Ngaba amalungu esisu somntwana wakho aphumile? Masifunde ngale nto kuthiwa yi-cloacal exstrophy!

Umama okanye utata ebenokoyika kangakanani ukuba bebona ukuba isisu sosana olusandul’ ukuzalwa asikakhiwa kakuhle kwaye amanye amalungu afanele ukuba ngaphakathi aphumile? Kunzima kakhulu ukuyicinga. Kodwa ungakhathazeki. Nangona esi sisifo esingaqhelekanga, kukho unyango lwaso. Masithethe ngesi sifo esibizwa ngokuba yiCloacal Exstrophy ngendlela elula onokuyiqonda.

Yintoni le cloacal exstrophy?

Ngamafutshane, iCloacal Exstrophy sisiphene sokuzalwa esenzeka xa udonga lwesisu lomntwana lungakheki kakuhle ngelixa ekhula esibelekweni. Khawucinge nje, kuba inxalenye esezantsi yesisu ayivali kakuhle, isinyi somntwana kunye nenxalenye yekholoni, okanye ezinye izitho, zigqunywe yi-membrane encinci kwaye ziphuma emzimbeni. Oku kunzima ukukubona. Le meko ikwachaphazela amalungu esini omntwana.

Oku kwaziwa ngokuba yi -congenital urinary anomaly . Oku kuthetha ukuba yingxaki eyenzeka ngelixa umntwana esesesibelekweni. Kodwa ungakhathazeki, emva kotyando lokulungisa izinto ezimbalwa, oluqala ekuzalweni luze luhlale okwethutyana, uninzi lwabantwana abanale meko baphila ubomi obuqhelekileyo nobonwabisayo.

Oku kuyichaphazela njani umntwana? Yintoni i-OEIS complex?

I-Cloacal Exstrophy ikwaziwa ngokuba yi -OEIS complex okanye i-OEIS syndrome kuba ihamba nezinye iingxaki ezininzi. Makhe sibone ukuba zeziphi:

Yintoni i-Omphalocele?

Oku kwenzeka xa izihlunu zesisu somntwana, kufutshane neqhosha lesisu, zingadibani kakuhle, nto leyo edala umngxuma. Ngalo mngxuma, isinyi, amathumbu amakhulu, kwaye ngamanye amaxesha nezinye izitho, ezifana nesibindi, ziyaphuma. Kodwa ezi zitho aziphumi nje kuphela, zigqunywe yi-membrane ekhuselayo.

Yintoni i-exstrophy?

Oku kuxa udonga lwesinyi somntwana lujika lubheke ngaphandle endaweni yokungena ngaphakathi. Oku kubizwa ngokuba yi-bladder exstrophy . Isinyi sithe tyaba endaweni yokuba singqukuva, kwaye sinokwahlulwa kabini. Kwakhona, izihlunu zesisu kunye namathambo esinqeni, okanye amathambo ajikeleze isinqe, awadibani kakuhle. Ngenxa yoko, isinqe sisasazeka kumacala omabini, njengencwadi evulwe ngokubanzi.

Yintoni i-imperforate anus?

Kwimeko enjalo, i-anus yomntwana, umngxuma esidlula kuwo indle, awukakheki kakuhle. Isenokuba ivalekile, okanye ingabikho loo mngxuma konke konke. Ikholoni imfutshane kakhulu, kwaye isenokuba idibene nesinyi.

Zithini iziphene zomqolo?

Malunga neentsana ezintathu kwabane ezine-cloacal exstrophyKusenokubakho imeko ebizwa ngokuba yi-spina bifida, apho amathambo omqolo angavaleki kakuhle, nto leyo ebangela ukuba ingxowa egcwele ulwelo ejikeleze umthambo womqolo (mhlawumbi enemithambo-luvo) iphume phakathi kwesithuba.

Kubalulekile: Usana lunokuba nazo zonke ezi zinto, okanye ezinye zazo kuphela. Oogqirha baza kuzihlola ngononophelo zonke ezi zinto.

Ingaba oku kunefuthe kumalungu esini?

Ewe, iCloacal Exstrophy ikwachaphazela amalungu esini omntwana.

