Ngamanye amaxesha, ezinye izifo ezifunyanwa ngabantwana bethu azixhaphakanga. Kwaye unyango lwazo lukwakhethekile kakhulu. Namhlanje siza kuthetha ngesitofu esikhethekileyo esinikwa ezi zifo zingaqhelekanga nezinzima zenkqubo yokuzikhusela komzimba. Igama laso yiPegademase Bovine. Mhlawumbi ugqirha wakho ukuxelele ngale yeza. Ngoko ke, masisuse uloyiko kunye namathandabuzo ngale nto size siziqonde nje ezi zinto.
Lithini eli yeza libizwa ngokuba yiPegademase Bovine?
Ngamafutshane, iPegademase Bovine yindlela yangaphandle yokwenziwa kwe-enzyme eveliswa ngokwendalo emizimbeni yethu, kodwa engekho kwabanye abantu. Cinga ngemizimba yethu njengomzi-mveliso omkhulu. Lo mzi-mveliso ufuna iintlobo ezahlukeneyo zabasebenzi (ii-enzymes) ukuze usebenze ngokufanelekileyo. Ngamanye amaxesha, ngenxa yezizathu zemfuza, omnye waba basebenzi usenokungabikho kwasekuzalweni.
Okushiyekileyo apha yi-enzyme ebizwa ngokuba yi- Adenosine Deaminase (ADA) . Le enzyme ibalulekile ukuze inkqubo yethu yokuzikhusela komzimba isebenze kakuhle. Xa ingekho, inkqubo yokuzikhusela komzimba iba buthathaka kakhulu. Le meko ibizwa ngokuba yiSevere Combined Immunodeficiency Disease (SCID) .
Ngoko ke into eyenziwa lolu gonyo lwePegademase Bovine kukubonelela umzimba nge-enzyme ye-ADA engekhoyo. Olu luguqulelo oluguquliweyo lwe-enzyme ethathwe kwiinkomo.
Kubaluleke kakhulu: Oku akuyonyango lwesi sifo. Nangona kunjalo, kuyanceda ukulawula iimpawu, kuncede inkqubo yomzimba yokuzikhusela ukuba yenze umsebenzi wayo, kwaye kukuvumela ukuba uphile ubomi obuqhelekileyo.
Izinto ekufuneka uzixelele ugqirha wakho ngaphambi kokuba uqale amayeza
Ngaphambi kokuba uqale olu nyango, kubalulekile ukunika ugqirha inkcazo epheleleyo ngemeko yakho okanye yomntwana wakho. Qiniseka ukuba ubaxelela ngezi zinto zilandelayo ngokukodwa.
| Ulwazi oluza kuxelwa | Kalula nje... |
|---|---|
| Iingxaki zokopha | Ukuba ukrweleka lula, okanye ukuba ukopha akupheli nokuba kukwinxeba elincinci. |
| Ukuncipha kweeplatelets zegazi | Ukuba uvavanyo lwakho lwegazi lubonisa ukubala iiplatelet ezisezantsi. |
| Usulelo lwangoku | Ukuba okwangoku unentsholongwane efana nomkhuhlane, ukukhwehlela, okanye umkhuhlane. |
| Ii-aleji | Ukuba une-aleji kweli yeza lePegademase Bovine, amanye amayeza, ukutya, izithinteli, okanye iidayi. |
| Ukukhulelwa kunye nokuncancisa | Ukuba ukhulelwe, uzama ukukhulelwa, okanye uncancisa. |
Isetyenziswa njani le gonyo?
Olu luhlaselo kwisihlunu . Olu luhlaselo ludla ngokwenziwa yingcali yezempilo esibhedlele okanye ekliniki. Nangona kunjalo, kwezinye iimeko, uya kuyalelwa ukuba uzihlabe olu hlaselo ekhaya. Ukuba kunjalo, landela imiyalelo njengoko ikuxelela, ngaphandle kokutshintsha unobumba omnye . Kubaluleke kakhulu ukusela iyeza ngexesha elimiselweyo.
Ulwazi olukhethekileyo malunga neenaliti kunye neesirinji
Ukuba unika isitofu ekhaya, kufuneka ulumke kakhulu ngeenaliti kunye neesirinji ozisebenzisayo.
- Ungaze ulahle iinaliti ezisetyenzisiweyo enkunkuma.
- Kukho isitya esikhethekileyo sezinto ezibukhali apho zinokulahlwa khona.
- Ukuba awunayo, thetha nogqirha wakho umbuze ukuba ungayifumana njani.
Xa inikwa abantwana?
Kukho iimeko apho eli yeza linikwa kwanakwiintsana ezisandul’ ukuzalwa. Nangona kunjalo, kufuneka kuthathwe ingqalelo ekhethekileyo xa kunikwa abantwana eli yeza. Ngoko ke, thetha nogqirha wezingane ngononophelo malunga nokunika umntwana wakho olu nyango uze umchazele yonke into.
