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He kuiti hoki ō oko toto i roto i ō pukahukahu? Me kōrero tātou mō te Pulmonary Arterial Hypertension (PAH)!

He kuiti hoki ō oko toto i roto i ō pukahukahu? Me kōrero tātou mō te Pulmonary Arterial Hypertension (PAH)!

He wā poto te manawa e pā mai ana ki a koe? He wā poto rānei te tawhiti e ngenge ana koe ahakoa e hikoi ana? Kua kite koe kua kikorangi ō matimati me ō ngutu, me te mamae, te kikī rānei o tō uma? Kaua e waiho ēnei hei mea noa iho. Nā te mea i ētahi wā, kei muri i ēnei tohu, tera pea he mate hauora e hiahia ana kia arohia. Ko tētahi o aua mate ko te Pulmonary Arterial Hypertension (PAH) . Ahakoa he ahua whakamataku te ingoa, me kōrero noa tātou mō tēnei mea, me te mārama hoki.

He aha te toto toto tiketike o te pūkahukahu (PAH)? He māmā noa iho...

Ki te whakarāpopototanga, ko te Pulmonary Arterial Hypertension (PAH) he āhuatanga e whaiti ai ngā oko toto iti i roto i ō pūkahukahu (ngā uaua pūkahukahu) . Whakaarohia he rite ki te paipa wai kua āraia, ā, he uaua ki te wai te rere mā roto. Ina whaiti ēnei oko toto, kāore e taea e te toto te rere tika mā roto i ō pūkahukahu. Nā tēnei ka nui rawa te pēhanga i roto i ēnei oko toto, te pēhanga toto rānei. Ko ēnei oko toto ngā mea e kawe ana i te toto rawakore-hāora mai i tō ngākau ki ō pūkahukahu, ki reira ka horoia.

Nā, he aha te mea ka tupu ina tupu tēnei? Me kaha ake te mahi a te taha matau o tō ngākau i te mea noa ki te pupuhi toto ki ngā pukahukahu. He rite ki te hiki i tētahi taumaha taumaha me te piki i tētahi maunga. Ina me kawe e te ngākau tēnei kawenga tāpiri i roto i te wā, ka tīmata te ngoikore haere. Ki te kore e rongoatia tika, ka taea e tēnei āhuatanga, PAH, te whakararu i te maha o ngā raruraru ehara i te mea mō tō ngākau me ō pukahukahu anake, engari mō tō tinana katoa.

Kia maumahara, ko te PAH tētahi momo motuhake o tētahi wāhanga nui e kiia nei ko te toto toto tiketike pūkahukahu . Ko te toto toto tiketike pūkahukahu he pikinga o te pēhanga i roto i ngā oko toto o ngā pūkahukahu nā tetahi take.

He aha te pānga o te PAH ki tō tinana?

Ko te toto toto tiketike o te pūkahukahu (PAH) te nuinga o te wā ka pēhia te taha matau o tō ngākau. Nā te mea ka panaia e tēnei wāhanga o te ngākau te toto kore-hāora ki ngā pūkahukahu. I roto i te wā, ka taea e tēnei toto toto tiketike te arahi ki te ngoikore o te ngākau o te taha matau .

Ehara i te mea koinā anake, ka whakaroa hoki te PAH i te rere o te toto i waenga i te ngākau me ngā pukahukahu. Ko te tikanga he iti iho te toto e tae atu ana ki ngā pukahukahu ki te tiki hāora hou. Nō reira, he iti iho te hāora e tae atu ana ki ētahi atu okana me ngā kiko o tō tinana. Inaa, me whai hāora ia wāhanga o tō tātou tinana kia ora ai. Ki te kore e ranea, ka puta pea ngā raruraru.

He pēhea te kino o te PAH i huaina ai tēnei mate?

He tino kino te mate toto toto tiketike o te pūkahukahu (PAH), ā, i ētahi wā ka morearea ki te ora . Heoi, ki te kitea wawetia, ā, ka rongoātia wawetia, ka roa ake tō oranga, ka pai ake hoki. Koia te mea nui kia aro nui ki ngā tohu.

Ko wai te hunga e tino pāngia ana e te PAH?

Ka pāngia ngā pakeke o ngā tau katoa e te PAH. Heoi, he nui ake te kitea i roto i ngā wāhine , e kitea ana i waenga i te 30 me te 60 tau te pakeke. Kua kitea hoki ko ngā tāne neke atu i te 65 tau te pakeke e pāngia ana e te PAH, he nui ake te tūponotanga ki te pāngia e te mate.

Ka pāngia hoki ngā pēpi nohinohi e tēnei āhuatanga. Mēnā ka pā ki ngā pēpi hou, ka kiia ko te toto toto tiketike pumau i roto i te pēpi hou (PPHN) .

He pēhea te noa o te PAH?

Ki te whakatauritea ki ētahi atu momo toto toto tiketike pūkahukahu, pērā i te toto toto tiketike pūkahukahu i puta mai i te mate manawa, i te mate pūkahukahu rānei, ehara te PAH i te mate tino noa . Ahakoa i roto i tētahi whenua pērā i te Hononga o Amerika, e 500 ki te 1,000 noa iho ngā kēhi hou o te PAH ka kitea i ia tau. I ngā whenua o te Hauāuru, ko te auau he tata ki te 25 i ia miriona.

He aha ngā tohu o te toto toto tiketike o te pūkahukahu (PAH)?

Kāore pea koe e kite i tētahi tohu i ngā wāhanga tōmua o te PAH. Ko te nuinga o te tangata ka tīmata noa te kite i ngā tohu i te whanaketanga haere o te mate. Ko ētahi o ēnei tohu ko:

  • Te tae kikorangi o ngā pito o ngā maihao me ngā ngutu: Me te mea nei kāore he hāora i roto i te toto.
  • Te mamae o te uma, te kikī rānei: Me te mea kei te pēhia tō uma e tetahi.
  • Te whanoke, te ngoikore rānei: Ka puta pea tēnei ina heke te rere o te toto ki te roro.
  • Ngenge: Te tino ngenge , ehara i te mea ko te ngenge anake.
  • Te tere o te manawa, te pakū rānei o te ngakau.
  • Te poto o te manawa: Ka piki ake tēnei i te roanga o te wā. Ahakoa te mahi i ngā mahi iti nei, ka taea te poto o te manawa.
  • Te pupuhi (Edema): Ka tīmata pea te pupuhi i ngā waewae me ngā pona, kātahi ka horapa ki te puku me te kaki.

Ki te kore e rongoatia, ka kino haere ēnei tohumate PAH i roto i te wā. Tērā pea ka kitea e koe kāore e taea e koe te mahi i ngā mahi tino taketake o ia rā me te kore e hiahia ki te manawa, ki te okioki rānei.

He aha ngā take o te toto toto tiketike o te pūkahukahu (PAH)?

Ko te tino take o te PAH ko te pakaru o te arai o ngā uaua toto i roto i ō pukahukahu. Heoi, kāore i te mārama tonu te take o tēnei pakaru.

Ngā take kāore e kitea he pūtake (IPAH Idiopathic)

I ētahi wā, kāore e kitea he tino take . Ka kiia e mātou ngā tākuta he toto toto tiketike pūkahukahu "idiopathic" . He rite ki te mea ngaro.

