Chinhu chikuru chinoitika mumiviri yedu ndechekuti chikafu chatinodya chinotipa simba. Zvakafanana nekuisa gasi mumota. Pano, muviri wedu unowana simba kubva mushuga (glucose). Maitiro ese aya anodzorwa nehormone inonzi
insulin . Ndiyo insulin iyi inoudza shuga iri muropa kuti itumirwe mumasero anoda simba. Zvakafanana nekuvhura magonhi emasero uye kubvumidza shuga kupinda. Zvisinei, mumuviri wemunhu ane Rabson-Mendenhall Syndrome, maitiro aya haaitike nemazvo. Kureva kuti, muviri wavo haugone kushandisa insulin nemazvo. Ichi chirwere chisingawanzoitiki.
Saka chirwere ichi chii chaizvo?
Kana insulin ikasakwanisa kuita basa rayo nemazvo, inokanganisa zvakananga kukura kwemwana. Fungidzira, mhedzisiro yeizvi inotanga kunyangwe mwana asati aberekwa, ndiko kuti, achiri mudumbu raamai. Vacheche vane chirwere ichi vanowanzova vadiki. Kunyangwe mushure mekuzvarwa,
kuwedzera kwavo huremu nekukura kwemuviri kunoitika zvishoma nezvishoma. Panyaya yezvekurapa, chirwere cheRabson-Mendenhall chirwere chiri muboka guru rinonzi severe insulin resistance syndromes. Chirwere cheDonohue nechirwere cherudzi rweA insulin resistance syndrome zvimwe zvirwere zviviri zviri muboka iri.
Chii chiri kukonzera mamiriro ezvinhu aya?
Zvichitaurwa zviri nyore, ichi chirwere chemajini. Kureva kuti,
chinotorwa kubva kuvabereki kuenda kumwana . Izvi zvinokonzerwa nekanganiso mujini inonzi `INSR` mumuviri wedu. Iye zvino ngationei kuti izvi zvinoitika sei. Musero rega rega remuviri wedu, mune makopi maviri ejini rega rega. Rimwe kubva kuna amai, uye rimwe kubva kuna baba. Kuti mwana awane chirwere cheRabson-Mendenhall, makopi ese ejini re`INSR` anogamuchirwa nemwana anofanira kunge aine kanganiso iyoyo. Kana kopi imwe chete ine kanganiso, chirwere hachizobuki. Nemamwe mashoko, kuti mwana awane chirwere ichi, amai nababa vanofanira kunge vaine kopi imwe yejini iri rakakanganisika uye kopi imwe yejini rine hutano. Zvadaro, mwana anofanira kugamuchira makopi ese akakanganisika kubva kwavari vese netsaona. Ndokusaka zvisingawanzoitiki nekuti hazviwanzoitiki katatu pakana.
Ndezvipi zviratidzo zvechirwere ichi?
Zviratidzo zvinowanzotanga kuonekwa
mukati megore rekutanga rehupenyu hwemwana. Zvakare, kuoma kwezviratidzo izvi kunogona kusiyana kubva pamunhu kusvika pamunhu. Ngatitarisei zviratidzo zvikuru zvinogona kuonekwa.
| Chikamu/sisitimu yemuviri | Zvinhu zvinoonekwa |
|---|
| Musoro nechiso | Ganda rakashata, mukaha wakakura pakati pemaziso, migero yakadzika parurimi, yakakura kupfuura nzeve, miromo, neshaya. |
| nzara | Yakakora kupfuura yakajairika. |
| Ganda | Ganda rakaoma. Kusviba uye kukora kwenzvimbo dzakati wandei dzeganda (kunyanya mumakonzo akadai semuhapwa nemutsipa). Izvi zvinozivikanwa seacanthosis nigricans . Nzvimbo idzi dzinogona kunzwa sedzakanaka kana ukadzibata. |
| Mazino | Kuva hombe kupfuura zvakajairika, kuungana pamwe chete, kana kubuda mazino nguva isati yakwana. |
| Nhengo dzemukati | Itsvo, moyo, uye nhengo dzepabonde (nhengo yemurume muvakomana, nhengo yemukadzi muvasikana) zvakakura kupfuura zvakajairika. |
| Zvimwe zvinhu zvakajairika | Kukura kwebvudzi remuviri zvakanyanya, kukura zvishoma nezvishoma mwana asati aberekwa uye mushure mekusununguka, kuzvimba mudumbu, mafuta mashoma pasi peganda, uye kushaya simba kwetsandanyama. |
Zvimwe zvirwere zvinogona kuitika nekuda kweizvi
Kuwedzera kune zviratidzo izvi zvepakutanga, chirwere ichi chinogonawo kukonzera mamwe matambudziko akakomba.