Kuthekani ukuba ndithatha amayeza amaninzi kakhulu?
Ukuba ucinga ukuba usele kakhulu eli yeza, yiya kwiSebe lezeMpilo eziNgxamisekileyo (ETU) esibhedlele esikufutshane ngoko nangoko . Okanye, fowunela iZiko loLwazi lweePoisons kwiSibhedlele sikaZwelonke saseColombo .
Zeziphi iziphumo ebezingalindelekanga ekufuneka uzazi?
Njengayo nayiphi na iyeza, eli linokuba nemiphumo emibi. Ezinye zazo kufuneka zixelwe ngoko nangoko, ngelixa ezinye ziqhelekile. Makhe sizijonge.
| Uhlu lweziphumo ebezingalindelekanga | |
|---|---|
| Izinto omele uzixelele ugqirha wakho ngoko nangoko | |
| Iimpendulo ze-Allergic | Ukurhawuzelela kwesikhumba, ukurhawuzelela, ukudumba kobuso, imilebe, okanye ulwimi. |
| Ubunzima bokuphefumla | Ndivakalelwa ngathi kunzima ukuphefumla. |
| Ukudinwa kunye nokulahlekelwa zingqondo | Ukuba nesiyezi, amehlo aluhlaza okwesibhakabhaka, ukuquleka, okanye ukuwa. |
| Ubuthathaka obungaqhelekanga | Ukudinwa kakhulu okanye ubuthathaka ngaphandle kwesizathu. |
| Izinto ezingaqhelekanga ukuba zimbi, kodwa kufuneka zixelwe kugqirha ukuba ziyaqhubeka | |
| Intloko ebuhlungu | Intloko ebuhlungu eqhelekileyo. |
| Intlungu kwindawo yokutofa | Intlungu okanye ukubomvu kwindawo efakwe kuyo inaliti. |
Ukuba ubona into engaqhelekanga engakhankanywanga kolu luhlu, thetha nogqirha wakho ngayo.
Amanye amanqaku ambalwa abalulekileyo
- Kuthekani ukuba ndiphosakele idosi? Kubaluleke kakhulu ukuba ndingaphoswa yidosi yale yeza. Ukuba uya ekliniki ukuyokusela amayeza akho, fowunela ugqirha wakho kwangethuba ukuba awukwazi ukuya. Ukuba usela amayeza akho ekhaya, fowunela ugqirha wakho ngoko nangoko ukuba uphosakele idosi. Ungaze uthathe idosi ephindwe kabini ngaxeshanye.
- Ukusebenzisana namanye amayeza: Amanye amayeza, anjengeVidarabine , asenokusebenzisana nalo mgonyo. Ngoko ke, xelela ugqirha wakho ngawo onke amayeza owasebenzisayo (kuquka iivithamini, amayeza esintu, kunye nezongezo). Kwakhona, xelela ugqirha wakho ukuba utshaya okanye usela utywala.
- Indawo yokugcina: Ukuba ugcina eli yeza ekhaya, ligcine efrijini kubushushu obuphakathi kwe-2 kunye ne-8 degrees Celsius . Ungaze ulibeke efrijini. Kwakhona, ligcine kude nokufikelela kwabantwana. Lahla naliphi na iyeza eliphelelwe lixesha.
Kuyo yonke le nkqubo yonyango, kubalulekile ukuya kuhlolwa ngemihla emiselweyo njengoko ugqirha ecebisile. Kuya kufuneka wenze uvavanyo lwegazi rhoqo ukujonga ukusebenza kwenkqubo yakho yokuzikhusela komzimba.
Umyalezo Wokuya Ekhaya
- IPegademase Bovine lunyango lokutshintsha iienzymes kwisifo esingaqhelekanga sokuzikhusela komzimba esibizwa ngokuba yi-SCID. Ayilonyango, kodwa yindlela yokulawula.
- Ngaphambi kokuba uqale unyango, xelela ugqirha wakho ngembali yakho epheleleyo yempilo, amanye amayeza owasebenzisayo, kunye nazo naziphi na izinto ezibangela ukuba ungabi naso isifo.
- Musa ukutsiba iidosi. Ukuba uphoswe yidosi, tsalela umnxeba ugqirha wakho ngoko nangoko. Ungaze uthathe idosi ephindwe kabini.
- Ukuba ufumana iziphumo ebezingalindelekanga ezinje ngobunzima bokuphefumla okanye ukudumba kobuso, funa ingcebiso kagqirha ngokukhawuleza.
- Gcina iyeza ngokufanelekileyo efrijini. Musa ukulifaka efrijini.
- Lahla iinaliti kunye neesirinji ezisetyenzisiweyo ngokukhuselekileyo kwisitya esikhethekileyo.











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