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Masithethe ngeSifo sikaWilson, imeko apho ubhedu luqokelelana emzimbeni.

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📅 Updated: Jul 16, 2026 • ⏱ 5 min read • Umgaqo-nkqubo woHlelo
Masithethe ngeSifo sikaWilson, imeko apho ubhedu luqokelelana emzimbeni.
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I-Copper, i-mineral copper, ibalulekile ekusebenzeni kakuhle kwethu sonke ngamanani amancinci kakhulu. Kodwa khawucinge ukuba kwenzeka ntoni ukuba le copper ibalulekileyo iqokelelana emzimbeni ngaphezu komlinganiselo ofunekayo? Kulapho ke kuvela imeko engaqhelekanga kodwa enokuba yingozi ebizwa ngokuba yiWilson's Disease. Musa ukoyika ukuva oku. Kungalawulwa ngempumelelo ngokwaziswa ngokufanelekileyo ngayo nangokufuna unyango olufanelekileyo. Namhlanje, siza kuthetha ngale nto ngokulula, ngolwimi onokuluqonda.

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Yintoni kanye kanye isifo sikaWilson?

Ngamafutshane, isifo sikaWilson sisifo semfuza . Sidluliselwa kwizizukulwana ngezizukulwana. Isibindi sisitho esiphambili emzimbeni wethu esihluza ubhedu olungena emzimbeni wethu. Sifana nesihluzo samanzi. Kodwa kumntu onesifo sikaWilson, kukho isiphene kwijini (ijini ye-ATP7B) enxulumene nale nkqubo yokucoca ubhedu.

Oku kubangela ukuba isibindi singakwazi ukwenza umsebenzi waso ngokufanelekileyo. Ngenxa yoko, ithusi elongezelelweyo liqala ukuqokelelana kwizitho eziphambili ezifana nesibindi, ingqondo, kunye namehlo endaweni yokuba lisuswe emzimbeni. Ekuhambeni kwexesha, oku kuqokelelana kwethusi kungonakalisa la malungu kwaye kubangele iimpawu ezahlukeneyo.

Into ebalulekileyo kukuba ekubeni esi sisifo semfuza, ukuze esi sifo senzeke, umntwana kufuneka afumane esi sigulo semfuza esinesiphene kumama nakutata. Ukuba sifunyenwe kumzali omnye kuphela, iimpawu aziyi kubonakala, kodwa loo mntu usenokuba ngumthwali wesifo. Oku kuthetha ukuba banokudlulisela esi sigulo kubantwana babo.

Zithini iimpawu zesi sifo?

Iimpawu zesifo sikaWilson azibonakali kwangoko. Ekubeni i-copper ithatha ixesha ukuqokelelana emzimbeni, iimpawu ziqala ukubonakala emva kwexesha elithile. Kwakhona, iimpawu zinokwahluka ngokuxhomekeke kwisitho apho i-copper ibekwe khona kakhulu. Makhe sibone ukuba zeziphi ezi mpawu ziphambili.

Isitho/inkqubo echaphazelekayo Iimpawu ezibonakalayo
Iimpawu ezinxulumene nesibindi
Isibindi
  • Ukudinwa nobuthathaka obungachazekiyo
  • Ukulahlekelwa ngumdla wokutya kunye nokunciphisa umzimba
  • Isicaphucaphu nokuhlanza
  • Ulusu olurhawuzelelayo
  • Ukutyheli kolusu namehlo (i-Jaundice)
  • Intlungu yesisu kunye nokudumba
  • Ukuqaqamba kwemisipha
  • I-spider angiomas (imithambo yegazi ebomvu efana ne-spider webs eluswini)
Iimpawu ze-neurological ezinxulumene nengqondo kunye nenkqubo ye-nervous
Ingqondo
  • Ubunzima bokuthetha okanye ukuthintitha
  • Ubunzima bokuginya nokuvuza amathe
  • Ukungcangcazela okanye iintshukumo ezingalawulekiyo zamalungu
  • Utshintsho kwindlela yokuhamba (Ukuhamba ngendlela engafanelekanga)
  • Utshintsho kubuntu, ukucaphuka
  • Iingxaki zenkumbulo kunye nokubona
  • Uxinzelelo kunye nokuxhalaba
  • Ukungalali
Iimpawu zamehlo
Amehlo

Olu luphawu oluthile. Kuvela indandatho yegolide-mdaka ejikeleze iliso elimnyama. Oogqirha babiza le ndandatho ngokuthi yiKayser-Fleischer . Olu luphawu oluphambili lweentsalela zobhedu ngaphakathi kweliso. Abanye abantu banokuba ne-sunflower cataracts, ezibonakala njenge-sunflowers.

