Ushobora kuba warumvise indwara ya Sickle Cell . Mu magambo make, ni indwara igira ingaruka ku buryo umubiri wacu ukora uturemangingo dutukura tw’amaraso . Urabizi, utwo turemangingo dutukura tw’amaraso ni two dutwara umwuka wa ogisijeni mu mibiri yacu yose. Ubusanzwe, utwo turemangingo tuba dufite utubumbe duto, tuzingiye kandi tworoshye. Ariko umuntu urwaye sickle cell agira uturemangingo dutukura tw’amaraso dukomeye, dufite ishusho nk’iy’umuhoro. Rero, iyi miterere idasanzwe ishobora gutera ibibazo byinshi by’ubuzima, cyangwa ' ingorane '. Ariko ntugahangayike, muganga wawe ashobora kugufasha kuvura byinshi muri ibyo bibazo, ndetse no gukumira bimwe muri byo. Reka tuvuge kuri buri kimwe muri byo.
Ububabare - ikibazo gikunze kugaragara cyane
Ingorane ikunze kugaragara kandi ibabaza iterwa n'indwara ya sickle cell ni ububabare . Ibi biterwa nuko uturemangingo tureshya n'umuhoro dufata imiyoboro mito y'amaraso . Tekereza uko bigenda iyo imodoka nini ifatiwe mu muhanda muto. Ibyo ni ko bigenda iyo utwo turemangingo dufunze imiyoboro y'amaraso.
Ubu bubabare bushobora kugaragara mu gice cyo hasi cy'umugongo, amaguru, amaboko, inda, cyangwa igituza. Bushobora kugaragara mu buryo butunguranye nk'igitero gikomeye (ikibazo cyangwa ikindi gihe). Ku bakiri bato n'abakuze, rimwe na rimwe bushobora kuba ububabare bw'igihe kirekire.
Ubusanzwe, iyo ufite ububabare nk'ubu, ushobora kuruhuka ukoresheje imiti igabanya ububabare nka Paracetamol cyangwa Ibuprofen . Ariko ibuka ko utagomba guha aspirine umuntu uri munsi y'imyaka 19. Hari igihe, iyo ububabare bukabije, muganga ashobora kukwandikira imiti ikomeye igabanya ububabare yo mu itsinda ry’abafata imiti ya opioid. Hari n'abantu bagomba kujya mu bitaro kugira ngo bavurwe.
Muganga wawe ashobora kukugira inama zikurikira kugira ngo wirinde cyangwa ugabanye ubu bubabare:
- Nywa amazi menshi.
- Irinde ubushyuhe bukabije n'ubukonje bukabije.
- Ntukamara umwanya munini ahantu hirengeye, nko mu misozi miremire.
- Umuti witwa Hydroxyurea ufasha kugabanya inshuro ubu bubabare bukunze kugaragara ku bana no ku bantu bakuru.
Anemia
Iyi ni indi ngorane ikunze kugaragara ku ndwara ya sickle cell. Aha niho uturemangingo dutukura tw’amaraso dusa n’umuhoro dupfa vuba kurusha uturemangingo dusanzwe.. Bityo rero umubiri ntushobora gukora uturemangingo dushya ku gipimo kimwe n’icyo dupfa. Kubera iyo mpamvu, ingano ya ogisijeni igera ku turemangingo tw’umubiri iragabanuka, kandi ushobora kumva unaniwe cyane, ufite intege nke, kandi ukagira isereri . Ushobora kandi guhura n’ibintu nko gutera umutima vuba no kugorwa no guhumeka. Ku mwana, kubura amaraso bishobora no gutuma akura nabi.
Iyo amaraso afite ikibazo gikomeye cyo kubura amaraso, bishobora kuba ngombwa ko umuntu aterwa amaraso . Ariko, guterwa amaraso kenshi bishobora gutuma urugero rw'icyuma rwiyongera kandi bikangiza umutima, umwijima na pancreas. Kubwibyo, muganga wawe azasuzuma urugero rw'icyuma ufite buri gihe kugira ngo abafashe kubigenzura. Ku bantu bakuru, umuti wa Hydroxyurea ushobora no gufasha kubura amaraso.
| Ingorane | Ibimenyetso by'ingenzi | Icyo gukora |
|---|---|---|
| Gufata Splenic | Kubabara mu nda uruhande rw'ibumoso, kugaragara nk'igicuri, gusinzira cyane, umutima utera vuba cyane. | Iki ni ikibazo gishyira ubuzima mu kaga. Jya mu bitaro byita ku barwayi barembye (ETU) vuba. |
| Indwara yo mu gituza ikabije | Umuriro, guhumeka bigoranye, kubabara mu gatuza, inkorora. | Iyi nayo ni indwara ikomeye cyane. Jya mu bitaro byita ku barwayi ba ETU byihutirwa. |
Kwandura indwara n'ibindi bibazo byihutirwa
Kongera kwandura indwara
Abantu barwaye indwara ya sickle cell, cyane cyane abana bato, baba bafite amahirwe menshi yo kwandura. Ibi biterwa nuko iyo ndwara yangiza agahu . Urabizi, agahu ni urugingo rw'ingenzi rukuraho mikorobe nka bagiteri mu maraso yacu. Rero iyo idakora neza, indwara zishobora kwinjira mu mubiri byoroshye.
