Nubwo haba hari igisebe gito ku mubiri wacu, kuva amaraso birahagarara nyuma y'igihe runaka maze amaraso akagwa, sibyo? Mu by'ukuri ni uburyo butangaje umubiri wacu wirinda. Ariko, niba uku kuzura kw'amaraso kwiyongera birenze uko bikenewe, cyangwa niba amaraso akagwa mu mubiri nta mpamvu? Icyo gihe bishobora kuba ikibazo. Uyu munsi tugiye kuvuga ku mpamvu yihariye ituma amaraso agwa bitari ngombwa. Iyo ni Antithrombin Deficiency , bamwe banayita Antithrombin III Deficiency.
Kubura Antithrombin mu by'ukuri ni iki?
Muri make, kubura antithrombin ni ikibazo kijyanye n’imikorere y’amaraso yacu. Muri ibi, hari igabanuka rya poroteyine yitwa antithrombin, ikintu cy’ingenzi mu mubiri wacu kibuza amaraso kuzura cyane, cyangwa ntikore neza.
Tekereza muri ubu buryo. Urimo wuzuza amazi mu bwogero. Umuntu agomba kuzimya robine mbere yuko yuzura, bitabaye ibyo amazi yose azavamo. Ni muri ubwo buryo, iyo amaraso yacu atangiye kuziba, ni ikintu cyitwa antithrombin "kiyihagarika" mu gihe gikwiye, kikayibuza kubaho cyane. Rero, niba udafite antithrombin ihagije mu mubiri wawe, cyangwa niba idakora neza, ushobora kugira amaraso aguma aziba, nk'ubwogero bukomeza kuzura. Niyo mpamvu uri mu kaga ko kugira amaraso asanzwe aziba .
Abantu bafite iyi ndwara bafite ibyago byinshi byo kurwara amaraso mu mitsi yo mu birenge (`Deep Vein Thrombosis` cyangwa `DVT`) ndetse n'ibyago byo kuvura amaraso no kuyafata mu mitsi yo mu bihaha (`Pulmonary Embolism` cyangwa `PE`) . Ibi bishobora kuba indwara zikomeye cyane.
Iyi ndwara ikunze kugaragara gute?
Kubura Antithrombin mu by'ukuri ni indwara idakunze kugaragara . Bivugwa ko umuntu umwe gusa mu bantu 2,000 kugeza ku 3,000 aba afite iyi ndwara. Ibyo ntibivuze ko bitaba kuri buri wese.
Ni ibihe bimenyetso by'ibura rya antithrombin?
Si abantu bose bafite iyi ndwara bazagira ibimenyetso bimwe. Hari abantu bashobora kutagira ibimenyetso na gato. Ariko akenshi amaraso ya mbere atangira kubyimba mbere y'imyaka 40 .
Ibimenyetso bikunze kugaragara ni ibi bikurikira:
- Deep Vein Thrombosis (DVT): Ibi bishobora gutuma ukuguru kubyimba, gutukura, kubabara, no kumva gushyushye iyo ubikozeho.
- Kubura umwuka mu gifu (PE): Ibi bishobora gutera guhumeka nabi mu buryo butunguranye, kubabara mu gituza (cyane cyane iyo uhumeka), guhumeka vuba, gukorora (rimwe na rimwe amaraso), no guhumeka nabi. Iyi ni indwara isaba ubuvuzi bwihutirwa.
Uretse ibi, nubwo bidakunze kubaho, mu mitsi yo mu bwonko , cyangwa mu mitsi yo mu ndaHari amahirwe yo kuzura amaraso.
Kuki habaho uku kubura kwa antithrombin?
Akenshi, impamvu y'iki kibazo ni imiterere y'umubiri , bivuze ko ari ikintu dukura ku babyeyi bacu.
- Impinduka mu ngirabuzimafatizo: Kubura kwa antithrombin bibaho ku bantu bafite impinduka mu ngirabuzimafatizo yitwa `SERPINC1`. Iyi ngirabuzimafatizo itegeka umubiri gukora antithrombin.
