Kodi mudamvapo za matenda a Behçet? Dzinali lingamveke lachilendo pang'ono. Koma kwenikweni ndi vuto lovuta, koma lotha kuthetsedwa lomwe lingakhudze ziwalo zosiyanasiyana za thupi lathu. Chifukwa chake, tiyeni tikambirane za izi mwatsatanetsatane lero, mwachidule, monga kulankhula ndi mnzanu.
Kodi matenda a Behçet ndi chiyani?
Mwachidule, matenda a Behçet ndi
kutupa kosatha kwa mitsempha yamagazi m'matupi athu. Madokotala amatchanso kuti "vasculitis." Uwu ndi mkhalidwe womwe mitsempha yamagazi imatupa, kufiira, komanso kupweteka. Imatha kukhudza mitsempha ikuluikulu yamagazi (mitsempha) komanso mitsempha yaying'ono yamagazi (mitsempha). Matendawa nthawi zina amatchedwa "matenda a Silk Road" chifukwa amapezeka kwambiri m'madera omwe ali m'mbali mwa Silk Road m'mbiri.
Ndani amene ali ndi mwayi waukulu wopeza matendawa?
Matenda a Behçet amatha kukhudza aliyense padziko lonse lapansi. Komabe, amapezeka kwambiri m'maiko ena. Mwachitsanzo, amapezeka kwambiri kumpoto kwa Turkey, mayiko ozungulira Nyanja ya Mediterranean, Middle East ndi East Asia. Siwofala kwambiri m'maiko ngati United States. Zizindikiro nthawi zambiri zimayamba kuonekera
pakati pa zaka 20 ndi 30. Komabe, amatha kuchitika pa msinkhu uliwonse. Ngakhale poyamba ankaganiza kuti amakhudza amuna ndi akazi mofanana, maphunziro ena akusonyeza kuti
amuna ali ndi mwayi wochuluka wopeza matendawa .
Kodi zizindikiro za matendawa ndi ziti? Kodi timamva bwanji?
Ichi ndiye chinthu chofunikira kwambiri. Zizindikiro za matenda a Behçet zimatha kusiyana malinga ndi munthu. Izi zikutanthauza kuti zizindikiro zomwe muli nazo sizingakhale zofanana ndi za munthu wina. Koma pali zizindikiro zingapo zazikulu zomwe zimapezeka kawirikawiri.
Zilonda pakamwa
Ichi ndi
chizindikiro choyamba chomwe anthu ambiri amachizindikira . Chili ngati zilonda za mkamwa zomwe nthawi zambiri timazipeza mkamwa mwathu, koma zimakhala
zazikulu, zofala, komanso zopweteka kwambiri . Anthu ena amatha kukhala ndi zilonda za mkamwa izi zizindikiro zina zisanachitike. Zitha kuwonekera pamilomo, lilime, komanso mkati mwa masaya.
Tangoganizirani, mumakhala ndi zilonda mkamwa nthawi zonse, zimapweteka kwambiri moti simungathe kudya kapena kumwa, ndipo ngakhale mutamwa mankhwala, zimabwereranso patatha masiku angapo. Zimenezi ndi choncho.
Zilonda za m'mimba
Monga zilonda za mkamwa, zilonda zoberekera zimathanso kuchitika. Izi zimathanso kukhala zopweteka. Zithanso kuchitika pa chidendene mwa amuna komanso m'chimake mwa akazi. Komabe, sizili zofala ngati zilonda za mkamwa.
Kutupa kwa maso
Kutupa kwa maso ndi chizindikiro chachikulu cha matendawa. Izi zingayambitse
kufiira, kupweteka, kusawona bwino, kufooka kwa kuwala, komanso maso otuluka madzi . Ngati simunalandire chithandizo choyenera,
zingayambitse kutayika kwa masomphenya.Pali mwayi. Pali malipoti akuti mtundu uwu wa kuwonongeka kwa maso ndi wofala kwambiri m'maiko monga Middle East ndi Japan.
