Kei te pāngia koe e ngā whara kiri ohorere, kino hoki? Me ako tātou mō te Pyoderma Gangrenosum!

Kua pāngia koe e tētahi kiri pupuhi iti, whero rānei i te tīmatanga, ā, ka huri hei mate pukupuku nui, mamae? Ka pā pea tēnei ki ngā wāhi maha, engari ka pā pea ki ētahi wāhi o tō tinana. He mate tēnei e hiahia ana kia arohia, ā, he uaua pea. I tēnei rā ka kōrero tātou mō tētahi mate kiri e kiia nei ko te Pyoderma Gangrenosum, he mate onge engari he mea nui kia mōhiotia. Kaua e manukanuka, kia māmā noa iho.

He aha tēnei Pyoderma Gangrenosum?

He māmā noa iho, he mate kiri mau tonu te pyoderma gangrenosum, arā, he roa te wā e mau tonu ana, ā, ka hokihoki mai . Ko te mea ka tupu, ka tīmata tō kiri ki te puta he mirumiru iti, he rerekē te tae (tērā pea he whero, he papura, he kikorangi, he parauri, he mangu rānei), he mirumiru kī tonu i te wai (bullae). Ko te mea mōrearea ake , ka tere te tipu haere o ēnei, ka honoa, ka huri hei mate hōhonu, tuwhera (ngā mate pukupuku) .

Whakaarohia te āhua mēnā i tīmata mai he whewhe iti, ā, i roto i ētahi rā ka huri hei mate puku mamae, he rite te rahi ki te nikara? Koinei te āhua o tēnei. Tērā pea ka pāngia ētahi tāngata e te mate puku kotahi, engari i ngā wā tino kino, ka puta mai pea ngā mate puku maha i te wā kotahi. Ka tino mamae ēnei mate puku.

He mea nui, he maha ngā wā e hono ana te pyoderma gangrenosum ki ētahi atu mate pūnaha , arā, ehara i te mea he raruraru kiri anake.

Ko wai te mea tino tūpono ka pāngia e tēnei?

Ka pā te Pyoderma gangrenosum i ngā tau katoa, engari he tino onge i roto i ngā tamariki . He mea noa i roto i ngā wāhine i waenga i te 20 me te 50 tau te pakeke. Tērā pea ka nui ake te tūponotanga ka pāngia koe e te pyoderma gangrenosum mēnā kei a koe tētahi o ēnei āhuatanga e whai ake nei:

• Te mate rumatiki - He mate tēnei e mumura ai ngā hononga.
• Te mate puku nui - He mate mumura e puta ai ngā mate puku i roto i te whekau nui.
• Te mate a Crohn - Ko tētahi atu mate mumura e puta ana i roto i te ara nakunaku.
• Ko ētahi momo mate pukupuku, hei tauira, ngā mate pukupuku toto pērā i te leukemia, te lymphoma rānei.

E kiia ana ka pā tēnei mate ki te kotahi i roto i te kotahi rau mano tāngata i te Hononga o Amerika . Ko te tikanga, ehara i te mea noa.

He aha ngā pānga o tēnei ki te tinana? He aha ngā tohu?

Ka puta mai i te Pyoderma gangrenosum ngā pupuhi iti, kua memeha te tae, me te mumura, arā, te pupuhi me te whero, i runga i tō kiri. Ka puta pea ēnei pupuhi ki ngā wāhi katoa o te tinana, engari ko te nuinga o te wā ka kitea i ngā waewae, i ngā pona waewae, me ngā waewae (ngā pito o raro) .

Ka tere te pahū o ēnei mirumiru, ka huri hei mate pukupuku nui, mamae, kātahi ka horapa.Ko ngā tohu matua ko:

• He iti, he rerekē te tae (whero, papura, kikorangi, parauri, mangu rānei) ngā pupuhi kapi tonu i te pūkahukahu. Ka tere te whakanui ake .
• Ka puta ngā mate pukupuku tuwhera (ngā whewhe). Ka ara ake ngā taha huri noa i ēnei mate, ā, ka kitea mārama .
• Te pupuhi me te mamae nui huri noa i te patunga.
• Ka pāngia pea ētahi tāngata e te kirika .
• Tērā pea ka pā mai te mamae o ngā hononga .

I ētahi wā ka tino nui, ka tino hōhonu hoki ēnei patunga, ā, kāore e taea te manawanui ki te mamae.