Ngā take e mōhiotia ana

Heoi, i ētahi wā, he mārama ngā take. Ko ētahi o ngā take e mōhiotia ana o te PAH ko:

  • Ētahi āhuatanga hauora:
  • Mate ngakau whānau
  • Ngā mate rokiroki glycogen
  • Mate HIV
  • Mate ate
  • Ngā mate autoimmune pēnei i te lupus
  • Te toto toto tiketike (te pikinga o te pēhanga i roto i ngā oko toto e anga atu ana ki te ate)
  • Te hemangiomatosis o te capillary pūkahukahu (te tipu rerekē o ngā capillaries i roto i ngā pukahukahu)
  • Te mate ārai-aukati o te manawa (te aukati i ngā uaua i roto i ngā pukahukahu)
  • Schistosomiasis (he mate i puta mai i te pirinoa)
  • Scleroderma (te matotoru o te kiri me te kiko honohono)
  • Ngā whakarerekētanga ira:
  • I te nuinga o te wā, nā te whakarerekētanga o tō ira BMPR2 tēnei. Ko tēnei ira te kaiwhakahaere o te maha o ngā pūtau i roto i ētahi kiko o tō tātou tinana. Nō reira, ina whakarerekētia tēnei ira, ka nui rawa te tipu o ngā pūtau i roto i ngā oko toto iti i roto i ō pūkahukahu. Ina kī tonu ēnei pūtau, ka whaiti ngā pūaha o ngā oko toto.
  • Ka taea e te PAH te horapa i roto i ngā whānau. Ka kiia e mātou he PAH tuku iho . Tata ki te 80% o te hunga whai mate pēnei he whakarerekētanga ira kei roto i te ira BMPR2.
  • Kei ētahi tāngata tēnei ira kua whakarerekētia, engari kāore e whanaketia he PAH e rātou.
  • Ka pāngia pea ētahi tāngata e te PAH ahakoa kāore he whānau e pāngia ana e tēnei mate, nā te whakarerekētanga ira. Ka kiia tēnei ko te PAH tūpono .
  • Ko ētahi rongoā me ngā rongoā:
  • Kua āraia ētahi pire kai , pērā i te rongoā tawhito "fen-phen", engari ka taea tonu te whakaputa PAH i muri i ngā tau maha o te whakamahinga.
  • Ngā raau taero whakangahau , hei tauira ko te kōkaini me te methamphetamine.

Me pēhea te tātaritanga o te toto toto tiketike o te pūkahukahu (PAH)?

He uaua te tautuhi i te PAH nā te mea he rite ngā tohu o te PAH ki ērā o ētahi atu mate. Ka tirotirohia e tō tākuta ō tohu me ō hītori hauora. Ka mahia e rātou he maha ngā whakamātautau (tae atu ki ngā whakamātautau whakaahua me ngā whakamātautau toto) hei kimi mēnā he toto toto tiketike tōu, ā, mēnā he pērā, he aha te momo.

Tērā pea ka tukuna koe e tō tākuta ki tētahi tākuta manawa , ki tētahi tākuta ngakau rānei. Ka whakahaerehia e ēnei tohunga ngā whakamātautau motuhake hei tirotiro i te mahi a tō ngākau me ō pukahukahu. Mā rātou e whakatau mēnā kei a koe te PAH, tētahi atu momo toto toto tiketike rānei. Ka aromatawaihia hoki e rātou te kaha o tō mate.

He maimoatanga motuhake kei reira mō te PAH kāore e wātea ana mō ētahi atu momo toto toto tiketike. Nō reira, me mōhio tō rōpū hauora ki ngā mea katoa e pā ana ki ō pukahukahu me tō ngākau. Mā ēnei mōhiohio ka āwhina i a rātou ki te whakawhanake i te mahere maimoatanga pai rawa atu māu.

He aha ngā whakamātautau e whakamahia ana hei tautuhi i te PAH?

Ka whakamahia e tō tīma hauora he huinga o ngā whakamātautau hei whakakore i ētahi atu mate me te tautuhi i te PAH.

Ki te whakapae tō tākuta kei a koe te PAH i muri i tō whakamātautau tinana, ko te whakamātautau tuatahi ka tonoa e rātou he echocardiogram transthoracic . Ka aromatawaihia e tēnei whakamātautau te hanganga whānui me te mahi a tō ngākau.

Ko ētahi atu whakamātautau ka uru atu ki:

  • Ngā whakamātautau toto: Tirohia te mahi a ngā okana, ngā taumata homoni, me te tautuhi i ngā mate pūtake. Ina koa ngā whakamātautau pēnei i te panera pākia katoa me te tatau toto katoa .
  • Matawai CT o te uma: Hei tirotiro me te whakakore i ētahi atu āhuatanga pēnei i te mate tākihi. (Tērā pea ko te mate tākihi i roto i te tuhinga taketake ko te mate pūkahukahu. Ka tirohia e te matawai CT o te uma ngā pūkahukahu me ngā whekau o te uma. Me kī tātou kei te titiro tātou ki te āhua o ngā pūkahukahu.
  • X-ray o te uma: Hei tirotiro mēnā he nui ake tō ngākau, ō uaua pūkahukahu rānei i te mea noa.
  • MRI o te Ngākau: Arotakehia te āhua o te ventricle matau o tō ngākau (koinei te rūma o te ngākau e pupuhi ana i te toto ki ngā pukahukahu).
  • Polysomnogram (PSG): He tirotiro mō te apnea moe, ka taea te whakararu i te PAH. Ko te PSG he momo whakamātautau moe ka mahia i te pō.
  • Ngā whakamātautau mahi a ō pukahukahu: Tirohia te pai o te mahi a ō pukahukahu.
  • Matawai whakapūngao/whakapūngao toto (VQ): Ka tirohia mēnā he toto totoka i roto i ngā pukahukahu. Mā tēnei whakamātautau ka taea te whakakore i tētahi āhuatanga e kiia nei ko te toto toto tiketike thromboembolic mau tonu .
  • Te whakaurunga o te catheter o te ngākau matau: Ka ine i te pēhanga i roto i ngā oko toto i roto i ō pukahukahu (ngā pēhanga o te uaua pūkahukahu). He mea nui tēnei whakamātautau hei tautuhi i te PAH.
  • Whakamātautau hikoi ono meneti: Tirohia te nui o te whakakori tinana ka taea e koe te manawanui me te nui o te hāora e rere ana i roto i tō toto ina neke koe.

Kōrero ki tō tākuta mō ngā whakamātautau e tika ana kia mahia e koe, me pēhea hoki te whakarite mō aua whakamātautau.

He aha ngā paearu mō te tautuhi i te toto toto tiketike o te pūkahukahu?

Mā te ine i te pēhanga i roto i ngā uaua toto o ōu pūkahukahu ka tātarihia e ngā tākuta te toto toto tiketike o te pūkahukahu. Ko ngā paearu tātaritanga ko te pēhanga o te uaua toto o te pūkahukahu i roto i ōu pūkahukahu he nui ake i te 20 mirimita o te mercury (20 mmHg) i a koe e okioki ana . Ka inehia tēnei uara mā te whakaurunga catheter o te ngākau matau .

