Khawucinge nje ukuba ngequbuliso ukhe waba nentloko ebuhlungu, umbono ofipheleyo, kunye nokulahlekelwa kukuva? Usenokucinga ukuba ezi ziingxaki ezintathu ezingadibaniyo. Kodwa namhlanje sithetha ngemeko engaqhelekanga kakhulu edibanisa zonke ezi mpawu zintathu, kodwa engaxoxwa kakhulu kuluntu. Oku kubizwa ngokuba yi "Susac Syndrome." Eli gama lisenokuba litsha kuwe. Kodwa kubaluleke kakhulu ukuqaphela oku.
Ngamafutshane, yintoni iSusac Syndrome?
I-Susac Syndrome yimeko apho inkqubo yokuzikhusela yomzimba wethu, inkqubo yokuzikhusela komzimba, ihlasela ngempazamo imizimba yethu. Oku sikubiza ngokuba yimeko yokuzikhusela komzimba. Khawuthelekelele umkhosi ukhusela ilizwe elihlasela abantu balo ngempazamo.
Kwesi sifo, inkqubo yethu yomzimba yokuzikhusela ijolise kwimithambo yegazi emincinci kwiindawo ezintathu ezibalulekileyo emzimbeni wethu. Ezo ndawo zintathu zezi:
1. Ingqondo
2. I-retina
3. Indlebe yangaphakathi (iCochlea)
Xa oku kusenzeka, iindonga zangaphakathi zale mibhobho yegazi ziyadumba. Kanye xa umbhobho wamanzi uvalekile, ukuhamba kwamanzi kule mibhobho yegazi kuyancitshiswa, kwaye ngamanye amaxesha kuvalwe ngokupheleleyo. Oku kuncitshisa ingqondo, amehlo, neendlebe ioksijini kunye nezondlo abazidingayo. Kulapho ke iimpawu zesi sifo ziqala ukubonakala khona.
Ziziphi iimpawu eziphambili zesi sifo?
KwiSusac Syndrome, iimpawu ezinxulumene nezi nxalenye ziphambili zintathu zinokuvela kunye okanye ngokwahlukeneyo. Kodwa ngokuqhelekileyo zonke ezi nxalenye zintathu ziyachaphazeleka. Makhe sibone ukuba zeziphi ezi mpawu.
| Inxalenye echaphazelekayo | Iimpawu ezinokwenzeka |
|---|---|
| 1. Ingqondo |
|
| 2. Amehlo |
|
| 3. Indlebe Yangaphakathi |
|
Into ebalulekileyo kukuba ayinguye wonke umntu ozibona ezi mpawu ngaxeshanye. Abanye abantu banokuzibona ezi mpawu kube kanye baze bangaphindi bazibone. Abanye banokuzibona iminyaka eliqela.
Kutheni oku kusenzeka kwaye ngubani osengozini enkulu?
Njengoko besitshilo ngaphambili, unobangela woku awukafunyanwa . Into eyaziwayo kuphela kukuba yimeko yokuzikhusela komzimba. Ayisosifo esidluliselwa kwilifa . Oko kuthetha ukuba akukho bungqina bokuba abantwana baya kuba naso ukuba abazali babo babenaso.
Nangona kunjalo, xa sijonga izinto ezithile, singabachonga abantu abasengozini ethile yokuhlaselwa sesi sifo:
- Isini: Abafazi banamathuba aphindwe kathathu okufumana esi sifo kunamadoda.
- Ubudala: Ezi mpawu zihlala ziqala ukubonakala kubantu abaphakathi kweminyaka engama-20 ukuya kwengama-40 ubudala .
Oogqirha bayifumana njani le nto?
I-Susac Syndrome inokuba nzima ukuyifumanisa kuba iimpawu zayo zifana nezezinye izifo ezininzi. Umzekelo, iimpawu zifana kakhulu nezezifo ezifana ne-Multiple Sclerosis (MS), istroke, kunye nosulelo lobuchopho (encephalitis). Ngoko ke, ugqirha unokucinga ngempazamo ukuba sisifo esahlukileyo.
Ngoko ke, kwenziwa iimvavanyo ezikhethekileyo ezininzi ukuze kufunyanwe isifo ngokuchanekileyo.
- Uvavanyo lomzimba
- Uvavanyo lwe-neurological
- Uvavanyo lwamehlo
Ukongeza, ezi mvavanyo zikhethekileyo zibaluleke kakhulu ukuqinisekisa isifo.
| Uvavanyo | Ufuna ntoni kule nto? |
|---|---|
| Iskeni se-MRI (Umfanekiso weMagnetic Resonance) | Oku kuthatha imifanekiso eneenkcukacha zobuchopho. Kumntu oneSusac Syndrome, izilonda ezimhlophe ezibonakala ngathi "ziibhola zekhephu" zinokubonakala kwi-corpus callosum, inxalenye yobuchopho edibanisa ii-hemispheres zobuchopho zasekunene nezasekhohlo. Olu luphawu oluphawulekayo lwesifo. |
| I-angiography ye-Fluorescein | Le yinkqubo ehlola imithambo yegazi kwi-retina yeliso. Kule nkqubo, kufakwa idayi ekhethekileyo emthanjeni osengalweni kwaye kuthathwe imifanekiso yemithambo yegazi engaphakathi kweliso. Oku kunokubona ngokucacileyo ukuba imithambo yegazi ivaliwe na. |
| I-Audiogram | Olu luvavanyo olulinganisa ukuva. Abantu abaneSusac Syndrome banokuba nobunzima bokuva, ingakumbi izandi eziphantsi, kwaye banokuba nobunzima bokuqonda intetho. Olu vavanyo lunokukuchonga oku. |
Luthini unyango?