Ni ngombwa kwivuza nubwo bwandura gato mbere yuko bukomera. Niba wowe cyangwa umwana wawe mufite umuriro urenze 38.3°C, reba muganga cyangwa ujye mu ishami ryita ku barwayi b’ibitaro (ETU) ako kanya.
Gufata Splenic
Iki ni ikibazo cyihutirwa cyane cyane ku bana bato. Ibi bibaho iyo uturemangingo tw’imitsi tubuza amaraso gutembera mu ruhu. Uruhu rurabyimba kandi rukababaza. Hari abana bashobora kutagira ibimenyetso bikomeye bafite. Ariko, abandi bashobora kugira ibimenyetso nko gucika intege, uruhu rwerurutse n’iminwa, gusinzira cyane, kubabara mu gice cy’ibumoso cy’inda, no gutera k’umutima vuba . Nubona ibi bimenyetso, jya kwa muganga vuba .
Indwara yo mu gituza ikabije
Iyi nayo ni indwara ikomeye cyane. Aha niho indwara ya sickle cell ifunga imiyoboro y'amaraso mu bihaha. Niba ufite ibimenyetso nk'umuriro , kugorwa no guhumeka, kubabara mu gatuza no gukorora , jya kwa muganga ako kanya. Abaganga bashobora kuguha ogisijeni, imiti yica udukoko, ndetse wenda no guterwa amaraso.
Izindi ngorane z'igihe kirekire
Indwara y'uturemangingo ishobora guteza ibibazo byinshi uko igihe kigenda gihita.
- Gutakaza amagufwa (Avascular Necrosis): Iyo amaraso atembera mu ngingo nini (nk'ikibuno) aciwe, igufwa ritangira gupfa. Ibi bikunze kugaragara ku bantu bato n'abakuze. Imiti igabanya ububabare ishobora gutanga ubutabazi, ariko hari abantu bashobora gukenera kubagwa.
- Kwangirika kw'izindi ngingo: Ibibazo by'amaso, umutima, impyiko n'umwijima biri mu kaga ko kubyimba kw'amaraso no gucika intege mu bwonko. Niyo mpamvu muganga wawe azajya agenzura imikorere y'izi ngingo buri gihe.
Gutera Umwobo w'Amagufwa n'Ubuvuzi Bugezweho
Ku bantu bakunze kugira ibibazo bikomeye, uburyo bwo kuvura bwitwa "bone marrow transplant" . Ibi bikubiyemo gusimbuza uturemangingo tw’umusemburo dukora uturemangingo tw’umusemburo n’uturemangingo tuzima. Ibi bishobora gukiza burundu indwara.
Ariko iki si ikintu buri wese ashobora gukora. Ugomba gushaka umutanga utanga ukwiriye ingingo zawe. Nanone, niba ufite ibibazo ku ngingo nk'umutima cyangwa impyiko, ubu buryo bwo kubagwa bushobora guteza akaga. Ushobora kumara igihe kirekire mu bitaro. Hari igihe ubu buryo bwo kuvura bushobora kutagenda neza. Kubwibyo, umuryango ugomba kuganira na muganga witonze hanyuma ukemeza niba ubu buryo bubereye.
Byongeye kandi, hari imiti mishya, nka Crizanlizumab, ishobora kugabanya ububabare. Baza muganga wawe ibi kandi.
Ubutumwa bwo kujyana mu rugo
- Indwara ya Sickle cell ni indwara iterwa n’uturemangingo (genetic) ihindura imiterere y’uturemangingo dutukura tw’amaraso. Ibi bishobora guteza ingorane zikomeye nko kubabara, kubura amaraso, no kwangirika kw’ingingo.
- Niba ugize ibimenyetso nko kubabara, umuriro, guhumeka bigoranye, cyangwa kutagira ububabare bukabije, shaka ubufasha bwa muganga ako kanya cyangwa ujye mu bitaro byita ku barwayi ba ETU.
- Ingorane nyinshi zishobora kugenzurwa no kunywa amazi menshi, kugira ubuzima bwiza, no gufata imiti (nka Hydroxyurea) nk'uko muganga yabigutegetse.
- Ku bana, ni ingenzi cyane kwirinda kwandura indwara, bagahabwa inkingo zose ku gihe kandi bakabaha imiti igabanya ubukana bwa antibiyotike buri munsi.
- Niba ufite ikibazo cyangwa impungenge ku buzima bwawe cyangwa ubw'umwana wawe, buri gihe ganira na muganga wawe. Ushobora kubaho neza ufite iyi ndwara nta bwoba, umenyeshejwe.











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Kwipimisha kanseri y'ibere, kwisuzuma no kwirinda byakozwe byoroshye. Kanseri y'ibihaha
Ishyirireho intego ya calorie hanyuma ubare itariki yo kugabanya ibiro.