He aha ngā maimoatanga mō te toto toto tiketike o te pūkahukahu (PAH)?

Ko ngā whāinga matua o te maimoatanga mō te PAH he whakahaere i te haere whakamua o te mate, me te whakapai ake i te kounga o te oranga. Kāore he maimoatanga kotahi e pai ana mō te PAH katoa. Ka mahi tahi tō tākuta me koe ki te whakatau i te maimoatanga pai rawa atu mō ō hiahia.

Kei roto pea i tō mahere maimoatanga PAH:

  • Te pokanga atrial balloon (BAS): Ko te tikanga o tēnei mahi he mea mahi mā ngā pēpi he whānautanga ngā hapa ngākau, engari i ētahi wā ka whakamahia mā ngā pakeke he PAH. Ka āwhina te pokanga atrial balloon ki te whakaiti i te pēhanga ki te taha matau o te ngākau, ka nui ake te hāora e rere ana i roto i te toto. Ka taea hoki te mahi hei piriti ki te whakawhitinga pūkahukahu.
  • Ngā aukati hongere konupūmā: Ka āwhina ēnei rongoā ki te whakaheke i te toto toto i roto i ngā oko toto o ōu pukahukahu me tō tinana katoa.
  • Ngā rongoā whakaheke toto: E mōhiotia ana ko ngā "pire wai," ka āwhina ēnei rongoā ki te tango i te wai nui mai i te tinana me te whakaiti i te pupuhi.
  • Whakaora hāora: Tērā pea ka hiahiatia tēnei maimoatanga mēnā kāore i te nui te hāora i roto i ō toto. Ka taea e te hāora tāpiri te āwhina i a koe e okioki ana, e moe ana, e whakakorikori tinana ana rānei.
  • Ngā rongoā whakawhanui i ngā oko toto o te pūkahukahu: Ka āwhina ēnei rongoā i ngā oko toto i roto i ō pūkahukahu kia wātea, kia whānui ake hoki te whakatuwheratanga. Ka whakaitihia te taumahatanga ki tō ngākau, ā, ka āwhina hoki ki te whakamama i ō tohumate.

Mō ētahi tāngata he nui te PAH , ko te whakawhitinga pūkahukahu pea te kōwhiringa whakamutunga. Mā tēnei pokanga ka taea e koe te hoatu i tētahi, i ētahi rānei pūkahukahu hou. Ka taea hoki e te whakawhitinga ngākau-pūkahukahu te hoatu i tētahi ngākau hou ki a koe.

He aha ngā rongoā e hoatu ana mō te PAH?

He rerekē ngā momo rongoā hei rongoā i te PAH:

  • Rongoā ā-waha: Ka āwhina ēnei rongoā ki te whakangāwari i ngā oko toto i roto i ngā pukahukahu, ā, ka ārai i te whaiti o aua oko toto. Ka āwhina hoki ēnei rongoā i a koe kia kaha ake te mahi tinana.
  • Ngā rongoā manawa: Whakaorahia ngā uauatanga manawa.
  • Papu werohanga kawe: Ka āwhina tēnei ki te whakatuwhera i ngā oko toto me te whakanui ake i te rere o te toto. Tērā pea ka āwhina tēnei ki te whakapai ake i ō tohu.
  • Ngā rongoā ā-uaua (IV): Ka whakatuwhera i ngā uaua toto, ka whakaora i ngā tohu pēnei i te mamae o te uma me te uaua ki te manawa.

Anei ētahi rongoā kua whakaaetia e te US Food and Drug Administration (FDA) mō ngā tūroro PAH:

  • Ambrisentan (ā-waha)
  • Bosentan (ā-waha)
  • Epoprostenol (IV)
  • Iloprost (manawa)
  • Macitentan (ā-waha)
  • Riociguat (ā-waha)
  • Selexipag (ā-waha)
  • Sildenafil (ā-waha)
  • Tadalafil (ā-waha)
  • Treprostinil (waha, inhalation, papu, IV)

Ngā pānga taha o ngā rongoā PAH

Ko ētahi o ngā pānga taha noa o ngā rongoā e whakamahia ana hei rongoā i te PAH ko:

  • Te pōuri, te ngoikore rānei.
  • Te māhana o te mata, te kaki, ngā ringaringa rānei (te whero).
  • Ngā tohu o te puku pērā i te pupuhi, te whakapairuaki, te ruaki, me te mate korere.
  • Mamae upoko (mamae upoko).
  • Te toto toto iti (hypotension) .
  • Te pupuhi o ngā waewae me ngā pona waewae (Pedal edema) .
  • Te kiri mākūkū.
  • Te ahua o te pupuhi o te ara manawa o runga.

Tērā pea he pānga taha anō kei ētahi rongoā. Kōrero ki tō tākuta mō te whakahaere i ngā pānga taha. I ētahi wā, me whakarerekē pea e tō tākuta te horopeta o tō rongoā.

Ka taea te whakaora katoa i te toto toto tiketike o te pūkahukahu (PAH)?

Ahakoa ka taea e ngā rongoā o nāianei te whakahaere i te whanaketanga o te PAH, kāore e taea te whakakore i te kino kua puta kē . Heoi, kei te rangahau ngā kairangahau i ngā rongoā hou e whakaaro ana rātou ka taea te whakakore i te PAH. Ka taea e ēnei rongoā te whakatika i te kino o ngā pūtau endothelial e whakarārangi ana i ngā oko toto i roto i ō pukahukahu.

Kōrero ki tō tākuta kia mōhio ai koe ki ngā rangahau hou me ngā whakamātautau haumanu mō te maimoatanga PAH.

He aha ngā āhuatanga ka whakanui ake i te mōrearea o te tangata ki te whakawhanake i te Pulmonary Arterial Hypertension (PAH)?

He maha ngā āhuatanga e whakanui ake ai i te mōrearea o te whakawhanake i te PAH:

  • Te mate o te kiko honohono .
  • Te mate Down syndrome .
  • Hītori whānau mō te toto toto tiketike pūkahukahu.
  • Te mate HIV .
  • Te whakamahi i ngā rongoā whakaiti taumaha pērā i te "fen-phen" (dexfenfluramine me te phentermine).
  • Te whakamahi i ngā raau taero turekore (ngā raau taero o te tiriti).

Mena kei te pāngia tētahi o tō whānau e te PAH, pātai atu ki tō tākuta mō ngā whakamātautau ira. Mena kua tāpaetia koe kei te pāngia e te PAH, he mea pai kia pātai atu ki tō whānau kia whakaarohia hoki te whakamātautau ira.

Me pēhea te ārai i te toto toto tiketike o te pūkahukahu (PAH)?

Kāore e taea e tātou te whakahaere i ētahi āhuatanga mōrearea mō te PAH (pērā i ngā whakarerekētanga ira). Heoi, mā te karo i ngā raau taero ture kore ka taea te whakaiti i tō tupono ki te PAH, tae atu ki ngā raruraru hauora maha atu. Me kōrero hoki ki tō tākuta i mua i te tango i tētahi rongoā whakaiti taumaha.

I runga i ngā āhuatanga mōrearea e pā ana ki a koe, ka tūtohu pea tō tākuta i ngā whakamātautau ārai mate pāwera (PAH).