• Ukuba yinkwenkwe: Ipenisi isenokuba tyaba, imfutshane, okanye yahlulwe ngamacala angasekunene nangasekhohlo.
• Ukuba yintombazana: I-clitoris inokwahlulwa ibe ngamacandelo amabini, elinye lingasekunene nelinye lingasekhohlo. Kunokubakho nemingxunya emibini yesini.

Ixhaphake kangakanani le meko?

Esi sisifo esingaqhelekanga kakhulu . Xa sithetha nje, sichaphazela malunga nesinye kwiintsana ezingama-250,000 ukuya kwesinye kwiintsana ezingama-400,000 ezizalwayo. Kwakhona, abafana banamathuba amabini ukuya kwamathathu okuba nale meko kunamantombazana.

Ziziphi iintlobo ze-exstrophy-epispadius complex (EEC)?

I-cloacal exstrophy yenye yeqela leziphene zokuzalwa ezibizwa ngokuba yi -Exstrophy-Epispadias Complex (EEC) . Enyanisweni, lolona hlobo lubi kakhulu lweqela. Umntwana unokuba nemeko enye kuphela kweli qela, okanye banokuba neenye ezininzi kunye.

Eminye imiqathango kudidi lwe-EEC yile:

• I-Epispadias: Kule meko, i-urethra yomntwana, ityhubhu ekhupha umchamo emzimbeni, ayenziwanga kakuhle.
• Ukuphuma kwe-Bladder: Kule meko, i-bladder yomntwana ijika ngaphakathi iphume.

Yintoni ebangela i-cloacal exstrophy?

Oogqirha abazi kakuhle ukuba kutheni ezinye iintsana zikhula nale meko, kodwa bakholelwa ukuba iyenzeka xa izicubu ezibizwa ngokuba yi-cloacal membrane zikrazuka okanye ziqhekeka ngexesha le-trimester yokuqala yokukhulelwa.

I- cloaca yindawo apho inkqubo yokuzala yomntwana, inkqubo yokugaya ukutya, kunye nenkqubo yomchamo zidibana khona. Ngokwesiqhelo, amalungu ezi nkqubo ahlukaniswa yi-cloacal membrane. Ngoko ke xa le membrane igqabhuka, udonga lwesisu alukheki ngokupheleleyo. Amalungu awakhuli kakuhle, kwaye asenokudibaniswa ngokuchanekileyo. Ekugqibeleni, amanye amalungu aphuma ngesithuba esiswini.

Zithini iimpawu zale meko?

Iimpawu ze-cloacal exstrophy zinokubonakala kwangoko emva kokuzalwa. Umntwana wakho unokufumana oku kulandelayo:

• Amalungu omzimba aphume emngxunyeni esiswini, ngaphakathi kwesakhiwo esifana nengxowa.
• Isakhiwo esifana nesikhwama siphuma kwindawo evulekileyo ngasemva komqolo (le yiSpine Bifida).
• Ipenisi okanye isini sangasese sibonakala ngathi sahlulwe kubini.

Oogqirha bayibona njani le nto?

I-cloacal exstrophy idla ngokuchongwa ngexesha lokuhlolwa kwe-ultrasound ngaphambi kokukhulelwa. Ugqirha wakho unokucebisa ukuba kwenziwe i-MRI yosana olusandul ’ ukuzalwa. Oku kunokubonelela ngemifanekiso ecacileyo yamalungu omzimba omntwana wakho. Ezi scan zinokubonisa izinto ezinje:

• Umchamo awuphumi kakuhle kwisinyi.
• Amathambo e-pubic ahlukene.
• Zincinci kunobukhulu obuqhelekileyo bezitho zangasese.
• I-omphalocele ithetha ukuba intambo yomntwana inamathele kakhulu esiswini somntwana.

Emva kokuba umntwana wakho ezelwe, ugqirha wakho unokuyalela ukuba kwenziwe i -MRI scan , i -ultrasound yesisu , okanye ezinye ii-imaging scans . Ezi zinokuvavanya ukusebenza kwamalungu omzimba kunye nobunzima besifo. Esebenzisa lonke olu lwazi, ugqirha wakho uya kuyila isicwangciso sonyango esifanelekileyo somntwana wakho.

Iphathwa njani iCloacal Exstrophy?

Wonke umntwana osandul’ ukuzalwa one-cloacal exstrophy uya kufuna utyando . Olu tyando lubandakanya ukubuyisela amalungu aphumayo emzimbeni kunye nokuvala izikhewu esiswini nasemqolo. Umntwana wakho uya kwenziwa utyando oluninzi kwiminyaka eliqela. Oku kubizwa ngokuba yi -staged reconstruction .