Kua whakaatuhia e ētahi rangahau tae atu ki te 70% o te hunga whai pyoderma gangrenosum ka pāngia pea e te neke atu i te kotahi ngā mate (ngā mate honohono) i te wā kotahi. Ina honoa te pyoderma gangrenosum ki ētahi atu mate, e kiia ana ka piki ake te mōrearea o te mate tae atu ki te 30%. Nō reira, ehara tēnei i te mea hei mea māmā noa iho.

He mate pūnaha ārai mate tēnei?

Ae, e whakaponohia ana ko te pyoderma gangrenosum he mate pūnaha ārai mate . I roto i ngā kupu māmā, ko te pūnaha ārai mate o tō tinana, arā, ko te pūnaha ārai mate, ka whakaeke i ō ake pūtau kiri. Mō ētahi tāngata, ka ora te pyoderma gangrenosum ina rongoatia ngā mate kua whakahuatia ake nei.

He aha te whanaketanga o te pyoderma gangrenosum?

Kāore anō kia mōhiotia e ngā tohunga hauora te tino take , engari neke atu i te haurua o te hunga whai pyoderma gangrenosum he mate kē atu ā rātou (pērā i te mate rumatiki, te leukemia, me te mate a Crohn), e ai ki te kōrero i mua ake nei.

Hei tāpiritanga, ka puta pea te pyoderma gangrenosum i muri i te whara kiri, te karawarawa, te pokanga rānei (pathergy) . Whakaarohia he karawarawa iti i tō ringaringa, i tētahi pokanga iti rānei, ā, koinei te wāhi ka tīmata ai tēnei mate. I ētahi wā ka puta anō ēnei patunga i te taha o te wāhi stoma i muri i te pokanga. Ka kiia tēnei ko te peristomal pyoderma gangrenosum.

He mate hopuhopu tēnei?

Kāo. Kāore te Pyoderma gangrenosum e horapa . Kāore e taea te horapa mai i tētahi tangata ki tētahi atu mā te pa o te kiri ki te kiri. He āwangawanga tēnei mō te tini o te tangata, nō reira he mea nui kia mārama ki tēnei.

Me pēhea te mōhio o ngā tākuta ki tēnei?

Ki te pono, he uaua te tautuhi i te pyoderma gangrenosum . Kāore he whakamātautau tuturu hei whakaū koinei te mate. Nō reira, he maha ngā wā ka whakahaerehia e ngā tākuta he whakamātautau hei whakakore i ētahi atu mate ka puta he raruraru kiri rite. Arā, ka whakarite tuatahi rātou kāore he mate kē atu he rite ngā tohu. Hei tauira:

• Ngā momo mate urutā.
• Ngā mate pukupuku kiri.
• Te mumura o te kiri i roto i ngā oko toto.
• Te mate Lupus.
• He āhuatanga e kiia nei ko te mate Sweet.

Ko ngā whakamātautau mō tēnei pea ko:

• Ngā whakamātautau toto.
• Te tango i tētahi wahi iti o te kiri hei tirotiro (Biopsy).
• Te whakamātautau i te hinu wheua - ina koa mēnā kei te whakapaetia he mate pēnei i te mate pukupuku toto.
• Te tirotiro i te pūrotu.
• Koronokopiko - mēnā e whakapaetia ana he mate pēnei i te mate a Crohn.

I muri i te otinga o ēnei whakamātautau katoa, me te whakakore i ngā mea katoa, kātahi ka whakatau te tākuta he pyoderma gangrenosum tēnei.

He aha ngā maimoatanga?

He maha ngā huarahi maimoatanga mō te pyoderma gangrenosum. He mea nui te tautuhi wawe me te maimoatanga hei ārai i te whara .

Te maimoatanga mō ngā mate noa, iti iho te kino

Ki te kore e tino kino ngā patunga, ka tohua pea e te tākuta he kirīmi, he hinu rānei hei pani. Kei roto i ēnei:

• Corticosteroids: He rongoā ēnei hei whakaiti i te mumura. Ka taea te pani ki ngā patunga hei kirīmi, hei pire rānei. Hei tauira: cortisone, prednisone. Heoi anō, ka pā mai pea ngā pānga taha pēnei i te hiahia kai nui, te taumaha nui, te rerekētanga o te wairua, te hakihaki, me te kore moe.
• Ngā rongoā anti-inflammatory kore-steroidal (NSAID): He rongoā mamae ēnei. Hei tauira: aspirin, ibuprofen. Ka puta te hau , te pupuhi, te mamae o te puku, te whakapairuaki, te ruaki, te korere, me te mate puku.
• Kirimi kiri hiriwa sulfadiazine: He kirimi paturopi tēnei e pania ana ki ngā wera hei ārai i te mate. I ētahi wā ka whakamahia hoki mō tēnei mate. Ka pā mai te mākūkū, te kirika, te makariri, te whara o te kiri, me te aro ki te rā.