He aha te tirohanga ā-muri mō te hunga e pāngia ana e te mate toto tiketike pūkahukahu (PAH)?

Nā te whanaketanga o te maimoatanga, kua roa ake te ora o te hunga whai PAH i mua. Ko te roanga o tō oranga e whakawhirinaki ana ki ngā āhuatanga maha, tae atu ki te kaha o tō mate me te wawe o te tautuhi i a koe. Kōrero ki tō tākuta mō tō mate.

Ko te mea nui ko te haere tonu i tō maimoatanga me te āta whai i ngā tohutohu a tō tākuta. E rua ngā mea ka taea e koe te mahi hei whakapai ake i tō tupono ki te ora:

  • Hangaia he kete āwhina ohorere. Me mau tonu ētahi taputapu me ngā mōhiotanga. Pātai atu ki tō tākuta he aha ngā mea hei whakauru ki roto i tō kete āwhina, ā, kaua rawa e wehe i te kāinga me te kore he mea pēnei.
  • Tikina ngā kano ārai mate ā-wā e ai ki ngā taunakitanga a tō tākuta. He mea tino nui kia tiakina koe i te rewharewha me te niumōnia.
  • Puritia ngā wā tirotiro katoa. He mea nui ngā tirotiro auau hei tirotiro i te mahi a ō pukahukahu me tō ngākau, me te ine i te ahunga whakamua o tō maimoatanga.
  • Tangohia ō rongoā kia rite ki tā te tākuta i tohutohu ai, i te wā kotahi i ia rā. Kaua e whakarerekē i te huarahi e tangohia ai e koe ō rongoā me te kore he tohutohu a tō tākuta.

He aha ngā huringa āhua noho me mahi e au?

Whāia ngā tohutohu a tō tākuta mō ngā huringa āhua noho e hiahia ana koe ki te mahi. I te nuinga o te wā, anei ētahi tohutohu nui:

  • Āta karohia te haere ki ngā kaukau wera, ki ngā sauna, me te haere ki ngā teitei.
  • Whakaarohia te whakamahi i te ārai whānau. He mea mōrearea pea te hāputanga mō te hunga whai PAH. Kōrero ki tō tākuta mēnā kei te whakaaro koe kia hāpu, mēnā rānei ka hāpu koe.
  • Whakakorikori tinana, kia kaha hoki te tinana i ngā wā katoa e taea ana. Kōrero ki tō tākuta mō ngā mahi whakakorikori tinana e haumaru ana māu, me te nui o te mahi e tika ana kia mahia e koe i ia rā. Pātai atu ki tō tākuta i mua i te tīmatanga o tētahi kaupapa whakakorikori tinana hou.
  • Whaia he kai hauora mō te ngākau. Kei roto i tēnei ko ngā kai he iti te ngako kukū, te ngako whakawhiti, me te konutai.
  • Kati te momi hikareti me te whakamahi i ngā hua tupeka. Āta karohia hoki te momi hikareti tuarua.
  • Rapua he tautoko, kaua e ngana ki te haere ko koe anake i roto i tō haerenga PAH. Pātai atu ki tō tākuta mō ngā rōpū tautoko me ngā rauemi.

Āhea ahau me waea atu ki taku tākuta?

Waea atu ki tō tākuta mēnā he pātai āu:

  • Mena he nui ake te tere o te manawa i te 120 ngā pātaki i te meneti (he tere te manawa).
  • Mena ka kino haere te mate manawa, te maremare rānei.
  • Mena he maha ngā wā ka pōuri koe, ka ngoikore rānei.
  • Mena ka pāngia koe e te mamae o te uma, e te kore whakamarie rānei i a koe e mahi ana i te tinana.
  • Mena ka pāngia koe e te ngenge nui, e te ngoikore rānei o tō kaha ki te mahi i ngā mahi o ia rā.
  • Te whakapairuaki, te ngaro rānei o te hiahia kai.
  • Te kore okiokinga, te pōhēhē rānei.
  • Mena ka kino haere tō manawa poto, ina koa ka pōrearea koe i te oho ake.
  • Mena ka kino haere te pupuhi o ō pona waewae, ō waewae, tō puku rānei.
  • Te uaua ki te manawa i ngā mahi o ia rā, i te wā okioki rānei.
  • Te pikinga o te taumaha (2 pauna ia rā, 5 pauna rānei ia wiki).

Āhea ahau me haere ki te Wāhanga Maimoatanga Ohotata (ETU) ?

Mena kei a koe ētahi o ēnei mea, haere ki te rūma whawhati tata, waea atu rānei ki tō nama whawhati tata ā-rohe:

  • Ki te kore te tere o te manawa (120-150 ngā pao i te meneti) e heke iho.
  • Te ngoikore, te ngaronga o te māramatanga.
  • Ngā raruraru mai i tō papu werohanga IV, i tō papu werohanga rānei (pēnei i te mate, te wehenga o te catheter, te turuturu o te wai, te toto, te hē o te papu werohanga IV).
  • Ki te kore te poto o te manawa e memeha ahakoa kua okioki.
  • Te mamae ohorere me te kino o te uma.
  • He mamae ānini ohorere, kino hoki.
  • Te ngoikore ohorere, te pararutiki rānei o ngā ringa, o ngā waewae rānei.

Hei whakamutunga, he karere hei maumahara

He mate whakarerekē te toto toto tiketike o te pūkahukahu (PAH). Mena kua kitea kētia koe, tō whanaunga rānei, kua pāngia e tēnei mate, me whai wā koe ki te ako mō te āhua me ngā mea ka taea e koe te tumanako. Pātai atu ki tō tākuta mō ngā rauemi e whakamārama ana i te mahi a te PAH me te āwhina a ngā maimoatanga.

Ko tētahi o ngā rauemi tino nui ka taea e koe te whiwhi ko te tautoko a ētahi atu i roto i tō ao. Kaua e ngana ki te whakahaere i tēnei mate ko koe anake. Ki te kore tō whānau me ō hoa i te taha, pātai atu ki tō tākuta mō ngā rōpū tautoko me ngā rauemi hapori.

Mena kua tāpaetia tō hoa aroha ki tēnei mate, me mahi i ngā mea katoa kia tautokona ai rātou, kia hono atu hoki ki ētahi atu. Ka taea e te mate te mea kia noho mokemoke tātou i ētahi wā, engari ka taea hoki e ia te whakatata atu i a tātou. Whakamahia tēnei wā hei hanga i tētahi hapori hei āwhina i a koe, i tō hoa aroha rānei kia anga whakamua.


Te toto toto tiketike o te pūkahukahu, PAH, te toto toto tiketike o te pūkahukahu, te poto o te manawa, te mate manawa, te mate pūkahukahu, ngā tohu

Frequently Asked Questions (FAQ)

He aha ngā whakamātautau e whakamahia ana hei tautuhi i te PAH?

Ka whakamahia e tō tīma hauora he huinga o ngā whakamātautau hei whakakore i ētahi atu mate me te tautuhi i te PAH.

He aha ngā rongoā e hoatu ana mō te PAH?