Mavuto a khungu
Mavuto a pakhungu nawonso ndi ofala. Nthawi zina, ziphuphu zonga ziphuphu ndi tinthu tofiira (erythema nodosum) zimatha kuwoneka. Ziphuphu zimenezi zimakhala zopweteka kuzikhudza. Nthawi zina, zilonda za pakhungu zimatha kuyamba. Zina mwa izi zimakhala zakunja, pomwe zina zimakhala zakuya. Chinthu china chachilendo ndichakuti
ngati khungu lakanda kapena kubayidwa, malowo amasanduka ofiira ndipo chiphuphu chaching'ono chidzawonekera mkati mwa masiku ochepa . Madokotala amatcha izi kuti "kuyesa kwabwino kwa matenda."
Kupweteka kwa mafupa
Kupweteka kwa mafupa ndi kofala pakati pa odwalawa. Kumakhudza
akakolo, mawondo, zigongono, ndi chiuno makamaka . Mafupa amatha kutupa, kufiira, komanso kupweteka akakhudza. Komabe, nthawi zambiri sawononga mafupa kwamuyaya.
Kutupa kwa mitsempha
Kutupa mkati mwa mitsempha yamagazi kungayambitse
magazi kuundana, kutsekeka , kapena kutsekeka kwathunthu kwa mitsempha yamagazi. Izi zingakhudze mitsempha yakunja, yomwe ili pafupi ndi khungu, komanso mitsempha yakuya, yomwe ili mkati mwa thupi. Nthawi zina, mtsempha waukulu kwambiri m'thupi lathu, vena cava, ungakhudzidwe, zomwe zingayambitse mavuto aakulu azaumoyo. Mavuto a mitsempha yamagazi amenewa amayamba chifukwa cha kutupa, osati chifukwa cha vuto la magazi kuundana.
Kulowerera muubongo
Nthawi zina matendawa amathanso kukhudza ubongo. Makamaka, nembanemba zomwe zimaphimba ubongo (meninges). Kenako zizindikiro
monga malungo, mutu waukulu, kuuma kwa khosi, kuvutika kugwirizanitsa kuyenda poyenda zimatha kuoneka. Nthawi zina
, sitiroko imathanso kuchitika. Izi zimachitika pamene mtsempha wamagazi muubongo watsekedwa kapena kuphulika.
Makhalidwe a m'mimba (GI)
Mavuto angachitikenso m'mimba, kutanthauza m'matumbo. Mutha kuwona zinthu monga
kupweteka m'mimba ndi magazi m'chimbudzi . Izi zili choncho chifukwa mabala mkamwa ndi m'malo oberekera, komanso mabala mkati mwa matumbo. Mabala awa m'matumbo ndi owopsa pang'ono, chifukwa angayambitse kutuluka magazi m'matumbo kapena kuphulika.
Zotsatirapo pa ziwalo zina
Ngakhale kuti matendawa ndi osowa kwambiri, amathanso kukhudza ziwalo zina monga mapapo, impso, ndi mitsempha yayikulu yamagazi (aorta).
N’chifukwa chiyani matenda a Behçet amachitika? Kodi chifukwa chake n’chiyani?
Chifukwa chenicheni cha matendawa sichinadziwikebe . Asayansi akufufuzabe. Lingaliro limodzi ndilakuti mwina ndi "matenda a autoimmune." Mwachidule, zikutanthauza kuti
chitetezo chathu chamthupi, chomwe chimatiteteza ku matenda, chimaukira maselo athu athanzi molakwika.Kuukira kumeneku ndi komwe kumayambitsa matenda otupa omwe atchulidwa pamwambapa. Zizindikiro zina za majini, monga `(HLA-B5)` ndi `(HLA-B51), zimapezeka mwa anthu ena omwe ali ndi matendawa. Komabe, si aliyense amene ali ndi zizindikiro za majini amenewa amene amakhala ndi matenda a Behçet. Chifukwa chake, majini okha sanganenedwe kuti ndi omwe amachititsa. Ofufuza amakhulupiriranso kuti
mwa anthu omwe ali ndi matenda amenewa m'majini awo, pali lingaliro lakuti matendawa angachitike chifukwa cha matenda (mabakiteriya kapena mavairasi) . Izi zikutanthauza kuti zinthu zonse za majini ndi zachilengedwe zingakhudze matendawa.
