki o te mate. I tēnei wā, kua horapa te kiko whara puta noa i te ate, kua matotoru te ate, ā, kua puta he puku. Ka kiia tēnei mate ko te cirrhosis. I tēnei wāhanga, kua tino ngoikore te mahi a te ate.

He aha te tino take o te PBC?

He raruraru tēnei e pā ana ki te tini o te tangata. Ina hoki, kāore anō kia kitea e ngā tākuta te tino pūtake o te PBC. Heoi, ko te whakaaro whānui o nāianei he mate pūnaha ārai mate tēnei e hua mai ana i te huinga o ngā āhuatanga ira me te taiao .

Āe, he aha tēnei mate pūnaha ārai mate?

He kupu ngāwari tēnei, he hapa kei roto i te pūnaha ārai mate o tō tātou tinana. I te nuinga o te wā, ka whawhai ā tātou pūtau toto mā (ina koa ko ngā pūtau-T) ki ngā iroriki e puta ai te mate. Engari i roto i te PBC, ka huri kino ēnei pūtau ārai mate ka tīmata ki te whakaeke i ngā pūtau awaawa aukume hauora i roto i te ate. He rite ki tā tātou ake ope taua e whakaeke hē ana i ō tātou ake iwi.

Ko te wā e whakaeke tonu ai ō tātou ake pūtau i ngā awaawa au i tēnei ara, ka tīmata te kino i kōrerotia e au i mua ake nei.

Kāore e taea te kī he mate tēnei e tukuna iho ana i tētahi whakatipuranga ki tētahi whakatipuranga mā roto i ngā ira. Arā, kāore he ture e kī ana nā te mea kei te whaea tēnei mate, ka pāngia anō hoki tana tamāhine e tēnei mate. Heoi, ki te pāngia tētahi o te whānau, inā koa he whanaunga tata (whaea, tuahine, tungāne rānei), he paku teitei ake te tūponotanga ka pāngia ētahi atu e tēnei mate i te tangata noa. Nō reira, ka taea te kī he hononga ira kei reira.

Ko wai kei te nui ake te mōrearea ki te whakawhanake i te PBC?

Ahakoa ka taea e te tangata katoa te pāngia e te PBC, he nui ake te mōrearea o ētahi tāngata. Me titiro tātou ko wai rātou.

Tauwehenga Mōrearea Ētahi atu taipitopito
Ira Tangata (Ira Tangata) He mea miharo tēnei. He nui ake te kitea o te PBC i roto i ngā wāhine. E 9 ki te 10 ngā wā ka nui ake te tūponotanga o ngā wāhine ki te pāngia e te mate i ngā tāne.
Tau Ko te nuinga o te hunga kua pāngia e tēnei mate kei waenga i te 30 me te 60 tau te pakeke , engari ka pā anō hoki ki te hunga rangatahi, pakeke ake rānei i taua wā.
Hītori Whānau E ai ki taku kōrero i mua, mēnā he PBC tō tētahi o tō whānau (ina koa ko tō whaea, ko tō tuahine rānei), he nui ake tō tūponotanga ki te pāngia e te mate i tērā o te taupori whānui.
Papamuri Ira Ao whānui, ko te nuinga o ngā pūrongo mō tēnei mate ko te hunga nō te Raki o Ūropi (pērā i a Kōtirana me ngā whenua o Scandinavia). Heoi, ka taea te pā ki tētahi whenua, ki tētahi iwi rānei o te ao.

He aha ngā tohu?

Koinei te mea tino nui. Ko te mea whakamataku mō te PBC ko te kore e whakaatuhia e te nuinga o te tangata tetahi tohu i ngā wāhanga tōmua. I ētahi wā ka kitea noa iho i te wā e mahia ana he whakamātautau toto mō tētahi atu mate.

Engari i te whanaketanga o te mate, ka puta pea ēnei tohu:

  • Ngenge: Ko tētahi tohu nui ko te tino ngenge, ahakoa te kore take e kitea ana.
  • Kiri Mākūkū: Tērā pea ka pāngia koe e te mākūkū e kore e taea te tohe puta noa i tō tinana, inā koa i ō nikau me ō kapu waewae.
  • Ngā kanohi me te waha maroke: Ka heke te hanga roimata i roto i ngā kanohi me te huware i roto i te mangai, ka puta te maroke.
  • Te mamae o ngā hononga me ngā wheua.
  • He mamae ngawari, he koretake rānei i te taha matau o runga o te puku.