He rerekē ngā momo rongoā hei rongoā i te PAH:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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He kuiti hoki ō oko toto i roto i ō pukahukahu? Me kōrero tātou mō te Pulmonary Arterial Hypertension (PAH)!

He kuiti hoki ō oko toto i roto i ō pukahukahu? Me kōrero tātou mō te Pulmonary Arterial Hypertension (PAH)!

He wā poto te manawa e pā mai ana ki a koe? He wā poto rānei te tawhiti e ngenge ana koe ahakoa e hikoi ana? Kua kite koe kua kikorangi ō matimati me ō ngutu, me te mamae, te kikī rānei o tō uma? Kaua e waiho ēnei hei mea noa iho. Nā te mea i ētahi wā, kei muri i ēnei tohu, tera pea he mate hauora e hiahia ana kia arohia. Ko tētahi o aua mate ko te Pulmonary Arterial Hypertension (PAH) . Ahakoa he ahua whakamataku te ingoa, me kōrero noa tātou mō tēnei mea, me te mārama hoki.

He aha te toto toto tiketike o te pūkahukahu (PAH)? He māmā noa iho...

Ki te whakarāpopototanga, ko te Pulmonary Arterial Hypertension (PAH) he āhuatanga e whaiti ai ngā oko toto iti i roto i ō pūkahukahu (ngā uaua pūkahukahu) . Whakaarohia he rite ki te paipa wai kua āraia, ā, he uaua ki te wai te rere mā roto. Ina whaiti ēnei oko toto, kāore e taea e te toto te rere tika mā roto i ō pūkahukahu. Nā tēnei ka nui rawa te pēhanga i roto i ēnei oko toto, te pēhanga toto rānei. Ko ēnei oko toto ngā mea e kawe ana i te toto rawakore-hāora mai i tō ngākau ki ō pūkahukahu, ki reira ka horoia.

Nā, he aha te mea ka tupu ina tupu tēnei? Me kaha ake te mahi a te taha matau o tō ngākau i te mea noa ki te pupuhi toto ki ngā pukahukahu. He rite ki te hiki i tētahi taumaha taumaha me te piki i tētahi maunga. Ina me kawe e te ngākau tēnei kawenga tāpiri i roto i te wā, ka tīmata te ngoikore haere. Ki te kore e rongoatia tika, ka taea e tēnei āhuatanga, PAH, te whakararu i te maha o ngā raruraru ehara i te mea mō tō ngākau me ō pukahukahu anake, engari mō tō tinana katoa.

Kia maumahara, ko te PAH tētahi momo motuhake o tētahi wāhanga nui e kiia nei ko te toto toto tiketike pūkahukahu . Ko te toto toto tiketike pūkahukahu he pikinga o te pēhanga i roto i ngā oko toto o ngā pūkahukahu nā tetahi take.

He aha te pānga o te PAH ki tō tinana?

Ko te toto toto tiketike o te pūkahukahu (PAH) te nuinga o te wā ka pēhia te taha matau o tō ngākau. Nā te mea ka panaia e tēnei wāhanga o te ngākau te toto kore-hāora ki ngā pūkahukahu. I roto i te wā, ka taea e tēnei toto toto tiketike te arahi ki te ngoikore o te ngākau o te taha matau .

Ehara i te mea koinā anake, ka whakaroa hoki te PAH i te rere o te toto i waenga i te ngākau me ngā pukahukahu. Ko te tikanga he iti iho te toto e tae atu ana ki ngā pukahukahu ki te tiki hāora hou. Nō reira, he iti iho te hāora e tae atu ana ki ētahi atu okana me ngā kiko o tō tinana. Inaa, me whai hāora ia wāhanga o tō tātou tinana kia ora ai. Ki te kore e ranea, ka puta pea ngā raruraru.

He pēhea te kino o te PAH i huaina ai tēnei mate?

He tino kino te mate toto toto tiketike o te pūkahukahu (PAH), ā, i ētahi wā ka morearea ki te ora . Heoi, ki te kitea wawetia, ā, ka rongoātia wawetia, ka roa ake tō oranga, ka pai ake hoki. Koia te mea nui kia aro nui ki ngā tohu.

Ko wai te hunga e tino pāngia ana e te PAH?

Ka pāngia ngā pakeke o ngā tau katoa e te PAH. Heoi, he nui ake te kitea i roto i ngā wāhine , e kitea ana i waenga i te 30 me te 60 tau te pakeke. Kua kitea hoki ko ngā tāne neke atu i te 65 tau te pakeke e pāngia ana e te PAH, he nui ake te tūponotanga ki te pāngia e te mate.

Ka pāngia hoki ngā pēpi nohinohi e tēnei āhuatanga. Mēnā ka pā ki ngā pēpi hou, ka kiia ko te toto toto tiketike pumau i roto i te pēpi hou (PPHN) .

He pēhea te noa o te PAH?

Ki te whakatauritea ki ētahi atu momo toto toto tiketike pūkahukahu, pērā i te toto toto tiketike pūkahukahu i puta mai i te mate manawa, i te mate pūkahukahu rānei, ehara te PAH i te mate tino noa . Ahakoa i roto i tētahi whenua pērā i te Hononga o Amerika, e 500 ki te 1,000 noa iho ngā kēhi hou o te PAH ka kitea i ia tau. I ngā whenua o te Hauāuru, ko te auau he tata ki te 25 i ia miriona.

He aha ngā tohu o te toto toto tiketike o te pūkahukahu (PAH)?

Kāore pea koe e kite i tētahi tohu i ngā wāhanga tōmua o te PAH. Ko te nuinga o te tangata ka tīmata noa te kite i ngā tohu i te whanaketanga haere o te mate. Ko ētahi o ēnei tohu ko:

  • Te tae kikorangi o ngā pito o ngā maihao me ngā ngutu: Me te mea nei kāore he hāora i roto i te toto.
  • Te mamae o te uma, te kikī rānei: Me te mea kei te pēhia tō uma e tetahi.
  • Te whanoke, te ngoikore rānei: Ka puta pea tēnei ina heke te rere o te toto ki te roro.
  • Ngenge: Te tino ngenge , ehara i te mea ko te ngenge anake.
  • Te tere o te manawa, te pakū rānei o te ngakau.
  • Te poto o te manawa: Ka piki ake tēnei i te roanga o te wā. Ahakoa te mahi i ngā mahi iti nei, ka taea te poto o te manawa.
  • Te pupuhi (Edema): Ka tīmata pea te pupuhi i ngā waewae me ngā pona, kātahi ka horapa ki te puku me te kaki.

Ki te kore e rongoatia, ka kino haere ēnei tohumate PAH i roto i te wā. Tērā pea ka kitea e koe kāore e taea e koe te mahi i ngā mahi tino taketake o ia rā me te kore e hiahia ki te manawa, ki te okioki rānei.

He aha ngā take o te toto toto tiketike o te pūkahukahu (PAH)?

Ko te tino take o te PAH ko te pakaru o te arai o ngā uaua toto i roto i ō pukahukahu. Heoi, kāore i te mārama tonu te take o tēnei pakaru.

Ngā take kāore e kitea he pūtake (IPAH Idiopathic)

I ētahi wā, kāore e kitea he tino take . Ka kiia e mātou ngā tākuta he toto toto tiketike pūkahukahu "idiopathic" . He rite ki te mea ngaro.