He paku nanakia?

Mena he kino rawa te whara, ka tohua pea e te tākuta ngā maimoatanga penei:

• Ngā rongoā ārai mate: Ka mahi ēnei mā te whakaiti i te kaha o tō pūnaha ārai mate ki te kino i tōna ake tinana. Hei tauira: mycophenolate, cyclosporine.
• Ngā rongoā koiora: He momo rongoā hou ēnei. Ka mahi mā te aro ki ngā pūmua motuhake o te tinana e puta ai te mumura. Hei tauira: infliximab, adalimumab, ustekinumab.
• Te whakaora hāora hyperbaric: Kei roto i tēnei ko te tuku i te 100% hāora ki roto i tētahi rūma motuhake. E kiia ana ka tere ake te whakaora o ngā kiko o te tinana.

Me ako anō hoki tātou mō te pokanga.

I ētahi wā, he pai pea te tango pokanga i ngā kiko mate mai i te patunga (te tango i ngā kiri pakaru). Heoi, he mōrearea anō hoki tēnei .Nā te mea ka taea e te kino o te kiri (pathergy) te whakararu i ngā tohu o te pyoderma gangrenosum, me tino tupato te mahi i tēnei, me te whai whakaaro anō hoki a tō tākuta.

I ētahi wā ka taea te mahi i te tāmi kiri . Ko te tikanga ka tangohia te kiri mai i tētahi wāhanga hauora o te tinana ka whakatōkia ki te wāhi i whara ai.

He aha ngā mea me mōhio koe hei tangata whai i tēnei mate?

Mena kei a koe te pyoderma gangrenosum, ka taea e tetahi momo whara ki tō kiri – motu, karawarawa, marō – te whakararu i ō tohumate . Nō reira, me tino tupato koe. Whakaarohia kei te mahi koe i te māra, i te kīhini rānei, ā, ahakoa he karawarawa iti noa iho, ka taea te noho hei raruraru nui.

He mea nui anō hoki te pupuri i te ma o ngā patunga hei ārai i te mate .

• Horoia rawatia ngā patunga ki te wai ma, ki te hopi me te wai rere.
• Kātahi ka āta hipokina te patunga ki tētahi takai kore-piri. Mā tēnei ka ārai i te paru me ngā huakita kei uru mai.
• Mā tō tākuta kiri koe e hoatu ētahi atu kōrero mō te pupuri i te patunga kia ma, me te whakamahi i ngā takai. Me āta whai i aua tohutohu.
• Ki te mea kua hoatu he hinu kakara ki a koe, horoia te patunga, pania te hinu kakara, kātahi ka takai.

Mō ngā patunga kino, ka tūtohu pea tō tākuta i tētahi takai hydrocolloid . Mā ēnei ka tiaki i te patunga mai i te mirimiri me te mate. Ka "rewa" ēnei ki roto i te kiri i roto i ngā rā e rua, e toru rānei.

Kia pēhea te roa o te wā e ora ai?

He uaua te rongoā i te mate Pyoderma gangrenosum. Ahakoa te rongoā tika, ka roa pea ngā wiki, i ētahi wā he marama, hei whakaora i ngā patunga. Nō reira, me manawanui koe.

Ka taea te ārai i tēnei?

Nā te mea kāore i te mōhiotia te tino take, he uaua ki te kī me pēhea te ārai . Heoi, ki te mea he āhuatanga mōrearea tōu pērā i te mate toto toto, te mate mumura rānei o te puku, ā, ka puta he raruraru kiri hou ki a koe (ina koa ko ngā mate kiri e tere tipu ana) , me kōrero tonu atu ki tō tākuta . Me tono atu ki tō tākuta kia tukuna koe ki tētahi tohunga kiri, ki tētahi atu tohunga rānei he wheako ki te pyoderma gangrenosum.

Āhea ahau me toro atu ki te tākuta?