I te haere whakamua o te mate (ki te wāhanga o te cirrhosis), ka puta pea ngā tohu pēnei i te pupuhi o ngā waewae, te wai i roto i te puku, me te kōwhai o ngā kanohi me te kiri (jaundice).

Āhea koe me toro atu ki te tākuta?

Ki te mea kei te pāngia koe e ngā tohu pēnei i te ngenge tonu me te mākūkū o te kiri, kāore he take e kitea ana, kaua e kīia he "kaumātuatanga noa iho" he "nui rawa te mahi" rānei. Haere tonu ki te kōrero ki tō tākuta.

Ka tirohia koe e te tākuta, ā, ki te tika, ka tonoa e ia ētahi whakamātautau toto. Ka taea te tautuhi ngāwari i tēnei mate mā te tirotiro i ngā whākōkī ate me ngā paturopi motuhake (AMA - Antimitochondrial Antibodies). Nō reira kaua e warewarehia ngā tohu. Ko te wawe o te tautuhi, ko te nui ake o te tūponotanga ka rongoatia, ka whakahaeretia hoki.

Karere Tangohia ki te Kāinga

  • He mate mau tonu te PBC e kino ai ngā awaawa aukume iti i roto i te ate.
  • Ehara tēnei i te mate hopuhopu. He maha ngā wā ka puta mai i te hapa o te pūnaha ārai mate o tō tātou tinana (autoimmune).
  • I ngā wāhanga tōmua, kāore pea he tohu e kitea ana. Ko ngā tohu tōmua e tino kitea ana ko te ngenge me te mākūkū o te kiri.
  • Ko tēnei mate te mea tino noa i waenga i ngā wāhine, inā koa ko te hunga i waenga i te 30 me te 60 tau te pakeke.
  • Ki te mea he ruarua, he tohu rānei āu mō tēnei, me tātaritanga e koe anō (Taria, he hapa reo Tai tēnā. He hapa tāpae taku i roto i taku whakaaro. Me tūpato). Kaua e tātaritanga e koe anō, engari me toro atu ki tētahi tākuta whai tohu, me rapu tohutohu.

PBC, Kolangitis Piripiri Tuatahi, ate, mate ate, awaawa piri, cirrhosis, mate pūnaha ārai mate, mate ate, kiri mākūkū
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Kei te mōhio koe ki te PBC, he mate puku e pā ana ki te ate? (Te Korokorotanga o te Waipiro Matua)

Kei te mōhio koe ki te PBC, he mate puku e pā ana ki te ate? (Te Korokorotanga o te Waipiro Matua)

Ko te ate tētahi o ngā okana tino nui o te tinana. He rite ki tētahi wheketere nui. He maha ngā mahi nui e mahia ana e ia, pērā i te tango i ngā paitini mai i ngā kai e kainga ana e tātou, te penapena pūngao, me te hanga au, e āwhina ana i a tātou ki te nakunaku i te kai. Nō reira, he mea tino nui te pupuri i tēnei wheketere kia mahi tika mō te hauora o tō tātou tinana katoa. Engari i ētahi wā ka pā puku mai ngā mate ki te ate, arā, ngā mate kāore e tino rangona ana e tātou. I tēnei rā ka kōrero tātou mō tētahi o aua mate. Ko te Primary Biliary Cholangitis, ko te PBC rānei te ingoa poto.

He aha te PBC?

Āe, kia māmā noa iho tēnei. E ai ki taku kōrero i mua ake nei, ka puta he wai e kiia nei ko te au o te ate. Koinei te mea e āwhina ana i a tātou ki te nakunaku i ngā ngako i roto i te kai e kainga ana e tātou, ki te mimiti i ētahi huaora, me te tango atu i te cholesterol me ngā paitini kāore e hiahiatia ana mai i te tinana.

Whakaarohia, kei roto i te ate he whatunga o ngā awaawa au, he rite ki te pūnaha ngongo iti. Ko te au e hangaia ana e te ate ka haere i roto i ēnei ngongo iti, ā, ka rongoa ki reira, hei āwhina i te nakunaku kai ina hiahiatia. Ko te mea e tupu ana i roto i te PBC ko te pakaru o ēnei awaawa au.