Ndani ali pachiwopsezo chachikulu chotenga matendawa?
Anthu ena ali pachiwopsezo chachikulu chotenga matendawa kuposa ena:
- Anthu okhala m'madera omwe matendawa amapezeka kwambiri (monga Turkey, Middle East).
- Anthu azaka zapakati pa 20 ndi 40 .
- Anthu omwe ali ndi majini enaake (HLA-B5 kapena HLA-B51)
- Amuna (amuna ali pachiwopsezo chachikulu chotenga matendawa kuposa akazi).
Kodi matendawa amapezeka bwanji molondola? (Kuzindikira)
Palibe njira imodzi yoyezera matenda a Behçet yomwe yachitika m'ma laboratories . Madokotala amazindikira matendawa kutengera zizindikiro zanu. Amafufuza makamaka:
- Kubwerezabwereza kwa zilonda pakamwa pafupipafupi (nthawi zambiri katatu pachaka).
- Kuphatikiza apo, ziyenera kukhala ndi makhalidwe awiri mwa awa :
- Kuvulala m'malo oberekera.
- Kutupa kwa maso.
- Mavuto a khungu.
- Kuyesa kwabwino kwa matenda - Izi zikutanthauza kuti ziphuphu zofiira, ngati matuza zimawonekera patatha masiku ochepa kuchokera pamene khungu labayidwa kapena kubayidwa. Izi zikupereka lingaliro la momwe chitetezo cha mthupi chikugwira ntchito.
Kuti mudziwe matendawa molondola, ndikofunikira kuchotsa matenda ena omwe amayambitsa zilonda pakamwa zomwe zimafanana ndi
matenda a Behçet . Mwachitsanzo, `(systemic lupus)`, `(matenda a Crohn)` (matenda otupa m'matumbo), ndi mitundu ina ya `(vasculitis)`. Dokotala wanu angafune kuti muyesedwe magazi kuti athetse matenda ena awa.
Kodi iyi ndi matenda obadwa nawo?
Palibe umboni womveka bwino wosonyeza kuti matenda a Behçet ndi obadwa nawo . Milandu yambiri imachitika mwachisawawa, popanda mbiri ya banja. Ngakhale kuti milandu yochepa kwambiri yanenedwa mwa anthu angapo a m'banja limodzi, palibe njira yodziwikiratu yobadwira nawo.
Kodi mankhwala a izi ndi otani? (Chithandizo)
Palibe mankhwala a matendawa pakadali pano . Komabe, pali mankhwala angapo omwe angathandize kuchepetsa zizindikiro:
- Mankhwala a Corticosteroids (monga prednisone): Awa ndi mankhwala akuluakulu. Mankhwalawa amachepetsa kutupa ndi kugwira ntchito mopitirira muyeso kwa chitetezo cha mthupi.
- Colchicine (Colcrys®): Izi zimathandiza ndi zilonda za mkamwa, zilonda zoberekera, komanso nthawi zina kupweteka kwa mafupa.
- Other immunosuppressant mankhwala : Zitsanzo ndi methotrexate (Trexall®, Rasuvo®), azathioprine (Imuran®, Azasan®), cyclophosphamide (Cytoxan®, Neosar®), ndi cyclosporine (Gengraf®, Neoral®, Sandimmune®). Pazovuta kwambiri, anti-TNF (Tumor Necrosis Factor) biologics monga infliximab (Remicade®), etanercept (Enbrel®), ndi tocilizumab (Actemra®) amagwiritsidwanso ntchito.