Me toro atu koe ki te tākuta i roto i ēnei āhuatanga:

• Mena kei a koe te mate mumura o te puku, te mate rumatiki, te mate toto rānei, ā, ka puta he mirumiru, he mate pukupuku rānei ka tere te rahi .
• Mena kei te āhua pangia tō patunga (whero, papura, hina, mā rānei, pupuhi, mamae rānei).
• Mena ka puta he tohu hou ki a koe.
• Mena ka pāngia koe e ngā pānga taha kino i muri i te tango i te rongoā.

Ngā pātai nui hei pātai atu ki tō tākuta

Ina haere koe ki te tākuta, he mea tino nui kia pātai koe i ēnei pātai:

• He aha te āhua o tō kī he pyoderma gangrenosum tōku?
• Ki te kore he pyoderma gangrenosum i roto i ahau, he aha atu anō te mate kiri?
• He aha ngā momo whakamātautau e tumanakohia ana e koe?
• He aha te momo rongoā, maimoatanga rānei e taunaki ana koe?
• Ka taea e koe te homai he kirīmi hei pani māku, he rongoā rānei hei inu māku?
• He aha te rārangi katoa o ngā pānga taha o ēnei rongoā me ngā maimoatanga?
• He aha atu anō taku mahi hei whakaiti i aku tohumate?
• Me toro atu ahau ki tētahi tākuta kiri, ki tētahi taote pokanga kirihou, ki tētahi tākuta puku, ki tētahi tākuta ārai mate, ki tētahi atu tohunga rānei?

He mea tino nui kia pātaihia ēnei pātai, kia mārama ai hoki koe ki tōu āhuatanga.

He aha te rerekētanga i waenga i te Pyoderma Gangrenosum me te Ecthyma Gangrenosum?

He āhua ōrite ēnei ingoa e rua, nō reira ka pōhēhē pea.

He mate kiri onge te Ecthyma gangrenosum i puta mai i te Pseudomonas bacteraemia, he huakita e kitea nuitia ana i roto i te wai me te oneone. Ka taea hoki e ia te whakararu i te kiri me te pirau o ngā kiko e karapoti ana. Ko te nuinga o te wā ka pā ki te hunga he ngoikore te pūnaha ārai mate .

Ka puta hoki ngā whara kiri i te Pyoderma gangrenosum . Kāore i te mōhiotia te tino take. E whakaarohia ana he mate pūnaha ārai mate. Heoi, ehara i te mea he mate e pā ana ki te hunga ngoikore te pūnaha ārai mate .

He rerekē ngā momo whara pyoderma gangrenosum?

Āe, e whā ngā momo matua o ngā whara pyoderma gangrenosum:

• Te pyoderma gangrenosum matarohia: Koinei te momo tino noa. Ko ngā mate pāwera ka puta i ngā waewae.
• Pyoderma gangrenosum kāore i te tino kitea, he bullous rānei: Ka puta mai tēnei momo he pupuhi kī tonu i te wai. Ka kitea i ngā ringaringa. He nui ake te kitea i roto i te hunga e pāngia ana e te leukemia.
• Pustular pyoderma gangrenosum: Ka puta mai he pupuhi iti, kī tonu i te pus (pustules) i runga i ngā ringa me ngā waewae. He nui ake te kitea o tēnei i roto i te hunga e pāngia ana e te mate puku mumura.
• Pyoderma gangrenosum huawhenua: Kāore tēnei momo whara e mamae i te nuinga o te wā.

Hei whakamutunga, ngā mea hei maumahara

He mate te Pyoderma gangrenosum e tīmata ana hei pupuhi iti i runga i te kiri, ā, ka tere te huri hei whara nui. He uaua ki te tautuhi me te rongoā , nō reira me manawanui kōrua ko tō tākuta.

Kia maumahara, he mea tino nui kia tūpato ki ngā whara katoa ki tō kiri, nā te mea ka ara ake pea he whara hou.

Mena he kino te pyoderma gangrenosum, ā, he maha atu anō ō mate tāpiri, ka pā mai he mamae nui, he kōhatu, tae atu ki ngā raruraru e morearea ana ki te ora. Nō reira, ki te mea he mate pūnaha ārai mate tōu, ā, kei te tere te tipu o ngā whara kiri, rapua tonutia he awhina hauora. Mā te kitenga wawe me te maimoatanga ka āwhina i a koe kia ora ake. Kaua e mataku , engari kia tūpato.

Pyoderma Gangrenosum, Ngā Mate Kiri, Ngā Whara, Ngā Mate Pukupuku, Te Pūnaha Ārai Mate, Te Kiri, Ngā Mate Pūmau