Ngā take e mōhiotia ana

Heoi, i ētahi wā, he mārama ngā take. Ko ētahi o ngā take e mōhiotia ana o te PAH ko:

  • Ētahi āhuatanga hauora:
  • Mate ngakau whānau
  • Ngā mate rokiroki glycogen
  • Mate HIV
  • Mate ate
  • Ngā mate autoimmune pēnei i te lupus
  • Te toto toto tiketike (te pikinga o te pēhanga i roto i ngā oko toto e anga atu ana ki te ate)
  • Te hemangiomatosis o te capillary pūkahukahu (te tipu rerekē o ngā capillaries i roto i ngā pukahukahu)
  • Te mate ārai-aukati o te manawa (te aukati i ngā uaua i roto i ngā pukahukahu)
  • Schistosomiasis (he mate i puta mai i te pirinoa)
  • Scleroderma (te matotoru o te kiri me te kiko honohono)
  • Ngā whakarerekētanga ira:
  • I te nuinga o te wā, nā te whakarerekētanga o tō ira BMPR2 tēnei. Ko tēnei ira te kaiwhakahaere o te maha o ngā pūtau i roto i ētahi kiko o tō tātou tinana. Nō reira, ina whakarerekētia tēnei ira, ka nui rawa te tipu o ngā pūtau i roto i ngā oko toto iti i roto i ō pūkahukahu. Ina kī tonu ēnei pūtau, ka whaiti ngā pūaha o ngā oko toto.
  • Ka taea e te PAH te horapa i roto i ngā whānau. Ka kiia e mātou he PAH tuku iho . Tata ki te 80% o te hunga whai mate pēnei he whakarerekētanga ira kei roto i te ira BMPR2.
  • Kei ētahi tāngata tēnei ira kua whakarerekētia, engari kāore e whanaketia he PAH e rātou.
  • Ka pāngia pea ētahi tāngata e te PAH ahakoa kāore he whānau e pāngia ana e tēnei mate, nā te whakarerekētanga ira. Ka kiia tēnei ko te PAH tūpono .
  • Ko ētahi rongoā me ngā rongoā:
  • Kua āraia ētahi pire kai , pērā i te rongoā tawhito "fen-phen", engari ka taea tonu te whakaputa PAH i muri i ngā tau maha o te whakamahinga.
  • Ngā raau taero whakangahau , hei tauira ko te kōkaini me te methamphetamine.

Me pēhea te tātaritanga o te toto toto tiketike o te pūkahukahu (PAH)?

He uaua te tautuhi i te PAH nā te mea he rite ngā tohu o te PAH ki ērā o ētahi atu mate. Ka tirotirohia e tō tākuta ō tohu me ō hītori hauora. Ka mahia e rātou he maha ngā whakamātautau (tae atu ki ngā whakamātautau whakaahua me ngā whakamātautau toto) hei kimi mēnā he toto toto tiketike tōu, ā, mēnā he pērā, he aha te momo.

Tērā pea ka tukuna koe e tō tākuta ki tētahi tākuta manawa , ki tētahi tākuta ngakau rānei. Ka whakahaerehia e ēnei tohunga ngā whakamātautau motuhake hei tirotiro i te mahi a tō ngākau me ō pukahukahu. Mā rātou e whakatau mēnā kei a koe te PAH, tētahi atu momo toto toto tiketike rānei. Ka aromatawaihia hoki e rātou te kaha o tō mate.

He maimoatanga motuhake kei reira mō te PAH kāore e wātea ana mō ētahi atu momo toto toto tiketike. Nō reira, me mōhio tō rōpū hauora ki ngā mea katoa e pā ana ki ō pukahukahu me tō ngākau. Mā ēnei mōhiohio ka āwhina i a rātou ki te whakawhanake i te mahere maimoatanga pai rawa atu māu.

He aha ngā whakamātautau e whakamahia ana hei tautuhi i te PAH?

Ka whakamahia e tō tīma hauora he huinga o ngā whakamātautau hei whakakore i ētahi atu mate me te tautuhi i te PAH.

Ki te whakapae tō tākuta kei a koe te PAH i muri i tō whakamātautau tinana, ko te whakamātautau tuatahi ka tonoa e rātou he echocardiogram transthoracic . Ka aromatawaihia e tēnei whakamātautau te hanganga whānui me te mahi a tō ngākau.

Ko ētahi atu whakamātautau ka uru atu ki:

  • Ngā whakamātautau toto: Tirohia te mahi a ngā okana, ngā taumata homoni, me te tautuhi i ngā mate pūtake. Ina koa ngā whakamātautau pēnei i te panera pākia katoa me te tatau toto katoa .
  • Matawai CT o te uma: Hei tirotiro me te whakakore i ētahi atu āhuatanga pēnei i te mate tākihi. (Tērā pea ko te mate tākihi i roto i te tuhinga taketake ko te mate pūkahukahu. Ka tirohia e te matawai CT o te uma ngā pūkahukahu me ngā whekau o te uma. Me kī tātou kei te titiro tātou ki te āhua o ngā pūkahukahu.
  • X-ray o te uma: Hei tirotiro mēnā he nui ake tō ngākau, ō uaua pūkahukahu rānei i te mea noa.
  • MRI o te Ngākau: Arotakehia te āhua o te ventricle matau o tō ngākau (koinei te rūma o te ngākau e pupuhi ana i te toto ki ngā pukahukahu).
  • Polysomnogram (PSG): He tirotiro mō te apnea moe, ka taea te whakararu i te PAH. Ko te PSG he momo whakamātautau moe ka mahia i te pō.
  • Ngā whakamātautau mahi a ō pukahukahu: Tirohia te pai o te mahi a ō pukahukahu.
  • Matawai whakapūngao/whakapūngao toto (VQ): Ka tirohia mēnā he toto totoka i roto i ngā pukahukahu. Mā tēnei whakamātautau ka taea te whakakore i tētahi āhuatanga e kiia nei ko te toto toto tiketike thromboembolic mau tonu .
  • Te whakaurunga o te catheter o te ngākau matau: Ka ine i te pēhanga i roto i ngā oko toto i roto i ō pukahukahu (ngā pēhanga o te uaua pūkahukahu). He mea nui tēnei whakamātautau hei tautuhi i te PAH.
  • Whakamātautau hikoi ono meneti: Tirohia te nui o te whakakori tinana ka taea e koe te manawanui me te nui o te hāora e rere ana i roto i tō toto ina neke koe.

Kōrero ki tō tākuta mō ngā whakamātautau e tika ana kia mahia e koe, me pēhea hoki te whakarite mō aua whakamātautau.

He aha ngā paearu mō te tautuhi i te toto toto tiketike o te pūkahukahu?

Mā te ine i te pēhanga i roto i ngā uaua toto o ōu pūkahukahu ka tātarihia e ngā tākuta te toto toto tiketike o te pūkahukahu. Ko ngā paearu tātaritanga ko te pēhanga o te uaua toto o te pūkahukahu i roto i ōu pūkahukahu he nui ake i te 20 mirimita o te mercury (20 mmHg) i a koe e okioki ana . Ka inehia tēnei uara mā te whakaurunga catheter o te ngākau matau .