Ezinye iimpawu

Ukongeza kwiimpawu eziphambili ezikhankanyiweyo apha ngasentla, ezinye iingxaki ezininzi zinokwenzeka ngenxa yokwanda kobhedu emzimbeni.

  • Amatye ezintso
  • Imijikelo yokuya exesheni engaqhelekanga kubafazi
  • Ubunzima obuphantsi bamathambo kunye neemeko ze-arthritis
  • Ukutshintsha kombala weenzipho okwesibhakabhaka

Ngubani osengozini enkulu yokuhlaselwa sesi sifo?

Ekubeni esi sisifo esibangelwa lufuzo, eyona nto iphambili ebangela umngcipheko yimbali yosapho .

Ukuba kukho umntu kusapho lwakho, ingakumbi abazali bakho, umnakwenu, okanye udadewenu, onesifo sikaWilson, usengozini yokuba nesi sifo okanye ube ngunobangela waso.

Iimpawu zihlala ziqala ukubonakala phakathi kweminyaka emi-5 nengama-40 ubudala. Nangona kunjalo, kukho iingxelo zeempawu ezibonakala ebuntwaneni kakhulu, kuquka nosana oluneenyanga ezili-9 ubudala kunye nomntu omdala oneminyaka engama-70 ubudala.

Ukuba kukho umntu kusapho lwakho onesi sifo, eyona nto ingcono onokuyenza kukubona ugqirha wakho uze uthethe ngaso ngaphandle kokuthandabuza. Ukuba kuyimfuneko, uvavanyo lwemfuza lunokwenziwa ukuqinisekisa imeko.

Iphathwa njani?

Nangona ukuva ngesifo sikaWilson kunokuba yinto eyoyikisayo, iindaba ezimnandi zezokuba kukho unyango olusebenzayo lwaso . Unyango luneenjongo ezimbini eziphambili.

1. Ukususa ubhedu olugqithisileyo olusele luqokelelene emzimbeni:

Ngenxa yoku, oogqirha banika uhlobo oluthile lwamayeza. La mayeza abizwa ngokuba yi-'chelating agents'. La mayeza asebenza ngokuncamathisela kwiinxalenye zobhedu ezingaphezulu emzimbeni aze azisuse emzimbeni ngomchamo. Xa olu nyango luqhubeka, inqanaba lobhedu emzimbeni linokulawulwa. Nangona kunjalo, ngelixa usela la mayeza, ukuphiliswa kwamanxeba kunokulibaziseka. Ke ngoko, ukuba uza kwenziwa utyando, kufuneka uxelele ugqirha wakho ngalo nto kwangaphambili.

2. Ukuthintela ukufunxwa kobhedu ekutyeni emzimbeni:

Izithako zeZinc ziyamiselwa oku. IZinc inciphisa ukufunxwa kobhedu kwinkqubo yokugaya ukutya. Ngamanye amaxesha, oogqirha baqala olu nyango lweZinc nakubantu abafunyenwe benesifo kodwa bengekabi nazimpawu.

Kubaluleke kakhulu ukusela olu nyango ubomi bakho bonke , njengoko ugqirha wakho ecebisa, ngaphandle kokulahlekelwa lusuku olunye. Ugqirha wakho unokukucebisa ukuba unciphise ukutya okune-copper eninzi (umz. i-shellfish, isibindi, itshokolethi, amantongomane).

Umyalezo Wokuya Ekhaya

  • Isifo sikaWilson sisifo esingaqhelekanga esibangelwa kukuqokelelana kobhedu emzimbeni.
  • Oku kuchaphazela kakhulu isibindi, ingqondo kunye namehlo.
  • Iimpawu eziphambili zingabandakanya i-jaundice engachazwanga, utshintsho kubuntu, kunye nendandatho yegolide-mdaka ejikeleze iliso elimnyama (indandatho kaKayser-Fleischer).
  • Ukuba kukho umntu kusapho lwakho onesi sifo, bona ugqirha wakho ngoko nangoko ukuze akunike icebiso, nokuba akukho zimpawu.
  • Ukufunyanwa kwangoko kunye nonyango lobomi bonke kunokukunceda uphile ubomi obusempilweni nobuqhelekileyo. Ungaze uyeke unyango ngaphandle kwengcebiso kagqirha.
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