Unyango lokubeleka

Unyango olufana nolu luqala kwangoko emva kokuba umntwana ezelwe:

• Ukwakha kwakhona isinyi, ukubuyisela amalungu ngaphakathi esiswini, nokuvala umsantsa esiswini.
• Ukudala i- stoma . Lo ngumngxuma esiswini ovumela indle ukuba idlule isuka emathunjini amakhulu. Le ndle iqokelelwa kwingxowa engaphandle (ingxowa ye-colostomy). Le ngxowa ye-colostomy isenokuba yeyokwexeshana, de kwenziwe olunye utyando.
• Ukuvala umsantsa kumqolo.

Unyango kwasebuntwaneni

Xa umntwana ekhulile kancinci, oko kukuthi, ebuntwaneni bokuqala, unyango lwenziwa ngolu hlobo:

• Utyando lwethambo (i-osteotomy) lwenziwa ukuze kunqunyulwe amathambo e-pelvic. Oku kuvumela i-pelvis ukuba ivaleke lula kwaye kunika inkxaso engcono kwisinyi njengoko umntwana ekhula.
• Izitho zokuzala kunye nomgudu womchamo ziyahlelwa ngokutsha.
• Kuvulwa umngxuma wempundu. Ukuba i-colon inde ngokwaneleyo, ugqirha angenza utyando lokutsala i-colon kwi-anus. Emva koko i-stoma iyavalwa. Umntwana akasayi kufuna isikhwama se-colostomy.

Zeziphi iingxaki ezinokuvela kule meko?

Emva kotyando, uninzi lwabantwana abane-cloacal exstrophy baphila ubomi obupheleleyo nobusebenzayo . Abanye abantwana banokufuna utyando olungakumbi njengoko bekhula.

I-cloacal exstrophy ingabangela ezi meko zilandelayo zomngcipheko:

• Ukungazali.
• Isifo sezintso, usulelo lwezintso, amatye ezintso, kunye nokungasebenzi kakuhle kwezintso.
• Ukungasebenzi kakuhle ngokwesondo, ukungasebenzi kakuhle kwe-erectile, njl.
• Ukungakwazi ukuzibamba komchamo kunye nokungakwazi ukuzibamba lindle.

Izinto onokuzibuza ugqirha wakho

Ungabuza ugqirha womntwana wakho izinto ezifana nezi:

• Ingaba umntwana wam usengozini enkulu yokuba nezinye izifo?
• Yeyiphi indlela engcono kakhulu yonyango lweCloacal Exstrophy?
• Zingaphi utyando oluya kufuneka umntwana wam alwenze?
• Zeziphi iingxaki ekufuneka ndiziqaphele emva kotyando?
• Ngawaphi amathuba okuba umntwana wam olandelayo abe neCloacal Exstrophy?

Kuqhelekile ukuba noloyiko kwaye ukhathazeke xa ufumanisa ukuba umntwana wakho une-Cloacal Exstrophy, okanye i-OEIS syndrome. Kodwa khumbula, awuwedwa.

Eyona nto ibalulekileyo ekufuneka uyikhumbule

Kungokwemvelo ukuziva uxinezelekile kwaye usoyika xa ufumanisa ukuba umntwana wakho uneCloacal Exstrophy. Kodwa ungakhathazeki . Oogqirha bakho kunye neqela lezonyango bakulungele ukukunceda wena nomntwana wakho. Umntwana wakho uza kufuna utyando oluninzi emva nje kokuzalwa, aze emva koko kwenziwe utyando olongezelelweyo ukuze kulungiswe amalungu omzimba.

Kodwa eyona nto ilungileyo kukuba, xa unyango olufanelekileyo luphumelela, uninzi lwabantwana abazalwa nale meko baphila ubomi obuqhelekileyo nobonwabisayo . Thetha nogqirha wakho ngayo nayiphi na imibuzo okanye iinkxalabo onokuba nazo. Baza kukuchazela yonke into.

I- Cloacal Exstrophy, Iziphene zokuzalwa, i-OEIS Complex, i-Omphalocele, i-Bladder Exstrophy, utyando lwabantwana