Kuongororwa kwechirwere kunoitwa sei?
Chimwe chezvinetso pakuongorora chirwere ichi ndechekuchisiyanisa nezvimwe zvirwere zvakafanana (seDonahue syndrome).
Chiremba wemwana wako achaita ongororo yakakwana yemuviri, obvunza nezvezviratidzo zvemwana wako uye nhoroondo yehutano hwemhuri, uye angangoda kuti aongorore ropa kakawanda kuti aone
huwandu hweshuga yeropa remwana wako uye insulin . Iyi ndiyo chete nzira yekuita kuti chirwere ichi chiongororwe nemazvo.
Inorapwa sei?
Kurapwa kweRabson-Mendenhall syndrome kunowanzoda rubatsiro rwechikwata chikuru, kusanganisira nyanzvi dzakasiyana-siyana, vanachiremba vekuvhiya, uye vanachiremba vemazino. Kupa mazano kunogonawo kukosha kumhuri kuti dzigadzirise kushushikana nemanzwiro anouya nekuva nemwana ane chirwere ichi chisingawanzoitiki.
Parizvino hapana mushonga usingaperi wechirwere ichi. Kurapa kwakanangana nekudzora nekubata zviratidzo.
Kurapa kunowanzoenderana nechiratidzo chimwe nechimwe. Semuenzaniso, kuvhiyiwa kubvisa ma cysts emuzai, kurapwa kwemazino ematambudziko emazino, nezvimwewo. Mune zvimwe zviitiko, vanachiremba vanopa mishonga yakawanda ye insulin kana mimwe mishonga inokurudzira kushandiswa kwe insulin, asi kazhinji haishande kwenguva refu.
Kurapa kutsva kuri kuferefetwa
Nyanzvi dziri kuramba dzichitsvaga nzira dziri nani dzekurapa huwandu hweshuga muropa (hyperglycemia) hune chekuita nekusakwanisa kwakasimba kwe insulin. Kunyangwe kurapwa uku kwakaratidza mhedzisiro yakanaka, tsvakiridzo yakawanda inodiwa.
- Biguanides: Iyi imhando yemishonga inoderedza kugadzirwa kweshuga mumuviri uye inowedzera kushandiswa kwe insulin .
- Leptin: Puroteni iyi yakawanikwa ichibatsira kudzora huwandu hweshuga muropa uye huwandu hweinsulin.
- rhIGF-I (Recombinant insulin-like growth factor I): Puroteni iyi inoshandiswa kurapa ketoacidosis, chirwere chinokonzerwa nekusakwanisa kwakasimba kwe insulin .
Mharidzo Yekuenda Nayo Kumba
- Rabson-Mendenhall Syndrome chirwere chisingawanzoitiki chemajini umo muviri usingakwanise kushandisa insulin nemazvo.
- Izvi zvinokonzerwa nejini risina kunaka (jini rekuti `INSR`) iro mwana anogara nhaka kubva kuvabereki vese.
- Zviratidzo zvinotanga muhudiki uye zvinokanganisa kukura kwemuviri , chitarisiko chechiso , ganda, mazino, uye nhengo dzemukati.
- Hapana mushonga wekusingaperi weizvi, uye kurapwa kwakagadzirirwa kugadzirisa zviratidzo. Izvi zvinoda rutsigiro rwechikwata chevanachiremba vane hunyanzvi.
- Kana mwana wako achiratidza chimwe chezviratidzo izvi, zvakakosha zvikuru kuona chiremba ane hunyanzvi nekukasika kuti akupe mazano.
Rabson-Mendenhall Syndrome, kuramba insulin, zvirwere zvemajini, zvirwere zvevana, acanthosis nigricans, ketoacidosis, chirwere cheshuga
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