Ina pakaru ēnei awaawa, kāore e taea e te au te rere tika, ā, ka tīmata te kohikohi ki roto i te ate. He rite ki te paipa wai pakaru e whakakī ana i te whare ki te wai. Ko te au e kohikohi ana i tēnei ara ka tīmata te kino i ngā pūtau ate. Ina puta tēnei kino i roto i te wā, ka tīmata te hanga kiko whara , kaua ki ngā pūtau ate hauora. Ka kiia tēnei mate ko te cirrhosis . Ina whara te ate i tēnei ara, ka tata kore e mahi noa.

Ngā wāhanga e whā o te mate PBC

Kāore te PBC e kino haere i te wā kotahi. Ka whanake haere mārire, mā roto i ētahi wāhanga. E whā ngā wāhanga matua i te nuinga o te wā.

Atamira He aha te mea ka tupu
Wāhanga 1 (Wāhanga Kūaha) Koinei te wāhanga tuatahi. Ko te mea e tupu ana i konei ko te mumura, te pupuhi rānei, huri noa i ngā awaawa au. Ka tīmata tēnei huringa i te rohe tomokanga o te ate, te wāhi e hono ai ngā oko toto me ngā awaawa au.
Wāhanga 2 (Wāhanga Periportal) Kua horapa haere te mumura, ā, kua tīmata te puta mai ki te taha o ngā awaawa o te ate. I tēnei wā ka tīmata te hanga o ngā kiko whara iti (fibrosis).
Wāhanga 3 (Wāhanga Hepatum) I nāianei, kua horapa atu taua kiko whara, ka hanga hononga i waenga i ngā wāhanga o te ate. He rite ki te whatunga whara, he rite ki te tukutuku pungawerewere, e horapa ana puta noa i te ate.
Wāhanga 4 (Atiroto Piripiri) Koinei te wāhanga tino kino, te wāhanga whakamutunga hoki o te mate. I tēnei wā, kua horapa te kiko whara puta noa i te ate, kua matotoru te ate, ā, kua puta he puku. Ka kiia tēnei mate ko te cirrhosis. I tēnei wāhanga, kua tino ngoikore te mahi a te ate.

He aha te tino take o te PBC?

He raruraru tēnei e pā ana ki te tini o te tangata. Ina hoki, kāore anō kia kitea e ngā tākuta te tino pūtake o te PBC. Heoi, ko te whakaaro whānui o nāianei he mate pūnaha ārai mate tēnei e hua mai ana i te huinga o ngā āhuatanga ira me te taiao .

Āe, he aha tēnei mate pūnaha ārai mate?

He kupu ngāwari tēnei, he hapa kei roto i te pūnaha ārai mate o tō tātou tinana. I te nuinga o te wā, ka whawhai ā tātou pūtau toto mā (ina koa ko ngā pūtau-T) ki ngā iroriki e puta ai te mate. Engari i roto i te PBC, ka huri kino ēnei pūtau ārai mate ka tīmata ki te whakaeke i ngā pūtau awaawa aukume hauora i roto i te ate. He rite ki tā tātou ake ope taua e whakaeke hē ana i ō tātou ake iwi.

Ko te wā e whakaeke tonu ai ō tātou ake pūtau i ngā awaawa au i tēnei ara, ka tīmata te kino i kōrerotia e au i mua ake nei.

Kāore e taea te kī he mate tēnei e tukuna iho ana i tētahi whakatipuranga ki tētahi whakatipuranga mā roto i ngā ira. Arā, kāore he ture e kī ana nā te mea kei te whaea tēnei mate, ka pāngia anō hoki tana tamāhine e tēnei mate. Heoi, ki te pāngia tētahi o te whānau, inā koa he whanaunga tata (whaea, tuahine, tungāne rānei), he paku teitei ake te tūponotanga ka pāngia ētahi atu e tēnei mate i te tangata noa. Nō reira, ka taea te kī he hononga ira kei reira.

Ko wai kei te nui ake te mōrearea ki te whakawhanake i te PBC?

Ahakoa ka taea e te tangata katoa te pāngia e te PBC, he nui ake te mōrearea o ētahi tāngata. Me titiro tātou ko wai rātou.