- Umurage: Ushobora kuragwa iyi gene mutation iturutse ku mubyeyi umwe. Niba ari uko bimeze, ufite amahirwe 50% yo kurwara iyi ndwara. Ntacyo bitwaye niba ari umukobwa cyangwa umuhungu. Ariko, abana bakuragwa iyi gene mutation iturutse ku babyeyi bombi akenshi ntibabaho. Ibi ni gake cyane.
Igikuru ni uko atari buri wese ufite iyi mihindagurikire y’uturemangingo urwara amaraso. Hari abantu bashobora kubaho ubuzima bwabo bwose nta kibazo.
Abaganga babimenya bate?
Niba ufite ibi bimenyetso, cyangwa uzi ko hari umuntu wo mu muryango wawe ufite iyi ndwara, ni byiza kujya kwa muganga no kwisuzumisha. Muganga asanzwe azakora ibi bikurikira:
- Isuzuma ry'umubiri: Umubiri wawe uzasuzumwa.
- Amateka y'ubuvuzi: Uzabazwa ibimenyetso byawe n'uko hari umuntu wo mu muryango wawe wigeze agira ibibazo nk'ibyo.
- Gupima amaraso: Ikintu cy'ingenzi ni ugupima amaraso byihariye bigenzura urugero rwa antithrombin mu maraso yawe.
Ibi bizamini ni bwo buryo bwonyine bwo kwemeza niba iyi ndwara ihari cyangwa idahari.
Urimo gukora iki nk'ubuvuzi?
Uburyo bwo kuvura buterwa n'uko amaraso yawe afite cyangwa adafite.
- Niba ufite ikibazo cyo kuvura amaraso: Muganga wawe ashobora gufata icyemezo cyo kugutangira imiti igabanya amaraso . Iyi akenshi iba warfarin (ushobora kuba warumvise ko ari Coumadin). Ibi bishobora gufata amezi menshi, cyangwa bikaba ubuzima bwawe bwose.
- Niba utigeze ugira amaraso adafite uburibwe: Nubwo waba ufite ikibazo cyo kubura amaraso ahagije, niba utigeze ugira amaraso adafite uburibwe, ntabwo ukeneye gukomeza gufata imiti igabanya uburibwe bw'amaraso. Ariko, mu bihe bimwe na bimwe (urugero, mbere yo kubagwa cyane) ishobora guhabwa igihe gito.
- Mu gihe cyo gutwita: Kubera ko hagati ya 3% na 50% by'abagore batwite bafite iyi ndwara bashobora kugira amaraso afunganye mu gihe batwite, muganga ashobora gufata icyemezo cyo gutera umuti witwa `Heparin` kugira ngo hirindwe ko amaraso afunganye muri icyo gihe.
Nkwiye kwiyitaho nte? (Mu gihe ndi kuvurwa)
Niba ufata imiti igabanya amaraso nka Warfarin cyangwa Heparin, ni ngombwa cyane gufata imiti neza nk'uko muganga wawe abikubwira.Nanone, menya neza ko ujya kuri gahunda yose ugiye kubonana na muganga.
Kubera ko uyu muti ufite ibyago byo kuva amaraso, muganga wawe agomba guhora agenzura ko uhawe igipimo gikwiye. Ibipimo by'amaraso nka 'Prothrombin Time' (PT) bikoreshwa kugira ngo harebwe niba igipimo cya Warfarin ari cyo.
Mu kugenzura neza urugero rw'imiti muri ubu buryo, amaraso ashobora kugabanuka mu buryo buteje akaga kandi kuva amaraso bitari ngombwa bishobora kwirindwa.
Ni iki nakora kugira ngo tugabanye ibyago byo kubyimba kw'amaraso?
Niba ufite ikibazo cyo kubura antithrombin, hari ibintu byinshi wakora kugira ngo ugabanye ibyago byo kubyimba kw'amaraso:
- Irinde gufata ibinini byo kuboneza urubyaro: cyane cyane ibirimo estrogen. Vugana na muganga wawe kuri ibi.