He aha ngā maimoatanga mō te toto toto tiketike o te pūkahukahu (PAH)?

Ko ngā whāinga matua o te maimoatanga mō te PAH he whakahaere i te haere whakamua o te mate, me te whakapai ake i te kounga o te oranga. Kāore he maimoatanga kotahi e pai ana mō te PAH katoa. Ka mahi tahi tō tākuta me koe ki te whakatau i te maimoatanga pai rawa atu mō ō hiahia.

Kei roto pea i tō mahere maimoatanga PAH:

  • Te pokanga atrial balloon (BAS): Ko te tikanga o tēnei mahi he mea mahi mā ngā pēpi he whānautanga ngā hapa ngākau, engari i ētahi wā ka whakamahia mā ngā pakeke he PAH. Ka āwhina te pokanga atrial balloon ki te whakaiti i te pēhanga ki te taha matau o te ngākau, ka nui ake te hāora e rere ana i roto i te toto. Ka taea hoki te mahi hei piriti ki te whakawhitinga pūkahukahu.
  • Ngā aukati hongere konupūmā: Ka āwhina ēnei rongoā ki te whakaheke i te toto toto i roto i ngā oko toto o ōu pukahukahu me tō tinana katoa.
  • Ngā rongoā whakaheke toto: E mōhiotia ana ko ngā "pire wai," ka āwhina ēnei rongoā ki te tango i te wai nui mai i te tinana me te whakaiti i te pupuhi.
  • Whakaora hāora: Tērā pea ka hiahiatia tēnei maimoatanga mēnā kāore i te nui te hāora i roto i ō toto. Ka taea e te hāora tāpiri te āwhina i a koe e okioki ana, e moe ana, e whakakorikori tinana ana rānei.
  • Ngā rongoā whakawhanui i ngā oko toto o te pūkahukahu: Ka āwhina ēnei rongoā i ngā oko toto i roto i ō pūkahukahu kia wātea, kia whānui ake hoki te whakatuwheratanga. Ka whakaitihia te taumahatanga ki tō ngākau, ā, ka āwhina hoki ki te whakamama i ō tohumate.

Mō ētahi tāngata he nui te PAH , ko te whakawhitinga pūkahukahu pea te kōwhiringa whakamutunga. Mā tēnei pokanga ka taea e koe te hoatu i tētahi, i ētahi rānei pūkahukahu hou. Ka taea hoki e te whakawhitinga ngākau-pūkahukahu te hoatu i tētahi ngākau hou ki a koe.

He aha ngā rongoā e hoatu ana mō te PAH?

He rerekē ngā momo rongoā hei rongoā i te PAH:

  • Rongoā ā-waha: Ka āwhina ēnei rongoā ki te whakangāwari i ngā oko toto i roto i ngā pukahukahu, ā, ka ārai i te whaiti o aua oko toto. Ka āwhina hoki ēnei rongoā i a koe kia kaha ake te mahi tinana.
  • Ngā rongoā manawa: Whakaorahia ngā uauatanga manawa.
  • Papu werohanga kawe: Ka āwhina tēnei ki te whakatuwhera i ngā oko toto me te whakanui ake i te rere o te toto. Tērā pea ka āwhina tēnei ki te whakapai ake i ō tohu.
  • Ngā rongoā ā-uaua (IV): Ka whakatuwhera i ngā uaua toto, ka whakaora i ngā tohu pēnei i te mamae o te uma me te uaua ki te manawa.

Anei ētahi rongoā kua whakaaetia e te US Food and Drug Administration (FDA) mō ngā tūroro PAH:

  • Ambrisentan (ā-waha)
  • Bosentan (ā-waha)
  • Epoprostenol (IV)
  • Iloprost (manawa)
  • Macitentan (ā-waha)
  • Riociguat (ā-waha)
  • Selexipag (ā-waha)
  • Sildenafil (ā-waha)
  • Tadalafil (ā-waha)
  • Treprostinil (waha, inhalation, papu, IV)

Ngā pānga taha o ngā rongoā PAH

Ko ētahi o ngā pānga taha noa o ngā rongoā e whakamahia ana hei rongoā i te PAH ko:

  • Te pōuri, te ngoikore rānei.
  • Te māhana o te mata, te kaki, ngā ringaringa rānei (te whero).
  • Ngā tohu o te puku pērā i te pupuhi, te whakapairuaki, te ruaki, me te mate korere.
  • Mamae upoko (mamae upoko).
  • Te toto toto iti (hypotension) .
  • Te pupuhi o ngā waewae me ngā pona waewae (Pedal edema) .
  • Te kiri mākūkū.
  • Te ahua o te pupuhi o te ara manawa o runga.

Tērā pea he pānga taha anō kei ētahi rongoā. Kōrero ki tō tākuta mō te whakahaere i ngā pānga taha. I ētahi wā, me whakarerekē pea e tō tākuta te horopeta o tō rongoā.

Ka taea te whakaora katoa i te toto toto tiketike o te pūkahukahu (PAH)?

Ahakoa ka taea e ngā rongoā o nāianei te whakahaere i te whanaketanga o te PAH, kāore e taea te whakakore i te kino kua puta kē . Heoi, kei te rangahau ngā kairangahau i ngā rongoā hou e whakaaro ana rātou ka taea te whakakore i te PAH. Ka taea e ēnei rongoā te whakatika i te kino o ngā pūtau endothelial e whakarārangi ana i ngā oko toto i roto i ō pukahukahu.

Kōrero ki tō tākuta kia mōhio ai koe ki ngā rangahau hou me ngā whakamātautau haumanu mō te maimoatanga PAH.

He aha ngā āhuatanga ka whakanui ake i te mōrearea o te tangata ki te whakawhanake i te Pulmonary Arterial Hypertension (PAH)?

He maha ngā āhuatanga e whakanui ake ai i te mōrearea o te whakawhanake i te PAH:

  • Te mate o te kiko honohono .
  • Te mate Down syndrome .
  • Hītori whānau mō te toto toto tiketike pūkahukahu.
  • Te mate HIV .
  • Te whakamahi i ngā rongoā whakaiti taumaha pērā i te "fen-phen" (dexfenfluramine me te phentermine).
  • Te whakamahi i ngā raau taero turekore (ngā raau taero o te tiriti).

Mena kei te pāngia tētahi o tō whānau e te PAH, pātai atu ki tō tākuta mō ngā whakamātautau ira. Mena kua tāpaetia koe kei te pāngia e te PAH, he mea pai kia pātai atu ki tō whānau kia whakaarohia hoki te whakamātautau ira.

Me pēhea te ārai i te toto toto tiketike o te pūkahukahu (PAH)?

Kāore e taea e tātou te whakahaere i ētahi āhuatanga mōrearea mō te PAH (pērā i ngā whakarerekētanga ira). Heoi, mā te karo i ngā raau taero ture kore ka taea te whakaiti i tō tupono ki te PAH, tae atu ki ngā raruraru hauora maha atu. Me kōrero hoki ki tō tākuta i mua i te tango i tētahi rongoā whakaiti taumaha.

I runga i ngā āhuatanga mōrearea e pā ana ki a koe, ka tūtohu pea tō tākuta i ngā whakamātautau ārai mate pāwera (PAH).