Chofunika: Mankhwala oletsa chitetezo chamthupi awa amatha kuchepetsa mphamvu ya thupi lanu yolimbana ndi matenda, zomwe zimawonjezera chiopsezo chanu chotenga matenda ena.
- Apremilast (Otezla®) : Iyi ndi piritsi yomwa. Yavomerezedwa kuchiza zilonda pakamwa mwa anthu omwe ali ndi matenda a Behçet.
Kutengera ndi kuopsa kwa vuto lanu, dokotala wanu angayese kuwongolera zizindikiro pogwiritsa ntchito zinthu monga madontho a m'maso, zotsukira pakamwa, ndi mafuta a pakhungu musanagwiritse ntchito mankhwalawa.
Kodi mungakhale ndi chiyembekezo chotani pamene mukukhala ndi matendawa?
Matenda a Behçet ndi
matenda osatha . Izi zikutanthauza kuti, ngakhale atalandira chithandizo, nthawi zina amatha kutha ndikubwereranso. Izi zimapangitsa kuti zikhale zovuta kunena momwe chithandizocho chimayendera bwino. Odwala ambiri amakumana ndi zizindikirozi nthawi zina m'miyoyo yawo yonse. Komabe,
anthu ambiri amatha kukhala ndi moyo wabwinobwino komanso wodzaza ndi zinthu .
Kodi mungatani kuti muthane bwino ndi matendawa?
Pali njira zingapo zothandizira mukakhala ndi matendawa:
- Kusamala pakati pa kupuma ndi kuchita masewera olimbitsa thupi : Kuchita masewera olimbitsa thupi nthawi zonse kungathandize thupi lanu kumva bwino, kuchepetsa kupweteka kwa mafupa ndi madera ena ovuta. Komanso, kupuma pang'ono zizindikiro zikakula kwambiri ndikwabwino pa thanzi lanu la maganizo ndipo kungachepetse mphamvu ya zizindikirozo.
- Kugawana zomwe mwakumana nazo komanso kukhala ndi anthu ammudzi : Izi zikutanthauza kupeza ndikulankhula ndi anthu ena omwe ali ndi vuto lomweli. Izi zitha kukhala zovuta chifukwa vutoli silichitika kawirikawiri. Koma dokotala wanu angakuthandizeni kupeza anthu omwe adakumanapo ndi vuto lomweli.
Kodi matendawa angakhale oopsa?
Chiwerengero cha imfa chifukwa cha matendawa
ndi pafupifupi 5%.Zomwe zimayambitsa imfa ndi kubooka kwa matumbo, sitiroko, ndi kuphulika kwa aneurysms. Ngakhale kuti matenda a Behçet si oopsa mwachindunji, angayambitse mavuto osiyanasiyana azaumoyo ndi matenda m'thupi lonse, ambiri mwa iwo ndi opweteka. Komabe,
n'zotheka kuthana ndi matendawa bwino ndikukhala moyo wabwinobwino . Makamaka ngati mumachita masewera olimbitsa thupi nthawi zonse, kupuma, komanso kulankhula ndi ena omwe akukumana ndi vuto lomweli.
Pomaliza, kumbukirani zinthu izi!
Matenda a Behçet akhoza kukhala ovuta komanso osasangalatsa. Koma kumbukirani:
- Uwu ndi matenda omwe angathe kuchiritsidwa .
- Ngati muli ndi zizindikiro izi, funsani upangiri wa dokotala nthawi yomweyo .
- Mungayesere kukhala moyo wabwinobwino ndi chithandizo choyenera komanso kusintha moyo wanu.
- Musavutike nokha, lumikizanani ndi magulu othandizira kapena odwala ena .
Ndikukhulupirira kuti izi zikuthandizani. Khalani ndi thanzi labwino!
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