Eyona njongo yokunyanga esi sifo kukulawula inkqubo yethu yomzimba yokuzikhusela, engasebenzi kakuhle. Oko kukuthi, ukuthintela ukusebenza kwayo. Sibiza amayeza anikwe le njongo njenge -immunosuppressants .
Olu nyango lunokufuneka luthathwe ixesha elide. Amanye amayeza asetyenziswa kakhulu ngala:
- Ii-Corticosteroids - umz. i-prednisone
- I-immunoglobulin efakwa kwimithambo yegazi (IVIG)
- I-Mycophenolate
- I-Azathioprine
- I-Cyclophosphamide
- I-Rituximab
Kukho iindlela ezahlukeneyo zokunika la mayeza. Amanye anikwa njengeepilisi, amanye anikwa njengeenaliti, kwaye amanye anikwa ngemithambo yegazi (IV) njengesicombululo setyuwa.
Kubaluleke kakhulu: Kubalulekile ukuthatha la mayeza kanye njengoko ugqirha wakho ekuyalele, lonke ixesha lekhosi. Ukuba uyawushiya unyango okanye uyeke ngokwakho, kukho ithuba elikhulu lokuba iimpawu zakho ziya kuphinda zivele.
Njengazo zonke amayeza, le inokuba nemiphumo emibi. Ngoko ke thetha nogqirha wakho ngayo phambi kokuba uqale unyango. Ukuba kukho nayiphi na imiphumo emibi, mxelele ngoko nangoko.
Singaba nethemba njani ngekamva?
Nangona igama elithi Susac Syndrome lisenokuvakala lisoyikisa, kukho unyango olufanelekileyo kakhulu kwesi sifo. Ingakumbi ukuba isifo sifunyenwe kwaye sinyangwa kwangethuba, iziphumo zilungile kakhulu. Unyango lwangethuba lunokuthintela umonakalo ongunaphakade engqondweni, emehlweni nasezindlebeni.
Nangona kunjalo, ukuba unyango lulibaziseka, ngamanye amaxesha ukubona nokuva kunokulahleka ngonaphakade. Nangona kunjalo, oku kunqabile kakhulu.
Esi sifo asisoloko sisongela ubomi. Oko kukuthi, asifinyezi ixesha lokuphila. Nangona kunjalo, sinokuchaphazela umgangatho wobomi bemihla ngemihla. Xa izinto ezifana nokubona nokuva, ezazilungile ngaphambili, zitshintsha, kunye notshintsho kwindlela ocinga ngayo nokhumbula ngayo, kunokuba nempembelelo enkulu engqondweni. Ke ngoko, ukuthetha nomcebisi wezempilo yengqondo emva kokuxilongwa ngolu hlobo kuzisa isiqabu kubantu abaninzi.
Ndifanele ndimbone nini ugqirha?
Ukuba wena okanye umntu omaziyo ufumana olunye okanye ngaphezulu kwezi nguqu zilandelayo ngaxeshanye, bonana nogqirha ngokukhawuleza .
- Utshintsho olukhawulezileyo embonweni (amabala amnyama, ukuziva ngathi ugqunywe ngumkhusane).
- Ukulahlekelwa yindlebe ngequbuliso, isiyezi, okanye ukukhala ezindlebeni.
- Ubunzima bokucinga okanye ukukhumbula (utshintsho ekusebenzeni kwengqondo).
- Utshintsho olungachazwanga kwindlela yokuziphatha okanye ubuntu .
- Ukuba ezi mpawu ziphazamisana nobomi bakho bemihla ngemihla .
Ugqirha wakho unokubona unobangela ochanekileyo wezi mpawu aze akunike unyango olufunekayo, olunokukunceda ukuthintela iingxaki ezihlala ixesha elide.
Umyalezo Wokuya Ekhaya
- I-Susac Syndrome sisifo esingaqhelekanga apho amajoni ethu omzimba ahlasela imithambo yegazi emincinci engqondweni, emehlweni nasezindlebeni.
- Iimpawu eziphambili zesi sifo ziimpawu ezintathu: iingxaki zokusebenza kwengqondo (intloko ebuhlungu, ukudideka), iingxaki zokubona, kunye neengxaki zokuva (isiyezi, ukulahlekelwa kukuva).
- Esi asisosifo esizuzwa njengelifa, kwaye sixhaphake kakhulu kwabasetyhini.
- Ukubona ugqirha kwangoko xa iimpawu zibonakala kwaye ufumane uxilongo ngokukhawuleza kunokuthintela umonakalo ongunaphakade.
- Unyango luquka amayeza alawula inkqubo yomzimba yokuzikhusela (ii-immunosuppressants), kwaye kubaluleke kakhulu ukulandela imiyalelo kagqirha wakho.
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