- Irinde uburyo bwo kuvura imisemburo: Uburyo bumwe bwo kuvura imisemburo bufatwa nyuma yo gucura nabwo bushobora kongera ibyago byo kubyara.
- Ntukagume mu mwanya umwe igihe kirekire: Cyane cyane iyo ugiye mu rugendo rurerure cyangwa ukorera ahantu hamwe igihe kirekire, haguruka nibura buri masaha abiri ugende buhoro buhoro uzunguze amaguru yawe.
- Ntukanywe itabi kandi ntugakoreshe ibikomoka ku itabi: Kunywa itabi byangiza cyane imiyoboro y'amaraso kandi byongera cyane ibyago byo kubyimba kw'amaraso.
- Gumana ibiro byiza: Umubyibuho ukabije ni indi mpamvu itera kubyimba kw'amaraso.
Byongeye kandi, ibintu nk'ihungabana rikomeye, kubagwa, gutwita, kubyara, no gusaza nabyo byongera ibyago byo kuvura amaraso. Niba ukeneye kubagwa cyangwa utwite umwana, bwira muganga wawe uko umerewe. Ashobora kuguha inshinge zidasanzwe zo mu mitsi (IV), nibiba ngombwa.
Ese hari uburyo bwo gukumira iki kibazo?
Ikibabaje ni uko kubera ko ari indwara iterwa n’uturemangingo, nta buryo bwo kwirinda kubura antithrombin mu buryo bw’umubiri . Ntidushobora guhindura uturemangingo dukomoka ku babyeyi bacu. Ariko hari ibyo dushobora gukora kugira ngo tugabanye ibyago byo kubyimba kw’amaraso.
Ni iki wakwitega niba ufite ikibazo cyo kubura antithrombin?
Umuntu umwe kuri batatu bafite iyi ndwara azarwara amaraso amaze gukura.
- Kubagwa no kutagenda: Niba urimo kubagwa kandi ukaba udashobora kugenda igihe kirekire (urugero, niba ugomba kuguma mu buriri), uba ufite ibyago byinshi byo kurwara amaraso.
- Gusaza: Ibi byago nabyo byiyongera gato uko imyaka igenda ishira.
- Gutwita: Abantu bafite ikibazo cyo kubura amaraso menshi bashobora kugira amaraso adafite ishingiro mu gihe batwite cyangwa nyuma yo kubyara, bityo rero ibyo bigomba kwitabwaho cyane.
Iki kibazo kizamara igihe kingana iki?
Kubera ko ari indwara iterwa n'uturemangingo, uvukana na yo. Ni ikintu kiramba ubuzima bwawe bwose. Ibyo bivuze ko idashobora gukira burundu. Ariko, iyo ivuwe neza, ushobora kubaho ufite ibibazo bike cyane.
Ni iki giteganyijwe kuri iki kibazo?
Uko ubibona biterwa nuko waba warigeze kugira amaraso adafunze cyangwa utafunze. Gufata imiti igabanya amaraso bishobora gufasha gukumira ko amaraso adafunze ukundi. Ariko, ni ngombwa gufata imiti neza nk'uko muganga wawe yabikubwiye, mu gipimo gikwiye, kandi mu gihe gikwiye.
Ni iki nkwiye kwitondera cyane cyane?
Niba ufite ikibazo cyo kubura antithrombin, ni ngombwa kumenya ibimenyetso by'umuburo bya `DVT` (amaraso apfunditse mu kaguru) na `PE` (amaraso apfunditse mu bihaha) kugira ngo ubashe kubona ubufasha vuba.
- Ibimenyetso bya DVT: kubyimba, ububabare, gutukura, no gushyuha uko ukoze ku kuguru kumwe (ubusanzwe rimwe gusa).
- Ibimenyetso bya PE: Guhumeka nabi mu buryo butunguranye, kubabara mu gatuza (birushaho kwiyongera iyo uhumeka), guhumeka vuba, guhumeka nabi, inkorora (rimwe na rimwe amaraso).