He aha te tirohanga ā-muri mō te hunga e pāngia ana e te mate toto tiketike pūkahukahu (PAH)?

Nā te whanaketanga o te maimoatanga, kua roa ake te ora o te hunga whai PAH i mua. Ko te roanga o tō oranga e whakawhirinaki ana ki ngā āhuatanga maha, tae atu ki te kaha o tō mate me te wawe o te tautuhi i a koe. Kōrero ki tō tākuta mō tō mate.

Ko te mea nui ko te haere tonu i tō maimoatanga me te āta whai i ngā tohutohu a tō tākuta. E rua ngā mea ka taea e koe te mahi hei whakapai ake i tō tupono ki te ora:

  • Hangaia he kete āwhina ohorere. Me mau tonu ētahi taputapu me ngā mōhiotanga. Pātai atu ki tō tākuta he aha ngā mea hei whakauru ki roto i tō kete āwhina, ā, kaua rawa e wehe i te kāinga me te kore he mea pēnei.
  • Tikina ngā kano ārai mate ā-wā e ai ki ngā taunakitanga a tō tākuta. He mea tino nui kia tiakina koe i te rewharewha me te niumōnia.
  • Puritia ngā wā tirotiro katoa. He mea nui ngā tirotiro auau hei tirotiro i te mahi a ō pukahukahu me tō ngākau, me te ine i te ahunga whakamua o tō maimoatanga.
  • Tangohia ō rongoā kia rite ki tā te tākuta i tohutohu ai, i te wā kotahi i ia rā. Kaua e whakarerekē i te huarahi e tangohia ai e koe ō rongoā me te kore he tohutohu a tō tākuta.

He aha ngā huringa āhua noho me mahi e au?

Whāia ngā tohutohu a tō tākuta mō ngā huringa āhua noho e hiahia ana koe ki te mahi. I te nuinga o te wā, anei ētahi tohutohu nui:

  • Āta karohia te haere ki ngā kaukau wera, ki ngā sauna, me te haere ki ngā teitei.
  • Whakaarohia te whakamahi i te ārai whānau. He mea mōrearea pea te hāputanga mō te hunga whai PAH. Kōrero ki tō tākuta mēnā kei te whakaaro koe kia hāpu, mēnā rānei ka hāpu koe.
  • Whakakorikori tinana, kia kaha hoki te tinana i ngā wā katoa e taea ana. Kōrero ki tō tākuta mō ngā mahi whakakorikori tinana e haumaru ana māu, me te nui o te mahi e tika ana kia mahia e koe i ia rā. Pātai atu ki tō tākuta i mua i te tīmatanga o tētahi kaupapa whakakorikori tinana hou.
  • Whaia he kai hauora mō te ngākau. Kei roto i tēnei ko ngā kai he iti te ngako kukū, te ngako whakawhiti, me te konutai.
  • Kati te momi hikareti me te whakamahi i ngā hua tupeka. Āta karohia hoki te momi hikareti tuarua.
  • Rapua he tautoko, kaua e ngana ki te haere ko koe anake i roto i tō haerenga PAH. Pātai atu ki tō tākuta mō ngā rōpū tautoko me ngā rauemi.

Āhea ahau me waea atu ki taku tākuta?

Waea atu ki tō tākuta mēnā he pātai āu:

  • Mena he nui ake te tere o te manawa i te 120 ngā pātaki i te meneti (he tere te manawa).
  • Mena ka kino haere te mate manawa, te maremare rānei.
  • Mena he maha ngā wā ka pōuri koe, ka ngoikore rānei.
  • Mena ka pāngia koe e te mamae o te uma, e te kore whakamarie rānei i a koe e mahi ana i te tinana.
  • Mena ka pāngia koe e te ngenge nui, e te ngoikore rānei o tō kaha ki te mahi i ngā mahi o ia rā.
  • Te whakapairuaki, te ngaro rānei o te hiahia kai.
  • Te kore okiokinga, te pōhēhē rānei.
  • Mena ka kino haere tō manawa poto, ina koa ka pōrearea koe i te oho ake.
  • Mena ka kino haere te pupuhi o ō pona waewae, ō waewae, tō puku rānei.
  • Te uaua ki te manawa i ngā mahi o ia rā, i te wā okioki rānei.
  • Te pikinga o te taumaha (2 pauna ia rā, 5 pauna rānei ia wiki).

Āhea ahau me haere ki te Wāhanga Maimoatanga Ohotata (ETU) ?

Mena kei a koe ētahi o ēnei mea, haere ki te rūma whawhati tata, waea atu rānei ki tō nama whawhati tata ā-rohe:

  • Ki te kore te tere o te manawa (120-150 ngā pao i te meneti) e heke iho.
  • Te ngoikore, te ngaronga o te māramatanga.
  • Ngā raruraru mai i tō papu werohanga IV, i tō papu werohanga rānei (pēnei i te mate, te wehenga o te catheter, te turuturu o te wai, te toto, te hē o te papu werohanga IV).
  • Ki te kore te poto o te manawa e memeha ahakoa kua okioki.
  • Te mamae ohorere me te kino o te uma.
  • He mamae ānini ohorere, kino hoki.
  • Te ngoikore ohorere, te pararutiki rānei o ngā ringa, o ngā waewae rānei.

Hei whakamutunga, he karere hei maumahara

He mate whakarerekē te toto toto tiketike o te pūkahukahu (PAH). Mena kua kitea kētia koe, tō whanaunga rānei, kua pāngia e tēnei mate, me whai wā koe ki te ako mō te āhua me ngā mea ka taea e koe te tumanako. Pātai atu ki tō tākuta mō ngā rauemi e whakamārama ana i te mahi a te PAH me te āwhina a ngā maimoatanga.

Ko tētahi o ngā rauemi tino nui ka taea e koe te whiwhi ko te tautoko a ētahi atu i roto i tō ao. Kaua e ngana ki te whakahaere i tēnei mate ko koe anake. Ki te kore tō whānau me ō hoa i te taha, pātai atu ki tō tākuta mō ngā rōpū tautoko me ngā rauemi hapori.

Mena kua tāpaetia tō hoa aroha ki tēnei mate, me mahi i ngā mea katoa kia tautokona ai rātou, kia hono atu hoki ki ētahi atu. Ka taea e te mate te mea kia noho mokemoke tātou i ētahi wā, engari ka taea hoki e ia te whakatata atu i a tātou. Whakamahia tēnei wā hei hanga i tētahi hapori hei āwhina i a koe, i tō hoa aroha rānei kia anga whakamua.


Te toto toto tiketike o te pūkahukahu, PAH, te toto toto tiketike o te pūkahukahu, te poto o te manawa, te mate manawa, te mate pūkahukahu, ngā tohu

Frequently Asked Questions (FAQ)

He aha ngā whakamātautau e whakamahia ana hei tautuhi i te PAH?

Ka whakamahia e tō tīma hauora he huinga o ngā whakamātautau hei whakakore i ētahi atu mate me te tautuhi i te PAH.

He aha ngā rongoā e hoatu ana mō te PAH?

He rerekē ngā momo rongoā hei rongoā i te PAH:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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