Tauwehenga Mōrearea Ētahi atu taipitopito
Ira Tangata (Ira Tangata) He mea miharo tēnei. He nui ake te kitea o te PBC i roto i ngā wāhine. E 9 ki te 10 ngā wā ka nui ake te tūponotanga o ngā wāhine ki te pāngia e te mate i ngā tāne.
Tau Ko te nuinga o te hunga kua pāngia e tēnei mate kei waenga i te 30 me te 60 tau te pakeke , engari ka pā anō hoki ki te hunga rangatahi, pakeke ake rānei i taua wā.
Hītori Whānau E ai ki taku kōrero i mua, mēnā he PBC tō tētahi o tō whānau (ina koa ko tō whaea, ko tō tuahine rānei), he nui ake tō tūponotanga ki te pāngia e te mate i tērā o te taupori whānui.
Papamuri Ira Ao whānui, ko te nuinga o ngā pūrongo mō tēnei mate ko te hunga nō te Raki o Ūropi (pērā i a Kōtirana me ngā whenua o Scandinavia). Heoi, ka taea te pā ki tētahi whenua, ki tētahi iwi rānei o te ao.

He aha ngā tohu?

Koinei te mea tino nui. Ko te mea whakamataku mō te PBC ko te kore e whakaatuhia e te nuinga o te tangata tetahi tohu i ngā wāhanga tōmua. I ētahi wā ka kitea noa iho i te wā e mahia ana he whakamātautau toto mō tētahi atu mate.

Engari i te whanaketanga o te mate, ka puta pea ēnei tohu:

  • Ngenge: Ko tētahi tohu nui ko te tino ngenge, ahakoa te kore take e kitea ana.
  • Kiri Mākūkū: Tērā pea ka pāngia koe e te mākūkū e kore e taea te tohe puta noa i tō tinana, inā koa i ō nikau me ō kapu waewae.
  • Ngā kanohi me te waha maroke: Ka heke te hanga roimata i roto i ngā kanohi me te huware i roto i te mangai, ka puta te maroke.
  • Te mamae o ngā hononga me ngā wheua.
  • He mamae ngawari, he koretake rānei i te taha matau o runga o te puku.

I te haere whakamua o te mate (ki te wāhanga o te cirrhosis), ka puta pea ngā tohu pēnei i te pupuhi o ngā waewae, te wai i roto i te puku, me te kōwhai o ngā kanohi me te kiri (jaundice).

Āhea koe me toro atu ki te tākuta?

Ki te mea kei te pāngia koe e ngā tohu pēnei i te ngenge tonu me te mākūkū o te kiri, kāore he take e kitea ana, kaua e kīia he "kaumātuatanga noa iho" he "nui rawa te mahi" rānei. Haere tonu ki te kōrero ki tō tākuta.

Ka tirohia koe e te tākuta, ā, ki te tika, ka tonoa e ia ētahi whakamātautau toto. Ka taea te tautuhi ngāwari i tēnei mate mā te tirotiro i ngā whākōkī ate me ngā paturopi motuhake (AMA - Antimitochondrial Antibodies). Nō reira kaua e warewarehia ngā tohu. Ko te wawe o te tautuhi, ko te nui ake o te tūponotanga ka rongoatia, ka whakahaeretia hoki.

Karere Tangohia ki te Kāinga

  • He mate mau tonu te PBC e kino ai ngā awaawa aukume iti i roto i te ate.
  • Ehara tēnei i te mate hopuhopu. He maha ngā wā ka puta mai i te hapa o te pūnaha ārai mate o tō tātou tinana (autoimmune).
  • I ngā wāhanga tōmua, kāore pea he tohu e kitea ana. Ko ngā tohu tōmua e tino kitea ana ko te ngenge me te mākūkū o te kiri.
  • Ko tēnei mate te mea tino noa i waenga i ngā wāhine, inā koa ko te hunga i waenga i te 30 me te 60 tau te pakeke.
  • Ki te mea he ruarua, he tohu rānei āu mō tēnei, me tātaritanga e koe anō (Taria, he hapa reo Tai tēnā. He hapa tāpae taku i roto i taku whakaaro. Me tūpato). Kaua e tātaritanga e koe anō, engari me toro atu ki tētahi tākuta whai tohu, me rapu tohutohu.

PBC, Kolangitis Piripiri Tuatahi, ate, mate ate, awaawa piri, cirrhosis, mate pūnaha ārai mate, mate ate, kiri mākūkū
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Kaore ano kia tukuna he korero. Tāpirihia to korero ki konei mo te wa tuatahi.

Tāpirihia to korero

Tātaihia koa: 6 + 9 =