Niba ufata imiti igabanya amaraso (urugero: Warfarin), menya ibi bikurikira kuko hari ibyago byo kuva amaraso:
- Witondere cyane iyo ukoresha intwaro zityaye (imihoro, imashini zogosha, nibindi)
- Irinde siporo zishobora gutera imvune (urugero: rugby, boxe) uko bishoboka kose. Bitabaye ibyo, wambare imyenda ikwiye yo kwirinda.
- Niba kuva amaraso bitabujije no kuva ku gikomere gito, cyangwa niba ugize ibisebe nta mpamvu, bwira muganga wawe.
Ni ryari ngomba kubonana na muganga?
Niba ukeka ko ufite DVT, jya kwa muganga vuba. Ni ngombwa kuvura DVT vuba, kuko amaraso apfutse mu kaguru ashobora gucika akagera mu bihaha, bigatuma habaho PE.
Niba ufata imiti nka Warfarin, bwira muganga wawe ako kanya niba uguye cyangwa niba uva amaraso adasanzwe (urugero: mu mazuru, mu ishinya, cyangwa mu mwanda).
Ni ryari ugomba kujya mu Kigo cyita ku Buvuzi bw’Ingoboka (ETU) ?
Mu gihe nk'iki , ugomba guhita ujya mu ishami ryita ku barwayi ba ETU (ETU) ku bitaro:
- Niba ufite ibimenyetso bya `Pulmonary Embolism (PE)` (nk'ubuhumekero butunguranye, ububabare mu gatuza).
- Bite ho niba utekereza ko ufite ibimenyetso bya DVT , ariko ntushobora kuvugana na muganga wawe?
- Niba ufata imiti igabanya amaraso, niba ukubita umutwe, niba urimo kuruka amaraso, cyangwa niba udashobora guhagarika kuva amaraso mu gisebe.
Ibi ni ibintu byihutirwa bishobora gushyira ubuzima mu kaga, bityo ntugatinde.
Ni ibihe bibazo by'ingenzi ngomba kubaza muganga wanjye?
Umaze kumenya ko ufite iyi ndwara, ushobora kubaza muganga wawe ibibazo nk'ibi:
- Ese ngomba gufata Warfarin cyangwa indi miti igabanya amaraso? Nkeneye kuyifata igihe kingana iki?
- Ese ni byiza gupimisha abandi bagize umuryango wanjye (ababyeyi, abavandimwe, abana) kugira ngo barebe niba hari ikibazo cyo kubura amaraso mu mubiri?
- Ni iyihe myitozo nshobora gukora nta nkomyi kuri iyi ndwara?
- Ese hari ibintu byihariye ngomba kumenya mbere yo gutwita?
Baza ibibazo nk'ibi kugira ngo usobanukirwe neza uko ibintu bimeze.
Hanyuma, ibintu ugomba kwibuka (Ubutumwa bwo kujyana mu rugo)
Kubera ko ikibazo cyo kubura amaraso mu mubiri ari indwara iterwa n’uturemangingo, ntabwo dushobora kuyigenzura. Ariko, iyo umenye iyi ndwara kandi ugafata ingamba zikenewe, ushobora kubaho ubuzima bwiza cyane.
Igikuru ni uko wowe n'umuryango wawe mugomba kumenya ibimenyetso by'umuburo bya DVT na PE kugira ngo niba hari ikibazo kibaye, mushobore kubimenya hakiri kare kandi mushake ubuvuzi vuba.
Kugenzura ibiro byawe, gukomeza gukora imyitozo ngororamubiri (imyitozo ngororamubiri ihoraho), no kwirinda kunywa itabi bishobora kugufasha kugabanya ibyago byo kurwara amaraso adakenewe. Muri ubu buryo, ushobora kugenzura ingaruka iyi ndwara igira ku buzima bwawe ku rugero runaka. Vugana na muganga wawe buri gihe kandi ukurikize inama ze witonze. Ntugahangayike, nturi wenyine!
kubura antithrombin, kuvura amaraso, DVT, embolism y'ibihaha, indwara za genetiki, imiti igabanya amaraso, warfarin, heparin

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